He puʻupuʻu i ʻike ʻole ʻia ma kou kino? Hiki paha i kēia ke Angiomatoid Fibrous Histiocytoma? E kamaʻilio kākou e pili ana!

Ua ʻike anei ʻoe i kahi mea e like me ka puʻupuʻu liʻiliʻi ma kou kino, a i ʻole ma kāu keiki? He mea maʻamau ka makaʻu iki ke ʻike ʻoe i kahi mea e like me ia, ʻeā? "He aha kēia? No ke aha e hana nei kēia?" Manaʻo ʻoe i kekahi mea ma hope o kekahi. ʻO ka hapa nui o ka manawa, hiki i kēia mau mea ke lilo i mau mea liʻiliʻi wale nō. Eia naʻe, i kekahi manawa pono mākou e hopohopo iki a nānā i nā kūlana e pono ai ke noiʻi ʻia. I kēia lā, e kamaʻilio mākou e pili ana i kahi puʻupuʻu i kakaʻikahi iki, ʻo ia hoʻi, ʻaʻole i loaʻa i nā kānaka a pau, akā he mea pono ke ʻike. Ua kapa ʻia kēia ʻo Angiomatoid Fibrous Histiocytoma , a i ʻole AFH no ka pōkole. ʻOiai he lōʻihi iki ka inoa, e hoʻomaopopo maʻalahi kākou.

He aha maoli ka Angiomatoid Fibrous Histiocytoma?

I ka ʻōlelo maʻalahi, he puʻupuʻu laha ʻole kēia e hana ʻia ana i loko o nā ʻiʻo palupalu o kou kino, e like me ka ʻili a me nā ʻiʻo. Hoʻomohala pinepine kēia mau mea ma kou mau lima, nā wāwae, a i kekahi manawa kou mau poho lima a me nā kapuwaʻi.

I kēia manawa, e wehewehe iki kākou i ke ʻano o kēia inoa lōʻihi. A laila e ʻoi aku ka maopopo.

He aha ke ʻano o kēia mau huaʻōlelo?

• Histiocytoma: He puʻupuʻu kēia e hana ʻia i ka wā e hui pū ai nā histiocytes, kahi ʻano o nā cell pale maʻamau i loko o kou kino. Loaʻa kēia mau cell ma nā ʻāpana like ʻole o ko mākou kino a kōkua i ka pale ʻana iā mākou mai nā maʻi.
• Angiomatoid: Pili kēia huaʻōlelo i ke ʻano o ka puʻupuʻu. ʻO ia hoʻi, ke nānā ʻoe i kēia puʻupuʻu, ua like ia me nā kīʻaha koko liʻiliʻi. Ua like ia me ka nui o nā kīʻaha koko i hui pū ʻia.
• ʻOiʻoi: Pili kēia i ke ʻano o ke knot. ʻO ia hoʻi, hiki iā ia ke loaʻa kahi ʻano fibrous iki, kaulaʻi, a me ke ʻano uaua.

No laila, ke hoʻohui ʻoe i kēia mau huaʻōlelo ʻekolu, ʻo Angiomatoid Fibrous Histiocytoma ke ʻano he puʻu o nā pūnaewele i kapa ʻia ʻo histiocytes nona ke ʻano fibrous a like me nā kīʻaha koko. Maopopo iā ʻoe?

ʻO wai ka mea i hoʻopilikia nui ʻia e kēia maʻi? Ma hea ia e hana ʻia ai?

ʻO kēia ʻano maʻi, i kapa ʻia ʻo AFH, ka mea maʻamau i nā keiki, nā ʻōpio, a me nā mākua ʻōpio . ʻO ka ʻoiaʻiʻo, 88% o ka poʻe i ʻike ʻia me ka maʻi aia ma lalo o 30 mau makahiki. ʻO ka awelika o ka makahiki o ka ʻike ʻia ʻana ma kahi o 14 mau makahiki.

ʻO ka hapa nui, ulu pinepine kēia mau nodules i loko o ka ʻili (dermis ), ka papa ma lalo o ka ʻili, ma kou mau lima a me kou mau wāwae. Eia nō naʻe, he mea kākaʻikahi loa, i nā hihia kākaʻikahi loa, hiki i kēia mau nodules AFH ke ulu pū i loko o nā ʻiʻo palupalu i loko o kou kino (nā ʻiʻo palupalu somatic). No ka laʻana, hiki iā lākou ke ulu i loko o ka lolo, nā māmā, ka ʻāpana ma waenakonu o kou umauma kahi o kou puʻuwai (mediastinum) , a i ʻole ka ʻiʻo e hoʻopili ai i kou ʻōpū i ke koena o kou mau ʻōpū ʻōpū (omentum) . Eia naʻe, he mea kākaʻikahi loa kēia.

