Ua ʻike anei ʻoe i kahi mea ʻē a puʻupuʻu paha ma kou kino? He mea maʻamau ke manaʻo iki i ka makaʻu a hopohopo paha i ka wā e hana ʻia ai kēlā. I kēia lā e kamaʻilio mākou e pili ana i kahi puʻupuʻu kakaʻikahi, akā ʻaʻole maʻamau loa. Ma nā ʻōlelo lapaʻau, ua kapa ʻia kēia he Solitary Fibrous Tumor (SFT) . ʻOiai paha he paʻakikī ke kani ʻana o ka inoa, e mālama kākou i ka maʻalahi a maopopo.
I ka ʻōlelo maʻalahi, he aha ka Solitary Fibrous Tumor (SFT)?
Pili kēia i kahi puʻupuʻu e hoʻomaka ana i loko o nā ʻiʻo palupalu o ko kākou kino. E noʻonoʻo i nā mea e like me nā ʻiʻo, nā ʻiʻo momona, a me nā aʻalolo i loko o ko kākou kino. Ua kapa ʻia kēia mau mea he mau ʻiʻo palupalu. No laila, hiki i kēia mau puʻupuʻu SFT ke ulu aʻe ma nā wahi āpau o ke kino. Eia naʻe, ʻike pinepine ʻia lākou i loko o ka uhi pale a puni nā māmā (pleura) .
ʻO ke ʻano o kēia mau puʻupuʻu hiki ke ʻano o ʻelua ʻano:
- Lohi loa ka ulu ʻana o kekahi a ʻaʻole e laha i nā ʻāpana ʻē aʻe o ke kino (ʻaʻole maʻi kanesa - benign) .
- Ulu wikiwiki kekahi a hiki ke laha i nā wahi ʻē aʻe (maʻi kanesa) .
ʻOiai he mau puʻupuʻu ʻaʻole ia he maʻi kanesa, ʻōlelo pinepine nā kauka e wehe loa i ka puʻupuʻu, ma o ke ʻoki ʻana a i ʻole kekahi lāʻau ʻē aʻe, i mea e pale ai iā ia mai ka hoʻopilikia ʻana i ka wā e hiki mai ana.
Aia kekahi mau inoa ʻē aʻe no kēia mau puʻupuʻu?
ʻAe, i ka wā ma mua, he inoa ʻokoʻa no kēia. I kēlā manawa, ua manaʻo nā kauka ua hoʻokumu wale ʻia kēia mau puʻupuʻu i loko o ka lua o ka umauma, ʻo ia hoʻi, i loko o ka membrane e hoʻopuni ana i nā māmā. Kāhea mākou i kēia membrane ʻo ka pleura . ʻO kēia ka mea e kōkua ai i nā māmā e hana maʻalahi i loko o ka umauma i ka wā e hanu ai mākou. No laila, i kēlā manawa, ua kapa ʻia kēia mau puʻupuʻu he "benign fibrous tumors of the pleura."
Eia nō naʻe, ua ʻike ʻia ma hope mai nā noiʻi hiki i kēia mau puʻupuʻu ke hana ʻia ma nā wahi āpau o ke kino, ʻaʻole wale ma nā māmā, e like me ke akepaʻa, ka lolo, ka ʻāʻī, a me ke poʻo. No laila, ʻaʻole i hoʻohana nui ʻia kēlā inoa kahiko a lōʻihi.
ʻO ka mea nui, ʻaʻole i hoʻokumu ʻia kēia mau nodules SFT e ka hōʻike ʻana i ka asbestos ma kekahi ʻano. Hoʻokumu ʻia lākou e kahi maʻi ʻokoʻa, ʻo `Pleural Mesothelioma`.
He aha ka ʻokoʻa ma waena o SFT a me Pleural Mesothelioma?
E huikau paha kekahi poʻe no ka mea hiki ke loaʻa nā mea ʻelua i loko o nā māmā. Eia naʻe, he ʻokoʻa loa kēia mau mea ʻelua. E hoʻomaopopo pono kākou i kēia ʻokoʻa me ke kōkua o kahi papa.
| Hiʻona | ʻO ka puʻupuʻu fibrous hoʻokahi (SFT) | ʻO ka Mesothelioma Pleural |
|---|---|---|
| Kumu nui | ʻAʻohe kumu kikoʻī i ʻike ʻia. | Ka hōʻike ʻia ʻana i ka asbestos. |
| ʻAno maʻi kanesa | ʻO ka hapa pinepine ʻaʻole ia he maʻi kanesa (benign), akā aia kahi hiki ke lilo i maʻi kanesa. | He maʻi kanesa mau. |
| Nā wahi e hana ʻia ai | Hiki ke loaʻa ia ma nā wahi a pau o ke kino, akā ʻoi aku ka nui o ia mea ma ka ʻili o nā māmā. | ʻIke pinepine ʻia ia ma ka paia o nā māmā (pleura) a me ka paia o ka ʻōpū. |
ʻO wai ka mea i ʻoi aku ka nui o ka pilikia o ka loaʻa ʻana o kēia mau puʻupuʻu?
