Skip to main content

Peb puas yuav tham txog ib yam kab mob tsis tshua muaj hu ua C3G (Complement 3 Glomerulopathy), uas cuam tshuam rau lub raum?

Peb puas yuav tham txog ib yam kab mob tsis tshua muaj hu ua C3G (Complement 3 Glomerulopathy), uas cuam tshuam rau lub raum?

Koj puas muaj tej lub sij hawm koj muaj ntshav hauv koj cov zis, lossis o ntawm koj ob txhais ceg? Los yog koj puas nkees tas li? Tej zaum tej zaum cov no yog vim muaj teeb meem nrog koj lub raum. Hnub no peb yuav tham txog ib qho mob uas tsis tshua muaj tab sis tseem ceeb heev uas cuam tshuam rau lub raum. Qhov ntawd yog C3G (C Peb G) lossis "Complement 3 Glomerulopathy"

C3G (Complement 3 Glomerulopathy) yog dab tsi?

Hais yooj yim xwb, C3G yog ib pawg kab mob uas cuam tshuam rau koj lub raum ua haujlwm zoo li cas. Koj paub, lub raum zoo li ob lub lim dej hauv peb lub cev. Lawv txoj haujlwm tseem ceeb yog lim cov ntshav, tshem tawm cov khoom pov tseg tsis tsim nyog thiab dej ntau dhau, thiab ua zis.

"Complement 3" yog ib qho protein tshwj xeeb hauv peb cov ntshav. Nws tseem ceeb heev rau lub cev tiv thaiv kab mob uas tawm tsam cov kab mob hauv peb lub cev. "Glomerulopathy" yog kev puas tsuaj rau glomeruli, uas yog cov hlab ntsha me me hauv lub raum, uas zoo li cov meshes me me. Cov glomeruli no yog cov uas lim cov ntshav.

Ces C3G yog ib yam kab mob uas muaj cov protein "complement 3", ua rau lub "glomeruli" puas tsuaj thiab ua rau lub raum tsis ua haujlwm zoo. Yav dhau los, ua ntej xyoo 2013, cov kws kho mob hu qhov no ua "Membranoproliferative glomerulonephritis (MPGN) hom I, II lossis III" lossis "Mesangioproliferative glomerulonephritis". Tab sis tam sim no pawg kab mob no hu ua C3G.

Puas muaj hom C3G?

Yog, muaj ob hom C3G tseem ceeb. Cov kws kho mob txiav txim siab ob hom no los ntawm kev muab ib daim me me ntawm lub raum (peb hu ua 'kidney biopsy ') thiab saib nws hauv qab lub tshuab microscope, raws li qhov puas tsuaj thiab o ntawm 'glomeruli'.

  • Kab mob pob zeb ntom ntom (DDD): Yav tas los hu ua MPGN hom II, tus mob no yog tus yam ntxwv los ntawm kev tsim cov pob zeb ntom ntom, zoo li daim kab xev hauv daim nyias nyias glomerular basement (GBM), uas yog daim ntaub ntawm glomeruli. Feem ntau nws cuam tshuam rau cov menyuam yaus thiab cov tub ntxhais hluas hnub nyoog 20 xyoo.
  • `C3 glomerulonephritis` (C3GN): Yav tas los hu ua `MPGN hom I` lossis `III`. Hauv qhov no, cov pob zeb ntom ntom zoo li cov uas pom hauv DDD tsis pom. Qhov no feem ntau cuam tshuam rau cov neeg hnub nyoog tshaj 30 xyoo.

C3G puas yog ib qho kab mob ntev?

Yog, C3G yog ib yam kab mob ntev. Qhov no txhais tau tias nws tsis yog ib yam dab tsi uas yuav tshwm sim sai sai thiab zoo dua, thiab kev puas tsuaj rau lub raum tuaj yeem nce ntxiv raws sijhawm. Yog li ntawd, nws yog ib qho tseem ceeb heev uas yuav tsum ceev faj txog qhov no.

C3G no muaj pes tsawg leej neeg siv?

Qhov no yeej yog ib yam kab mob uas tsis tshua muaj.Cov kws kho mob kwv yees tias qhov no tshwm sim rau kwv yees li ob mus rau peb tus neeg ntawm ib puas txhiab tus neeg. Yog li ntawd, tej zaum koj yuav tsis tau hnov ​​​​​​ntau txog nws. Tab sis txawm tias nws tsis tshua muaj, nws yog ib qho tseem ceeb uas yuav tsum paub txog nws.

Cov tsos mob ntawm tus kab mob C3G yog dab tsi?

Tam sim no cia peb saib seb cov tsos mob ntawm tus kab mob C3G no yog dab tsi. Ob hom kab mob no muaj ntau yam zoo sib xws, uas yog ib qho tseem ceeb uas yuav tsum paub txog:

  • Ntshav nyob rau hauv cov zis ( hematuria ): Qee zaum cov zis yuav zoo li liab, lossis nws yuav yog ib qho me me uas tsuas pom tau hauv qab lub tshuab microscope xwb.
  • Muaj protein ntau dhau hauv cov zis (proteinuria): Qhov no tuaj yeem ua rau cov zis zoo li ua npuas ncauj.
  • Tso zis tsawg dua li qub (oliguria).
  • Cov protein hauv cov ntshav tsawg dua (hypoalbuminemia).
  • O (edema): Tshwj xeeb tshaj yog nyob rau hauv tes, pob luj taws, thiab taw. Xav txog, yog tias koj sawv thaum sawv ntxov thiab koj txhais taw o, nws yuav yog ib yam dab tsi zoo li no.
  • Ntshav siab (ntshav siab).
  • Cov kab mob rov tshwm sim.
  • Xav tias nkees heev ('Qaug zog'): Tsis yog tsuas yog nkees xwb, tab sis kuj xav tias qaug zog txawm tias koj pw tsaug zog npaum li cas los xij.
  • Ib txhia neeg yuav muaj mob xws li gout .

Ob qho tsos mob no tuaj yeem ua rau lub raum tsis ua haujlwm . Lub raum tsis ua haujlwm kuj tseem tuaj yeem ua rau muaj cov tsos mob xws li:

  • Ib txwm nkees.
  • Xeev siab, ntuav.
  • Nyuaj siab txiav txim siab, poob siab tag nrho.
  • Lub cev o.
  • Tso zis ntau dua li niaj zaus (qee zaum qhov no tuaj yeem pom thaum ntxov ntawm kev ua tsis tau haujlwm ntawm lub raum).

