Ke pilikia nei kāu keiki liʻiliʻi i ka hanu ʻana e like me kēia? E kamaʻilio kākou e pili ana i ka "Double Aortic Arch"!

Ke manaʻo nei kāu keiki liʻiliʻi i kekahi manawa e like me ka pilikia o ka hanu ʻana? Ke ʻū nei ʻo ia i ka wā e hānai ana a hānai waiū paha? A i ʻole ke hana nei ʻo ia i nā leo ʻē i ka wā e hanu ana? ʻOiai he mau maʻi maʻamau kēia i nā kamaliʻi, aia paha kekahi maʻi koʻikoʻi, akā hiki ke mālama ʻia, ma hope o kēia. ʻO kekahi maʻi kakaikahi akā koʻikoʻi e makaʻala ai ʻo ia ka mea i kapa ʻia ʻo "Double Aortic Arch." E kamaʻilio kākou e pili ana i kēia lā.

I ka ʻōlelo maʻalahi, ʻo ke kīʻaha koko nui e lawe ana i ke koko mai ka puʻuwai o kāu pēpē a i ke koena o kona kino ʻo ia ka aorta . He kīʻaha koko hoʻokahi ia, nui. ʻO ka ʻāpana piʻo o kēia kīʻaha koko ma luna o ka puʻuwai ua kapa ʻia ʻo ke aortic arch .

Eia nō naʻe, i loko o kahi pēpē me ka "Double Aortic Arch", ua hana ʻia kēia "aortic arch" i ʻelua. ʻO ia hoʻi, ua hoʻopili ʻia kekahi kīʻaha koko hou i kēia "aortic arch" nui, e hana ana i kahi lua. Ua hui pū kēia mau ʻāpana ʻelua, e hana ana i kahi apo a puni ka ʻōpū hanu o ka pēpē (trachea) a me ka paipu meaʻai (esophagus) . E noʻonoʻo, he aha ka mea e hana ai inā paʻa kēia apo? ʻO ia ka manawa e hoʻomaka ai ka pēpē e loaʻa nā hōʻailona koʻikoʻi e like me ka paʻakikī o ka hanu ʻana, ka hana ʻana i nā walaʻau i ka wā e hanu ana, a me ka paʻakikī o ka moni ʻana i ka meaʻai.

Hoʻokumu ʻia kēia "aortic arch" i nā wā mua loa o ka hāpai ʻana, ma waena o ʻelua a me ʻehiku pule. I loko o kēia wā, ulu ka puʻuwai a me nā kīʻaha koko ma ke ʻano paʻakikī loa. Hoʻokumu ʻia kekahi mau ʻāpana, a ma hope o kekahi manawa ʻaʻole pono hou lākou a nalowale. Hoʻokumu ʻia ka "double aortic arch" ma muli o kekahi mea e like me kēia. Ma kahi o ka pule ʻelima o ka hāpai ʻana, ʻaʻole nalowale kahi kīʻaha koko i pono e nalowale, no kekahi kumu i ʻike ʻole ʻia, a hoʻokumu ʻia kēia "double aortic arch". He kīnā puʻuwai hānau kēia, ʻo ia hoʻi, ua hānau ʻia ke pēpē me ia.

ʻO kēia kūlana, i kapa ʻia ʻo "double aortic arch," no kahi hui o nā kīnā puʻuwai hānau i kapa ʻia ʻo "vascular rings." ʻO kēia ke kumu e ʻomi ai ka ʻōpū o ka pēpē a me ka esophagus.

He aha kēia mau "apo vascular"?

ʻAe, ʻo "Vascular Rings", e like me kaʻu i ʻōlelo ai ma mua, nā kūlana kahi e ulu ai ke "aortic arch" i kahi ʻano ʻē, hiki ke hoʻopili ʻia ka windpipe (trachea), ka paipu meaʻai (esophagus), a i ʻole nā ​​mea ʻelua. He mau kīnā puʻuwai hānau kakaʻikahi loa kēia. E noʻonoʻo e pili ana i ia mea, ma kahi o hoʻokahi i loko o 100 mau pēpē i hānau ʻia me kekahi ʻano kīnā puʻuwai hānau. Akā, ʻo ka "vascular ring" e pili wale ana i hoʻokahi i loko o 10,000 mau pēpē. He mea kakaʻikahi ia.