He maʻi ʻaʻai anei kēia? Pono anei au e hopohopo?

ʻO kēia ka pilikia nui loa no nā kānaka he nui. Hoʻomaopopo pinepine ʻia nā nodules Angiomatoid Fibrous Histiocytoma he mau nodules palupalu maikaʻi . ʻO ke ʻano kēia, ʻaʻole lākou e hōʻeha nui a ʻaʻole e laha ma ke kino holoʻokoʻa.

Eia nō naʻe, i kekahi mau hihia, hiki i kēia mau mea ke lilo i mea ʻino . I kēlā hihia, ua kapa ʻia lākou he sarcoma ʻiʻo palupalu .

Akā, eia kahi mea nui. ʻOiai he maʻi kanesa ka AFH, ua manaʻo pinepine ʻia he puʻupuʻu ʻino haʻahaʻa . ʻO ia hoʻi, he haʻahaʻa loa ka hiki ke laha i nā ʻāpana ʻē aʻe o ke kino. No laila, ʻaʻohe mea e hopohopo ai ke lohe ʻoe i ka inoa.

Pehea ka maʻamau o kēia kūlana?

He maʻi laha ʻole ka AFH. ʻO nā puʻupuʻu palupalu a pau, he hapa liʻiliʻi loa ka AFH, ma kahi o 0.3%. ʻO ia hoʻi, pili ia i ʻekolu o kēlā me kēia tausani kānaka. No laila, ʻaʻole paha i lohe nā kānaka a pau i ia mea.

He aha nā hōʻailona o kēia? Loaʻa anei ia i nā kānaka a pau?

ʻO ka mea maikaʻi loa, ʻo ka hapa nui o ka poʻe me AFH ʻaʻole hōʻike i kekahi mau hōʻailona a ʻaʻole paha lākou e ʻike he puʻupuʻu ko lākou.

Eia nō naʻe, hiki i kekahi poʻe ke loaʻa nā hōʻailona. Inā loaʻa, hiki iā lākou ke komo pū me:

• kuni
• ʻO Anemia, ʻo ia hoʻi ka nele o ke koko
• Ka emi ʻana o ke kaumaha

ʻO kēia nā hōʻailona i ʻike pinepine ʻia. He mea kākaʻikahi loa ka ʻeha a me ke palupalu . He kakaikahi wale nō ka poʻe me kēia maʻi e hana ʻia ai kēia.

No ke aha e hana ʻia ai kēia ʻano puʻupuʻu? He aha ke kumu?

Hoʻomaka ka Histiocytoma i ka wā e ulu wikiwiki ai nā pūnaewele pale i ʻōlelo ʻia ma mua i kapa ʻia ʻo histiocytes a hana i nā pūnaewele histiocyte hou aʻe. ʻO ke ʻano kēia, ua māhele nui iki nā pūnaewele.

ʻAʻole maopopo ke kumu kikoʻī o ka AFH . Eia nō naʻe, ua hōʻike kekahi mau noiʻi e pili ana paha ia i nā mea e like me ka genetics , nā kūlana hoʻoilina , a me ka ʻike ʻia ʻana i ka lāʻau radiation . Eia nō naʻe, he mau mea kēia e pono e noiʻi hou ʻia.

Hiki i kēia puʻupuʻu ke laha i nā ʻāpana ʻē aʻe o ke kino?

He mea kēia e makaʻu ai ka poʻe he nui. Hiki i kahi puʻupuʻu AFH ke pālahalaha (metastasize) i nā ʻāpana ʻē aʻe o ke kino, akā he mea kākaʻikahi loa ia. Hana ʻia kēia ma lalo o 1% o nā hihia. ʻO ia hoʻi, ʻaʻole i hoʻokahi i loko o hoʻokahi haneli poʻe e laha. No laila, ʻaʻohe pono e hopohopo nui e pili ana i ia mea.

Pehea e ʻike ai nā kauka i kēia? (Diagnosis)

Ma muli o ke ʻano o nā nodules AFH, hiki ke huikau ʻia i kekahi manawa me nā kūlana ʻē aʻe. No ka laʻana, he hematoma, ʻo ia hoʻi kahi hōʻiliʻili o ke koko ma waho o kahi kīʻaha koko.Hiki ke huikau ʻia me ka hemangioma, kahi hōʻailona hānau ʻulaʻula i loaʻa i ka wā hānau.

