Yu gɛt Yuria Saykl Disɔda (UCD) bak? Lɛ wi tɔk bɔt di mɛrɛsin we dɛn kɔl Sodium Phenylbutyrate!

Difrεn kεmikכl prכsεs dεm de apin na wi bכdi fכ du difrεn wok dεm. So, sɔmtɛm if dɛn tin ya nɔ apin fayn, difrɛn sik dɛn kin apin. ‘Urea Cycle Disorders’ (UCD) na wan pan dɛn kayn tin ya. Wetin kin apin pan dis na dat, dɛn nɔ kin ebul fɔ pul wan dɔti we dɛn kɔl amonia we dɛn kin mek na wi bɔdi fayn fayn wan. Dɔn di lɛvɛl we di amonia de na di blɔd kin go ɔp ɛn difrɛn wɛlbɔdi prɔblɛm dɛn kin kam. Tide wi go tɔk bɔt wan mɛrɛsin we dɛn kɔl ‘Sodium Phenylbutyrate’, we dɛn kin gi pɔsin we gɛt UCD kɔndishɔn.

Wetin na dis mɛrɛsin? Wetin mek dɛn de gi am?

Fɔ tɔk am simpul wan, Sodium Phenylbutyrate na mɛrɛsin we dɛn kin gi pipul dɛn we gɛt yuria saykl dizayd (UCD). I de wok bay we i de ɛp fɔ ridyus di amonia we de gɛda na yu bɔdi. Dis kin ridyus di risk fɔ gɛt siriɔs wɛlbɔdi prɔblɛm we kin kam bikɔs ɔf di bɔku bɔku amonia. Bɔt mɛmba se, i nɔ de mɛn UCD ɔltogɛda. Na mɛrɛsin wae de ɛp fɔ kɔntrol di sik dɛm ɛn gi yu sɔm rilif.

Dɔktɔ dɛn kin yuz dis mɛrɛsin bak fɔ ɔda sik dɛn, so if yu gɛt ɛni ɔda kwɛstyɔn bɔt dis, i go fayn fɔ aks yu dɔktɔ ɔ fama.

Wetin na di tin dɛm we a nid fɔ tɛl mi dɔktɔ bifo a yuz dis mɛrɛsin?

Bifo yu bigin fɔ tek Sodium Phenylbutyrate, sɔm tin dɛn de we yu fɔ tɛl yu dɔktɔ ɔ di mɛdikal tim we de trit yu. Dis infɔmeshɔn go ɛp dɛn fɔ disayd if dis mɛrɛsin fayn fɔ yu ɛn ɔmɔs fɔ gi yu.

Si if yu gɛt ɛni wan pan dɛn tin ya:

If yu gɛt ɛni wan pan dɛn tin ya, yu fɔ rili tɛl yu dɔktɔ:

• Dayabitis: If yu gɛt dayabitis.
• Di it we nɔ gɛt sɔl: If yu de it tin we nɔ gɛt bɔku sɔl, ɔ if yu dɔktɔ dɔn tɛl yu fɔ it tin we nɔ gɛt bɔku sɔl.
• Hat failure: If yu gɛt wik at ɔ yu gɛt at sik.
• Kidni sik: If yu gɛt ɛni sik na yu kidni.
• Potassium we nɔ bɔku na yu blɔd: If dɛn bin dɔn no se yu nɔ gɛt bɛtɛ potashɔm na yu blɔd.
• Liva sik: If yu gɛt ɛni sik na yu liva.
• Swel na di ankles, fut, an: If yu leg ɛn an dɛn swel.
• Wan ɔda kayn ɔ alɛji we pɔsin kin gɛt wit sɔdiɔm fɛnilbutarayt, ɔda mɛrɛsin dɛn, it dɛn, day, ɔ tin dɛn we kin mek pɔsin nɔ pwɛl:If yu gɛt alɛji to dis mɛrɛsin ɔ ɛni ɔda tin.
• Bɛlɛ ɔ tray fɔ gɛt bɛlɛ: Ilɛksɛf yu de ɛkspɛkt pikin ɔ yu dɔn ɔlrɛdi gɛt bɛlɛ.
• If yu na mama we de gi pikin in bɛlɛ (Breast-feeding): If yu de gi yu pikin in bɛlɛ.

Aw ɛksaktɔli a fɔ yuz dis mɛrɛsin?

I rili impɔtant fɔ yuz dis mɛrɛsin jɔs lɛk aw di dɔktɔ tɛl yu.