He aha nā ʻano nui o nā "Apo Vascular"?

Aia kekahi mau ʻano nui o kēia mau "apo vascular". E nānā kākou i ke ʻano o lākou:

• ʻO ke apo aortic pālua: Ma kēia, ʻelua "apo aortic" (hema a me ka ʻākau) e hoʻopuni ana i ka trachea a me ka esophagus. ʻO kēia ke kumuhana nui a mākou e kamaʻilio nei.
• ʻO ke apo aortic ʻākau me ke aʻa subclavian hema aberrant a me ka ligamentum hema: Aia kekahi apo aortic ma ʻaneʻi, akā aia ma ka ʻaoʻao ʻākau o ka trachea (maʻamau ma ka hema). I kēia hihia, hoʻomaka ka aʻa subclavian hema, ka mea e hoʻolako i ke koko i nā lima o ka pēpē, ma ka aorta a hala ma hope o ka trachea a me ka esophagus. Hoʻopau ʻia kēia apo vascular ma ka hui ʻana me ka ligamentum arteriosus hema, kahi koena o kahi kīʻaha koko i loaʻa i ka wā o ke ola fetal a laila nalowale.
• ʻO ke kikoo aortic hema me ke aʻa subclavian ʻākau aberrant: Maanei, hele ke aʻa subclavian ʻākau ma hope o ka trachea a me ka esophagus, e ʻomi ana iā lākou.
• Ke kaomi ʻana o ke aʻa innominate: ʻO ke aʻa innominate (brachiocephalic) he lālā ia o ka aorta. I kēia hihia, hoʻomaka ia ma ka ʻaoʻao hema o ka trachea, a laila hele i mua o ka trachea ma ka ʻākau. Hoʻokomo kēia i ke kaomi ma luna o ka trachea.
• ʻO ke kaula pulmonary: Hoʻomaka ke aʻa pulmonary hema mai ke aʻa pulmonary ʻākau a hele ma waena o ka trachea a me ka esophagus.

ʻO ka mea e hana ʻia ana ma kēia mau mea a pau, ʻo ia ka hoʻopilikia ʻia ʻana o ke ala ea a i ʻole ka esophagus ma kekahi ʻano.

Aia kekahi mau ʻano o "Double Aortic Arch"?

ʻAe, aia ʻekolu mau ʻano nui o ka "double aortic arch." Hoʻokaʻawale ʻia kēia mau mea e ke ʻano o ke ʻano i ʻoi aku ka nui, a inā paha aia kēlā ʻano nui ma ka ʻaoʻao ʻākau a hema paha o ka trachea.

• ʻO ke kīʻaha ʻākau nui me kahi kīʻaha hema liʻiliʻi: ʻO kēia ke ʻano maʻamau, e kū ana ma kahi o 80 pakeneka o nā hihia.
• ʻO ke apo hema hema me kahi apo ʻākau liʻiliʻi: ʻIke ʻia kēia ma kahi o 10 pakeneka o nā hihia.
• Nā ʻanuʻu kaulike: ʻIke ʻia kēia ma kahi o 10 pakeneka o nā hihia.

He aha ke ʻano o ke "apo vascular" i ʻike pinepine ʻia?

Ua manaʻo nā kauka i ka wā ma mua ʻo ke "double aortic arch" ka ʻano maʻamau o ke "vascular ring." Akā ua ʻike ʻia e kahi noiʻi hou ua ʻoi aku ka maʻamau o ka "right aortic arch" .

Akā aia kekahi mea ʻē aʻe. ʻOi aku ka nui o ka loaʻa ʻana o nā kīnā puʻuwai hānau ʻē aʻe i nā pēpē me ka "double aortic arch." Eia nō naʻe, ʻaʻole hiki ke ʻike ʻia lākou i ka wā hānau. ʻO kēia no ka mea ʻaʻole paha e hōʻike ka "right aortic arch" i nā hōʻailona i nā pae mua. No laila, pono paha ke ʻoki ʻana no kēia pilikia ma waena o 6 a me 18 mau mahina o ka makahiki.