ʻOiai hiki ke ulu kēia mau puʻupuʻu i kēlā me kēia makahiki, ʻike pinepine ʻia lākou i nā poʻe ma waena o 50 a me 60 mau makahiki. He mea kakaikahi loa kēia ʻano i nā keiki ʻōpio.
He mea kākaʻikahi loa kēia e ʻike ʻia ai kēia ʻano SFT ma lalo o 2 o kēlā me kēia 100 mau puʻupuʻu palupalu.
Nā ʻāpana o ke kino kahi e hiki ai ke loaʻa nā puʻupuʻu SFT
- I loko o nā ʻiʻo hoʻopili e hoʻopuni ana i ka lolo a me ke kaula spinal
- I loko o ke akepaʻa
- Nā māmā a me ka pleura
- I loko o nā lua i loko o ka ihu (Paranasal sinuses)
- I loko o nā ʻiʻo palupalu i loko o ka iwi kuamoʻo (orbit) kahi i loaʻa ai nā maka
- I loko o ka ʻōpū thyroid
No ke aha i hana ʻia ai kēia mau puʻupuʻu? He aha ke kumu?
ʻOiaʻiʻo, ʻaʻole i loaʻa i nā kauka kahi kumu paʻa no kēia. Eia naʻe, ua hāʻawi mai nā noiʻi hou iā mākou i kekahi mau hōʻailona. ʻO ia nā ʻano genes ʻelua i loko o ko mākou kino, ʻo ia hoʻi ʻo `NAB2` a me `STAT6`Hiki ke hana ʻia kēia mau puʻupuʻu e ka hui pū ʻana o ʻelua mau genes (gene fusion). Hiki i kēia loli genetic ke hoʻoulu i nā cell e hoʻomaka e ulu me ke kāohi ʻole ʻia.
He aha nā hōʻailona o ka SFT?
Hoʻoulu pinepine kēia mau puʻupuʻu me ka lohi loa . ʻO ka hopena, ʻaʻole ʻike ka hapalua o ka poʻe me SFT i kekahi mau hōʻailona . Hoʻomaka pinepine nā hōʻailona i ka wā e ulu nui ai ka puʻupuʻu e paʻi i nā ʻōpū kokoke, nā iwi, a i ʻole nā ʻiʻo ʻē aʻe. No laila, hilinaʻi nā hōʻailona i kahi o ka puʻupuʻu.
E nānā kākou i nā hōʻailona e hōʻike ai kēia mau puʻupuʻu ke ʻike ʻia lākou ma nā ʻāpana like ʻole o ke kino.
| Kahi o ka puʻupuʻu | Nā hōʻailona hiki ke loaʻa |
|---|---|
| Ka lua o ka umauma (mama, pleura) |
|
| Kaʻapuni | |
| lolo | |
| ʻO ke kaula iwi kuamoʻo | |
| Ake |
Pehea e ʻike ai ke kauka i kēia maʻi?
Ma muli o kāu mau hōʻailona a me kahi i manaʻo ʻia o ka puʻupuʻu, e kuhikuhi kāu kauka iā ʻoe no nā hoʻokolohua like ʻole.
- Hoʻokolokolo lapaʻau: ʻO ka mea mua e hana ai, ʻo ia ke hoʻolohe pono i kāu mau hōʻailona a laila e hana i kahi hoʻokolokolo kino.
- Nā Kiʻi Kiʻi: Kōkua kēia i ka ʻike ʻana i kahi, ka nui, a me ke ʻano o ka puʻupuʻu. Hiki i kēia ke komo pū me nā X-ray, nā CT scan, nā MRI scan, nā ultrasound scan , a me nā PET scan .
- Nānā maka: Inā aia ka puʻupuʻu kokoke i ka maka, hana ʻia nā hoʻokolohua maka kūikawā (Optical Coherence Tomography - OCT) e hoʻoholo ai i ke kumu pololei o nā pilikia ʻike.
- Biopsy: ʻO kēia ka hoʻāʻo koʻikoʻi loa . Pili kēia i ka lawe ʻana i kahi ʻāpana liʻiliʻi loa o ka ʻiʻo mai ka puʻupuʻu a nānā iā ia ma lalo o kahi microscope. E haʻi kēia iā ʻoe me ka 100% maopopo i ke ʻano o ka puʻupuʻu a inā he maʻi kanesa a ʻaʻole paha.
Ka hoʻokaʻawale ʻana o ke koʻikoʻi o nā nodules SFT
Ua hoʻokaʻawale ka World Health Organization (WHO) i kēia mau puʻupuʻu SFT i kekahi mau papa e pili ana i ko lākou koʻikoʻi a me ka wikiwiki o ka ulu ʻana. Ua kapa ʻia kēia he grading.
- Papa I (Papa Haʻahaʻa): ʻO kēia nā ʻano ʻoi aku ka liʻiliʻi o ka huhū. ʻO ka hapa nui o kā lākou mau cell he mau cell maʻamau. Ulu mālie lākou.