Ntxiv rau lub raum, C3G kuj tseem tuaj yeem ua rau muaj lwm yam tsos mob. Cov no suav nrog:

  • Teeb Meem Pom Kev: Kev pom kev tsis zoo tuaj yeem tshwm sim vim muaj cov protein thiab calcium sib sau ua ke (drusen), tshwj xeeb tshaj yog nyob rau hauv macula.
  • Lipodystrophy: Qhov no yog ib qho mob uas cov rog poob rau qee qhov chaw ntawm lub cev (tshwj xeeb tshaj yog lub ntsej muag thiab ceg).

Vim li cas C3G no thiaj tsim los?

Zoo, tam sim no cia peb saib vim li cas C3G no thiaj li tsim. Qhov no nyuaj me ntsis, tab sis kuv yuav piav qhia yooj yim. Qhov no tshwm sim thaum "lub cev sib txuas" hauv peb lub cev tsis ua haujlwm zoo. Lub "tshuab sib txuas" no yog cov protein sib sau ua ke hauv peb cov ntshav. Qhov no yog ib feem ntawm peb lub cev tiv thaiv kab mob. Qhov no pab tawm tsam cov kab mob xws li cov kab mob thiab cov kab mob uas los ntawm sab nraud.

Qhov uas tshwm sim rau ib tug neeg uas muaj C3G yog tias lub 'complement system' no ua haujlwm ntau dhau, lossis tsis tswj tau. Tom qab ntawd cov protein 'complement 3 (C3)' raug puas tsuaj. Cov protein C3 uas puas tsuaj no tau daig hauv 'glomeruli'. Tom qab ntawd nws nyuaj rau 'glomeruli' lim ntshav thiab ua zis. Yog tias tsis kho, qhov kev puas tsuaj no tuaj yeem txuas ntxiv mus thiab ua rau lub raum tsis ua haujlwm.

Feem ntau, nws nyuaj rau txheeb xyuas qhov laj thawj tseeb vim li cas "kev qhuas" no thiaj li tsis ua haujlwm. Tab sis qee zaum:

  • C3G tuaj yeem tshwm sim vim muaj kev hloov pauv hauv peb cov noob caj noob ces (kev hloov pauv hauv cov noob caj noob ces uas cuam tshuam nrog lub kaw lus sib txuas, xws li "C3" thiab "CFH").
  • Ib yam kab mob ntshav hu ua "Monoclonal gammopathy" kuj tseem tuaj yeem ua rau lub raum puas tsuaj, cuam tshuam kev ua haujlwm ntawm "complement" system, thiab ua rau muaj C3G. Qhov "monoclonal gammopathy" no yog ib yam mob uas cuam tshuam rau cov hlwb plasma hauv peb cov pob txha.
  • Cov kws tshawb fawb kho mob xav tias qee yam hu ua "autoantibodies" kuj tseem yuav ua lub luag haujlwm. "Autoantibodies" yog cov protein uas peb lub cev tiv thaiv kab mob tsim tawm uas ua yuam kev tawm tsam peb cov nqaij noj qab haus huv. Txawm li cas los xij, tsis muaj kev tshawb fawb txaus los hais qhov tseeb tias cov "autoantibodies" no yog qhov ua rau C3G.

Leej twg raug kev txom nyem tshaj plaws los ntawm tus kab mob C3G no?

Tus kab mob C3G no tuaj yeem tshwm sim rau txhua tus neeg. Nws cuam tshuam rau txiv neej thiab poj niam sib npaug. Lub hnub nyoog nruab nrab uas kuaj pom yog li ntawm 23 xyoos. Txawm li cas los xij, hom 'DDD' uas peb tau hais ua ntej tuaj yeem tshwm sim thaum muaj hnub nyoog hluas dua li hom 'C3GN'.

Cov teeb meem uas yuav tshwm sim ntawm C3G yog dab tsi?

Qhov teeb meem loj tshaj plaws thiab txaus ntshai tshaj plaws yog tias kwv yees li 50% ntawm cov neeg uas muaj C3G, lossis ib ntawm ob tug, yuav muaj mob raum tsis ua haujlwm hauv 10 xyoo tom qab kuaj pom. Qhov no yog qhov peb txhua tus yuav tsum ntshai tshaj plaws.

Yuav kuaj mob C3G li cas?

Tus kws kho mob yuav ua ntau yam kev kuaj mob los xyuas seb koj lub raum puas noj qab haus huv thiab seb lawv ua haujlwm zoo li cas. Tej zaum yuav muaj xws li:

  • Kev kuaj ntshav: Yuav muab ib qho ntshav me me los ntawm cov leeg ntshav hauv koj txhais caj npab thiab lub chaw kuaj mob yuav kuaj seb koj cov protein puas zoo li qub lossis puas muaj cov khoom pov tseg ntau dhau (piv txwv li creatinine) hauv koj cov ntshav.
  • `Kwv yees li ntawm Glomerular Filtration Rate (eGFR): Qhov no yog ib qho kev xeem uas ntsuas seb koj lub raum lim koj cov ntshav zoo npaum li cas, raws li qhov ntau ntawm `serum creatinine` lossis `cystatin C` hauv cov qauv ntshav. Qhov no tuaj yeem muab lub tswv yim zoo rau koj txog seb koj lub raum ua haujlwm zoo npaum li cas.
  • Kev Kuaj Zis: Koj yuav tsum tau tso zis rau hauv ib lub khob tshwj xeeb thiab muab cov qauv rau koj tus kws kho mob. Lub chaw kuaj mob yuav kuaj seb puas muaj protein lossis ntshav nyob hauv cov zis, uas tsuas pom tau hauv qab lub tshuab microscope xwb.
  • Biopsy ntawm lub raum: qhov no yog dab tsiTxoj kev zoo tshaj plaws los kuaj mob C3G yog los ntawm kev kuaj nqaij. Hauv qhov no, tus kws kho mob yuav siv ib daim nqaij me me los ntawm koj lub raum los ntawm kev siv ib rab koob me me lossis ib qho me me thiab kuaj nws hauv chav kuaj. Yog tias cov qauv no muaj cov protein C3 uas puas lawm hauv koj lub glomeruli, nws yuav yog kab mob C3G. Daim biopsy no kuj tseem tuaj yeem qhia koj tias koj muaj hom C3G twg (DDD lossis C3GN), raws li seb koj puas muaj cov khoom khov kho ntawd.