ʻO ke ʻano i kapa ʻia ʻo "Double Aortic Arch" ke ʻano maʻamau o ke apo vascular. No laila, hiki i ke kauka o kāu pēpē ke ʻike mua i ka pilikia. Ke hoʻohālikelike ʻia me nā pēpē me nā ʻano apo vascular ʻē aʻe, pono paha nā pēpē me "Double Aortic Arch" i ke ʻoki kino ma hope koke iho o ka hānau ʻana.

He aha nā hōʻailona o ka "Double Aortic Arch"?

ʻIke pinepine ʻia nā hōʻailona o ka "double aortic arch" ke kaomi ʻia ka windpipe o ka pēpē, ka esophagus, a i ʻole nā ​​mea ʻelua. Hiki i kēia kaomi ke hoʻopilikia i ka hanu ʻana o ka pēpē, ka hānai ʻana, a i ʻole ka hana a ka puʻuwai.

ʻO ka hapa pinepine, ʻike ʻia kēia mau hōʻailona i ka wā kamaliʻi (ʻoi aku hoʻi inā koʻikoʻi ke ʻano), akā i kekahi manawa hiki ke ʻike ʻia i ka wā ʻekolu makahiki, a i ʻole i ka wā ʻōpio.

Hiki ke kuhi hewa ʻia kekahi mau keiki he hānō no ka mea ua like nā hōʻailona. Hoʻomaopopo wale ʻia ke ʻano ke hāʻule ka mālama ʻana i ka hānō a hana ʻia nā hoʻāʻo hou aʻe.

Nā hōʻailona hanu

Ma kahi o 91 pakeneka o nā pēpē a me nā keiki me ka "double aortic arch" e loaʻa i kēia mau hōʻailona e pili ana i ka hanu ʻana. ʻO lākou kēia:

• He leo ʻē i ka wā e hanu ana (he leo kiʻekiʻe i kapa ʻia ʻo 'stridor' a i ʻole he leo wheezing i kapa ʻia ʻo 'wheezing') .
• He ʻū ʻana e like me ka leo o ka "seal uwē ʻana." Ua like kēia me ke ʻū e kū mai ana i ka wā o ke kūlana i kapa ʻia ʻo "croup."
• Nā maʻi pinepine o ka ʻōpū hanu haʻahaʻa .

Nā hōʻailona gastrointestinal

Ma kahi o 40 pakeneka o nā pēpē a me nā keiki me ka "double aortic arch" e ʻike i kēia mau hōʻailona digestive. ʻO lākou pū kekahi:

• Ka ʻū ʻana i ka wā e hānai ana i ka waiū a i ʻole ka hānai ʻana.
• Paʻakikī i ka moni ʻana (dysphagia) . ʻIke pinepine ʻia kēia ma hope o ka hoʻomaka ʻana o ka pēpē e ʻai i nā meaʻai paʻa.
• Ka paʻakikī o ka loaʻa ʻana o ke kaumaha .
• Ke piʻi hou ʻana mai o ka meaʻai i loko o ka puʻu (`Regurgitation/reflux`) .

Nā hōʻailona o ka puʻuwai

Ma kahi o 30 pakeneka o nā pēpē a me nā keiki me ka "double aortic arch" e hoʻomohala i nā hōʻailona pili i ka puʻuwai. ʻO kēia mau mea:

• ʻEha ka umauma .
• He kani puʻuwai ʻē aʻe (ʻO ke kani ʻana o ka puʻuwai) .
• ʻIli polū (cyanosis) .

He aha ke kumu o ka "Double Aortic Arch"?

ʻAʻole i ʻike ʻia ke kumu kikoʻī o ka "double otic arch" . ʻOiai ʻike pinepine ʻia kēia ʻano i nā pēpē i hāpai ʻia ma o ka "in-vitro fertilization" (IVF) , ʻaʻole ʻike ʻia ke kumu kikoʻī.

Hiki ke pili pū ʻia ke kīkoʻo aortic pālua me nā kūlana olakino ʻē aʻe. Ma kahi o 12 pakeneka o nā pēpē me ke kīkoʻo aortic pālua he kīnā puʻuwai hānau ʻē aʻe, e like me ka ventricular septal defect (VSD) a me ka tetralogy o Fallot . Eia kekahi, ma kahi o 20 pakeneka o nā pēpē me ke kīkoʻo aortic pālua he mau kūlana genetic e like me ka chromosome 22q11 deletion a me ka trisomy 21 (Down syndrome) .

