Koj puas tau hnov txog ib qho mob uas qee qhov ntawm peb lub cev, xws li ceg thiab cov kabmob, tsis loj hlob zoo lossis tsis loj hlob tag nrho? Qhov no yog yam uas cov kws kho mob hu ua aplasia . Tej zaum koj yuav ntshai me ntsis thaum koj hnov lub npe no. Tab sis tsis txhob txhawj, peb yuav tham txog qhov no yooj yim thiab meej. Tom qab ntawd koj tuaj yeem nkag siab zoo dua txog qhov no.
Aplasia yog dab tsi tiag?
Hais yooj yim xwb, aplasia yog ib qho mob uas ib feem ntawm koj lub cev, txawm tias nws yog ib daim ntaub so ntswg, ib lub cev, lossis lwm qhov ntawm koj lub cev, tsis loj hlob lossis ua haujlwm zoo. Feem ntau, cov mob no tshwm sim thaum lossis ua ntej yug los, thaum tus menyuam tseem nyob hauv plab. Qee zaum, thaum tus kws kho mob kuaj xyuas tus menyuam hauv plab lossis tus menyuam mos, lawv yuav pom tias ib feem, xws li caj npab lossis ceg, ploj lawm lossis tsis tsim zoo. Txawm li cas los xij, qee qhov mob aplasia, tshwj xeeb tshaj yog cov uas cuam tshuam nrog cov ntaub so ntswg sab hauv xws li pob txha, tuaj yeem kuaj pom thaum yau lossis txawm tias laus.
Qhov tseem ceeb yog tias aplasia tsis yog ib yam kab mob xwb. Nws yog ib lo lus uas cov kws kho mob siv los piav txog txhua yam mob uas ib feem ntawm lub cev tsis tau tsim tag nrho.
(Aplasia) txawv li cas ntawm (Agenesis), (Hypoplasia), thiab (Dysplasia)?
Cov lus no yuav ua rau kuv tsis nkag siab me ntsis, vim lawv lub ntsiab lus zoo ib yam. Tiam sis muaj qee qhov txawv me ntsis. Cia peb saib seb lawv yog dab tsi.
- (Agenesis): Qhov no yog thaum ib feem ntawm lub cev tsis loj hlob li . Hauv qee cov lus kho mob, (Aplasia) txhais tau tias muaj qee qhov qauv ntawm lub cev tseem ceeb, tsis tau loj hlob zoo. Tab sis hauv (Agenesis), tsis muaj ib feem ntawm lub cev ntawd tau loj hlob. Piv txwv li, yog tias lub raum tsis loj hlob li, nws hu ua (Renal Agenesis).
- Hypoplasia: Qhov no yog thaum ib feem ntawm lub cev tsis tau loj hlob txaus . Uas yog, nws tseem muaj tab sis me me lossis tsis tiav. Qee zaum, aplasia raug suav hais tias yog ib qho mob ntawm agenesis (tsis muaj) thiab hypoplasia (tsis loj hlob txaus).
- Dysplasia: Qhov no yog qhov tsis zoo li qub, tsis zoo li qub ntawm ib feem ntawm lub cev. Tsis zoo li aplasia, dysplasia tsis yog ib txwm tshwm sim los ntawm teeb meem kev loj hlob thaum ntxov (piv txwv li, ib feem pib loj hlob thiab tom qab ntawd nres). Dysplasia feem ntau yog kev loj hlob tsis zoo ntawm cov hlwb lossis cov nqaij. Piv txwv li, thaum ntxov ntawm mob qog noj ntshav, kev hloov pauv tsis zoo hauv cov hlwb ('dysplasia') tshwm sim, uas tom qab ntawd hloov mus ua mob qog noj ntshav.
Yog tias koj tsis paub meej txog cov lus no, nco ntsoov nug koj tus kws kho mob kom piav qhia rau koj . Qhov no yuav pab koj nkag siab meej dua txog qhov mob uas koj lossis koj tus menyuam muaj.
Cov hom aplasia tseem ceeb yog dab tsi?
