Ðe nèse le ɖokuiwò me kpɔ abe ɖe nèle nu yibɔ suesuesuewo kpɔm wole tsia dzi le wò ŋkumea? Alo ɖewohĩ wò nukpɔkpɔ me mekɔ o viea? Esiawo ate ŋu asɔ, gake ɣeaɖewoɣi la, woate ŋu anye kuxi aɖe si le wò ŋku me ƒe dzesi. Egbea míele nu ƒom tso ŋkudɔ mawo dometɔ ɖeka si mebɔ o si dzi woate ŋu aɖu ne wodae nyuie ŋu.
Nukae nye esia (Birdshot Chorioretinopathy)?
Kpuie ko la, Birdshot Chorioretinopathy, alo BSCR kpuie, nye dɔdzẽ ƒe dɔléle si mebɔ o si dzɔna le ŋkua me. Menye dɔléle si nɔa anyi didie wònye o, si fia be mehayana le ɣeyiɣi kpui aɖe me o, ke boŋ enye nɔnɔme si nɔa anyi ɖaa. Ne womewɔ atike na ame nyuie o la, ate ŋu ana ame ƒe ŋkuwo natrɔ tegbee alo ame ƒe ŋkuwo nabu keŋkeŋ gɔ̃ hã .
(BSCR) nye nɔnɔme sesẽ aɖe si le dɔlélewo ƒe ƒuƒoƒo aɖe si woyɔna be ``Uveitis'' me, si gblẽa nu le lãkusi siwo le ŋkua me ŋu. Eƒe akpa vevitɔe nye be:
- Retina : Esiae nye lãkusi si sea kekeli gɔme le míaƒe ŋku ƒe megbe. Ele abe sinima si le fotoɖemɔ̃ me ene. Wolé nɔnɔmetata siwo míekpɔna la ɖe afisia.
- Choroid : Esia le ŋku ƒe ŋkume ƒe akpa si le ŋkume. Esiae nye lãkusi si doa ka kple ŋkua ƒe akpa si le ɣie, eye wònaa ʋu ŋkua ƒe ŋkume, si fia be enaa nunyiame.
Nusi ɖe dzesi wu le dɔléle sia ŋue nye teƒe suesuesue siwo le abe krem ene ƒe dzedzeme le ŋkume ƒe akpa si goglo kple ŋkume ƒe akpa si le etame. Zi geɖe la, dzesi gbãtɔwo dometɔ aɖewoe nye nu yibɔ siwo le tsia dzi le ŋkuwo ŋgɔ (floaters) , nukpɔkpɔ si me mekɔ o , alo evea siaa. Zi geɖe la , nɔnɔme sia gblẽa nu le ŋku eveawo siaa ŋu .
Le ɣeyiɣi aɖe megbe la, nugbegblẽ sia ate ŋu ahe nɔnɔmewo abe cystoid macular edema alo glaucoma ene vɛ. Togbɔ be atike aɖeke meli o hã la, Birdshot Chorioretinopathy nye dɔléle si woate ŋu ada . Ele vevie be woade dzesii kaba hafi woate ŋu ada dɔa dzidzedzetɔe.
Amekae xɔa Birdshot Chorioretinopathy?
Le nyateƒe me la, dɔléle sia ate ŋu adze ame sia ame dzi. Gake ebɔ wu le ƒe titina, yevu tsitsi siwo xɔ tso ƒe 40 va ɖo ƒe 60. Ƒã ŋutɔ be ɖeviwo naxɔ dɔléle sia.
Ðe dɔléle bubu aɖewo li siwo ɖi esia (Birdshot Chorioretinopathy)?
Ẽ, dɔléle bubu geɖe, siwo dome dɔléle bubu siwo le Uveitis ƒe ƒuƒoƒoa me hã le, ate ŋu akpɔ dzesi siwo sɔ kple Birdshot Chorioretinopathy tɔ. Eyata ele vevie ŋutɔ be nàkpɔ dɔlélea nyuie ale be nàte ŋu axɔ atike si sɔ. Dɔléle siwo ate ŋu asɔ kple BSCR dometɔ aɖewoe nye:
- Lymphoma (kansa ƒomevi aɖe) .
- Sarcoidosis (dɔléle si nana ame ƒe ŋutilã ƒe akpa vovovowo vuvu suesuesue) .
- `(Sympathetic ophthalmia)` (Uveitis ƒomevi aɖe si mebɔ o si tso ŋku ƒe abixɔxɔ gbɔ)
- Syphilis (dɔléle si woxɔna to gbɔdɔdɔ me) .