Pehea e ʻike ai i ka "Double Aortic Arch"?

ʻIke ʻia ke kīkoʻo aortic pālua ma ka hanana a i ʻole ke hoʻomaka nā hōʻailona. I kekahi manawa, ʻike ʻia ia ma ke ʻano ulia i ka wā hāpai, ma hope o ka hānau ʻana, a i ʻole i ka wā o nā hoʻokolohua kiʻi i hana ʻia no kekahi kumu ʻē aʻe. Mai ka makahiki 2004, ua piʻi ka nui o ka poʻe i ʻike ʻia me kēia maʻi ma o nā scan i ka wā hāpai. He mea pono loa kēia, no ka mea hiki ke hoʻolālā ʻia ka lāʻau lapaʻau i ka wā e hānau ai ka pēpē.

A i ʻole, hiki ke ʻike ʻia ke ʻike ʻia nā hōʻailona ma hope o ka hānau ʻana o ka pēpē. E kamaʻilio ke kauka o kāu pēpē me ʻoe e pili ana i nā hōʻailona a laila hana i kekahi mau hoʻokolohua.

Nā hoʻāʻo e ʻike ai i ka "Double Aortic Arch"

ʻO nā hoʻokolohua nui i hoʻohana ʻia e ʻike i kēia maʻi:

• X-ray o ka umauma: ʻO kēia ka hoʻāʻo mua i hana ʻia.
• Kiʻi CT.
• Hoʻāʻo Echocardiogram (Echo): He mea kōkua nui kēia i ka ʻike ʻana inā he mau kīnā puʻuwai ʻē aʻe.
• Hoʻāʻo MRI (MRI).

I kekahi manawa, hiki ke hana ʻia kahi bronchoscopy e nānā i ka ʻōpū hanu o ka pēpē. Hiki ke hana ʻia kēia ma muli o nā pilikia hanu ma mua o ka ʻike ʻia ʻana o kahi ʻāʻī aortic pālua. A i ʻole, hiki ke hana ʻia ma mua o ke ʻoki ʻana e kōkua i ke kauka ʻoki e hoʻoholo i ke kumu o ka pilikia.

Kōkua ka hoʻāʻo ʻana i ka genetics i ka ʻike ʻana i nā kūlana genetic.

Pehea e ho'ōla ai i ka "Double Aortic Arch"?

Pono ke ʻoki kino e hoʻoponopono i ke kūlana o ka "double aortic arch." ʻOiai no nā pēpē i ʻike ʻole i nā hōʻailona, ​​ʻoi aku ka maikaʻi o ke ʻoki kino ma waena o 6 a me 9 mau mahina. ʻO nā pēpē i ʻike ʻia nā hōʻailona, ​​​​ʻoiai inā koʻikoʻi nā hōʻailona, ​​​​pono paha ke ʻoki kino ma mua.

E noʻonoʻo wale, ua ʻike mua ʻia ke kūlana "double aortic arch" i ka makahiki 1737. Ua hana ʻia ke ʻoki mua no ia mea i ka makahiki 1947. Auē ka mamao o kā mākou hele ʻana mai ia manawa! Ua hiki i nā pēpē me kēia kīnā hānau ke ola lōʻihi a olakino mahalo i ka mālama ʻoki ʻana.

ʻO ke ʻoki kino "Pālua Aortic Arch"

He palekana loa ke ʻoki ʻana "Double Aortic Arch", a ua holomua loa nā hopena . ʻAʻole pono e hoʻopili ʻia kāu pēpē i kahi "cardiopulmonary bypass" (mīkini puʻuwai-māmā) .

Hana ʻia ke ʻoki ʻana me ka hoʻohana ʻana i kahi ʻano hana i kapa ʻia ʻo "lateral thoracotomy." ʻO ke ʻano kēia, hana ke kauka ʻoki i kahi ʻoki ma kekahi ʻaoʻao o ka umauma o ka pēpē, ma waena o ʻelua mau iwi ʻaoʻao. Hana pinepine ʻia kēia ma ka ʻaoʻao hema, no ka mea, ʻo ia kahi i loaʻa ai i ka hapa nui o nā pēpē kēlā iwi ʻaoʻao liʻiliʻi "keu". ʻO nā hoʻokolohua kiʻi i hana ʻia ma mua o ke ʻoki ʻana e hiki ai i ke kauka ʻoki ke nānā pono i loko o ke kino o ka pēpē a hoʻolālā i ke ʻoki ʻana e like me ia.

