I fa te hmel pianzia hi i ngaihtuah em? Binder Syndrome chungchang hi han sawi ila!

I fa te a pian tirh khan an hmel pianziaah hian danglamna tlemte i hmu em? A châng chuan an hnar chu a hrual deuhin a lang thei a, a nih loh leh an hmui chunglam chu hmun dik takah a awm lo thei bawk. Nu emaw pa emaw hian hetiang thil an hmuh hian tlem a hlauhthawn hi thil pangngai tak a ni. Mahse, lungngai suh, vawiinah hian natna lan chhuah dan inang, mahse a tam vak lo, Binder Syndrome an tih chungchang kan sawi dawn a ni.

Binder Syndrome hi eng nge ni? A awlsam zawngin...

Binder syndrome hi a rare , congenital condition a ni a, pian tirh atanga lo awm thin a ni. Hmai lairil ruh, a bik takin hnar leh hmui chunglam ruhte a lo thang tha lo hle tih hriat a ni. In bang thenkhat siam that loh dan nen a inang hle. Hei hian naute hmel chu tlem a tidanglam thei a ni.

Ngaihtuah teh, kan hnar leh hmui chunglam hi a hnuaia ruh awm vangin a pianzia a ni. Chuvângin, chu ruhte chu a lo ṭhan tawh loh chuan an hmel chu a danglam ta a ni. Naupang thenkhat chuan he natna avang hian thawk harsatna an nei thei a, ei leh in lamah pawh harsatna an nei thei a, a bik takin nau hnute an pek hian . Mahse chanchin lawmawm tak chu, hei hi enkawl dan tur a awm a ni. A tlangpuiin naupang chu a upa deuh deuh a, chu chu tleirawl a nih hunah (a tlangpuiin kum 15-19 inkar) a ni a, heng ruhte hi a inrem leh thei a, hmai leh hmui surgery (`maxillofacial surgery`) hmangin a hmel lan dan chu a lo awm leh thei a ni.

Binder Syndrome tih hming dang a awm em?

Ni e, doctor-te chuan he natna hi hming dang an hmang fo thin. Hriat a tha a, a chhan chu heng hmingte hi i hre ve mai thei a ni:

• Binder phenotype - Hei hi Binder syndrome tih hming dang a ni.
• Binder chi hrang hrang nasomaxillary dysplasia a awm
• Maxillonasal dysplasia a awm thin
• Nasomaxillary hypoplasia a awm thin

Heng hmingte hi a buaithlak deuhin lang mahse, an awmzia a inang vek.

He natna hi Binder Syndrome an tih hi engtiang chiahin nge a awm?

Hei hi a takah chuan thil awm lo tak a ni . Report thenkhatah chuan he natna hi nau piang thar 10,000 zinga pakhat aia tlem loah a awm thin. Chuvangin hei hian hlauthawng suh. Mahse, a tlem hle nachungin, hriat chian a pawimawh hle.

Binder Syndrome natna lan chhuah dan chu engte nge ni?

Hetiang dinhmuna a lan dan ber chu hmai lai takah a lo thang lian lo a ni . Chumi avang chuan naupang hmelah hian a hnuaia inthlak danglamna te hi a lang thei a ni:

• Hnar chu a flat a, a hmui chunglam chu a flat . Hnar chhung lam hawia pil ang maiin a lang thei.
• A hnuai lam jaw chu hmalam hawiin a rawn chhuak a.Hetiang hian a lang. Hetianga lo lang hi a chhan chu a chunglam chu a chhungah a kal a, a hnuai lam chu hmalam a pan vang a ni.
• Ha chung leh hnuai lam chu a inmil tawk lo (`malocclusion`) . Hei hian ei leh in leh inbiaknaah harsatna a thlen thei a ni.
• Hnar kawngkhar te hian triangular emaw crescent emaw ang chi an nei a .

Hengte hi a lan chhuah dan tlangpui a ni. Mahse, chu bakah chuan a tlem berah chuan a hnuaia symptoms te hi i hmu thei bawk :

• Cleft palate a awm .
• Thinlung chhiatna pianpui .
• Hriatna lama harsatna nei .
• Thil hriatna lama harsatna nei .
• Spinal malformations a awm thin .
• Strabismus emaw mit crossed emaw .

Naupang zawng zawng hian heng symptoms zawng zawng hi an nei vek dawn lo. Naupang thenkhat chuan a natna lan chhuah dan bulpui chauh an nei thei.