No laila, inā kānalua kāu kauka i ka AFH, e wehe paha ʻo ia i kahi hapa a i ʻole ka puʻupuʻu āpau a nānā iā ia ma lalo o kahi microscope. Ua kapa ʻia kēia he biopsy .

Ke nānā nei kēia biopsy i kekahi mau ʻano kikoʻī i ka AFH, me:

• Nā pūnana paʻa o nā pūnaewele histiocyte-like
• Nā hakahaka e like me ka cyst i piha i ka wai
• ʻO ka hōʻiliʻili ʻana o nā pūnaewele mumū mau loa

Inā loaʻa kēia mau ʻano i loko o ka hāpana, e hōʻoia nā kauka i ke kūlana he AFH.

He aha nā lāʻau lapaʻau?

ʻO ke ʻano lapaʻau nui no ka AFH, ʻo ia ka wehe ʻana i ka puʻupuʻu ma ke ʻoki kino . ʻAʻole wale ka puʻupuʻu e wehe ai kāu kauka ʻoki, akā, ʻo kekahi o nā ʻiʻo olakino a puni. Hiki i kēia ke hōʻemi i ka pilikia o ka hoʻi hou ʻana mai o ka puʻupuʻu ma kahi hoʻokahi (recurrence).

ʻoki kino

ʻO kēia ʻoki kino ka lāʻau lapaʻau nui. He holomua kēia ʻano hana, ʻoiai inā ʻaʻole i pālahalaha ka puʻupuʻu.

ʻO ka Chemotherapy a me ka Radiation Therapy

Eia nō naʻe, i kekahi manawa hiki ke paʻakikī ke ʻoki ʻana ma muli o ka wahi o ka puʻupuʻu. No ka laʻana, inā aia ia ma kahi paʻakikī e like me ke poʻo a i ʻole ka ʻāʻī. A i ʻole, kākaʻikahi, inā ua pālahalaha ka puʻupuʻu i nā ʻāpana mamao o ke kino, hiki ke ʻōlelo ʻia ka chemotherapy a i ʻole ka radiation therapy .

• ʻO ka Chemotherapy kahi lāʻau lapaʻau e hoʻopau ai i nā hunaola kanesa.
• ʻO ka radiation therapy kahi ʻano hana e luku ai i nā hunaola kanesa me ka hoʻohana ʻana i nā kukuna ikehu kiʻekiʻe.

Hana ʻia kēia mau lāʻau ʻelua ma lalo o ka nānā ʻana a nā kauka loea.

He aha nā pilikia e hiki ke kū mai i ka wā o ka mālama ʻana?

E like me nā hana ʻoki kino a pau, aia kekahi mau hopena ʻaoʻao e hiki ke kū mai i ka wā o kēia kaʻina hana, e like me:

• Aia kahi pilikia o ka maʻi .
• I kekahi manawa hiki ke hōʻeha ʻia nā aʻalolo .
• Hiki ke loaʻa ka ʻeha .
• Aia paha ke kahe ʻana o ke koko .

ʻO kēia nā mea i hiki ke hoʻomalu ʻia.

Hiki i nā poʻe e hana ana i ka chemotherapy a i ʻole ka radiation therapy ke loaʻa i nā hopena ʻaoʻao like ʻole. ʻO kekahi o kēia mau mea:

• ʻO ke anemia ke ʻano o ka helu koko haʻahaʻa.
• Ka hāʻule ʻana o ka lauoho .
• Luhi .
• Ka luaʻi a me ka luaʻi.

E wehewehe pono ana kāu kauka iā ʻoe i ke ʻano o ka lāʻau e hāʻawi ʻia iā ʻoe a me nā mea āu e manaʻo ai mai ia mea.

Aia kekahi ala e pale aku ai i kēia mai ka hana ʻana?

ʻO ka ʻoiaʻiʻo, ʻaʻohe ala i ʻike ʻia i kēia manawa e pale aku ai i ka ulu ʻana o ka Angiomatoid Fibrous Histiocytoma . No ka mea, ʻaʻole ʻike ʻia ke kumu pololei, he paʻakikī ke ʻōlelo pehea e pale aku ai.

He aha kaʻu e hana ai inā loaʻa iaʻu a i ʻole kaʻu keiki kēia maʻi? He aha kaʻu e manaʻo ai?

Inā ʻike kāu kauka he AFH kou a i ʻole kāu keiki, e kūkākūkā kikoʻī ʻo ia i kāu mau koho.