Hoʻohana ke kauka lapaʻau i kahi ʻano hana "ligating and dividing" . ʻO ia hoʻi, ua nakinaki ʻia ke apo liʻiliʻi e hoʻōki i ke kahe ʻana o ke koko ma o ia mea. A laila ʻoki ʻia a humuhumu ʻia. Hana hou ʻia kēia kaʻina hana a hiki i ka wā e kaʻawale loa ai ke apo a hoʻopau ʻia ke kaomi ma ka ʻōpū a me ka esophagus.

E noho ana kāu pēpē i ka haukapila no hoʻokahi pule, a laila e ola a hoʻi mai i ka home.

Lapaʻau ʻana o "Kommerell diverticulum" (`Kommerell diverticulum - KD`)

I kekahi manawa, hiki i kekahi mau pēpē me ka "double aortic arch" ke loaʻa i kahi mea i kapa ʻia ʻo "Kommerell diverticulum (KD)." ʻOi aku ka maʻamau o kēia i nā pēpē me ka "right aortic arch," akā he mea kakaikahi loa hoʻi me ka "double aortic arch."

He ʻano ʻaneurysm kēia `KD`, he kīʻaha koko e ulu ana ma ka `aorta` iho kokoke i ka `aortic arch`. Hiki i kēia puʻupuʻu ke lawe i kahi ākea a kaomi i ka ʻōpū hanu a me ka paipu meaʻai o ka pēpē. ʻAʻole paha ia e hana koke i nā pilikia. Eia nō naʻe, makemake nā kauka ʻoki e wehe i kēia i ka wā e hana ai i ka `double aortic arch` e pale aku i nā pilikia ma hope.

Ka mālama ʻana i nā kīnā puʻuwai ʻē aʻe

Inā he mau kīnā puʻuwai ʻē aʻe ko kāu pēpē e pono ai ke ʻoki ʻana, hiki ke mālama ʻia i ka manawa like me ke kīkoʻo aortic pālua. Pono paha kēia i kahi kaʻina hana i kapa ʻia he "median sternotomy" , ʻo ia hoʻi ka hana ʻana i kahi ʻoki ma waena o ka umauma. E kūkākūkā ke kauka lapaʻau o kāu pēpē i ke koho maikaʻi loa nāu, ma muli o nā pilikia e pono ai ke mālama ʻia.

He aha nā pilikia e hiki ke loaʻa mai ke ʻoki kino?

He haʻahaʻa loa ka pilikia o nā pilikia mai ke ʻoki ʻana i ke kīkoʻo aortic pālua . I kekahi manawa, pilikia paha ka pēpē i ka hānai ʻana a i ʻole nā ​​pilikia hanu mau. Inā he mau pilikia hanu mau, nalo pinepine lākou i loko o hoʻokahi makahiki o ke ʻoki ʻana.

Hiki ke ʻokoʻa nā pilikia o nā ʻoki ʻana e hoʻoponopono i ke kīkoʻo aortic pālua a me nā kīnā puʻuwai ʻē aʻe. E kūkākūkā i kēia mau pilikia a me nā pilikia me ke kauka lapaʻau o kāu pēpē.

Hiki ke pale ʻia ka "Double Aortic Arch"?

ʻAʻole, ʻaʻole hiki ke pale ʻia kahi kūlana i kapa ʻia ʻo "double aortic arch". He mea ia e ulu ana i ka wā mua o ka hāpai ʻana a loaʻa i ka wā hānau.

He aha ka wā e hiki mai ana o ka poʻe me ka "Double Aortic Arch"?

He wā e hiki mai ana ko nā pēpē a me nā keiki i hana ʻia i ke ʻoki "Double Aortic Arch". Hiki iā lākou ke ola a komo i nā hana maʻamau me ke kaohi ʻole ʻia.