Tsis yog txhua hom aplasia yog ib yam uas pom muaj ntau. Txawm li cas los xij, muaj ob peb hom aplasia uas peb hnov txog feem ntau, lossis paub zoo dua txog. Cov no suav nrog cov qe ntshav liab, daim tawv nqaij, pob txha, thiab cov qe noob caj noob ces (piv txwv li, phev thiab qe). Aplasia kuj tseem tuaj yeem cuam tshuam rau lwm yam kabmob, xws li lub ntsws thiab cov hlab ntsha pom.
Cia peb tham txog Pure Red Cell Aplasia (PRCA)
Hauv qhov xwm txheej no, koj cov qe ntshav liab ('Cov Qog Ntshav Liab') tsis loj hlob zoo. Feem ntau, peb cov pob txha ('Cov Qog Ntshav Pob Txha') tsim cov qe ntshav liab tshiab txhua 120 hnub. Thaum lub sijhawm no, cov qe ntshav liab pib loj hlob los ntawm lawv theem pib, "Erythroblast" mus rau hauv cov qe ntshav liab uas loj hlob tag nrho.
Yog tias koj muaj PRCA , koj cov pob txha pob txha yuav tsim tau tsawg heev lossis tsis muaj erythroblasts. Qhov no ua rau lub cev poob cov qe ntshav liab uas nws xav tau, ua rau muaj ntshav tsis txaus. Qhov no hu ua "ntshiab" vim nws tsuas cuam tshuam rau cov qe ntshav liab xwb. Lwm cov qe ntshav - cov qe ntshav dawb thiab cov platelets - raug tsim tawm li qub. Txawm li cas los xij, yog tias tag nrho peb hom qe ntshav tsis raug tsim tawm kom zoo, nws hu ua aplastic anemia .
PRCA tuaj yeem muaj thaum yug los (congenital PRCA), lossis nws tuaj yeem tshwm sim thaum lub sijhawm nws tseem muaj sia nyob. Hom PRCA uas muaj txij thaum yug los hu ua Diamond-Blackfan Anemia .
Aplasia Cutis Congenita yog dab tsi?
Qhov no yog thaum koj tus menyuam mos daim tawv nqaij, tshwj xeeb tshaj yog lub taub hau, tsis tau loj hlob zoo lossis ploj tag nrho hauv qee qhov chaw. Qee zaum, cov nqaij thiab pob txha hauv qab daim tawv nqaij ntawd tsis loj hlob tag nrho. Daim tawv nqaij kuj tseem yuav ploj ntawm qee qhov chaw ntawm tus menyuam lub cev, caj npab, thiab ceg.
(Aplasia Cutis Congenita) tej zaum yuav zoo li ib qho caws pliav ntawm lub taub hau, tsis muaj plaub hau nyob hauv qab. Los yog, daim tawv nqaij uas tsis tau loj hlob zoo li ib daim nyias nyias, tsis muaj plaub hau.
Raws li lub npe qhia ('Congenita'), qhov no yog ib qho mob uas muaj txij thaum yug los.
Cia peb kawm txog Radial Aplasia
Qhov no yog thaum ib qho ntawm ob lub pob txha hauv koj txhais caj npab, lub radius, tsis loj hlob. Muaj ob lub pob txha ntev hauv koj txhais caj npab, lub radius thiab ulna. Lub ulna khiav ntawm koj lub luj tshib mus rau koj lub dab teg, ntawm sab uas koj tus ntiv tes me nyob. Lub radius khiav ntawm koj lub luj tshib mus rau koj lub dab teg, ntawm sab uas koj tus ntiv tes xoo nyob. Ib tug neeg uas muaj radial aplasia yuav muaj ib txhais tes deformed, khoov. Tus ntiv tes xoo yuav ploj lossis tej zaum yuav luv dua li qub.
(Kev puas tsuaj ntawm cov hlab ntsha radial)Qhov tsis txaus ntawm Radial Ray yog ib hom mob. Nws yog ib qho teeb meem nrog kev loj hlob ntawm pob txha Radius. Qhov tsis txaus ntawm Radial Ray tuaj yeem sib txawv ntawm qhov me me mus rau qhov hnyav. Qee zaum pob txha Radius tau tsim, tab sis nws luv dua li qub. Lwm lub sijhawm, pob txha Radius tsis loj hlob kiag li.
