Ke manaʻo pinepine nei ʻoe i ka luhi a me ke ola ʻole? I kekahi manawa manaʻo mākou he mea maʻamau kēia, he luhi e loaʻa mai ana mai ka hana nui ʻana. Eia nō naʻe, aia paha kekahi kumu koʻikoʻi i hūnā ʻia ma lalo o kēia luhi. I kēia lā e kamaʻilio mākou e pili ana i kēlā ʻano anemia, a i ʻole kahi kūlana kūikawā e pili ana i ka nele o ke koko i loko o ke kino. Ua kapa ʻia kēia ʻo Heinz Body Anemia.
I ka ʻōlelo maʻalahi, he aha kēia mau kino Heinz?
I mea e hoʻomaopopo ai i kēia, pono mua kākou e ʻike iki e pili ana i ko kākou koko. Aia i loko o ko kākou koko kahi ʻano cell i kapa ʻia he mau cell koko ʻulaʻula. ʻO kēia nā cell e lawe ana i ka oxygen ma o ko kākou kino. E noʻonoʻo i kēia mau cell koko ʻulaʻula e like me nā kaʻa liʻiliʻi e lawe ana i ka oxygen. ʻO ka ʻāpana nui o kēia mau kaʻa e lawe ana i ka oxygen ua kapa ʻia ʻo hemoglobin . ʻO kēia protein i kapa ʻia ʻo hemoglobin ka mea e hāʻawi i ko kākou koko i kona kala ʻulaʻula.
Eia nō naʻe, no kekahi kumu, hiki ke hōʻino ʻia kēia mau molekula hemoglobin. E like me ka hōʻino ʻia ʻana o ke kahua hoʻouka o kahi kalaka. Hoʻopili pū ka hemoglobin i hōʻino ʻia, hoʻopili pū, a pipili i ka paia o ke koko ʻulaʻula. Kāhea mākou i kēlā mau puʻupuʻu he Heinz Bodies .
ʻO kēia mau kino Heinz ke kumu o ka nalowale ʻana o nā hunaola koko ʻulaʻula i ko lākou palupalu a lilo i mea paʻakikī. ʻO ka maʻamau, hiki i nā hunaola koko ʻulaʻula olakino ke hele maʻalahi ma o nā kīʻaha koko lahilahi loa. Akā, he paʻakikī i kēia mau hunaola paʻakikī ke hana pēlā. ʻO ko kākou spleen kahi ʻōkana e hoʻomaʻemaʻe i ko kākou koko. I kona hele ʻana ma o kēia kānana, ʻike ka spleen i nā hunaola koko ʻulaʻula me kēia mau kino Heinz paʻakikī a luku iā lākou. I kekahi manawa, ʻo ka ʻāpana kino Heinz wale nō ka mea i wehe ʻia, a ua like nā hunaola koko ʻulaʻula me he mea lā ua nahu kekahi i kahi ʻāpana o ka biscuit. Kāhea pū mākou i kēia mau hunaola nahu .
Ma kēia ʻano, ke wāwahi koke kēia mau hunaola koko ʻulaʻula i hōʻino ʻia ma mua o ka hiki i ko mākou kino ke hana i nā mea hou, e emi ana ka nui o ke koko i loko o ko mākou kino. ʻO ia ka mea a mākou e kapa nei he Heinz Body Anemia.
No ke aha i kū ai kēia kūlana? He aha nā kumu?
ʻO ke kumu nui o nā kino Heinz, ʻo ia ka hōʻino kemika a i ʻole ka oxidative i ko kākou mau hunaola koko ʻulaʻula. Hiki ke loaʻa kēia ma hope o ka hānau ʻana, a i ʻole hiki ke hana ʻia e kahi maʻi hānau ʻia.
Nā kumu o ka maʻi ma hope o ka hānau ʻana
ʻO ke kumu nui o kēia mau mea e komo ana i loko o ke kino mai waho.
| Kumu | Ka wehewehe a me nā laʻana |
|---|---|
| Kekahi mau lāʻau lapaʻau a me nā kemika | Hiki i ka hōʻike ʻana i kekahi mau lāʻau lapaʻau a me nā kemika ke hōʻino i nā hunaola koko ʻulaʻula. Nā laʻana:
|
| Nā hemahema o nā minelala | He mineral koʻikoʻi ka Selenium no ko kākou kino. Kōkua ia i ka hana ʻana i kahi antioxidant ikaika i kapa ʻia ʻo glutathione. ʻO kēia antioxidant ka mea e pale ai i ko kākou mau hunaola koko ʻulaʻula mai ka hōʻino ʻia. Inā he hemahema o ka selenium, e emi ana kēia pale a hiki ke hana ʻia nā kino Heinz. |
Nā kumu hānau (nā kūlana genetic)
He mau kūlana hoʻoilina kēia i hoʻoilina ʻia mai nā mākua a i nā keiki.