- `(Presumed ocular histoplasmosis syndrome (POHS))` (Nɔnɔme si gblẽa nu le ŋkuwo ŋu si fungi dɔlékui aɖe hena vɛ)
- `(Yɔmekpe)` (Yɔmekpe) .
- `(Vogt-Koyanagi-Harada syndrome)` (dɔléle si gblẽa nu le lãmekawo ŋu, si gblẽa nu le nukpɔkpɔ kple nusese ŋu)
Dɔléle siwo gblẽa nu le ame ŋu ƒe ƒuƒoƒo aɖe hã li si woyɔna be ``White dot syndromes'', si hã ateŋu aɖe BSCR ƒe dzesiwo afia. Esiawo hea ``abi'' vɛ na ŋku ƒe ŋkume kple ŋkume ƒe lãkusi. Kpɔɖeŋu aɖewoe nye:
- `(Acute megbe multifocal placoid amadede ƒe lãkusi ƒe dɔléle (APMPPE))`
- `(Aɖuɖɔtoedɔléle si le teƒe geɖe kple panuveitis (MCP))`
- `(Multiple evanescent white dot ƒe dɔléle (MEWDS))`
- `(Punctate ememe ʋumenugbagbeviɣidɔ (PIC))`
Nukatae woyɔa esia be (Birdshot Chorioretinopathy)?
Le nyateƒe me la, esia nye dɔléle yeye aɖe ŋutɔ, si ŋu woƒo nu tsoe zi gbãtɔ le ƒe 1949. Ƒe 1980 me hafi ŋkudɔdala eve tsɔ ŋkɔ nɛ be "(Birdshot Chorioretinopathy)". Nusitae nye be krem kple aŋutiɖiɖi ƒe teƒe siwo le abe oval ene kaka ɖe ŋku ƒe ŋkume katã. Ŋkɔa tso nyateƒe si wònye be teƒe siawo ƒe nɔnɔme ɖi tu suewo (xewo ƒe tu) siwo wozãna tsɔ daa xeviwo ƒe nɔnɔme. Bu eŋu kpɔ, teƒe aɖewo le ŋkua me, abe tu siwo kaka ne woda tu ene.
Ðe ŋkɔ bubuwo li na esia?
Ẽ, ŋkɔ bubu geɖewo li siwo wozãna na dɔlélea (Birdshot Chorioretinopathy):
- `(Xeviwo ƒe ʋuʋudedi ƒe chorioretinitis)`
- `(Xeviwo ƒe ŋkume ƒe dɔléle)`
- `(Xeviwo ƒe ŋkume ƒe dɔléle)`
- `(Xeviwo ƒe uveitis)`
- `(BSCR)` (ŋkɔ kpui) .
- `(Posterior uveitis)` (uveitis si dzɔna le ŋku megbe) .
- `(Vitiliginous choroiditis)`
Aleke gbegbee Birdshot Chorioretinopathy bɔe?
Esia nye dɔléle si mebɔ kura o . Numekulawo xɔe se be edzea ame siwo mede ɖeka le akpe alafa ɖeka me o. Esia fia be le Sri Lanka gɔ̃ hã la, ame siwo ŋu dɔléle sia le ate ŋu anɔ anyi, gake xexlẽmea le sue ŋutɔ.
Nukae hea Birdshot Chorioretinopathy vɛ?
Numekulawo menya nusi tututu gbɔ dɔlélea tso haɖe o , gake wosusui be dɔléle si dɔlélenutsiŋutete ŋutɔ hena vɛ . Kpuie ko la, míaƒe ŋutilã ŋutɔ ƒe ametakpɔnu, si nye dɔlélenutsiŋutete, dzea mía ŋutɔwo ƒe lãmeka siwo le lãmesẽ me dzi vodadatɔe.
Ame siwo wu 90% siwo wokpɔ be (BSCR) le dɔlékuiwutikewo ƒe domenyiŋusẽfianu (molekyul si doa ŋusẽ dɔlélenutsiŋutete) si woyɔna be `(HLA-A29)` le woƒe ŋutilã me. Esia nye nusi ƒe dome wonyi tso dzilawo gbɔ. Ke hã, `(HLA-A29)` mehiã be wòaxɔ (Birdshot Chorioretinopathy). Azɔ hã, anya wɔ be dɔlékuiwutike ƒe domenyiŋusẽfianu sia nanɔ ame si gake dɔlélea madze ame dzi o.