Ma hope o ke ʻoki ʻana, hiki i kāu pēpē ke hoʻomau i ka hanu walaʻau a hiki i hoʻokahi makahiki. ʻO kēia no ka mea ʻaʻole i ulu piha ka ʻōpū o ka pēpē ma muli o ka "double aortic arch." No laila, e lōʻihi ka manawa e ikaika ai ka ʻōpū.

He mea kākaʻikahi loa, loaʻa paha i nā pēpē a me nā keiki nā hōʻailona hanu ma mua o hoʻokahi makahiki ma hope o ke ʻoki ʻana.

ʻO ka mea nui loa, ʻo ia ke lawe i kāu pēpē no nā nānā maʻamau a haʻi i kāu kauka inā loaʻa iā ʻoe kekahi mau hōʻailona e hoʻomau nei. He mea nui loa ka mālama ʻana i ka wā lōʻihi no kēlā me kēia keiki i hana ʻia ke ʻoki puʻuwai.

Āhea wau e kāhea aku ai i ke kauka o kaʻu pēpē?

Inā ʻike ʻoe i kekahi mau hōʻailona hou, a inā paha e ʻoi aku ka ʻino o nā hōʻailona e kū nei, e kamaʻilio koke me ke kauka o kāu pēpē. Ua loli nui nā pēpē a me nā keiki liʻiliʻi a hiki i kekahi manawa ke paʻakikī ke ʻike i ka mea maʻamau a me ka mea ʻē. Akā inā loaʻa i kāu pēpē kēlā ʻū "seal-like" a i ʻole ke kani ʻana o ka wheezing , e haʻi koke i kāu kauka. He maʻi maʻamau paha ia o ka wā kamaliʻi. Akā, i kekahi manawa, he hōʻailona paha ia o kahi pilikia puʻuwai e hoʻopilikia ana i ka hiki i kāu pēpē ke hanu.

Āhea ʻoe e kāhea ai i ka 911 (helu pilikia)?

Hiki i kahi "double aortic arch" ke kau i ke kaomi weliweli i ke ola ma ka ʻōpū makani o kāu pēpē. Inā ʻike ʻia ka ʻili o kāu pēpē he uliuli (cyanosis) , a inā paha he paʻakikī nui ka hanu ʻana o kāu pēpē, e kāhea koke i ka 911.

He aha nā nīnau e pono iaʻu e nīnau aku i ke kauka o kaʻu pēpē?

Inā ua ʻike ʻia kāu pēpē me ka "double aortic arch," he mea maʻamau iā ʻoe ke loaʻa nā nīnau he nui. He mea nui e ʻike i ke kūlana o kāu pēpē, me ka wā e pono ai ke ʻoki ʻana, a inā he mau pilikia olakino ʻē aʻe kāu pēpē. Makemake paha ʻoe e nīnau i nā nīnau e like me:

• Āhea e pono ai ke ʻoki kino i kaʻu pēpē?
• Ma hea e hana ʻia ai ke ʻoki kino? ʻO wai ka mea e hana nei?
• He aha nā hōʻailona e pono iaʻu e makaʻala ma ka home?
• He aha kaʻu e hana ai e maʻalahi ai no kaʻu pēpē ke noho ma ka home?
• He mau kīnā puʻuwai ʻē aʻe ko kaʻu pēpē?
• Pono anei iaʻu e hana i nā hoʻāʻo genetic no kaʻu pēpē a i ʻole ke koena o koʻu ʻohana?
• Pehea lā ka wā e hiki mai ana o kaʻu pēpē?

He aha ka "Aortic Arch Syndrome"? He ʻokoʻa anei ia mai ka "Double Aortic Arch"?

ʻAe, mai huikau i nā mea ʻelua. ʻO "Aortic Arch Syndrome" kahi ʻano kakaikahi loa o "Vasculitis" . Ua kapa ʻia hoʻi ʻo "Takayasu's arteritis" .

ʻO "Vasculitis" kahi mumū o nā paia o kou mau kīʻaha koko. Hiki ke loaʻa i loko o kekahi kīʻaha koko, ʻoiai nā kīʻaha koko liʻiliʻi loa, ʻo nā capillaries. ʻO "Takayasu's arteritis" kahi mumū o nā kīʻaha koko waena a me nā kīʻaha koko nui. ʻO ka hapa nui o ia mea e loaʻa ma ka "aortic arch" a me kona mau lālā nui. ʻO ia ke kumu i kapa ʻia ai ʻo "aortic arch syndrome."

