Miiri k’a filɛ, mɔgɔ dɔ tɛ kɛnɛya kosɛbɛ kabini tile damadɔ, a hakili bɛ to ka wuli dɔɔni, a kolotugudaw bɛ dimi tuma dɔw la, wa a fari bɛ daminɛ ka nɛ. O la, n’i taara dɔgɔtɔrɔso la nin ɲɔgɔnna fɛn dɔ kama, n’u ye sɛgɛsɛgɛli suguya caman kɛ, u b’a ye ko nin bɛɛ ju ye kansɛri ye min dogolen don farikolo kɔnɔ. Yala o tɛ kabako ye wa? Kansɛri bɛ yɔrɔ kelen na, nka a nɔfɛkow kosɔn, taamasiɲɛ minnu bɛ i n’a fɔ u ni ɲɔgɔn cɛ pewu, olu bɛ bɔ farikolo yɔrɔw la minnu tɛ kelen ye pewu. An bɛ o de wele ko Paraneoplastique Syndrome furakɛli la.
N’an y’a fɔ cogo nɔgɔman na, Paranéoplastique Syndrome ye mun ye?
A bɛ se ka kɛ ko nin faamuyali ka gɛlɛn dɔɔnin, nka an k’a nɔgɔya. Ni kuru jugu dɔ bɔra aw fari la, a nɔ tilennen bɛ o la. Misali la, ni fogonfogon kansɛri bɛ aw la, sɔgɔsɔgɔ bɛ se ka kɛ aw la. Ni kɔnɔbara kansɛri bɛ aw la, joli bɛ se ka don aw ka banakɔtaa la. Olu ye kansɛri taamasiɲɛ tilennenw ye.
Nka Paranéoplastique Syndrome ye fɛn wɛrɛ ye min tɛ kelen ye. Min bɛ kɛ yan, o ye ko i farikolo bɛ taamasiɲɛ wɛrɛw dalajɛlen bɔ kansɛri jaabi la. O kɔrɔ ye ko a tɛ fɛn ye kansɛri bɛ min kɛ k’a ɲɛsin a ma, nka ikomi kansɛri bɛ farikolo la, farikolo kɔnɔ sigida wɛrɛw bɛ taa binkɛnɛ na i n’a fɔ ‘jaabi’ a ma.
O bɛ se ka kɛ cogoba fila de la:
1. Banakisɛfagalanw ka jaabi: Aw ye miiri an farikolo farikolo tangacogo la i n’a fɔ kɛlɛbolo min bɛ jamana dɔ lafasa. Kansɛribanakisɛw ye jugu ye min donna jamana kɔnɔ. O la an ka kɛlɛbolo (immune system) bɛ kɛlɛ daminɛ ni nin jugu in ye (kansɛri). O kama, u bɛ marifa kɛrɛnkɛrɛnnenw dilan, o kɔrɔ ye ko farikolo tangalanw . Nka tuma dɔw la, nin kɛlɛ in senfɛ, an ka kɛlɛbolo bɛ fili. U tɛ daminɛ ka bin juguw ka selilɛriw dɔrɔn kan, nka u bɛ binkanni daminɛ fana an yɛrɛ farikolo kɔnɔ selilɛri ɲumanw kan, k’a miiri k’u ye juguw ye. Misali la, u bɛ se ka bin farikolokisɛw kan, farikolokisɛw walima kolotugudaw la. O waati de la taamasiɲɛ minnu bɛ tali kɛ o farikolo yɔrɔw la, olu bɛ bɔ kɛnɛ kan.
2. Ɔrimɔni sɔrɔli kansɛribanakisɛw fɛ: Kansɛri suguya dɔw bɛ se ka fɛn caman bɔ, i n’a fɔ ɔrimɔni, an farikolo tɛ minnu dilan cogoya la, walima a tɛ fɛn caman bɔ. O ɔrimɔni minnu tɛ deli ka kɛ, olu bɛ ɲɔgɔn lajɛ joli la ka taa farikolo fan bɛɛ la, ka farikolo yɔrɔ suguya caman baara tiɲɛ. Misali la, o ɔrimɔni ninnu bɛ se ka kɛ sababu ye ka tansiyɔn wuli kojugu, walima ka kalisiyɔmu hakɛ wuli joli la.
