Thaum koj hnov tias koj tus menyuam mos muaj mob plawv, nws nyuaj rau piav qhia ua lus, puas yog? Tab sis tsis txhob txhawj. Qee zaum cov menyuam mos muaj ob lub hlab ntsha tseem ceeb hauv lawv lub siab hloov pauv thaum lawv yug los. Niaj hnub no peb tab tom tham txog ib qho mob zoo li no, hu ua '(Kev Hloov Pauv ntawm Cov Ntshav Loj)'. Qhov no yuav zoo li nyuaj me ntsis, tab sis cia peb ua kom yooj yim.
Kev Hloov Pauv ntawm Cov Kab Mob Loj yog dab tsi?
Hais yooj yim xwb, qhov no yog ib qho mob "yug los" uas tshwm sim thaum tus menyuam yug los. Qhov ntawd yog, qhov teeb meem no tshwm sim thaum tus menyuam tseem nyob hauv niam lub tsev menyuam. Peb muaj ob lub hlab ntsha tseem ceeb uas nqa ntshav los ntawm peb lub plawv mus rau lwm qhov ntawm peb lub cev. Ib qho yog
cov hlab ntsha hauv lub ntsws, uas nqa ntshav mus rau lub ntsws , thiab lwm qhov yog
aorta, uas nqa ntshav mus rau lwm qhov ntawm peb lub cev . Qhov tshwm sim hauv qhov mob no yog tias ob lub hlab ntsha loj no txuas nrog lub plawv rau qhov chaw tsis yog, tsis yog nyob rau qhov chaw zoo. Nws zoo li cov kav dej mus rau ob lub thoob dej raug hloov pauv.
Cov ntshav feem ntau mus ncig li cas? Yuav ua li cas hauv qhov xwm txheej no?
Feem ntau, qhov no yog qhov tshwm sim: lub cev cov ntshav uas tsis muaj oxygen (ntshav xiav) mus rau lub plawv, los ntawm qhov ntawd mus rau lub ntsws kom khaws cov pa oxygen. Tom qab ntawd cov ntshav tshiab, uas muaj oxygen ntau (ntshav liab) rov qab mus rau lub plawv, los ntawm qhov ntawd mus rau tag nrho lub cev los ntawm cov hlab ntsha loj. Tab sis nyob rau hauv qhov "Kev Hloov Chaw ntawm Cov Ntshav Loj" no, vim tias ob lub hlab ntsha tau hloov pauv, cov ntshav uas tsis muaj oxygen rov qab mus rau lub cev es tsis txhob mus rau lub ntsws. Ib yam li ntawd, cov ntshav uas muaj oxygen ntau los ntawm lub ntsws rov qab mus rau lub ntsws es tsis txhob mus rau lub cev. Xav txog seb qhov no yuav mus rau cov menyuam lub cev tsawg dua li cas.
Puas muaj cov hom no?
Yog, muaj ob hom tseem ceeb ntawm qhov no: 1.
Levo-transposition (Levo-transposition lossis l-TGA): Hauv qhov no, tus menyuam lub aorta nyob rau sab laug ntawm cov hlab ntsha hauv lub ntsws. Hauv qhov no, tsis yog tsuas yog ob lub hlab ntsha xwb, tab sis kuj tseem muaj cov chav qis dua ntawm lub plawv. Txawm li cas los xij, hauv hom no, cov ntshav tsis muaj pa oxygen mus rau lub ntsws thiab cov ntshav oxygen mus rau lub cev, yog li nws tsis ua rau muaj kev phom sij ntau. Qhov no tsis tshua muaj ntau. 2.
Dextro-transposition (Dextro-transposition lossis d-TGA): Hauv qhov no, tus menyuam lub aorta nyob rau sab xis ntawm cov hlab ntsha hauv lub ntsws. Qhov no yog hom feem ntau, thiab
nws kuj yog hom uas xav tau kev saib xyuas ntau dua. Peb yuav tham ntxiv txog qhov '(d-TGA)' no hauv tsab xov xwm no.