Puas kho tau C3G kom zoo tag nrho?

Tu siab kawg li, tam sim no tsis muaj tshuaj kho tau tus kab mob C3G no. Tiam sis tsis txhob txhawj, cov kws kho mob thiab cov kws tshawb fawb tseem tab tom kawm txog tus kab mob no thiab tab tom nrhiav kev kho mob tshiab. Peb vam tias yuav muaj kev kho mob zoo dua yav tom ntej.

Cov kev kho mob rau C3G yog dab tsi?

Tam sim no tsis muaj kev kho mob tshwj xeeb uas tau pom zoo los ntawm US Food and Drug Administration (FDA) rau C3G. Txawm li cas los xij, cov kws kho mob tuaj yeem sau ntau yam kev kho mob thiab kev txhawb nqa kom qeeb qeeb qhov kev loj hlob ntawm C3G, tswj cov tsos mob, thiab txo qhov kev puas tsuaj rau lub raum. Cov no suav nrog:

  • Cov tshuaj kho ntshav siab: Cov tshuaj xws li angiotensin-converting enzyme (ACE) inhibitors thiab angiotensin II receptor blockers (ARBs) txo qhov siab hauv glomeruli. Qhov no txo ​​cov protein hauv cov zis thiab txo qhov kev nyuaj siab rau lub raum.
  • Cov tshuaj txo cov roj cholesterol: Koj tus kws kho mob yuav sau ntawv rau cov tshuaj xws li statins kom txo cov roj cholesterol thiab txo qhov kev puas tsuaj rau koj lub raum.
  • Kev hloov pauv zaub mov: Tus kws kho mob raum yuav pab koj tsim ib txoj kev npaj zaub mov uas haum rau koj thiab pab koj tswj koj qhov hnyav kom noj qab nyob zoo. Kev txo koj cov ntsev (sodium), roj saturated, thiab cholesterol tuaj yeem pab txo qhov kev puas tsuaj raum.
  • Corticosteroids: Kuj hu ua "steroids," cov no yog cov tshuaj tiv thaiv kev o uas ua haujlwm los ntawm kev tiv thaiv lub cev tiv thaiv kab mob kom tsis txhob tawm tsam koj lub glomeruli.
  • Eculizumab: Qhov no yog ib hom tshuaj monoclonal antibody siv los kho cov kab mob ntshav tsawg tsawg. Nws yuav pab txhim kho kev ua haujlwm ntawm lub raum los ntawm kev txo cov protein hauv cov zis thiab ua kom glomerular filtration rate nce ntxiv rau qee tus neeg mob C3G.
  • Kev ntxuav ntshav: Kwv yees li 50% ntawm cov neeg uas muaj C3G tau hais tias muaj kev ua tsis tau haujlwm ntawm lub raum. Kev ntxuav ntshav yog thaum lub raum tsis ua haujlwm, thiab txoj haujlwm uas lub raum yuav tsum ua (ntxuav cov ntshav, tshem tawm cov khoom pov tseg, thiab cov kua dej ntau dhau) yog ua tiav nrog kev pab los ntawm lub tshuab.
  • Kev hloov raum: Qhov no yog lwm txoj kev kho mob rau kev ua tsis tau haujlwm raum. Tus kws phais yuav muab koj lub raum uas tsis ua haujlwm tshem tawm thiab muab lub raum noj qab haus huv los ntawm tus neeg pub hloov raum.

Yog tias koj muaj 'DDD' lossis 'C3GN' thiab kuj muaj 'monoclonal gammopathy', koj tus kws kho mob yuav pom zoo kom kuaj ntxiv kom paub seb puas muaj lwm yam mob.

Yuav ua li cas thiaj paub tias tus kab mob C3G yuav zoo li cas?

Kwv yees li ib nrab ntawm cov neeg mob uas muaj C3G yuav mob raum tsis ua haujlwm li ntawm 10 xyoo tom qab kuaj pom. Tam sim no tsis muaj tshuaj kho tau rau mob raum tsis ua haujlwm. Txawm li cas los xij, nrog kev kuaj mob kom raug thiab kev kho mob sai, koj tuaj yeem ua neej ntev thiab noj qab nyob zoo yam tsis muaj kev hloov pauv loj. Yog li ntawd, nws yog ib qho tseem ceeb kom nyob twj ywm thiab ua raws li koj tus kws kho mob cov lus qhia.

Kab mob C3G puas tiv thaiv tau?

Tu siab kawg li, tam sim no tsis muaj txoj hauv kev los tiv thaiv kab mob C3G, vim nws feem ntau yog los ntawm tej yam uas peb tswj tsis tau.

Kuv yuav saib xyuas kuv tus kheej li cas?

Yog koj muaj C3G, koj tus kws kho mob yuav tsim txoj kev kho mob zoo tshaj plaws rau koj. Qhov no yuav suav nrog kev siv tshuaj, kev txhawb nqa, thiab kev hloov pauv hauv koj txoj kev ua neej. Koj txoj kev npaj kho mob yuav suav nrog cov hauv qab no, thiab nws yog ib qho tseem ceeb uas yuav tsum ua raws li cov kauj ruam no kom zoo:

  • Noj koj cov tshuaj raws li koj tus kws kho mob tau hais. Tsis txhob ncua ib hnub li.
  • Hloov koj cov zaub mov noj, tshwj xeeb tshaj yog txo cov ntsev, roj, thiab qab zib, thiab noj ntau txiv hmab txiv ntoo thiab zaub.
  • Tsis txhob siv cov tshuaj non-steroidal anti-inflammatory drugs (NSAIDs) (piv txwv li, cov tshuaj tua kab mob xws li ibuprofen thiab diclofenac) yam tsis tau kev qhia los ntawm kws kho mob, vim tias lawv tuaj yeem ua rau lub raum puas tsuaj thiab ua rau lub raum tsis ua haujlwm sai dua.
  • Kev saib xyuas koj txoj kev noj qab haus huv ntawm lub hlwb. Muaj tus kab mob tsis tshua muaj no ua rau koj xav tias kho siab thiab ntshai. Tsis tas li ntawd, kev paub tias C3G tuaj yeem ua rau lub raum tsis ua haujlwm ua rau koj muaj feem yuav muaj kev nyuaj siab. Tham nrog koj tus kws kho mob txog koj txoj kev noj qab haus huv ntawm lub hlwb thiab nrhiav kev sab laj thiab kev kho mob yog tias tsim nyog. Nug koj tus kws kho mob txog cov pab pawg txhawb nqa rau cov neeg uas muaj C3G. Kev ntsib lwm tus neeg uas muaj C3G tuaj yeem pab txo kev kho siab thiab sib qhia cov kev paub dhau los.