Nukae nye Birdshot Chorioretinopathy ƒe dzesiwo?
Dɔléle sia ƒe dzesiwo ate ŋu ato vovo tso ame ɖeka gbɔ yi bubu gbɔ. Nu siaDɔléle si nu sẽna ɖe edzi nye dɔléle si nu sẽna ɖe edzi vivivi le ɣleti aɖewo va ɖo ƒe geɖe me.
Zi geɖe la, Birdshot Chorioretinopathy ƒe dzesi gbãtɔwoe nye:
- Nu yibɔ siwo le tsia dzi le ŋkume kpɔkpɔ (floaters) .
- Nukpɔkpɔ si me mekɔ o
Zi geɖe la , nɔnɔme sia menaa ŋku vea ame alo biãna o . Ke hã, àte ŋu ato nu siwo gbɔna la me:
- Nukpɔkpɔ trɔna alo nukpɔkpɔ dzi ɖena kpɔtɔna.
- Nukpɔkpɔ le gota gome dzi ɖe kpɔtɔ alo didiƒe ʋĩ ƒe ʋɔnudɔdrɔ̃ sesẽ.
- Nyaƒoɖeamenu sesẽ le ŋku me (ŋku me ʋusɔgbɔdɔ).
- Zã me ŋkumaʋumaʋu (nyctalopia) (nukpɔkpɔ nyuie le zã me).
- Amadedewo ƒe nukpɔkpɔ ƒe kuxiwo (`(amadede ƒe ŋkumaʋumaʋu)`), amadede aɖewo ƒe vovototodedeameme sesẽ (`(dyschromatopsia)`.
- Kekeli si klẽna alo keklẽ si klẽna ƒe seselelãme (fotovɔvɔ̃).
Ame aɖewo ate ŋu akpɔ tɔtrɔ siwo mebɔ o alo susu ƒe kuxiwo. Le kpɔɖeŋu me:
- Ceiling fan effect : Ne èmiã ŋku la, edzena abe ceiling fan alo yaƒoƒomɔ̃ aɖe le tsatsam ene.
- Kekeli alo keklẽ ƒe keklẽ (photopsia) alo nɔnɔme siwo tro kpɔkpɔ (metamorphopsia) .
- Nukpɔkpɔ si me kɔ o, si le keklẽm, abe ɖe wòle tsi alo ahuhɔ̃e ƒoɖi me kpɔm ene .
Le nɔnɔme sesẽwo me la, nɔnɔmewo abe ŋkudɔ alo ŋkudɔ ene ate ŋu ado mo ɖa. Esiawo ate ŋu ana ame ƒe ŋku nabu vevie le abi la dada vɔ megbe gɔ̃ hã. Birdshot Chorioretinopathy ate ŋu ahe kuxiwo hã vɛ le ŋkua ƒe titina, abe cystoid macular edema kple epiretinal membranes ene.
Aleke wokpɔa Birdshot Chorioretinopathy ƒe dɔlélea?
Dɔléle sia didi ate ŋu asesẽ vie ɣeaɖewoɣi elabena enye dɔléle si mebɔ o eye teƒe siwo ɖe dzesi le eŋu la mate ŋu adze le dɔlélea ƒe gɔmedzedze o.
Zi geɖe la, ŋkudɔdalawo toa ŋkudɔdada dzi dea dzesi BSCR. Wowɔa ʋudodokpɔ hã be woakpɔe ɖa be HLA-A29 dɔlékuiwutike le ŋuwò hã.
Ðɔktawo ate ŋu azã dodokpɔ vovovowo atsɔ alé ŋku ɖe ŋuwò le ɣeyiɣi aɖe megbe. Ele vevie be nànɔ kadodo me kple wò ɖɔkta be nàkpɔ beléle si nèhiã.
Ðe atike blibo aɖe li na Birdshot Chorioretinopathya?
Nublanuitɔe la, womekpɔ atike blibo aɖeke na dɔléle sia o. Gake ne wokpɔ dɔlélea dze sii hedae kaba , woate ŋu aɖe dzesiawo dzi akpɔtɔ eye woate ŋu axe mɔ na dɔlélea be wòagagblẽ ɖe edzi o.
Ðo ŋku edzi be: nu vevitɔe nye be nànya dɔlélea kaba eye nàdze edada gɔme!
Amekawoe ate ŋu anɔ nye atikewɔwɔ ƒe ƒuƒoƒoa me?