Vim li cas qhov mob no hu ua d-TGA thiaj txaus ntshai rau cov menyuam mos?
Zoo li kuv tau hais ua ntej lawm, yog tias muaj tus kab mob "(d-TGA), tus menyuam lub cev puv nrog cov ntshav uas tsis muaj oxygen txaus. Qhov no txhais tau tias txhua yam tseem ceeb ntawm tus menyuam, xws li lub hlwb, lub raum, thiab lub siab, tsis tau txais cov pa oxygen txaus. Qhov no txaus ntshai heev rau tus menyuam lub neej. Qee zaum, thaum cov menyuam no yug los, tej zaum yuav muaj qhov ntawm cov chav sab saud ntawm lub plawv "(Atrial Septal Defect lossis ASD)" lossis qhov ntawm cov chav sab qis ntawm lub plawv "(Ventricular Septal Defect lossis VSD)". Txawm hais tias cov qhov no yog cov mob tsis tshua muaj, tab sis thaum zoo li no, cov qhov no yuav pab tau me ntsis. Qhov ntawd yog, cov qhov no tso cai rau qee cov ntshav uas muaj oxygen sib xyaw nrog cov ntshav uas tsis muaj oxygen. Txawm li cas los xij, cov pa oxygen uas tau txais tsis txaus kiag li. Yog li ntawd, tus menyuam yeej xav tau kev kho mob.
Tsis txhob txhawj, muaj kev phais rau qhov mob no. Cov kws kho mob tau ua cov kev phais no tau zoo rau ntau xyoo.
Yog koj tus menyuam muaj tus mob no, cov cim thiab tsos mob yog dab tsi? (Cov tsos mob)
Cov menyuam mos uas muaj '(d-TGA)' yuav muaj tus mob hu ua '(cyanosis),' uas yog xim xiav/grey ntawm daim tawv nqaij vim tsis muaj oxygen. Lawv kuj tseem yuav muaj lub plawv tsis muaj zog. Cov tsos mob tseem ceeb yog:
- Ua pa nyuaj .
- Lub plawv dhia tsis muaj zog heev.
- Qhia tias tsis kam thiab nyuaj haus mis nyuj.
- Kuv lub plawv zoo li nws dhia nrov dhau, zoo li nws dhia ceev dhau.
- Daim tawv nqaij thiab lub qhov muag dawb yuav zoo li xiav (rau cov menyuam mos uas muaj daim tawv nqaij dawb) lossis xim grey (rau cov menyuam mos uas muaj daim tawv nqaij tsaus).
Cov tsos mob no pib thaum twg?
Ib tug me nyuam uas muaj '(d-TGA)' yuav pib pom cov tsos mob no thaum yug los. Txawm li cas los xij, qee zaum, vim yog tej yam zoo li '(ASD)', cov qhov me me hauv lub plawv ntawm tus me nyuam tuaj yeem ua rau cov ntshav uas muaj oxygen ntau mus rau hauv lub cev, yog li cov tsos mob yuav tsis pom tseeb. Tsis tas li ntawd, '(patent ductus arteriosus)', ib txoj hlab ntshav uas tus me nyuam siv thaum nyob hauv plab, tuaj yeem qhib rau ob peb hnub tom qab yug los, ua rau cov ntshav sib xyaw. Txawm li cas los xij, thaum cov qhov thiab cov raj no kaw, cov tsos mob tuaj yeem nce ntxiv sai sai. Yog li ntawd, tus me nyuam xav tau kev kho mob tam sim ntawd.
Vim li cas qhov no thiaj tshwm sim? (Vim li cas)
Cov kws kho mob tseem tsis tau paub meej tias yog dab tsi ua rau muaj Transposition of the Great Arteries. Ib yam li lwm yam kab mob plawv uas yug los, nws xav tias yog los ntawm kev hloov pauv caj ces lossis kev raug tshuaj lom thaum cev xeeb tub. Qee yam uas tuaj yeem ua rau muaj tus mob no suav nrog:
Tsis txhob ntshai tej yam no. Tsis yog txhua tus neeg uas tau muaj ib qho ntawm cov no yuav muaj qhov no.
