Puas muaj tej lub sij hawm koj kiv taub hau, koj lub hauv siab dhia ceev, lossis koj xav tias koj tsis nco qab dab tsi li? Txawm hais tias peb xav tias cov no yog tej yam ib txwm muaj, tej lub sij hawm tej zaum yuav muaj ib qho laj thawj loj dua tom qab cov tsos mob no uas peb tsis paub. Niaj hnub no peb tab tom tham txog ib qho mob plawv uas tsis tshua muaj, tab sis tej zaum yuav tseem ceeb heev. Ntawd yog Short QT Syndrome, lossis luv luv SQTS.
Hais yooj yim xwb, Short QT Syndrome (SQTS) yog dab tsi?
Kab mob QT luv luv (SQTS) yog ib yam mob plawv uas tsis tshua muaj, uas yog los ntawm noob caj ces. Qhov no yog thaum peb lub plawv dhia tsis xwm yeem. Hais yooj yim xwb, tom qab peb lub plawv dhia ib zaug, nws yuav tsum so ib ntus kom npaj rau lub plawv dhia tom ntej. Nws zoo li ib txoj hlua roj hmab raug rub thiab tom qab ntawd tso tawm, thiab tom qab ntawd nws rov qab mus rau qhov chaw. Hauv ib tus neeg uas muaj SQTS, qhov kev so no, lossis kev rov zoo, tshwm sim sai dua lossis luv dua li ntawm ib tus neeg ib txwm.
Qhov no yog qhov peb hu ua "kev luv ntawm QT lub sijhawm" ntawm lub plawv. Qhov kev nrawm no tuaj yeem ua rau muaj teeb meem hauv lub plawv lub zog hluav taws xob, ua rau lub plawv dhia tsis xwm yeem. Peb hu qhov no "arrhythmia". Qhov no tuaj yeem ua rau koj kiv taub hau, tsaus muag, thiab mob hauv siab. Hauv qee kis hnyav, lub plawv tuaj yeem nres tam sim ntawd (cardiac arrest). Yog li ntawd, nws yog ib qho tseem ceeb heev uas yuav tsum paub txog qhov no.
Cia peb nkag siab meej tias QT interval yog dab tsi?
Koj puas tau kuaj ECG dua li? Koj yuav pom ib daim duab kab ntawm daim ntawv qhia uas nce thiab nqis. Yog li ntawd cov kws kho mob ntsuas qhov hluav taws xob ntawm peb lub plawv. Xav txog ECG (Electrocardiogram) zoo li lub tshuab uas sau cov teeb liab hluav taws xob ntawm peb lub plawv.
Peb lub plawv dhia siv cov teeb liab hluav taws xob. Cov chav sab saud (atria) thiab cov chav sab hauv qab (mitra) ntawm lub plawv sib zog thiab tso ntshav vim yog cov teeb liab hluav taws xob no. Cov txheej txheem no yog sawv cev los ntawm cov nthwv dej P, Q, R, S, thiab T ntawm ECG.
- P nthwv dej: Qhov no yog tsim tawm thaum cov chav sab saud ntawm lub plawv (atria) cog lus.
- QRS complex: Qhov no tshwm sim thaum cov chav qis (cell) ntawm lub plawv cog lus.
- T nthwv dej: Qhov no tshwm sim thaum cov ventricles rov qab mus rau qhov qub thiab npaj rau qhov kev cog lus tom ntej.
Lub sijhawm "QT interval" yog lub sijhawm txij thaum pib ntawm QRS complex mus txog thaum kawg ntawm T wave. Qhov no ntsuas seb nws siv sijhawm ntev npaum li cas rau cov chav qis ntawm lub plawv kom qis thiab tom qab ntawd so dua kom rov qab mus rau qhov qub.
Feem ntau, lub sijhawm QT ntawm ib tus neeg noj qab haus huv yog nruab nrab ntawm 0.35 thiab 0.45 vib nas this. Txawm li cas los xij, rau ib tus neeg uas muaj SQTS, lub sijhawm no tsawg dua 0.34 vib nas this. Qhov no txhais tau tias lub plawv npaj rau lub plawv dhia tom ntej sai dua li qhov xav tau.
Qhov txawv ntawm Long QT thiab Short QT yog dab tsi?
Qhov no kuj tseem ceeb rau koj. Muaj ib yam mob hu ua Short QT thiab Long QT Syndrome.
- Kab Mob QT Luv (SQTS): Lub sijhawm QT luv dhau (tsawg dua 0.34 vib nas this). Lub plawv rov zoo sai dhau .