- Ka hemahema o G6PD: ʻO ka inoa piha o kēia ʻo Glucose-6-phosphate dehydrogenase deficiency. He ʻano kēia i ʻike ʻia ma ko mākou ʻāina. He enzyme koʻikoʻi loa kēia G6PD e pale ana i nā hunaola koko ʻulaʻula. I ka poʻe i nele i kēia enzyme, ke lawe lākou i kekahi mau lāʻau lapaʻau, ke loaʻa iā lākou kekahi mau maʻi, a i ʻole ke ʻai lākou i kekahi mau meaʻai (e laʻa me nā pīni fava), hoʻomaka koke ko lākou mau hunaola koko ʻulaʻula e wāwahi.
- Thalassemia: He kīnā genetic nō hoʻi kēia i ka hana ʻana o ka hemoglobin i mea maʻamau i ko mākou ʻāina. Hiki ke ʻike ʻia nā kino Heinz i loko o ke koko o nā maʻi thalassemia.
- Nā hemoglobinopathies paʻa ʻole: Hānau ʻia kekahi poʻe me nā ʻano hemoglobin ʻano ʻē a paʻa ʻole. He mea maʻalahi kēia mau mea e hōʻino a hoʻoulu i nā kino Heinz.
Loaʻa iā ʻoe kēia mau hōʻailona?
ʻAʻole hōʻike ka loaʻa ʻana o nā kino Heinz i nā hōʻailona. Eia nō naʻe, i ka wā e hoʻomaka ai ka nui o nā hunaola koko ʻulaʻula e haki, ulu ka anemia a ʻike ʻia nā hōʻailona like ʻole.
| Nā hōʻailona maʻamau o ka anemia kino Heinz | |
|---|---|
| Melemele o ka ʻili a me nā maka (Jaundice) | Manaʻo pinepine o ka luhi nui a me ka paupauaho |
| Paʻakikī ka hanu ʻana a me ka wheezing | ʻIli keʻokeʻo |
| Puʻuwai wikiwiki a ʻano ʻole paha | ʻO ke akepaʻa a i ʻole ka spleen e pehu ana (ʻeha ma ka ʻōpū o luna) |
Pehea ʻoe e ʻike ai i kēia? He aha nā hoʻokolohua e hana ʻia?
Inā loaʻa iā ʻoe nā hōʻailona e like me kēia, ʻo ka mea mua a kāu kauka e hana ai, ʻo ia ke nānā iā ʻoe a kauoha i kekahi mau hoʻokolohua koko.
- Helu Koko Piha (CBC): Ke ana kēia i ka helu o nā hunaola koko ʻulaʻula, nā hunaola koko keʻokeʻo, a me nā platelets i loko o kou koko. He mea nui kēia no ka nānā ʻana i ka anemia.
- Hemoglobin a me Hematocrit: Ke ana kēia i ka helu o nā hunaola koko ʻulaʻula a me nā pae hemoglobin.
- ʻO ka ʻIke Koko Peripheral: He hoʻāʻo koʻikoʻi loa kēia. Maanei, ua hamo ʻia kahi kulu koko ma kahi slide aniani a nānā ʻia ma lalo o kahi microscope. A laila, hiki ke ʻike ʻia ke ʻano a me ka nui o nā hunaola koko ʻulaʻula. Hiki ke ʻike ʻia nā "hunaola nahu" a mākou i kamaʻilio ai ma mua me kēia hoʻāʻo. No ka ʻike pololei ʻana i nā kino Heinz, pono e hoʻohana ʻia kahi kala kūikawā (stain) no kēia hoʻāʻo.
- Hoʻāʻo mimi: Ke haki nā hunaola koko ʻulaʻula, hiki ke hoʻokuʻu ʻia ka hemoglobin i loko o ka mimi. Hana ʻia kēia hoʻāʻo e ʻike inā aia.
He aha nā lāʻau lapaʻau?