Wò dɔnɔdzikpɔlawo aɖo aɖaŋu na wò, alé ŋku ɖe ŋuwò, eye woatrɔ asi le wò atikewo ŋu le wò nɔnɔmea kple eƒe nugbegblẽ le ame ŋu nu. Wò ƒuƒoƒoa ate ŋu anye:
- Ŋkudɔdala : Ðɔkta vevitɔ si kpɔa ŋkuwo gbɔ.
- Nephrologist : Elabena atikewɔwɔ aɖewo gblẽa nu le ayiku ŋu.
- Ŋku ƒe dɔlélenutsiŋutete ŋuti nunyala: Ðɔkta si xɔ hehe tɔxɛ le ŋku ƒe dɔlélenutsiŋutete ƒe kuxiwo ŋu.
- Lãmetsiŋutinunyala: Ðɔkta si bi ɖe dɔléle siwo do ƒome kple dɔdzẽ le ŋutilã me me, elabena esia hã nye dɔdzẽ ƒe dɔléle.
- Ƒumeŋutinunyala : Elabena atikewɔwɔ aɖewo gblẽa nu le ƒuwo ŋu.
Aleke wodaa Birdshot Chorioretinopathy ƒe dɔléleae?
Dɔléle sia dada nɔ te ɖe alesi wò nɔnɔmea nu sẽe kple alesi wòtrɔna le ɣeyiɣi aɖe megbe dzi. Taɖodzinu vevitɔ si le atikewɔwɔ ŋue nye be wòaɖe wò ŋkuwo ƒe vuvu dzi akpɔtɔ eye wòaxe mɔ ɖe nukpɔkpɔ si bu la dometɔ aɖewo nu alo agbugbɔe aɖo eteƒe .
Zi geɖe la, ɖɔktawo ŋlɔa corticosteroid (si nye steroid-tike ƒomevi aɖe) ƒe agbɔsɔsɔ gbogbo aɖe gbã be woatsɔ aɖu ŋku ƒe vuvu dzi. Emegbe, woɖea agbɔsɔsɔme si wozãna dzi kpɔtɔna vivivi be woaɖe afɔku si le eƒe nugbegblẽ le ame ŋu me dzi akpɔtɔ. Àte ŋu axɔ steroid-tikewo le mɔ siwo gbɔna nu:
- Ŋku ƒe ʋuʋudedi
- Atike siwo woano
- Mɔ̃ sue aɖe si wotsɔa amekoko dea ŋkua me (intravitreal implant) .
- Atike si wodona ɖe lãme na ame
- Wotsɔe de ʋuka me (IV - to ʋuka me) .
Ele be ame geɖe hã nano dɔlélenutsiŋutete ƒe atikewo ɣeyiɣi didi . Atike siawo xea mɔ na wò dɔlélenutsiŋutete be wòagadze wò ŋkuwo dzi o. Woate ŋu azã nusiwo gbɔna dometɔ ɖeka alo esi wu nenema:
- `(Alkylating nusiwo wotsɔna wɔa dɔe)`
- `(Atike siwo tsia lãmenugbagbeviwo ƒe dɔwɔwɔ nu)`
- `(Nu gbagbewo ƒe atikewo)` (nu gbagbewo ƒe atikewo) .
- `(T-lãmenugbagbeviwo ƒe tɔtrɔ/calcineurin mɔxenuwo)`
Ðe Birdshot Chorioretinopathy (Birdshot Chorioretinopathy) ƒe atikewɔwɔwo ate ŋu ahe kuxiwo vɛa?
Ẽ, steroid kple dɔlélenutsiŋutete zazã ɣeyiɣi didi ate ŋu ahe kuxi sesẽwo vɛ . Le kpɔɖeŋu me, dɔgbo ƒe kuxiwo (abi, abi) alo ƒu ƒe kuxiwo (ƒumeŋuɖui) ate ŋu ado mo ɖa. Atike siawo ate ŋu ana ŋkudɔ alo ŋkudɔ ƒe afɔku hã nadzi ɖe edzi.
Wò ɖɔkta alé ŋku ɖe wò nugbegblẽ le ame ŋu hã ŋu eye wòaŋlɔ atike bubuwo na wò ne ehiã. Ne èle steroid siwo woano zãm la, wò ɖɔkta alé ŋku ɖe ŋuwò be ƒu ƒe gbagbã (ƒu ƒe gbagbã) kple afɔku si le eme be ƒu gbagbã hã.
Wò ɖɔktaWoate ŋu akafui hã be woawɔ ƒu ƒe kpekpeme ŋuti numekuku. Woate ŋu aŋlɔ atikewo (bisphosphonates) hã na amewo be woatsɔ axe mɔ ɖe ƒu ƒe ŋeŋe nu.