Cov kws kho mob kuaj qhov no li cas ? (Kev kuaj mob)
Qee zaum, cov kws kho mob tuaj yeem kuaj pom qhov mob no thaum koj tseem cev xeeb tub. Qhov no ua tiav los ntawm kev kuaj ua ntej yug menyuam. Yog tias
koj tus kws kho mob xav tias muaj qee yam tsis raug thaum lub sijhawm ultrasound scan ntawm koj tus menyuam, nws yuav hais kom koj ua fetal echocardiogram. Qhov no zoo ib yam li ultrasound, tab sis nws saib lub plawv ntawm tus menyuam kom meej. Qhov no tuaj yeem lees paub seb koj puas muaj d-TGA. Yog tias nws tsis raug kuaj pom thaum cev xeeb tub, feem ntau nws raug kuaj pom hauv thawj lub lim tiam tom qab yug los.
Yuav ua li cas thiaj kuaj tau qhov no?
Cov kev kuaj uas cov kws kho mob siv los paub meej tias muaj tus mob no yog:
- Echocardiogram (Echo): Qhov no kuj yog kev ntsuas ultrasound ntawm lub plawv.
- Electrocardiogram (EKG): Ib qho kev kuaj uas saib xyuas kev ua haujlwm hluav taws xob ntawm lub plawv.
- Kev kuaj mob pulse oximetry rau cov menyuam mos: Qhov no feem ntau ua rau txhua tus menyuam mos.
- Kev kuaj mob X-ray hauv siab.
- Kev siv catheter rau lub plawv: Qhov no yog ib qho kev kuaj uas nyuaj dua. Ib lub raj nyias nyias ( catheter ) raug ntxig los ntawm ceg lossis caj npab mus rau hauv lub plawv. Qhov no ua tiav yog tias lwm yam kev kuaj tsis meej.
- Kev kuaj CT yog ib qho kev kuaj mob.
Yuav kho qhov no li cas? Koj tus menyuam xav tau kev pab sai sai!
Ib tug me nyuam mos uas yug los muaj '(d-TGA)'
yuav tsum tau phais kom thiaj li muaj sia nyob. Feem ntau, qhov kev phais no ua tiav
hauv thawj lub lim tiam ntawm kev yug los. Qhov kev phais no hu ua
kev hloov pauv ntawm cov hlab ntsha . Hais yooj yim xwb, qhov no cuam tshuam txog kev txuas ob lub hlab ntsha uas tau hloov pauv (aorta thiab pulmonary artery) rov qab mus rau lawv qhov chaw raug. Qhov no tso cai rau cov ntshav ntws kom zoo. Yog tias koj tus me nyuam muaj lub qhov hauv lawv lub plawv, xws li '(VSD)', qhov ntawd kuj yuav raug kho thaum lub sijhawm phais no.
Tej yam uas yuav tsum ua ib ntus ua ntej phais
Cov kws kho mob siv ntau txoj kev kho mob ib ntus los tswj tus menyuam kom txog thaum muaj kev phais loj. Cov no suav nrog:
- Prostaglandin: Cov tshuaj no siv los qhib lub ductus arteriosus, ib txoj hlab ntshav uas tus menyuam muaj thaum ub hauv plab tab sis kaw tom qab yug los. Thaum qhov no qhib lawm, qee cov ntshav uas muaj oxygen pib ntws mus rau hauv lub cev.
- Cov txheej txheem hu ua Balloon atrial septostomy:Hauv qhov no, ib lub raj nyias nyias (catheter) siv los ua kom qhov qhib ntuj ntawm ob lub chav sab saud ntawm lub plawv loj dua. Qhov no ua rau cov ntshav uas muaj oxygen thiab cov ntshav uas tsis muaj oxygen sib xyaw ua ke, muab qee cov pa oxygen rau lub cev.