Kab mob Germ Cell Aplasia lossis Sertoli-Cell-Only Syndrome yog dab tsi?
Qhov no yog thaum ib tug neeg poob cov qe menyuam ('Germ Cells') hauv lawv cov noob qes ('Testes'). Cov qe menyuam yog cov qe menyuam yug tshiab. Hauv cov txiv neej, nws yog cov qe menyuam uas tom qab ntawd dhau los ua phev ('Sperm'). Thaum cov qe menyuam ploj lawm, phev tsis tuaj yeem tsim tau. Qhov no txhais tau tias cov neeg uas muaj cov qe menyuam tsis muaj peev xwm muaj menyuam ('Infertility').
Qhov kev puas tsuaj ntawm cov qe menyuam tseem hu ua Sertoli-Cell-Only Syndrome . Qhov no yog vim tias, txawm tias cov qe menyuam ploj lawm los xij, cov qe menyuam Sertoli tseem nyob hauv lub cev yug me nyuam. Feem ntau, cov qe menyuam Sertoli pab cov qe menyuam loj hlob mus ua phev. Txawm li cas los xij, thaum cov qe menyuam ploj lawm, cov qe menyuam Sertoli tsis muaj lub luag haujlwm hauv kev tsim cov phev.
Cia peb kuj saib Pulmonary Aplasia.
Kab mob ntsws Aplasia yog ib yam mob uas ib tug neeg yug los nrog lub ntsws tsis loj hlob zoo. Qhov no tsis yog ib yam mob xwb, thiab muaj ntau theem sib txawv. Nws muaj txij li qhov tsis loj hlob kiag li ntawm lub ntsws ('Pulmonary Agenesis') mus txog rau qhov tsis loj hlob me ntsis ('Pulmonary Hypoplasia').
Kab mob ntsws Aplasia yog qhov chaw nruab nrab ntawm Kab mob ntsws Agenesis thiab Kab mob ntsws Hypoplasia. Hauv kab mob ntsws Aplasia, cov qauv ntsws pib tsim, tab sis nws tsis tuaj yeem ua haujlwm zoo li lub ntsws ua haujlwm tau zoo.
Feem ntau, ib lub ntsws ploj lawm lossis tsis loj hlob txaus, thaum lwm lub tseem zoo li qub.
Thymic Aplasia yog dab tsi?
Koj lub qog thymus yog ib lub qog uas tsim ib hom qe ntshav dawb hu ua T-cells. T-cells pab koj lub cev tawm tsam kev kis kab mob. Hauv Thymic Aplasia , koj lub qog thymus tsis loj hlob. Thaum koj yug los tsis muaj qog thymus, koj yuav muaj feem kis kab mob ntau dua.
Qhov tsis muaj cov qog thymus yog ib qho ntawm cov tsos mob ntawm tus mob hu ua DiGeorge Syndrome . DiGeorge Syndrome tuaj yeem cuam tshuam rau ntau lub cev. Nws tuaj yeem cuam tshuam rau koj lub cev tiv thaiv kab mob thiab lub plawv ua haujlwm, thiab tseem tuaj yeem ua rau kev loj hlob qeeb hauv menyuam yaus.
Cia peb kuj paub txog Optic Nerve Aplasia.
(Kev puas tsuaj ntawm cov hlab ntsha ntawm qhov muag)Nws yog qhov poob ntawm ib qho lossis ob lub qhov muag tseem ceeb, suav nrog cov hlab ntsha pom, thaum yug los. Koj cov hlab ntsha pom ua lub luag haujlwm tseem ceeb hauv koj qhov kev pom. Nws yog qhov uas tso cai rau koj lub qhov muag sib txuas lus nrog koj lub hlwb thiab ua cov ntaub ntawv pom. Ua tsaug rau cov hlab ntsha pom, thaum koj lub qhov muag pom tej yam xws li cov duab thiab xim, koj lub hlwb tuaj yeem hloov cov ntaub ntawv ntawd mus rau hauv ib daim duab pom uas nws tuaj yeem nkag siab.