Kuv yuav tsum mus ntsib kws kho mob thaum twg?

Yog tias koj muaj cov tsos mob ntawm C3G, tshwj xeeb tshaj yog kev hloov pauv hauv koj cov zis (ntshav, ua npuas dej, tsawg dua), o, lossis qaug zog heev, mus ntsib kws kho mob tam sim ntawd. Cov no yuav yog cov cim qhia tias koj lub raum tsis ua haujlwm zoo.

Yog koj kuaj pom tias koj muaj C3G, koj tus kws kho mob yuav xa koj mus rau tus kws kho mob tshwj xeeb hauv kev mob raum (tus kws kho mob nephrologist). Nws yuav yog tus uas yuav muab txoj kev kho mob zoo tshaj plaws rau koj.

Kuv yuav tsum nug kuv tus kws kho mob li cas?

Thaum koj mus ntsib kws kho mob, tsis txhob yig nug cov lus nug zoo li no:

  • Kuv yuav paub tseeb li cas yog tias kuv muaj C3G?
  • Yog tias kuv tsis muaj C3G, kuv yuav muaj lwm yam kab mob dab tsi ntxiv?
  • Kuv muaj hom C3G twg (DDD lossis C3GN)?
  • Koj xav kom kuv kho li cas? Puas muaj tej yam tshwm sim tsis zoo?
  • Kuv yuav tsum hloov dab tsi rau kuv cov zaub mov noj?
  • Koj puas xav tias kuv ob lub raum yuav tsis ua haujlwm? Kuv yuav ua li cas thiaj li tiv thaiv tau qhov ntawd kom tsis txhob tshwm sim?
  • Kuv puas mus ntsib kws kho mob nephrologist tau?

Thaum kawg, kuv yuav tsum hais tias ...

C3G yog ib yam kab mob uas tsis tshua muaj thiab nyuaj heev uas cuam tshuam rau cov chav lim dej me me hauv lub raum. Yog tias koj muaj C3G, koj yuav muaj kev hloov pauv hauv koj cov zis, o, mob pob qij txha, teeb meem pom kev, thiab qaug zog.

Tej zaum koj yuav muaj ntau yam kev xav thaum koj lees txais qhov kev kuaj mob no thiab hloov kho rau C3G yuav cuam tshuam li cas rau koj lub neej. Tsis txhob txhawj, koj tsis nyob ib leeg. Muab sijhawm thiab qhov chaw rau koj tus kheej kom kawm txog C3G thiab koj cov kev xaiv kho mob. Kev kawm txog koj cov kev xaiv thiab yam uas yuav tshwm sim tuaj yeem pab koj daws koj txoj kev xav hauv txoj kev noj qab haus huv thiab muaj txiaj ntsig. Cov kws kho mob nyob ntawd los muab cov ntaub ntawv thiab kev taw qhia. Yog tias koj muaj lus nug, xav tau lus qhia lossis kev txhawb nqa, tham nrog lawv. Nco ntsoov, nrog kev kuaj mob thaum ntxov thiab kev kho mob kom zoo, koj tuaj yeem tswj tau tus kab mob no thiab ua neej zoo.

👩🏽‍⚕️ Cov Lus Nug Ntxiv (FAQs)

💬 C3G (Complement 3 Glomerulopathy) yog hom kab mob raum twg?

Qhov no yog ib qho kab mob raum uas tsis tshua muaj thiab txawv txawv! Peb lub cev muaj ib qho protein tshwj xeeb hu ua 'Complement C3' los tua cov kab mob. Txawm li cas los xij, hauv tus kab mob no, vim muaj qhov tsis zoo ntawm peb lub cev (Autoimmune), cov protein C3 ntawd tawm tsam lub cev nws tus kheej, thiab cov protein ntawd tau tso rau hauv cov lim dej zoo heev (Glomeruli) ntawm lub raum, ua rau lub raum tsis ua haujlwm tag nrho.

💬 Cov tsos mob ntawm ib tus neeg uas muaj tus kab mob txaus ntshai no yog dab tsi?

Thaum lub lim dej ntawm lub raum (cov qauv) raug puas tsuaj, lawv cov zis cia li pib liab (ntshav-Hematuria) thiab ua npuas (protein-Proteinuria). Vim tias lub raum tsis tshem dej tawm ntawm lub cev, ob txhais ceg thiab ib ncig ntawm lub qhov muag o (Edema). Nrog rau qhov no, ntshav siab (Siab siab) kuj tshwm sim.

💬 Puas muaj tshuaj kho mob niaj hnub no los kho tus kab mob no?

Tsis muaj ib txoj kev kho tau qhov no kiag li. Qhov tseem ceeb tshaj plaws yog kom tsis txhob muaj cov protein no tawm tsam, muab cov tshuaj uas ua rau lub cev tiv thaiv kab mob tsis muaj zog (Immunosuppressants thiab Steroids). Tsis tas li ntawd, lawv muab cov tshuaj txo ntshav siab (ACE inhibitors). Yog tias tus kab mob hnyav heev, yuav tsum tau ntxuav ntshav thiab hloov raum.


C3G , kab mob raum, complement 3, glomerulopathy, ua tsis tau haujlwm raum, cov protein hauv zis, kev ntxuav ntshav

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

💬 Comments (0)

Tsis muaj lus teb tau muab tso tawm. Ntxiv koj cov lus tawm ntawm no thawj zaug.