Puas tiv thaiv tau qhov teeb meem no?
Tsis muaj ib txoj kev paub uas yuav tiv thaiv tau qhov Transposition of the Great Arteries. Txawm li cas los xij, nws yog ib qho tseem ceeb uas yuav tsum ua raws li kev coj ua zoo thaum koj cev xeeb tub. Mus txhaj tshuaj tag nrho raws sijhawm, noj koj cov multivitamin, thiab mus ntsib kws kho mob raws sijhawm. Yog tias leej twg hauv koj tsev neeg muaj keeb kwm ntawm tus kab mob plawv txij thaum yug los, tham nrog koj tus kws kho mob txog qhov ntawd. Nws yuav pom zoo kom muaj kev sab laj txog kev hloov pauv caj ces.
Tom qab phais lawm, yuav ua li cas? Yuav ua li cas thiaj nyob tau nrog TGA
Txawm hais tias kev phais mob tsis kho tau tag nrho tus mob no, ntau tus neeg uas muaj '(d-TGA)' nyob tau zoo thiab noj qab nyob zoo. Txawm li cas los xij, cov neeg uas muaj tus mob '(yug los)' no
xav tau kev saib xyuas mob tas mus li. Tus kws kho mob plawv yuav saib xyuas koj tus menyuam tus mob tas li thiab muab cov lus qhia tsim nyog. Tus nqi ciaj sia tom qab kev phais mob '(hloov cov hlab ntsha)' yog ntau dua 95%. Lawv hais tias tus nqi no tseem zoo ib yam txawm tias tom qab 25 xyoo.
Koj tus menyuam puas nyob tau zoo nrog TGA?
Yog, yeej muaj tseeb tiag. Tom qab kho tus mob '(Kev Hloov Pauv ntawm Cov Ntshav Loj)', koj tus menyuam tuaj yeem ua neej nyob li qub. Txawm li cas los xij, lub plawv yuav tsum tau saib xyuas thoob plaws lub neej. Qhov ntawd txhais tau tias:
- Koj yuav tsum tau sib cuag nrog kws kho mob plawv uas tshwj xeeb hauv cov mob no tsis tu ncua.
- Koj yuav tsum tau noj cov tshuaj raws nraim li tau qhia.
- Yuav tsum tau ua cov kev ntsuam xyuas uas xyuas seb lub plawv ua haujlwm li cas, xws li '(EKG), '(Holter monitor), '(kev ntsuam xyuas kev ntxhov siab thaum tawm dag zog),' thiab '(echocardiogram),' tsis tu ncua.
Muaj ntau tus kws kho mob plawv tsis pom zoo kom koj ua si kis las sib tw tom qab phais mob '(d-TGA)'. Yog li ntawd, koj thiab koj tus menyuam, koj tus kws kho mob menyuam yaus, thiab koj tus kws kho mob plawv yuav tsum ua haujlwm ua ke los txiav txim siab zoo tshaj plaws rau koj tus menyuam txoj kev noj qab haus huv. Muaj ntau tus poj niam uas tau phais mob '(d-TGA)' tau cev xeeb tub zoo. Txawm li cas los xij, nws yog ib qho tseem ceeb uas yuav tsum tham nrog koj tus kws kho mob thiab tus kws kho mob plawv ua ntej cev xeeb tub.
Puas yuav xav tau kev phais plawv ntxiv yav tom ntej?
Yog lawm, tej zaum yuav xav tau kev phais ntxiv tom qab. Feem ntau, lawv yog kho qhov teeb meem ntawm lub plawv dhia lossis kho cov qhov dej ntawm lub plawv.
Puas muaj kev pheej hmoo ntawm endocarditis?
Kab mob Endocarditis yog ib yam mob uas tshwm sim thaum muaj kab mob bacterial nkag mus rau hauv lub plawv. Cov neeg uas muaj mob plawv zoo li TGA yuav muaj qhov no ntau dua. Yog li ntawd, cov neeg uas tau phais hloov plawv yuav tsum tau noj tshuaj tua kab mob ua ntej kho hniav.