Min nafa ka bon, o ye ko tuma dɔw la, hali sani kansɛri ka sɔrɔ, taamasiɲɛ minnu bɛ tali kɛ nin Paraneoplastique Syndrome in na, olu bɛ bɔ fɔlɔ. O la, a nafa ka bon kosɛbɛ ka aw janto nin taamasiɲɛ ninnu na.
Nin bana in bɛ farikolo yɔrɔ jumɛnw de minɛ?
Paranéoplastique syndromes bɛ se ka farikolo yɔrɔ bɛɛ lajɛlen minɛ. Nka, u bɛ Ye kosɛbɛ o sigida ninnu na. An k’a lajɛ u ye fɛn minnu ye ani cogoya minnu bɛ se ka kɛ u ni ɲɔgɔn cɛ.
| Farikolo sigicogo min bɛ nɔ bila | Furakɛcogo minnu bɛ se ka kɛ (misaliw) . |
|---|---|
| Farikoloɲɛnajɛ (sugunɛ, kɔkolo, nɛrɛmuguma) . | Bana minnu bɛ i n’a fɔ Kunsɛmɛnasumaya, Kunsɛmɛnasumaya, Lambert-Eaton myasthenic syndrome, Myasthenia gravis, Periférique neuropathie, Stiff person syndrome. |
| Endocrine system (ɔrimɔni) . | Bana minnu bɛ sɔrɔ i n’a fɔ Cushing ka bana, Hypercalcémie (kalisiyɔmu caya joli la), ani Carcinoïde syndrome. |
| Jɛɲɔgɔnya yɔrɔw (kolo, kolotugudaw, farikolo yɔrɔw) . | Farikolodimi, Jolilabanaw (jolilabanaw), kolotugudaw ka banakisɛfagalanw (hypertrophique osteoarthropathie). |
| Joli | Bana basigilen jolidɛsɛ, Erithrocytose paranéoplastique, Trombocytose paranéoplastique. |
| Golo | Acanthosis nigricans (fari ka bonya ani ka a bonya yɔrɔw la i n’a fɔ kɔkiliw ni kɔkili), Farikolodɛsɛ, Dumuni duman, Pemphigus paraneoplastic. |
A taamasiɲɛ minnu bɛ sɔrɔ tuma caman na ani minnu bɛ kɛ kɛrɛnkɛrɛnnenya la, olu ye jumɛnw ye?
Taamaʃyɛn caman bɛ yen minnu ka teli ka ye, olu bɛ ye fɔlɔ paraneoplastique syndrome (banakisɛfagalan) la. Ninnu fana bɛ se ka ye bana wɛrɛw la, o la a man ɲi ka siran ni ninnu ye dɔrɔn.
Taamasiɲɛ minnu ka teli ka ye:
- Sumaya sababu tɛ
- Dumuninege
- Sumaya kojugu su fɛ
- Kisɛya dɔgɔyali min tɛ deli ka kɛ ni cɛsiri tɛ
Ka fara nin taamasiɲɛw kan minnu bɛ sɔrɔ tuma caman na, i n’a fɔ an y’a ɲɛfɔ cogo min na ka tɛmɛ, taamasiɲɛ kɛrɛnkɛrɛnnenw bɛ sɔrɔ ka kɛɲɛ ni farikolo yɔrɔ ye min banana.
| Sistɛmu min bɛ nɔ bila a la | Taamasiɲɛ kɛrɛnkɛrɛnnen minnu bɛ se ka ye |
|---|---|
| Nɛrɛmuguma | Taama gɛlɛya, balansi bɔnɛ, ɲɛnamini, yeli fila, hakilijagabɔ, hakiliɲagami, farikolo fanga dɔgɔyali, kuma gɛlɛya. |
| Endocrine (banakisɛfagalanw) ka sigida | Tansiyɔn jiginni, girinya jiginni min tɛ ɲɛfɔli kɛ, sukaro hakɛ cayalenba, sɛgɛnba. |
| Jɛɲɔgɔnya yɔrɔ | Joli dimi, kolotugudaw fununi, farikolodimi ani barikantanya. |
| Joli | Joli kuru suguya dɔ dɔgɔyali walima a caya cogo la min tɛ bɛn (misali la jolidɛsɛ, walima joli kuruli teli ka caya). |
| Golo | Kurukuru minnu tɛ kansɛri ye fari la, fari bilenni, nɛ kojugu, ani fari kulɛri caman cili. |
Jɔn de farati ka bon ka nin bana in sɔrɔ?