Aia ka lāʻau lapaʻau ma ke kumu o ke kūlana. Na kāu kauka e hoʻoholo i ke kumu a hāʻawi i ka lāʻau lapaʻau kūpono loa.
- Ke hoʻōki ʻana i ka lāʻau lapaʻau kumu: Inā hoʻoholo ʻia he lāʻau lapaʻau ke kumu o ke kūlana, e hoʻōki ʻia kēlā lāʻau lapaʻau a, inā pono, e hāʻawi ʻia kahi lāʻau lapaʻau palekana.
- Ke hāʻawi ʻana i nā mea hoʻopihapiha meaʻai: Inā loaʻa kēia ʻano ma muli o ka nele o kahi mineral e like me ka selenium, e hāʻawi ʻia nā mea hoʻopihapiha no ia mea.
- Nā lāʻau lapaʻau antibiotic: Inā hoʻonui ʻia ka anemia e kahi maʻi.
- Ka Hoʻoili Koko: Inā koʻikoʻi ka anemia, pono paha ka hoʻoili koko e hoʻihoʻi koke i nā pae koko.
- Ka Wehe ʻana i ka Spleen: I kekahi mau hihia koʻikoʻi, hiki ke ʻōlelo ʻia e wehe ʻoki ʻia ka spleen, ʻo ia ke kahua nui o ka luku ʻia ʻana o nā cell koko ʻulaʻula.
- Hiki ke hoʻohana ʻia nā lāʻau lapaʻau e like me nā lāʻau lapaʻau pale ʻana i ka maʻi a me nā hoʻoili cell kumu i nā hihia kakaikahi a koʻikoʻi loa.
ʻO ka mea nui loa: Mai ho'ōki i ka lawe ʻana i kekahi lāʻau lapaʻau a hoʻololi paha i ka nui me ka ʻole o ke kamaʻilio ʻana me kāu kauka. Hiki ke lilo i mea weliweli.
He aha nā pilikia e hiki ke hana ma muli o kēia ʻano?
Inā ʻaʻole mālama pono ʻia ka anemia kino Heinz, hiki ke loaʻa kekahi mau pilikia. ʻOkoʻa kēia ma muli o ke kumu a me ka mālama ʻana i ka maʻi.
- Nā ʻūpā koko (ʻoi aku hoʻi i loko o nā māmā)
- Nā pōhaku ʻōpū
- Ka hāʻule ʻana o ka puʻupaʻa
- Ka hāʻule ʻana o ka puʻuwai
- Pūʻiwa
- Nā hopena ʻaoʻao o nā lāʻau lapaʻau i lawe ʻia no ka mālama ʻana
ʻO kekahi o kēia mau pilikia he mau pilikia olakino. No laila, inā manaʻo koke ʻoe ua maʻi ʻoe, paʻakikī loa ka hanu ʻana, a i ʻole e ʻeha ka umauma, e hele koke i ka Emergency Department (ETU) o ka haukapila kokoke loa. Inā manaʻo ʻoe ua hana ʻia kēia ʻano ma muli o ka ʻai ʻana i kahi mea kemika, hiki iā ʻoe ke kelepona i ke National Poisons Information Centre ma ka Colombo National Hospital no ka ʻōlelo aʻoaʻo.
Leka Lawe-Home
- ʻO ka Heinz Body Anemia kahi kūlana kahi e wāwahi ai ke kino i nā hunaola koko ʻulaʻula ma mua o ka hiki ke hana i nā mea hou.
- Hiki ke hana ʻia kēia e kekahi mau lāʻau lapaʻau, nā kemika, a i ʻole nā kūlana hānau e like me ka hemahema o G6PD a me ka thalassemia.
- ʻO nā hōʻailona nui ka luhi pinepine, ka melemele o ka ʻili, a me ka keʻokeʻo.
- He mea nui nā hoʻāʻo koko no ka ʻike pololei ʻana i kēia maʻi.
- ʻO ke ʻano o ka lāʻau lapaʻau e pili ana i ke kumu o ka maʻi, no laila he mea nui loa ka ʻimi ʻana i ke kōkua lapaʻau.
- Mai ho'ōki i ka lawe ʻana i kekahi lāʻau lapaʻau me ka ʻole o ke kūkākūkā ʻana me ke kauka. Inā loaʻa iā ʻoe kekahi ʻano ʻeha, e kelepona koke aku i kāu kauka.











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