Ntxiv koj cov lus

Thov xam: 9 + 5 =
Peb puas yuav tham txog ib yam kab mob tsis tshua muaj hu ua C3G (Complement 3 Glomerulopathy), uas cuam tshuam rau lub raum?

Peb puas yuav tham txog ib yam kab mob tsis tshua muaj hu ua C3G (Complement 3 Glomerulopathy), uas cuam tshuam rau lub raum?

Koj puas muaj tej lub sij hawm koj muaj ntshav hauv koj cov zis, lossis o ntawm koj ob txhais ceg? Los yog koj puas nkees tas li? Tej zaum tej zaum cov no yog vim muaj teeb meem nrog koj lub raum. Hnub no peb yuav tham txog ib qho mob uas tsis tshua muaj tab sis tseem ceeb heev uas cuam tshuam rau lub raum. Qhov ntawd yog C3G (C Peb G) lossis "Complement 3 Glomerulopathy"

C3G (Complement 3 Glomerulopathy) yog dab tsi?

Hais yooj yim xwb, C3G yog ib pawg kab mob uas cuam tshuam rau koj lub raum ua haujlwm zoo li cas. Koj paub, lub raum zoo li ob lub lim dej hauv peb lub cev. Lawv txoj haujlwm tseem ceeb yog lim cov ntshav, tshem tawm cov khoom pov tseg tsis tsim nyog thiab dej ntau dhau, thiab ua zis.

"Complement 3" yog ib qho protein tshwj xeeb hauv peb cov ntshav. Nws tseem ceeb heev rau lub cev tiv thaiv kab mob uas tawm tsam cov kab mob hauv peb lub cev. "Glomerulopathy" yog kev puas tsuaj rau glomeruli, uas yog cov hlab ntsha me me hauv lub raum, uas zoo li cov meshes me me. Cov glomeruli no yog cov uas lim cov ntshav.

Ces C3G yog ib yam kab mob uas muaj cov protein "complement 3", ua rau lub "glomeruli" puas tsuaj thiab ua rau lub raum tsis ua haujlwm zoo. Yav dhau los, ua ntej xyoo 2013, cov kws kho mob hu qhov no ua "Membranoproliferative glomerulonephritis (MPGN) hom I, II lossis III" lossis "Mesangioproliferative glomerulonephritis". Tab sis tam sim no pawg kab mob no hu ua C3G.

Puas muaj hom C3G?

Yog, muaj ob hom C3G tseem ceeb. Cov kws kho mob txiav txim siab ob hom no los ntawm kev muab ib daim me me ntawm lub raum (peb hu ua 'kidney biopsy ') thiab saib nws hauv qab lub tshuab microscope, raws li qhov puas tsuaj thiab o ntawm 'glomeruli'.

  • Kab mob pob zeb ntom ntom (DDD): Yav tas los hu ua MPGN hom II, tus mob no yog tus yam ntxwv los ntawm kev tsim cov pob zeb ntom ntom, zoo li daim kab xev hauv daim nyias nyias glomerular basement (GBM), uas yog daim ntaub ntawm glomeruli. Feem ntau nws cuam tshuam rau cov menyuam yaus thiab cov tub ntxhais hluas hnub nyoog 20 xyoo.
  • `C3 glomerulonephritis` (C3GN): Yav tas los hu ua `MPGN hom I` lossis `III`. Hauv qhov no, cov pob zeb ntom ntom zoo li cov uas pom hauv DDD tsis pom. Qhov no feem ntau cuam tshuam rau cov neeg hnub nyoog tshaj 30 xyoo.

C3G puas yog ib qho kab mob ntev?

Yog, C3G yog ib yam kab mob ntev. Qhov no txhais tau tias nws tsis yog ib yam dab tsi uas yuav tshwm sim sai sai thiab zoo dua, thiab kev puas tsuaj rau lub raum tuaj yeem nce ntxiv raws sijhawm. Yog li ntawd, nws yog ib qho tseem ceeb heev uas yuav tsum ceev faj txog qhov no.

C3G no muaj pes tsawg leej neeg siv?

Qhov no yeej yog ib yam kab mob uas tsis tshua muaj.Cov kws kho mob kwv yees tias qhov no tshwm sim rau kwv yees li ob mus rau peb tus neeg ntawm ib puas txhiab tus neeg. Yog li ntawd, tej zaum koj yuav tsis tau hnov ​​​​​​ntau txog nws. Tab sis txawm tias nws tsis tshua muaj, nws yog ib qho tseem ceeb uas yuav tsum paub txog nws.

Cov tsos mob ntawm tus kab mob C3G yog dab tsi?

Tam sim no cia peb saib seb cov tsos mob ntawm tus kab mob C3G no yog dab tsi. Ob hom kab mob no muaj ntau yam zoo sib xws, uas yog ib qho tseem ceeb uas yuav tsum paub txog:

  • Ntshav nyob rau hauv cov zis ( hematuria ): Qee zaum cov zis yuav zoo li liab, lossis nws yuav yog ib qho me me uas tsuas pom tau hauv qab lub tshuab microscope xwb.
  • Muaj protein ntau dhau hauv cov zis (proteinuria): Qhov no tuaj yeem ua rau cov zis zoo li ua npuas ncauj.
  • Tso zis tsawg dua li qub (oliguria).
  • Cov protein hauv cov ntshav tsawg dua (hypoalbuminemia).
  • O (edema): Tshwj xeeb tshaj yog nyob rau hauv tes, pob luj taws, thiab taw. Xav txog, yog tias koj sawv thaum sawv ntxov thiab koj txhais taw o, nws yuav yog ib yam dab tsi zoo li no.
  • Ntshav siab (ntshav siab).
  • Cov kab mob rov tshwm sim.
  • Xav tias nkees heev ('Qaug zog'): Tsis yog tsuas yog nkees xwb, tab sis kuj xav tias qaug zog txawm tias koj pw tsaug zog npaum li cas los xij.
  • Ib txhia neeg yuav muaj mob xws li gout .

Ob qho tsos mob no tuaj yeem ua rau lub raum tsis ua haujlwm . Lub raum tsis ua haujlwm kuj tseem tuaj yeem ua rau muaj cov tsos mob xws li:

  • Ib txwm nkees.
  • Xeev siab, ntuav.
  • Nyuaj siab txiav txim siab, poob siab tag nrho.
  • Lub cev o.
  • Tso zis ntau dua li niaj zaus (qee zaum qhov no tuaj yeem pom thaum ntxov ntawm kev ua tsis tau haujlwm ntawm lub raum).