Paraneoplastique syndromes (banakisɛfagalanw) bɛ se ka kɛ mɔgɔ o mɔgɔ fɛ kansɛri bɛ mɔgɔ min na, o bɛ se ka kɛ teori la. Nka, u ka teli ka sɔrɔ kansɛri suguya dɔw la. Jateminɛw y’a jira ko kansɛribanatɔ 100 o 100, 8 ɲɔgɔn (8%) bɛ nin bana in sɔrɔ.
Kansɛri suguya minnu ka teli ka sɔrɔ nin bana in na, olu ye:
- Fogonfogon kansɛri (a ka teli ka ye ni nin suguya in ye) .
- Sinna kansɛri
- Kansɛri minnu bɛ sɔrɔ joli la (i n’a fɔ sɔgɔsɔgɔninjɛ, jolidɛsɛ) .
- Ovarie kansɛri
Dɔgɔtɔrɔ bɛ o sɔrɔ cogo di?
Ni aw taara dɔgɔtɔrɔso la ni nin taamasiɲɛ ninnu ye, a bɛna min kɛ fɔlɔ, o ye ka tariku sɛbɛn ka ɲɛ ani ka farikolo sɛgɛsɛgɛli kɛ. O kɔ, u bɛna yamaruya di sɛgɛsɛgɛli caman kɛli ma walasa k’a dɔn ni kansɛri walima furakɛli bana wɛrɛ de y’a taamasiɲɛw sɔrɔ.
- Joli sɛgɛsɛgɛliw : Joli sɛgɛsɛgɛli kɛcogo kɔrɔlenw bɛ se ka aw ka bana taamasiɲɛw sababu wɛrɛw lajɛ (misali la, banakisɛw, ɔrimɔni balanbaliya). Ani fana, joli sɛgɛsɛgɛli kɛrɛnkɛrɛnnen dɔw bɛ se ka farikolo tangalanw walima kuru taamasiɲɛw ɲini minnu bɛ tali kɛ paranéoplastique syndrome la.
- Ja lajɛ: Sɛgɛsɛgɛliw i n’a fɔ CT scan , MRI scan , walima ultrasound bɛ kɛ walasa ka a dɔn ni kansɛri kuru dɔ bɛ farikolo kɔnɔ.
- Farikoloɲɛnajɛ sɛgɛsɛgɛli : Ni siga bɛ a la ko aw ka bana taamasiɲɛw bɛ tali kɛ farikoloɲɛnajɛ la, aw ka dɔgɔtɔrɔ bɛna baara suguya caman kɛ walasa ka aw fanga, aw hakili to a la, aw ka balansi ani aw ka baara kɛcogo sɛgɛsɛgɛ.
- Kɔkolo tap/Lumbar Puncture: O ye ka kunsɛmɛji dɔɔni ta, o ye ji ye min bɛ aw kɔkolo lamini, ka a sɛgɛsɛgɛ walasa ka a dɔn ni farikolojidɛsɛbanakisɛ dɔw bɛ o ji la minnu bɛ bin farikolokisɛ kɛnɛmanw kan.
A bɛ furakɛ cogo di?
Fɛn min nafa ka bon kosɛbɛ ani min nafa ka bon kosɛbɛ paraneoplastique syndrome furakɛli la, o ye ka kansɛri furakɛ min ye a bɛɛ lase mɔgɔ ma. Ni kansɛri kunbɛnna walima ni a kɛnɛyara, taamasiɲɛ minnu bɛ sɔrɔ paraneoplastique syndrome la, olu ka teli ka nɔgɔya u yɛrɛ ma.
O waati kelen na, kansɛri furakɛli waati, furakɛli dɔw fana bɛ kɛ walasa ka bana taamasiɲɛ minnu bɔra kɛnɛ kan, olu kunbɛn. Nin furakɛli ninnu kunba ye ka farikolo tangalanw hakili sigi, o min bɛ fili ka bin farikolokisɛ kɛnɛmanw kan.
- Kɔritikositɛriw : Fura minnu bɛ i n’a fɔ Prednisolone. Olu bɛ baara kɛ ni funu ni funu dɔgɔyali ye farikolo la.
- Banakisɛfagalanw:Nin fura ninnu bɛ dɔ bɔ farikolo tangalanw ka baara la ani k’a bali ka bin farikolokisɛ kɛnɛmanw kan.