Engvangin nge Binder Syndrome hi a lo awm? A chhante chu engte nge ni?

Dik tak chuan, mithiamte chuan hei hi eng thil nge a thlen tih chiang takin an la hre lo . A tam zawkah chuan naupangte hian chhan hriat lohvin he natna hi an nei thin.

Mahse, chhungkaw ṭhenkhata naupang engemaw zât chuan he natna hi an neih avângin, thlahtute aṭanga thil awm thei, chu chu thlahtute aṭanga nghawng a awm thei niin rinhlelh a ni . Mahse, hei hi chiang taka finfiah a la ni lo.

Chu bakah, zirchiangtute chuan boruak thil engemaw zat pawhin hmun a chang thei niin an ngai bawk. Chutiang thilte chu:

• Naupai laiin nuin zu a hman thin.
• Naupai laiin damdawi thenkhat ei thin. Entirnan, anti-epileptic phenytoin (Dilantin®, Phenytek®) leh thisen tithianghlimtu warfarin (Coumadin®, Jantoven®) te hi a ni. (Heng damdawi te hi a tul chuan damdawi lam enkawlna hnuaiah ei tur a ni a, mahse naupai lai hian fimkhur bik tur a ni.)
• Naupai laiin Vitamin K tlakchhamna.
• Nau neih laiin lu emaw hmai emaw a trauma.

Hengte hi tuna risk factors hmuhchhuah te chu an ni.

Doctor ten Binder Syndrome hi engtin nge an hriat theih?

Doctor-te chuan naute hmel lan dan enin he natna hi an ringhlel hmasa ber a ni . Tichuan, chu rinhlelhna chu nemnghet emaw, tihbo emaw nân, hmai ruh awm dân chiang taka hmuh theihna tûr test bîk an nei a ni . Chungte chu:

• CT scan hmanga tih a ni
• MRI Scan (`MRIs`) hmanga tih a ni.
• Ultrasound hmanga scan (`ultrasounds`) hmanga tih a ni.

Heng scan hmang hian hmai ruh chhunga hmasawnna lama harsatna awm apiang chu dik takin kan hmu thei a ni.

Binder Syndrome hi eng enkawlna nge ni?

Hei hi naupang hrang hrangah enkawl dan a inang lo va, a natna lan chhuah dan nasat danah pawh a innghat bawk.A inang lo. Enkawl dan tlangpui pahnih a awm a, chungte chu:

1. Ha siam that enkawlna:

• Hei hian ka chhungah wire (`braces`) dah a, chu chuan jaw leh ha te chu a inrem tha thei ang .
• A chang chuan a natna lan chhuah dan a na lutuk lo a nih chuan he ha enkawlna ringawt hi a tawk mai thei.
• Thil dang dangah chuan he enkawlna hi operation hma emaw, operation hnuah emaw tih a ngai thei bawk.

2. Surgery tih tur: 1.1.

• Hei hi enkawl dan ber a ni. Craniofacial surgeon (doctor, luruh leh hmai lama tui tak) chuan heng surgery te hi a ti thin.
• Chutah chuan, naupang taksa aṭanga lak chhuah ruh, ruhro, a nih loh leh thil siam chhuah hmangin hnar pianzia chu siam danglam a ni . Hei hi rhinoplasty an ti bawk .
• Tin, surgery chi khat Le Fort I emaw II osteotomy emaw tih chu upper jaw chu a awmna tur dik takah dah theih a ni bawk. Hengte hi surgery buaithlak deuh a ni a, mahse doctor tawnhriat ngah tak takte chuan hlawhtling takin an ti thei a ni.
• Doctor-te chuan he surgery hi an tih hma hian naupang hmai ruhte chu a lo thang tawh lo vek hma chu nghah an rawt tlangpui a, hei hi kum 15 leh 19 inkar vel a ni tlangpui a, hei hi a chhan chu chumi hmaa tih a nih chuan ruh a lo thang zel avangin harsatna a lo awm leh thei a ni.

Pawimawh: Naupang zawng zawng hian enkawlna pahnih hi an mamawh vek dawn lo. Naupang thenkhat chuan enkawlna pakhat chauh an mamawh mai thei. Hei hi medical team-in naupang an enfiah hnuah an rel ang.

He Binder Syndrome an tih hi ven theih a ni em?

Hei hi a chhan dik tak hriat a nih loh avangin, ven theih vek theih a ni tih hi sawi chian theih a ni lo .