Ntxiv rau lub raum, C3G kuj tseem tuaj yeem ua rau muaj lwm yam tsos mob. Cov no suav nrog:

  • Teeb Meem Pom Kev: Kev pom kev tsis zoo tuaj yeem tshwm sim vim muaj cov protein thiab calcium sib sau ua ke (drusen), tshwj xeeb tshaj yog nyob rau hauv macula.
  • Lipodystrophy: Qhov no yog ib qho mob uas cov rog poob rau qee qhov chaw ntawm lub cev (tshwj xeeb tshaj yog lub ntsej muag thiab ceg).

Vim li cas C3G no thiaj tsim los?

Zoo, tam sim no cia peb saib vim li cas C3G no thiaj li tsim. Qhov no nyuaj me ntsis, tab sis kuv yuav piav qhia yooj yim. Qhov no tshwm sim thaum "lub cev sib txuas" hauv peb lub cev tsis ua haujlwm zoo. Lub "tshuab sib txuas" no yog cov protein sib sau ua ke hauv peb cov ntshav. Qhov no yog ib feem ntawm peb lub cev tiv thaiv kab mob. Qhov no pab tawm tsam cov kab mob xws li cov kab mob thiab cov kab mob uas los ntawm sab nraud.

Qhov uas tshwm sim rau ib tug neeg uas muaj C3G yog tias lub 'complement system' no ua haujlwm ntau dhau, lossis tsis tswj tau. Tom qab ntawd cov protein 'complement 3 (C3)' raug puas tsuaj. Cov protein C3 uas puas tsuaj no tau daig hauv 'glomeruli'. Tom qab ntawd nws nyuaj rau 'glomeruli' lim ntshav thiab ua zis. Yog tias tsis kho, qhov kev puas tsuaj no tuaj yeem txuas ntxiv mus thiab ua rau lub raum tsis ua haujlwm.

Feem ntau, nws nyuaj rau txheeb xyuas qhov laj thawj tseeb vim li cas "kev qhuas" no thiaj li tsis ua haujlwm. Tab sis qee zaum:

  • C3G tuaj yeem tshwm sim vim muaj kev hloov pauv hauv peb cov noob caj noob ces (kev hloov pauv hauv cov noob caj noob ces uas cuam tshuam nrog lub kaw lus sib txuas, xws li "C3" thiab "CFH").
  • Ib yam kab mob ntshav hu ua "Monoclonal gammopathy" kuj tseem tuaj yeem ua rau lub raum puas tsuaj, cuam tshuam kev ua haujlwm ntawm "complement" system, thiab ua rau muaj C3G. Qhov "monoclonal gammopathy" no yog ib yam mob uas cuam tshuam rau cov hlwb plasma hauv peb cov pob txha.
  • Cov kws tshawb fawb kho mob xav tias qee yam hu ua "autoantibodies" kuj tseem yuav ua lub luag haujlwm. "Autoantibodies" yog cov protein uas peb lub cev tiv thaiv kab mob tsim tawm uas ua yuam kev tawm tsam peb cov nqaij noj qab haus huv. Txawm li cas los xij, tsis muaj kev tshawb fawb txaus los hais qhov tseeb tias cov "autoantibodies" no yog qhov ua rau C3G.

Leej twg raug kev txom nyem tshaj plaws los ntawm tus kab mob C3G no?

Tus kab mob C3G no tuaj yeem tshwm sim rau txhua tus neeg. Nws cuam tshuam rau txiv neej thiab poj niam sib npaug. Lub hnub nyoog nruab nrab uas kuaj pom yog li ntawm 23 xyoos. Txawm li cas los xij, hom 'DDD' uas peb tau hais ua ntej tuaj yeem tshwm sim thaum muaj hnub nyoog hluas dua li hom 'C3GN'.

Cov teeb meem uas yuav tshwm sim ntawm C3G yog dab tsi?

Qhov teeb meem loj tshaj plaws thiab txaus ntshai tshaj plaws yog tias kwv yees li 50% ntawm cov neeg uas muaj C3G, lossis ib ntawm ob tug, yuav muaj mob raum tsis ua haujlwm hauv 10 xyoo tom qab kuaj pom. Qhov no yog qhov peb txhua tus yuav tsum ntshai tshaj plaws.

Yuav kuaj mob C3G li cas?

Tus kws kho mob yuav ua ntau yam kev kuaj mob los xyuas seb koj lub raum puas noj qab haus huv thiab seb lawv ua haujlwm zoo li cas. Tej zaum yuav muaj xws li:

  • Kev kuaj ntshav: Yuav muab ib qho ntshav me me los ntawm cov leeg ntshav hauv koj txhais caj npab thiab lub chaw kuaj mob yuav kuaj seb koj cov protein puas zoo li qub lossis puas muaj cov khoom pov tseg ntau dhau (piv txwv li creatinine) hauv koj cov ntshav.
  • `Kwv yees li ntawm Glomerular Filtration Rate (eGFR): Qhov no yog ib qho kev xeem uas ntsuas seb koj lub raum lim koj cov ntshav zoo npaum li cas, raws li qhov ntau ntawm `serum creatinine` lossis `cystatin C` hauv cov qauv ntshav. Qhov no tuaj yeem muab lub tswv yim zoo rau koj txog seb koj lub raum ua haujlwm zoo npaum li cas.
  • Kev Kuaj Zis: Koj yuav tsum tau tso zis rau hauv ib lub khob tshwj xeeb thiab muab cov qauv rau koj tus kws kho mob. Lub chaw kuaj mob yuav kuaj seb puas muaj protein lossis ntshav nyob hauv cov zis, uas tsuas pom tau hauv qab lub tshuab microscope xwb.
  • Biopsy ntawm lub raum: qhov no yog dab tsiTxoj kev zoo tshaj plaws los kuaj mob C3G yog los ntawm kev kuaj nqaij. Hauv qhov no, tus kws kho mob yuav siv ib daim nqaij me me los ntawm koj lub raum los ntawm kev siv ib rab koob me me lossis ib qho me me thiab kuaj nws hauv chav kuaj. Yog tias cov qauv no muaj cov protein C3 uas puas lawm hauv koj lub glomeruli, nws yuav yog kab mob C3G. Daim biopsy no kuj tseem tuaj yeem qhia koj tias koj muaj hom C3G twg (DDD lossis C3GN), raws li seb koj puas muaj cov khoom khov kho ntawd.