Puas yuav cuam tshuam rau kev loj hlob ntawm lub hlwb?
Tej tus menyuam uas muaj teeb meem ntawm cov hlab ntsha hauv lub hlwb (arterial switch) tej zaum yuav muaj ADHD (attention deficit hyperactivity disorder). Los yog lawv yuav xav tau kev pab tshwj xeeb nrog kev ua haujlwm hauv tsev kawm ntawv. Yuav tsum paub txog qhov no thiab.
Kuv yuav tsum mus ntsib kws kho mob thaum twg?
Yog koj tus menyuam muaj cov tsos mob no ...
- Yog koj xav tias koj ua pa tsis tau zoo.
- Yog tias lub zog ntawm lub cev tsis muaj zog heev.
- Yog tias daim tawv nqaij nyob ib ncig ntawm lub qhov ncauj tau hloov xiav/dawb.
Yog koj pom ib yam dab tsi zoo li no, mus ntsib kws kho mob tam sim ntawd.
Yog koj tau phais mob no thaum koj tseem yog menyuam yaus ...
Koj yuav tsum tau mus kuaj mob thiab saib xyuas koj tus kheej
tas li thoob plaws koj lub neej. Mus ntsib kws kho mob plawv uas muaj kev paub txog kab mob plawv rau cov neeg laus (yug los).
Koj yuav tsum nug tus kws kho mob li cas?
Yog koj tus menyuam muaj Transposition of the Great Arteries, koj tuaj yeem nug tus kws kho mob cov lus nug no:
- Puas yog kuv tus menyuam yuav tsum tau phais sai sai no?
- Kev kho mob zoo tshaj plaws yog dab tsi?
- Kuv tus me nyuam xav tau kev saib xyuas tom qab li cas?
- Puas yog nws yuav tsum tau phais dua?
- Puas muaj kev txwv rau nws cov dej num?
- Kuv yuav tsum saib xyuas kuv tus menyuam li cas tom qab phais lawm?
Yog tias koj tau phais rau qhov mob no thaum koj tseem yog menyuam yaus, koj tuaj yeem nug koj tus kws kho mob:
- Kuv puas yuav tsum tau phais dua?
- Kuv xav tau kev saib xyuas kev kho mob hom twg?
- Puas muaj kev txwv rau kuv cov dej num?
- Kuv puas muaj peev xwm muaj menyuam?
Thaum kawg, qhov tseem ceeb tshaj plaws (Cov Lus Qhia Coj Mus Tsev)
Kev nrhiav pom tias koj tus menyuam mos muaj mob plawv txij thaum yug los tsis yog ib yam dab tsi uas niam txiv xav tau. Nws tuaj yeem ua rau mob siab heev. Tab sis,
koj tsis yog tib leeg xwb. Cov kws kho mob ntawm koj tus menyuam tuaj yeem pab koj hla txoj kev no thiab coj koj mus rau hauv kev txiav txim siab uas koj ua.
Nco ntsoov tias, cov kws kho mob tau kho cov menyuam mos uas muaj TGA tau ntau xyoo, thiab cov txiaj ntsig tau zoo heev. Ua kom muaj zog rau koj tus menyuam. Tsis txhob ntshai nug koj tus kws kho mob txog txhua yam uas koj tsis nkag siab lossis tsis paub meej. Koj txoj kev paub yog lub zog loj tshaj plaws rau koj tus menyuam rau lub neej yav tom ntej noj qab nyob zoo.
Kev phais plawv, kab mob plawv txij thaum yug los, phais hloov cov hlab ntsha, mob cyanosis, kab mob plawv menyuam yaus, d-TGA, phais plawv
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Tsis muaj lus teb tau muab tso tawm. Ntxiv koj cov lus tawm ntawm no thawj zaug.
Ntxiv koj cov lus