Ɣeyiɣi didi ƒe ŋkuléleɖenuŋu ka ƒomevie mehiã na (BSCR)?
Nya tɔtrɔ alo kuxi ɖesiaɖe si ado mo ɖa le wò nɔnɔmea me. Wò ɖɔkta awɔ ʋu kple aɖuɖɔ dodokpɔ atsɔ akpɔ alesi wò ayiku, aklã, kple ƒumeŋuɖui le dɔ wɔm nyuie hã. Anɔ eme be ahiã hã be woado ŋku kpɔ edziedzi, woado ŋku ƒe dɔwɔwɔ kpɔ, eye woawɔ optical coherence tomography (OCT) scan.
Ðe mate ŋu aɖe afɔku si le Birdshot Chorioretinopathy xɔxɔ me dzi akpɔtɔa?
Fifia la, womenya mɔ aɖeke si dzi woato axe mɔ ɖe dɔléle sia nu o. Zi geɖe la, woxɔe se be dɔlékuiwutikewo ƒe domenyiŋusẽfianu (antigen) aɖe koŋ si ƒe dome wonyi tso ƒomea me tɔwo gbɔ gbɔe wòtso.
Ŋkudodokpɔ edziedzi ate ŋu akpe ɖe ŋuwò nàde dzesi dɔléle ƒe dzesiwo kaba, eyata àte ŋu akpɔ atike na wò ɖe game dzi ne ehiã. Gblɔe na wò ɖɔkta ne ŋkudɔ le ame aɖe ŋu le wò ƒomea me.
Nukae nye Birdshot Chorioretinopathy ƒe mɔkpɔkpɔ?
Dɔléle sia ƒe mɔkpɔkpɔ to vovo tso ame ɖeka gbɔ yi bubu gbɔ . Enɔ te ɖe alesi dɔlélea nu sẽe kple alesi atikewɔwɔa kpɔ dzidzedzee dzi. Le nɔnɔme siwo mesẽ o me la, atikewɔwɔ ate ŋu akpe ɖe ame ŋu wòalé ŋku ɖe nu ŋu alo ana wòanyo ɖe edzi gɔ̃ hã.
Ɣekaɣie wòle be madi atikewɔlawo ƒe aɖaŋuɖoɖo na (Birdshot Chorioretinopathy)?
Ele vevie be woadi ŋkudɔdala ƒe dɔléle si nye Birdshot Chorioretinopathy ƒe dɔlélea didi kaba ahadae . Ne edze abe wò nukpɔkpɔ le nyuie ene hã la, ŋkudodokpɔ ate ŋu ade dzesi abi si mebɔ o.
Gblɔ nu tso wò atikeawo ƒe nugbegblẽ le ame ŋu, dzesiwo ƒe tɔtrɔ, alo nukpɔkpɔ ɖesiaɖe ŋu na wò ɖɔkta. Woate ŋu ana atike bubu wò ne ehiã. Wò ɖɔkta aƒo nu tso tiatia siwo nyo na wò ŋu na wò.
Gbedasi Mamlɛtɔ si Wotsɔ Yi Aƒeme
(Birdshot Chorioretinopathy) nye dɔléle si mebɔ o gake woate ŋu adae . Eyata mègatsi dzodzodzoe o. Nu vevitɔe nye be nàdo wò ŋkuwo kpɔ edziedzi eye nàwɔ ɖe wò ɖɔkta ƒe aɖaŋuɖoɖowo dzi . Le ɣeyiɣi aɖe megbe la, wò ɖɔkta agblɔ alesi nàkpɔ wò ŋkumekpɔkpɔ ta ahaxe mɔ ɖe kuxiwo nu na wò. Ekema àte ŋu akpɔ xexeame nyuie hena ɣeyiɣi didi aɖe. Lé be na wò ŋkuwo, elabena woxɔ asi ŋutɔ!
` Birdshot Chorioretinopathy, Ŋkudɔlélewo, Nukpɔkpɔ ƒe Dɔmawɔmawɔ nyuie, Uveitis, Retina, Autoimmune Dɔlélewo, Ŋkudɔdada











💬 Comments (0)
Womeɖo nya aɖeke ɖe amewo haɖe o. Tsɔ wò nyaŋuɖoɖo kpe ɖe afisia zi gbãtɔ.
Tsɔ wò nyaŋuɖoɖo kpee