Puas kho tau C3G kom zoo tag nrho?

Tu siab kawg li, tam sim no tsis muaj tshuaj kho tau tus kab mob C3G no. Tiam sis tsis txhob txhawj, cov kws kho mob thiab cov kws tshawb fawb tseem tab tom kawm txog tus kab mob no thiab tab tom nrhiav kev kho mob tshiab. Peb vam tias yuav muaj kev kho mob zoo dua yav tom ntej.

Cov kev kho mob rau C3G yog dab tsi?

Tam sim no tsis muaj kev kho mob tshwj xeeb uas tau pom zoo los ntawm US Food and Drug Administration (FDA) rau C3G. Txawm li cas los xij, cov kws kho mob tuaj yeem sau ntau yam kev kho mob thiab kev txhawb nqa kom qeeb qeeb qhov kev loj hlob ntawm C3G, tswj cov tsos mob, thiab txo qhov kev puas tsuaj rau lub raum. Cov no suav nrog:

  • Cov tshuaj kho ntshav siab: Cov tshuaj xws li angiotensin-converting enzyme (ACE) inhibitors thiab angiotensin II receptor blockers (ARBs) txo qhov siab hauv glomeruli. Qhov no txo ​​cov protein hauv cov zis thiab txo qhov kev nyuaj siab rau lub raum.
  • Cov tshuaj txo cov roj cholesterol: Koj tus kws kho mob yuav sau ntawv rau cov tshuaj xws li statins kom txo cov roj cholesterol thiab txo qhov kev puas tsuaj rau koj lub raum.
  • Kev hloov pauv zaub mov: Tus kws kho mob raum yuav pab koj tsim ib txoj kev npaj zaub mov uas haum rau koj thiab pab koj tswj koj qhov hnyav kom noj qab nyob zoo. Kev txo koj cov ntsev (sodium), roj saturated, thiab cholesterol tuaj yeem pab txo qhov kev puas tsuaj raum.
  • Corticosteroids: Kuj hu ua "steroids," cov no yog cov tshuaj tiv thaiv kev o uas ua haujlwm los ntawm kev tiv thaiv lub cev tiv thaiv kab mob kom tsis txhob tawm tsam koj lub glomeruli.
  • Eculizumab: Qhov no yog ib hom tshuaj monoclonal antibody siv los kho cov kab mob ntshav tsawg tsawg. Nws yuav pab txhim kho kev ua haujlwm ntawm lub raum los ntawm kev txo cov protein hauv cov zis thiab ua kom glomerular filtration rate nce ntxiv rau qee tus neeg mob C3G.
  • Kev ntxuav ntshav: Kwv yees li 50% ntawm cov neeg uas muaj C3G tau hais tias muaj kev ua tsis tau haujlwm ntawm lub raum. Kev ntxuav ntshav yog thaum lub raum tsis ua haujlwm, thiab txoj haujlwm uas lub raum yuav tsum ua (ntxuav cov ntshav, tshem tawm cov khoom pov tseg, thiab cov kua dej ntau dhau) yog ua tiav nrog kev pab los ntawm lub tshuab.
  • Kev hloov raum: Qhov no yog lwm txoj kev kho mob rau kev ua tsis tau haujlwm raum. Tus kws phais yuav muab koj lub raum uas tsis ua haujlwm tshem tawm thiab muab lub raum noj qab haus huv los ntawm tus neeg pub hloov raum.

Yog tias koj muaj 'DDD' lossis 'C3GN' thiab kuj muaj 'monoclonal gammopathy', koj tus kws kho mob yuav pom zoo kom kuaj ntxiv kom paub seb puas muaj lwm yam mob.

Yuav ua li cas thiaj paub tias tus kab mob C3G yuav zoo li cas?

Kwv yees li ib nrab ntawm cov neeg mob uas muaj C3G yuav mob raum tsis ua haujlwm li ntawm 10 xyoo tom qab kuaj pom. Tam sim no tsis muaj tshuaj kho tau rau mob raum tsis ua haujlwm. Txawm li cas los xij, nrog kev kuaj mob kom raug thiab kev kho mob sai, koj tuaj yeem ua neej ntev thiab noj qab nyob zoo yam tsis muaj kev hloov pauv loj. Yog li ntawd, nws yog ib qho tseem ceeb kom nyob twj ywm thiab ua raws li koj tus kws kho mob cov lus qhia.

Kab mob C3G puas tiv thaiv tau?

Tu siab kawg li, tam sim no tsis muaj txoj hauv kev los tiv thaiv kab mob C3G, vim nws feem ntau yog los ntawm tej yam uas peb tswj tsis tau.

Kuv yuav saib xyuas kuv tus kheej li cas?

Yog koj muaj C3G, koj tus kws kho mob yuav tsim txoj kev kho mob zoo tshaj plaws rau koj. Qhov no yuav suav nrog kev siv tshuaj, kev txhawb nqa, thiab kev hloov pauv hauv koj txoj kev ua neej. Koj txoj kev npaj kho mob yuav suav nrog cov hauv qab no, thiab nws yog ib qho tseem ceeb uas yuav tsum ua raws li cov kauj ruam no kom zoo:

  • Noj koj cov tshuaj raws li koj tus kws kho mob tau hais. Tsis txhob ncua ib hnub li.
  • Hloov koj cov zaub mov noj, tshwj xeeb tshaj yog txo cov ntsev, roj, thiab qab zib, thiab noj ntau txiv hmab txiv ntoo thiab zaub.
  • Tsis txhob siv cov tshuaj non-steroidal anti-inflammatory drugs (NSAIDs) (piv txwv li, cov tshuaj tua kab mob xws li ibuprofen thiab diclofenac) yam tsis tau kev qhia los ntawm kws kho mob, vim tias lawv tuaj yeem ua rau lub raum puas tsuaj thiab ua rau lub raum tsis ua haujlwm sai dua.
  • Kev saib xyuas koj txoj kev noj qab haus huv ntawm lub hlwb. Muaj tus kab mob tsis tshua muaj no ua rau koj xav tias kho siab thiab ntshai. Tsis tas li ntawd, kev paub tias C3G tuaj yeem ua rau lub raum tsis ua haujlwm ua rau koj muaj feem yuav muaj kev nyuaj siab. Tham nrog koj tus kws kho mob txog koj txoj kev noj qab haus huv ntawm lub hlwb thiab nrhiav kev sab laj thiab kev kho mob yog tias tsim nyog. Nug koj tus kws kho mob txog cov pab pawg txhawb nqa rau cov neeg uas muaj C3G. Kev ntsib lwm tus neeg uas muaj C3G tuaj yeem pab txo kev kho siab thiab sib qhia cov kev paub dhau los.