ʻO ka arteritis o Takayasu (i ʻike ʻia hoʻi ʻo "aortic arch syndrome") e loaʻa i nā pākeke ʻōpio a me nā pākeke ʻōpio . He pilikia ʻokoʻa loa kēia ma mua o ka "double aortic arch" hānau mua a mākou i kūkākūkā ai, a ʻokoʻa ke ʻano o ka mālama ʻana e pono ai.

ʻO ka hānau ʻana o kahi pēpē he manawa ia o ka hauʻoli a me ka hoʻolauleʻa. Eia nō naʻe, ke ʻike ʻoe he maʻi puʻuwai ko kāu pēpē, i ka wā hāpai a ma hope paha o ka hānau ʻana, ua pani ʻia kēlā hauʻoli e ka hopohopo a me ke kānalua. Inā ua ʻike wale ʻoe he "double aortic arch" ko kāu pēpē, ke noʻonoʻo nei paha ʻoe i ka mea e hiki mai ana.

Mai hopohopo. E kōkua kāu hui lapaʻau iā ʻoe ma o kēia mau mea āpau i kēlā me kēia ʻanuʻu. Ua lawe mua ʻoe i ka hana mua, ʻo ia ke aʻo hou aʻe e pili ana i ke kūlana o kāu pēpē. ʻO ka nūhou maikaʻi, he palekana loa a holomua ke ʻoki ʻana i ke aortic arch pālua. Inā loaʻa i kāu pēpē nā kīnā puʻuwai ʻē aʻe a i ʻole nā ​​​​​​kūlana genetic, hiki ke paʻakikī iki ka mālama ʻana. Eia nō naʻe, me ka holomua o ka mālama ʻana i nā keiki hānau hou, hiki iā ʻoe ke kōkua i kāu pēpē e loaʻa ka mālama kūpono e pono ai lākou, hoʻōla, a loaʻa kahi wā kamaliʻi hauʻoli.

No laila, he aha nā mea nui e hoʻomanaʻo ai mai nā mea a mākou i kamaʻilio ai? (Leka Lawe-Home)

ʻAe, e hōʻuluʻulu kākou i kekahi o nā mea e pono ai ʻoe e hoʻomanaʻo mai nā mea a mākou i kamaʻilio ai e pili ana i kēia "Double Aortic Arch":

• ʻO ka "Double aortic arch" kahi kīnā puʻuwai hānau . Ua māhele ʻia ka aorta o ke pēpē i ʻelua mau ʻā, e hana ana i ke kaomi ʻana o ka trachea a me ka esophagus.
• ʻO nā hōʻailona nui ka paʻakikī o ka hanu ʻana, ka hanu ʻana, ka paʻakikī o ke ale ʻana, a me nā maʻi hanu pinepine .
• Hoʻomaopopo ʻia kēia maʻi ma o nā hoʻokolohua e like me ka `CT scan`, `MRI`, `Echocardiogram` . I kekahi manawa hiki ke ʻike ʻia i ka wā hāpai.
• He ʻoki kino ke ʻano o ka lāʻau lapaʻau. He palekana loa kēia ʻoki kino a he holomua hoʻi.
• No ke pēpē ma hope o ke ʻoki kinoHiki iā ʻoe ke ola i kahi ola maʻamau a olakino hoʻi.
• Inā loaʻa i kāu pēpē nā hōʻailona e like me ka paʻakikī o ka hanu ʻana a i ʻole ka ʻū ʻana, e ʻimi koke i ke kōkua lapaʻau .
• Mai hopohopo . Me ka holomua o ka lāʻau lapaʻau hou, hiki ke mālama pono ʻia kēia maʻi. E hāʻawi kāu hui lapaʻau iā ʻoe i ke kākoʻo āu e pono ai.

ʻO ke kīkoʻo aortic pālua, ka maʻi puʻuwai hānau, nā apo koko, ka asphyxia o nā pēpē, ke olakino o nā pēpē, ke ʻoki puʻuwai