Mahse, naupai i nih chuan a hmaa kan sawi tawh ang khan environment factor thenkhat i exposure tihtlem hian he natna hi i vei theihna tur chu eng emaw chen chu i tihtlem thei a ni. Hemi chungchangah hian i doctor nen in inbia thei ang:

• The safety of medications during pregnancy , a bik takin phenytoin leh warfarin (doctor-in a pek loh chuan damdawi engmah ei suh, a pek chuan i doctor nen sawiho rawh).
• Vitamin tlakchham chungchang, a bik takin vitamin K tlakchham chungchang . Naupai lai hian ei leh in tur dik tak kan neih a pawimawh hle.

Binder Syndrome vei naupang tan chuan eng nge a hmalam hun?

Hei hi chanchin tha ber a ni. Hetiang dinhmun hi a tlangpuiin thlirna tha tak a awm a ni .

Naupang tam zawk chuan rhinoplasty hnuah enkawlna dang an mamawh tawh lo. An thaw tha thei a, an ei dan pangngaiin an ei thei a, zai zawhah an hmel lan dan pawh a tha chho zel bawk .A theih a ni. Chuvangin ngaihtuahawm tur a awm lo, a pawimawh ber chu a rang thei ang bera damdawi lam thurawn lak hi a ni.

Doctor hnenah eng zawhna nge ka zawh ang?

Nangmah emaw, i fa emaw hian Binder Syndrome i nei tih i hriat chuan hetiang zawhna hi i doctor hnenah i zawt thei ang. Chûngte chuan dinhmun hriatthiamna a pe ang che:

• "Doctor, ka naute dinhmun chhan ber chu eng nge ni thei ang? "
• " He Binder Syndrome natna hi dik taka hriat theih nan eng test nge tih thin? "
• " Hemi atan hian eng enkawl dan nge awm? Ka naute tan eng nge tha ber?"
• " Nakin lawkah enkawl ngai leh theihna chance engzat nge awm? "
• " Naupang dang ka neih chuan ani pawhin he natna hi a neih theihna chance engzat nge awm? "

Heng zawhnate bakah hian i rilru a i neih apiang i doctor hnenah zawt la.

Eng dinhmun dang nge Binder Syndrome nen hian symptom inang nei?

Hmai ruh thanna tichhe thei leh Binder syndrome ang deuha lang thei natna dang engemaw zat a awm bawk. Doctor-te pawhin hengte hi an ngaihtuah hle. Entirna thenkhat chu:

• Acrodysostosis natna (acrodysostosis) a awm
• Apert natna a ni
• Chondrodysplasia punctata, rhizomelic chi hrang hrang (CDPR) a awm a ni.
• Fetal warfarin syndrome (naupai laiin warfarin ei avanga natna lo awm) .
• Keutel natna a ni
• Stickler natna a ni

Heng hmingte hi hre reng ang che. Doctor-te chuan i fain eng dinhmun nge a neih tih chiang takin an rel ang.

A tawp berah chuan thil hriat reng tur (Take-Home Message) .

Okay, chuvangin kan sawi tawh kha han khaikhawm ila:

• Binder Syndrome hi a awm lo hle a, pianpui atanga lo chhuak a ni .
• Hei hian hmai lai takah ruh a ti tlahniam a, a bik takin hnar leh hmui chunglam a ti tlahniam a ni . Hei hian hnar flat leh protruding lower jaw ang chi features a siam a ni.
• Hei hi a chhan dik tak hriat a ni lo , mahse genetic leh environmental factors hian hmun a chang thei.
• He natna hi orthodontic treatment leh/ emaw surgery hmangin hlawhtling takin enkawl theih a ni .
• Naupang tam tak chuan enkawl hnuah result tha tak tak an nei a , nun pangngai an hmang thei bawk.

I fate hmel lan dan chungchangah ngaihtuahna leh ngaihtuahna i neih chuan a rang thei ang bera doctor thiam tak pan rawh . A pawimawh ber chu hlauthawng ni lovin, thu leh hla dik leh kaihhruaina dik tak hmuh hi a ni. Doctor te tanpui turin an awm reng a ni.

He thu hi i tan a tangkai ngei ka beisei. Nang leh i chhungte hriselna tha ka duhsakna ka hlan e!

` Binder Syndrome, Binder Syndrome, hmai piansual, pianpui natna, naupang hriselna, maxillofacial surgery, craniofacial surgery