Kab mob Optic Nerve Aplasia tuaj yeem ua rau muaj teeb meem ntawm qhov muag sib txawv, nyob ntawm seb koj tus mob hnyav npaum li cas. Aplasia, ib qho mob uas cuam tshuam rau ob lub qhov muag, kuj tseem tuaj yeem ua rau muaj teeb meem nrog kev loj hlob ntawm lub hlwb.
Aplasia feem ntau tshwm sim li cas?
Aplasia yog ib yam mob tsis tshua muaj . Cov hom mob feem ntau yog `(Radial Aplasia)` thiab hom mob uas tau txais los ntawm ``Pure Red Cell Aplasia`` (PRCA). `(Radial Aplasia)` cuam tshuam txog li 1 ntawm 30,000 tus menyuam mos. `(Radial Ray Deficiencies)` (uas kuj suav nrog `(Radial Aplasia)`) yog qhov mob uas tshwm sim los ntawm tes uas tshwm sim los ntawm tes. Hom mob uas tshwm sim los ntawm tes (PRCA) kuj tsis tshua muaj, nrog rau kwv yees li ntawm 5 txog 7 tus neeg mob hauv ib lab tus menyuam yug. Hom mob uas tau txais los ntawm tes no feem ntau tshwm sim ntau dua me ntsis, tab sis peb tsis paub meej tias muaj pes tsawg tus neeg mob.
Dab tsi yog cov ua rau aplasia?
Muaj ntau hom aplasia yog tshwm sim los ntawm kev hloov pauv caj ces, uas tau txais los ntawm niam txiv. Koj cov noob caj ces muaj cov lus qhia uas txiav txim siab seb koj yuav muaj cov yam ntxwv ntawm lub cev li cas. Piv txwv li, cov lus qhia no txiav txim siab qhov twg thiab yuav ua li cas ib lub cev yuav loj hlob. Koj tau txais cov noob caj ces los ntawm koj niam thiab koj txiv. Yog tias ib lub noob caj ces muaj kev hloov pauv, lossis qhov tsis zoo, koj tuaj yeem tsim teeb meem zoo li aplasia.
Tsis tshua muaj, aplasia tuaj yeem tsim tau raws sijhawm. Piv txwv li, acquired PRCA yog tshwm sim los ntawm lwm yam ua rau thiab mob, suav nrog kev kis kab mob, autoimmune kab mob, thiab qee hom mob qog noj ntshav.
Muaj tej lub sij hawm, cov kws kho mob thiab cov kws tshawb fawb nrhiav tsis tau qhov ua rau muaj aplasia. Cov hom aplasia no hu ua idiopathic .
Yuav paub li cas (Aplasia)?
Qee hom aplasia tuaj yeem kuaj pom thaum cev xeeb tub los ntawm kev kuaj mob, xws li kev ntsuas ultrasound. Lwm hom aplasia tsis pom sab nraud thiab tsuas yog pom tseeb thaum yug los xwb.
Yog tias qhov mob tsis hnyav heev, lossis yog tias nws cuam tshuam nrog cov ntshav thiab pob txha, cov tsos mob yuav tsis tshwm sim txog thaum kawg ntawm lub neej. Nyob ntawm seb hom aplasia, koj yuav tsum tau ua ntau yam kev kuaj duab, kev kuaj ntshav, thiab kev kuaj noob caj noob ces kom kuaj tau koj tus mob.
Cov kev kho mob rau (Aplasia) yog dab tsi?
Cov kev xaiv kho mob sib txawv nyob ntawm koj tus mob. Kev phais yuav ua tau los txhim kho kev ua haujlwm ntawm ib txhais ceg lossis caj npab uas tsis loj hlob. Hauv cov xwm txheej hnyav ntawm PRCA, kev hloov ntshav yuav tsum tau ua. Nyob ntawm koj tus mob, cov tshuaj yuav raug muab los tswj cov tsos mob lossis tiv thaiv cov teeb meem ntawm aplasia.
Qee hom aplasia, xws li germ cell aplasia, tsis tuaj yeem kho tau.
Puas kho tau aplasia?