- Immunoglobuline intraveineuse (IVIG): O ye ka fɛn dɔ di min kɔnɔ, farikolo tangalanw bɛ sɔrɔ mɔgɔ kɛnɛmanw na, jolisira fɛ. Nin banakisɛfagalanw bɛ dɛmɛ ka farikolo tangalan juguw tiɲɛ minnu bɛ farikolo tiɲɛ.
- Plasmapheresis : Nin ye wale ye min ni joli saniyacogo bɛ tali kɛ ɲɔgɔn na. Aw bɛ aw joli ta, ka jilama yɔrɔ (plasma) faranfasi, farikolo tangalan jugumanw bɛ sama ka bɔ, ka joli saniyalen don kokura aw fari la.
- Farikolo, baara ani kuma furakɛli : Ni farikolo yɔrɔ dɔw tiɲɛna ani ni taama, kuma walima don o don baara kɛli gɛlɛyara, o furakɛli ninnu bɛ se ka dɛmɛ don ka o sekow jɔ kokura.
Aw ka kan ka taa dɔgɔtɔrɔso la tuma jumɛn?
Ni taamasiɲɛ dɔw bɛ aw la minnu tɛ deli ka kɛ i n’a fɔ a fɔra nin barokun in na, kɛrɛnkɛrɛnnenya la ni u ka jugu walima ni u bɛ tɛmɛ dɔgɔkun fila kan, aw ka kan ka taa dɔgɔtɔrɔso la sisan.
Aw ye aw hakili to a la ko nin taamasiɲɛ ninnu bɛ mɔgɔ o mɔgɔ la, kansɛri tɛ olu bɛɛ la. Nin taamasiɲɛ caman bɛ se ka sɔrɔ fana bana wɛrɛw fɛ minnu man jugu i n’a fɔ kansɛri. O la sa, kana a miiri ko a ka jugu kosɛbɛ ani ka siran. Nka, a nafa ka bon ka a dɔn tigitigi min bɛ a sababu ye. O la sa, aw ye aw jija ka dɔgɔtɔrɔ dɔ ka laadilikan ɲini.
Ni aw ye kansɛri furakɛ ka tɛmɛ, a fɔ san duuru tɛmɛnenw kɔnɔ, ni aw bɛ nin taamasiɲɛ suguw sɔrɔ sisan, a nafa ka bon kosɛbɛ ka segin ka sɛgɛsɛgɛli kɛ. O bɛ se ka dɛmɛ don ka a dɔn ni kansɛri seginna.
Ni kansɛri bɛ aw la, a ka ca a la, aw bɛ degun ni nin taamasiɲɛ ninnu faralen don ɲɔgɔn kan. Nka a nafa ka bon ka a faamu ko nin paraneoplastique syndrome furakɛcogo ɲuman ni kansɛri furakɛli ye kelen ye. Ni aw ye aw ka kansɛri furakɛli bolodacogo labato kosɛbɛ, o bɛna aw dɛmɛ ka nin taamasiɲɛ ninnu kunbɛn. Furakɛli caman bɛ yen minnu bɛ se ka lafiya di aw ma. Aw bɛ kuma aw ka dɔgɔtɔrɔ fɛ u ko la k’a jɛya.
Take-Home cikan
- Paraneoplastique syndrome tɛ kansɛri nɔ tilennen ye , nka a bɛ kɛ nɔ tilennen ye min bɛ sɔrɔ farikolo farikolo tangacogo walima ɔrimɔni fɛ kansɛri jaabi la.
- Tuma dɔw la, taamasiɲɛ minnu bɛ tali kɛ nin bana in na , olu bɛ bɔ fɔlɔ , hali sani kansɛri ka sɔrɔ.
- Nin bana in furakɛcogo kunba ye kansɛri basigilen furakɛli ye.
- Ni taamasiɲɛw bɛ aw la minnu tɛ deli ka kɛ (misali la, farikolo girinya dɔgɔyali, farikolo fanga dɔgɔyali, fari caman cili) minnu bɛ ye kun tɛ, ka tɛmɛ dɔgɔkun fila kan, aw bɛ taa dɔgɔtɔrɔso la ka sɔrɔ aw ma mɛn.
- Ikomi nin taamasiɲɛ ninnu bɛ se ka sɔrɔ furakɛli cogoya caman wɛrɛw fɛ, a nafa ka bon kosɛbɛ aw kana siran ani ka dɔgɔtɔrɔso sɛgɛsɛgɛli ɲuman ɲini .











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