- Papa II (Papa waena): ʻAno ʻē iki ke ʻano o kēia mau hunaola. Hiki iā lākou ke ulu wikiwiki aʻe ma mua o ka Papa I. ʻOi aku ka maʻalahi o ko lākou lilo ʻana i maʻi ʻaʻai.
- Papa III (Pae kiʻekiʻe): ʻO kēia nā ʻano ʻino loa. He ʻano ʻē loa nā pūnaewele. Ulu koke lākou. Loaʻa iā lākou kahi pilikia kiʻekiʻe o ka hoʻi hou ʻana mai, lilo i maʻi ʻaʻai, a laha aku i nā ʻāpana ʻē aʻe o ke kino.
He aha nā lāʻau lapaʻau?
ʻO ka lāʻau lapaʻau nui a maikaʻi loa no ka puʻupuʻu SFT, ʻo ia ka wehe loa ʻana iā ia ma o ke ʻoki ʻana .
I kekahi mau hihia, paʻakikī paha ke hana ʻoki ma muli o ka wahi o ka puʻupuʻu. A i ʻole he nui paha ka puʻupuʻu. I ia mau hihia,
- Hoʻōla radiation:Hāʻawi ʻia ka lāʻau lapaʻau radiation e luku a hoʻēmi paha i ka puʻupuʻu. I kekahi manawa, hāʻawi ʻia kēia lāʻau lapaʻau ma mua o ke ʻoki ʻana e hoʻemi i ka puʻupuʻu a maʻalahi hoʻi e wehe.
He aha nā pilikia e hiki ai i kēia ke hana?
ʻO ka makaʻu nui loa ke ʻike ʻoe he puʻupuʻu kou, ʻo ia ka lilo ʻana i maʻi kanesa a i ʻole e laha aku i nā wahi ʻē aʻe (maʻi kanesa metastatic). Ke hana ʻia ʻoe i ke ʻoki ʻana e wehe iā ia, ua emi nui kēlā pilikia.
Akā ʻo ka mea nui e hoʻomanaʻo ai, ʻoiai me ka mālama ʻia ʻana, hiki i kēia mau puʻupuʻu ke hoʻi hou mai i kekahi manawa. ʻO kahi puʻupuʻu e hoʻi hou mai ana, ʻoi aku ka nui o ka lilo ʻana i maʻi kanesa.
Ma waho aʻe o kēlā, hiki ke loaʻa nā pilikia ʻē aʻe ma muli o ka wahi o ka puʻupuʻu.
- Ka maʻi lolo: Inā he puʻupuʻu a puni ke kaula kuamoʻo.
- Ka hoʻokahe ʻana o ka wai i loko o ka ʻōpū o ka māmā: ka hōʻiliʻili ʻana o ka wai i loko o ka ʻōpū o ka māmā.
- ʻO ka atrophy optic: Ka hōʻino ʻana i ke aʻalolo e lawe ana i nā leka mai ka maka i ka lolo.
Pehea ke ʻano o ka hoʻōla ʻana ma hope o ka lāʻau lapaʻau?
Hoʻōla maikaʻi loa ka nui o ka poʻe ma hope o ka wehe ʻana i kahi puʻupuʻu ma ke ʻoki ʻana. Eia naʻe, e like me kā mākou i ʻōlelo ai ma mua, he mea kakaikahi ka hoʻi ʻana mai o kahi puʻupuʻu, no laila e hoʻomau kāu kauka i ka nānā ʻana iā ʻoe. ʻO ia hoʻi ka hana ʻana i nā mea e like me nā scan i nā manawa maʻamau e nānā ai i kahi puʻupuʻu e hoʻi mai ana. He mea nui loa kēia e hana ai e pale i kou olakino.
Leka Lawe-Home
- ʻO ka Solitary Fibrous Tumor (SFT) kahi ʻano puʻupuʻu kakaikahi e hana ʻia ana i loko o nā ʻiʻo palupalu.
- Hiki i kēia ke lilo i maʻi kanesa a i ʻole ʻaʻole he maʻi kanesa. ʻO ka hapa nui o ka manawa, ʻaʻole kēia he mau kūlana maʻi kanesa.
- ʻAʻole loaʻa i ka hapa nui o ka poʻe nā hōʻailona. Inā loaʻa nā hōʻailona, ʻokoʻa lākou ma muli o kahi o ka puʻupuʻu.
- ʻO ka lāʻau nui e mālama ai, ʻo ia ka wehe loa ʻana i ka puʻupuʻu ma o ke ʻoki ʻana.
- ʻOiai ma hope o ka lāʻau lapaʻau, aia kahi pilikia liʻiliʻi o ka hoʻi hou ʻana mai o ka puʻupuʻu, no laila he mea nui loa e hoʻomau i ka launa pū me kāu kauka a hana i nā nānā kino maʻamau.
- Inā loaʻa iā ʻoe kekahi mau puʻupuʻu ʻē, ʻeha, a i ʻole nā hōʻailona ʻē aʻe i loko o kou kino, mai hopohopo a nīnau koke aku i ke kauka no ka ʻōlelo aʻo.











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