- Kab Mob QT Ntev (LQTS): Lub sijhawm QT ntev dhau (ntau tshaj 0.45 vib nas this). Lub plawv siv sijhawm ntev dua los kho.
Ob qho tib si ntawm cov mob no tuaj yeem ua rau muaj teeb meem plawv dhia.
Leej twg muaj tus mob no? Dab tsi yog cov ua rau muaj tus mob no?
SQTS yog ib yam mob tsis tshua muaj . Tsis muaj cov ntaub ntawv tseeb txog pes tsawg tus neeg hauv ntiaj teb no muaj nws. Nws yog ib yam kab mob caj ces. Qhov no txhais tau tias nws tuaj yeem tau txais los ntawm niam txiv mus rau menyuam. Los yog nws tuaj yeem tshwm sim rau ib tus neeg uas tsis muaj keeb kwm tsev neeg, ua ib qho kev hloov pauv caj ces tshiab.
Muaj tej kev tshawb fawb pom tias cov tsos mob no feem ntau tshwm sim hauv thawj xyoo ntawm tus menyuam lub neej. Tom qab ntawd, cov tsos mob tuaj yeem rov tshwm sim dua thaum laus, ntawm hnub nyoog 20 thiab 40 xyoo.
Cov tsos mob tseem ceeb ntawm qhov no yog dab tsi?
Tsis yog txhua tus neeg uas muaj SQTS yuav muaj cov tsos mob. Ib txhia neeg ua neej nyob li qub yam tsis muaj cov tsos mob. Tab sis yog tias cov tsos mob tshwm sim, lawv yuav zoo li no.
| Cov tsos mob | Piav qhia yooj yim |
|---|---|
| Kev mob plawv dhia tsis xwm yeem (AFib) | Qhov no yog cov tsos mob uas pom ntau tshaj plaws. Cov teeb liab hluav taws xob hauv cov chav sab saud ntawm lub plawv (atria) raug cuam tshuam, ua rau lub plawv dhia ceev heev thiab tsis sib xws. |
| Kev mob plawv dhia ceev | Zoo li koj lub plawv dhia nrov nrov thiab nrawm, lossis zoo li muaj ib yam dab tsi co hauv koj lub hauv siab. |
| Kiv taub hau thiab Tsaus muag | Thaum lub plawv dhia tsis zoo, cov ntshav ntws mus rau lub hlwb yuav txo qis. Qhov no tuaj yeem ua rau kiv taub hau, qhov muag xiav, thiab tsis nco qab (syncope). |
| Kev Plawv Nres Sai Sai | Qhov no yog qhov mob hnyav thiab txaus ntshai tshaj plaws. Lub plawv cia li nres dhia vim muaj teeb meem txaus ntshai hauv cov chav qis ntawm lub plawv (ventricular fibrillation lossis ventricular tachycardia). Qhov no yog qhov xwm txheej ceev uas yuav tsum tau kho tam sim ntawd. |
Tu siab kawg li, qee tus neeg (kwv yees li ob ntawm tsib tus) thawj zaug kuaj pom tias muaj SQTS tom qab muaj kev mob plawv nres tam sim ntawd.
Yuav kuaj mob li cas?
Yog koj muaj cov tsos mob no, koj tus kws kho mob yuav nug koj txog koj cov tsos mob thiab kuaj koj ua ntej. Tom qab ntawd, yog tias lawv xav tias koj muaj SQTS, lawv yuav xaj cov kev kuaj mob hauv qab no:
- ECG (Electrocardiogram): Qhov no yog qhov kev kuaj tseem ceeb tshaj plaws. Nws ntsuas koj lub sijhawm QT. Yog tias nws tsawg dua 0.34 vib nas this, thiab yog tias koj muaj lwm yam tsos mob, tej zaum yuav muaj kev xav tias muaj SQTS.
- Kev Kuaj Genetic: Qhov no tuaj yeem lees paub seb puas muaj kev hloov pauv caj ces uas ua rau SQTS.
Qhov tseem ceeb tshaj plaws yog tias tsuas yog vim QT lub sijhawm ntawm ECG luv me ntsis xwb, nws tsis tuaj yeem hais tias txhua tus neeg muaj SQTS. Nws kuj tsis tuaj yeem hais tias muaj kev pheej hmoo ntawm kev nres plawv tam sim ntawd. Kev kuaj mob yuav tsum tau ua los ntawm tus kws kho mob uas muaj kev paub txog qhov no.
Yuav kho li cas?
SQTS raug kho los ntawm tus kws kho mob plawv. Muaj ntau txoj kev xaiv kho mob. Koj tus kws kho mob yuav txiav txim siab qhov kev kho mob zoo tshaj plaws rau koj tus mob.