• Inā ʻaʻole i pālahalaha ka puʻupuʻu i nā wahi ʻē aʻe, ʻoi aku ka maikaʻi o ke ʻoki ʻana e wehe iā ia . I ka hapanui o nā hihia, ʻaʻole e hoʻi hou ka puʻupuʻu ma hope o ke ʻoki ʻana.
• Eia nō naʻe, inā ua pālahalaha ka puʻupuʻu i nā ʻāpana mamao o ke kino mai kahi i ʻike mua ʻia ai, a laila hiki ke ʻōlelo ʻia ka chemotherapy a i ʻole ka radiation therapy . I kēlā mau hihia, pono ʻoe e hoʻomau i ka ʻike ʻana i kāu kauka no nā hahai ʻana a me nā hoʻokolohua e nānā i kou olakino.

Hiki ke ho'ōla loa ʻia kēia?

I ka hapanui o nā hihia, ʻae! Hiki ke ho'ōla loa ʻia ka AFH me ke ʻoki kino.

Eia nō naʻe, e like me ka mea i ʻōlelo ʻia ma mua, i nā hihia kakaikahi loa, hiki i kēia maʻi ke laha i nā ʻāpana ʻē aʻe o ke kino. Inā hana ʻia kēlā, hiki ke lilo i mea koʻikoʻi loa, a hiki ke hoʻoweliweli i ke ola. Akā e hoʻomanaʻo, he mea kakaikahi loa kēia.

I ka manawa hea e pono ai iaʻu ke ʻike i ke kauka?

Inā ʻike ʻoe i kahi loli koke i ke ʻano o kou ʻili, e like me kahi puʻupuʻu hou a i ʻole kahi kiko, mai hoʻowahāwahā iā ia a e ʻike koke i ke kauka . A laila hiki i ke kauka ke nānā iā ia a hana i nā hoʻokolohua hou aʻe inā pono. ʻO ka wikiwiki o ka ʻike ʻia ʻana, ʻo ka maʻalahi ka mālama ʻana.

He aha nā nīnau koʻikoʻi e nīnau aku ai i ke kauka?

Ke ʻike ʻoe ua loaʻa iā ʻoe kēia maʻi, he mea nui e aʻo i ka nui o ka hiki e pili ana i ia mea. E kōkua kēia iā ʻoe e hoʻoholo i nā hoʻoholo naʻauao e pili ana i kou olakino. Eia kekahi mau nīnau hiki iā ʻoe ke nīnau i kāu kauka:

• ʻAuhea kuʻu puʻupuʻu?
• He aha ka nui o kaʻu puʻupuʻu?
• He ʻano maikaʻi ʻole a he ʻano ʻino paha koʻu puʻupuʻu?
• Ua pālahalaha koʻu puʻupuʻu i nā wahi ʻē aʻe?
• He aha nā koho lapaʻau e loaʻa iaʻu?
• He aha nā kūlana o ka holomua ʻana o ke ʻoki kino?
• Pono anei iaʻu e noʻonoʻo i ka chemotherapy a i ʻole ka radiation therapy?
• Ma hea e hiki ai iaʻu ke aʻo hou aʻe e pili ana i kēia hōʻailona? (e.g. nā puke, nā pūnaewele)

Mai makaʻu e nīnau i kēia mau nīnau. He mea nui e hoʻomaopopo i nā kānalua āu e loaʻa nei.

ʻO ka mea hope loa, leka lawe i ka home

ʻAe, no laila, mai nā mea a mākou i kamaʻilio ai, eia nā mea nui loa e pono ai ʻoe e hoʻomanaʻo:

ʻO ka angiomatoid fibrous histiocytoma kahi ʻōpū palupalu laha ʻole.

ʻO ka hapa nui o ka manawa, ʻaʻole kēia he maʻi kanesa a hiki ke ho'ōla ʻia me ke ʻoki ʻana .

ʻO kēia ka mea maʻamau i waena o nā keiki a me nā ʻōpio .

ʻAʻole hōʻike ka nui o ka poʻe i nā hōʻailona.

I kekahi manawa, hiki i kēia ke lilo i maʻi kanesa a laha i nā wahi ʻē aʻe. Inā hana ʻia kēia , pono paha ka chemotherapy a i ʻole ka radiation therapy .

Inā ʻike ʻoe i kahi puʻupuʻu hou ma kou kino, e ʻike koke i ke kauka .

Manaʻolana wau he kōkua kēia ʻike iā ʻoe. E hoʻomanaʻo, inā he kānalua a nīnau paha kāu, mai kānalua e kamaʻilio me kāu kauka. ʻO ia ke kanaka maikaʻi loa e aʻo iā ʻoe.

ʻO ka histiocytoma fibrous angiomatoid, AFH, maʻi ʻaʻai palupalu, nā nodules ʻili, pediatrics, mālama ʻana i ka maʻi ʻaʻai, ʻoki kino