Seb koj tus mob yuav zoo dua lossis tsis zoo dua nyob ntawm hom aplasia uas koj muaj thiab cov yam uas ua rau nws. Piv txwv li, acquired pure red cell aplasia (PRCA) tuaj yeem kho tau, nyob ntawm seb dab tsi tiv thaiv koj lub cev los ntawm kev tsim cov qe ntshav liab. Kev kho tus mob hauv qab uas tiv thaiv kev tsim cov qe ntshav liab qee zaum tuaj yeem txhim kho aplasia.
Aplasia yog ib yam mob uas muaj txij thaum yug los uas tsis tuaj yeem kho tau, txhais tau tias nws tsis tuaj yeem kho tau tag nrho. Hauv cov xwm txheej zoo li no, tus kws kho mob yuav pom zoo kom phais, noj tshuaj, lossis kev kho mob tshwj xeeb. Cov no tuaj yeem pab txhim kho kev ua haujlwm ntawm caj npab, ceg, lossis ceg tawv, lossis tswj cov tsos mob.
Lo lus "(Aplasia)" muaj ntau lub ntsiab lus sib txawv. Nws nyob ntawm ntau yam, suav nrog qhov twg ntawm lub cev nws cuam tshuam, koj cov tsos mob yog dab tsi, thiab qhov mob tsis hnyav lossis hnyav npaum li cas. Tsis txhob yuam kev los ntawm cov lus no. Yog tias koj lossis koj tus menyuam qhov mob tau piav qhia los ntawm lwm lo lus zoo li "(Aplasia)," "(Agenesis)," lossis ib yam dab tsi zoo sib xws, nug koj tus kws kho mob seb cov lus ntawd txhais li cas thiab yuav xav li cas dhau sijhawm. Nug seb puas muaj kev kho mob thiab yog tias lawv xav tau. Yog tias muaj, tham txog hom kev kho mob twg yuav pab tau. Nug seb cov teeb meem kev loj hlob no cuam tshuam li cas (lossis tsis cuam tshuam) koj lub neej txhua hnub.
Tej yam tseem ceeb tshaj plaws uas peb yuav tsum nco ntsoov
Zoo, yog li, kuv vam tias koj muaj qee lub tswv yim los ntawm qhov peb tau tham txog (Aplasia). Hauv ntej:
- Aplasia txhais tau hais tias ib feem ntawm lub cev tsis tau loj hlob zoo.
- Qhov no tsis yog tib yam kab mob, nws tuaj yeem muaj ntau hom thiab ntau theem sib txawv .
- Qee hom aplasia yog yug los, thaum lwm tus tshwm sim thaum lub neej.
- Cov ua rau muaj ntau yam; cov ua rau los ntawm noob caj noob ces, kev kis kab mob, lwm yam kab mob, thiab qee zaum tsis muaj qhov ua rau.
- Kev kho mob nyob ntawm seb hom thiab qhov hnyav ntawm aplasia. Qee tus yuav xav tau phais, tshuaj, lossis lwm yam kev kho mob tshwj xeeb los tswj cov tsos mob thiab txhim kho lub neej zoo.
- Txawm hais tias tus kab mob aplasia uas muaj txij thaum yug los tsis tuaj yeem kho tau tag nrho, yog tias muaj kev tswj hwm thiab kev txhawb nqa zoo, nws muaj peev xwm ua neej nyob ib txwm muaj.
- Qhov tseem ceeb tshaj plaws yog mus ntsib kws kho mob thiab tau txais cov lus qhia thiab cov ntaub ntawv zoo yog tias koj lossis koj tus menyuam muaj kev xav txog qhov mob no.Tsis txhob ntshai, nug cov lus nug, thiab nkag siab qhov xwm txheej kom zoo.
Peb vam tias koj pom cov ntaub ntawv no muaj txiaj ntsig!
` Aplasia, Tsis loj hlob ntawm cov khoom ntawm lub cev, Cov teeb meem txij thaum yug los, Pure Red Cell Aplasia, Aplasia Cutis Congenita, Radial Aplasia, Germ Cell Aplasia











💬 Comments (0)
Tsis muaj lus teb tau muab tso tawm. Ntxiv koj cov lus tawm ntawm no thawj zaug.
Ntxiv koj cov lus