Kuv yuav tsum mus ntsib kws kho mob thaum twg?

Yog tias koj muaj cov tsos mob ntawm C3G, tshwj xeeb tshaj yog kev hloov pauv hauv koj cov zis (ntshav, ua npuas dej, tsawg dua), o, lossis qaug zog heev, mus ntsib kws kho mob tam sim ntawd. Cov no yuav yog cov cim qhia tias koj lub raum tsis ua haujlwm zoo.

Yog koj kuaj pom tias koj muaj C3G, koj tus kws kho mob yuav xa koj mus rau tus kws kho mob tshwj xeeb hauv kev mob raum (tus kws kho mob nephrologist). Nws yuav yog tus uas yuav muab txoj kev kho mob zoo tshaj plaws rau koj.

Kuv yuav tsum nug kuv tus kws kho mob li cas?

Thaum koj mus ntsib kws kho mob, tsis txhob yig nug cov lus nug zoo li no:

  • Kuv yuav paub tseeb li cas yog tias kuv muaj C3G?
  • Yog tias kuv tsis muaj C3G, kuv yuav muaj lwm yam kab mob dab tsi ntxiv?
  • Kuv muaj hom C3G twg (DDD lossis C3GN)?
  • Koj xav kom kuv kho li cas? Puas muaj tej yam tshwm sim tsis zoo?
  • Kuv yuav tsum hloov dab tsi rau kuv cov zaub mov noj?
  • Koj puas xav tias kuv ob lub raum yuav tsis ua haujlwm? Kuv yuav ua li cas thiaj li tiv thaiv tau qhov ntawd kom tsis txhob tshwm sim?
  • Kuv puas mus ntsib kws kho mob nephrologist tau?

Thaum kawg, kuv yuav tsum hais tias ...

C3G yog ib yam kab mob uas tsis tshua muaj thiab nyuaj heev uas cuam tshuam rau cov chav lim dej me me hauv lub raum. Yog tias koj muaj C3G, koj yuav muaj kev hloov pauv hauv koj cov zis, o, mob pob qij txha, teeb meem pom kev, thiab qaug zog.

Tej zaum koj yuav muaj ntau yam kev xav thaum koj lees txais qhov kev kuaj mob no thiab hloov kho rau C3G yuav cuam tshuam li cas rau koj lub neej. Tsis txhob txhawj, koj tsis nyob ib leeg. Muab sijhawm thiab qhov chaw rau koj tus kheej kom kawm txog C3G thiab koj cov kev xaiv kho mob. Kev kawm txog koj cov kev xaiv thiab yam uas yuav tshwm sim tuaj yeem pab koj daws koj txoj kev xav hauv txoj kev noj qab haus huv thiab muaj txiaj ntsig. Cov kws kho mob nyob ntawd los muab cov ntaub ntawv thiab kev taw qhia. Yog tias koj muaj lus nug, xav tau lus qhia lossis kev txhawb nqa, tham nrog lawv. Nco ntsoov, nrog kev kuaj mob thaum ntxov thiab kev kho mob kom zoo, koj tuaj yeem tswj tau tus kab mob no thiab ua neej zoo.

👩🏽‍⚕️ Cov Lus Nug Ntxiv (FAQs)

💬 C3G (Complement 3 Glomerulopathy) yog hom kab mob raum twg?

Qhov no yog ib qho kab mob raum uas tsis tshua muaj thiab txawv txawv! Peb lub cev muaj ib qho protein tshwj xeeb hu ua 'Complement C3' los tua cov kab mob. Txawm li cas los xij, hauv tus kab mob no, vim muaj qhov tsis zoo ntawm peb lub cev (Autoimmune), cov protein C3 ntawd tawm tsam lub cev nws tus kheej, thiab cov protein ntawd tau tso rau hauv cov lim dej zoo heev (Glomeruli) ntawm lub raum, ua rau lub raum tsis ua haujlwm tag nrho.

💬 Cov tsos mob ntawm ib tus neeg uas muaj tus kab mob txaus ntshai no yog dab tsi?

Thaum lub lim dej ntawm lub raum (cov qauv) raug puas tsuaj, lawv cov zis cia li pib liab (ntshav-Hematuria) thiab ua npuas (protein-Proteinuria). Vim tias lub raum tsis tshem dej tawm ntawm lub cev, ob txhais ceg thiab ib ncig ntawm lub qhov muag o (Edema). Nrog rau qhov no, ntshav siab (Siab siab) kuj tshwm sim.

💬 Puas muaj tshuaj kho mob niaj hnub no los kho tus kab mob no?

Tsis muaj ib txoj kev kho tau qhov no kiag li. Qhov tseem ceeb tshaj plaws yog kom tsis txhob muaj cov protein no tawm tsam, muab cov tshuaj uas ua rau lub cev tiv thaiv kab mob tsis muaj zog (Immunosuppressants thiab Steroids). Tsis tas li ntawd, lawv muab cov tshuaj txo ntshav siab (ACE inhibitors). Yog tias tus kab mob hnyav heev, yuav tsum tau ntxuav ntshav thiab hloov raum.


C3G , kab mob raum, complement 3, glomerulopathy, ua tsis tau haujlwm raum, cov protein hauv zis, kev ntxuav ntshav

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

💬 Comments (0)

Tsis muaj lus teb tau muab tso tawm. Ntxiv koj cov lus tawm ntawm no thawj zaug.

Ntxiv koj cov lus

Thov xam: 9 + 5 =