1. Lub Tshuab Ua Pa Hluav Taws Xob Rau Lub Plawv (ICD): Qhov no yog ib lub cuab yeej me me. Nws raug phais muab tso rau hauv qab daim tawv nqaij ntawm lub hauv siab ze ntawm lub plawv. Nws zoo li lub cuab yeej tiv thaiv me me rau lub plawv. Lub tshuab no saib xyuas lub plawv dhia tas li. Yog tias muaj lub plawv dhia tsis xwm yeem, nws yuav ntes tau thiab xa hluav taws xob me me mus rau lub plawv, ua rau lub plawv rov qab dhia li qub. Qhov no yog kev kho mob zoo tshaj plaws rau cov neeg laus.
2. Cov Tshuaj: Muaj cov tshuaj tiv thaiv kev mob plawv dhia tsis xwm yeem uas muab rau koj kom tswj tau lub plawv dhia. Piv txwv li, ib yam tshuaj hu ua quinidine pab kom QT interval zoo li qub. Koj tus kws kho mob kuj tseem yuav sau lwm yam tshuaj, xws li beta-blockers.
Qhov xwm txheej no cuam tshuam li cas rau koj lub neej?
Qhov no yog ib qho teeb meem rhiab heev. Ib txhia neeg uas muaj SQTS muaj feem yuav tuag sai sai hauv lub plawv. Qhov kev pheej hmoo no tau hais tias siab heev ntawm cov hnub nyoog 0-1 thiab 20-40. Thaum tus menyuam mos raug cuam tshuam los ntawm qhov mob no, qee zaum nws hu ua Sudden Infant Death Syndrome (SIDS).
Txawm li cas los xij, qhov no tsis tau txhais hais tias txhua tus neeg uas muaj SQTS muaj qhov kev pheej hmoo no.
Feem ntau cov neeg nyob lub neej zoo li qub, noj qab nyob zoo nrog kev kho mob kom zoo (tshwj xeeb tshaj yog kev cog ICD) thiab ua raws li lawv tus kws kho mob cov lus qhia. Qee tus neeg yuav tsis muaj tsos mob li. Vim tias qhov no yog ib qho mob tsis tshua muaj, kev tshawb fawb tseem tab tom ua mus. Yog li qhov zoo tshaj plaws uas koj tuaj yeem ua tau yog tham nrog koj tus kws kho mob plawv thiab tswj koj lub neej rau txoj kev uas haum rau koj tus mob.
Peb puas zam tau qhov kev pheej hmoo no?
Vim tias SQTS yog ib yam mob uas los ntawm noob caj ces, peb tsis muaj txoj hauv kev los tiv thaiv nws kom tsis txhob tshwm sim. Nws yog ib yam dab tsi uas peb tswj tsis tau.
Tab sis yog tias koj raug kuaj pom tias muaj SQTS, qhov zoo tshaj plaws uas koj tuaj yeem ua tau yog mus ntsib koj tus kws kho mob plawv tsis tu ncua thiab mus kuaj mob tsis tu ncua. Nws yuav saib xyuas koj lub plawv kom zoo tsis tu ncua thiab muab cov lus qhia thiab kev kho mob tsim nyog rau koj kom txo koj txoj kev pheej hmoo ntawm cov teeb meem loj, xws li lub plawv nres tam sim ntawd.
Cov Lus Qhia Txog Kev Coj Mus Tsev
- Short QT Syndrome (SQTS) yog ib qho mob caj ces tsis tshua muaj uas ua rau lub plawv dhia ceev tsis zoo.
- Tej zaum yuav muaj cov tsos mob xws li kiv taub hau, tsaus muag, thiab mob hauv siab. Qee zaum mob hnyav, lub plawv nres tam sim ntawd kuj yuav tshwm sim.
- Tus kws kho mob tuaj yeem kuaj mob no los ntawm kev kuaj ECG thiab kev kuaj noob caj noob ces.
- Tus mob no tuaj yeem tswj tau zoo nrog kev cog cov cuab yeej ICD thiab tshuaj.
- Yog koj muaj tus kab mob no los yog muaj cov tsos mob no, tsis txhob ntshai mus ntsib kws kho mob plawv thiab tau txais kev qhia. Yog tias koj tswj tau zoo, koj tuaj yeem ua neej nyob li qub.











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Tsis muaj lus teb tau muab tso tawm. Ntxiv koj cov lus tawm ntawm no thawj zaug.
Ntxiv koj cov lus