• Dis mɛrɛsin na fɔ tek am bay mɔt.
• Tek yu mɛrɛsin di sem tɛm ɛvride , jɔs lɛk aw dɛn rayt am na di prɛskrishɔn lɛbl.
• Yu nid fɔ yuz spɛshal mak spun fɔ mɛzhɔ dis mɛrɛsin. Aks na di famasi if yu nɔ ebul fɔ fɛn wan. Ti spɔnj ɛn tebul spɔnj dɛn we dɛn kin yuz ɔltɛm na os nɔ kin kɔrɛkt, so nɔ yuz dɛn.
• Dɛn fɔ miks di mɛrɛsin paoda wit smɔl wata, ɔda wata, ɔ ivin sɔm it fɔ drink.
• Swɛla am wantɛm wantɛm afta yu dɔn miks am. Nɔ ol am.
• Kɔntinyu fɔ tek di mɛrɛsin te yu dɔktɔ ɔ di mɛdikal tim tɛl yu fɔ stɔp.

Impɔtant: Yu dɔktɔ go mɔs tɛl yu fɔ fala di it we nɔ gɛt bɔku prɔtin we yu de tek dis mɛrɛsin. I rili impɔtant fɔ tek tɛm fala dis it. Dɛn kin tɛl sɔm pipul dɛn bak fɔ tek ɛkstra vaytamɛn ɛn tin dɛn we dɛn kin it.

If yu gi pikin dɛn dis mɛrɛsin:

Dɛn kin gi dis mɛrɛsin to pikin dɛn na sɔm tin dɛn we dɛn dɔn pik. Bɔt sɔm tin dɛn de we wi fɔ tek tɛm wit we wi de gi am. So, if dɛn dɔn gi yu pikin dis mɛrɛsin, tek tɛm tɔk to yu dɔktɔ bɔt am ɛn no di ditil dɛm.

If yu tek bɔku mɛrɛsin (Overdosage):

If yu tink se yu dɔn tek mɔ mɛrɛsin pas aw yu tink, go na di ɔspitul imejensi rum we de nia yu wantɛm wantɛm , ɔ kɔl pɔyzin kɔntrol sɛnta.

Wan ɔda tin: Dɛn dɔn gi yu dis mɛrɛsin fɔ yu nɔmɔ . So, nɔ gi am to ɔda pɔsin, ilɛksɛf dɛn se dɛn gɛt di sem sik we yu gɛt.

Wetin fɔ du if yu mis wan doz fɔ mɛrɛsin?

Sɔntɛnde, i pɔsibul fɔ mis wan doz, nɔto so? If na so, tek di doz we yu mis as yu mɛmba. Bɔt if i dɔn lɛf smɔl fɔ lɛ yu tek yu nɛks doz, skip di doz we yu mis ɛn tek yu nɛks doz di tɛm we yu dɔn sɛtul. Nɔ ɛva tek tu doz wan tɛm ɔ tek mɔ pas di doz we dɛn tɛl yu fɔ tek.

Us ɔda tin dɛn kin miks wit dis mɛrɛsin?

We yu tek Sodium Phenylbutyrate, i kin intarakt wit ɔda mɛrɛsin, ɛvbɔdi, vaytamɛn, ɔ drɔgs we nɔ gɛt prɛskrishɔn we yu de tek. If yu du dat, i go ambɔg aw dis mɛrɛsin de wok fayn ɔ i go mek yu gɛt sayd ɛfɛkt.

Dis dɔŋ ya na sɔm mɛrɛsin dɛm wae kin miks wit dis mɛrɛsin:

• Halopɛridɔl we dɛn kɔl
• Probenecid we dɛn kɔl Probenecid
• Stɛroyd mɛrɛsin dɛn, lɛk prɛdnison ɔ kɔtizɔn
• Valproik asid we dɛn kɔl

Dis list nɔto ɔltin we de insay di list. So, tɛl yu dɔktɔ bɔt ɔl di mɛrɛsin, ɔyl, vaytamɛn, ɛn it we yu de tek, ɛn if yu de smok, drink rɔm, ɔ yuz drɔgs we nɔ rayt. Dɛn kin gi yu patikyula advays.

Us ɔda tin dɛn a fɔ tek tɛm wit we a de tek dis mɛrɛsin?

If yu sik nɔr de bɛtɛ ɔr tan lɛk se yu de wɔs we yu de yuz dis mɛrɛsin, tɛl yu dɔktɔ ɔr mɛdikal tim kwik kwik wan.

Dɔn bak, yu dɔktɔ kin ɔda blɔd wok fɔ chɛk yu blɔd lɛvɛl (e.g., amonia lɛvɛl) we yu de tek dis mɛrɛsin. I impɔtant fɔ mek dɛn du dɛn tin ya ɔltɛm.

Wetin na di sayd ɛfɛkt dɛm we dis mɛrɛsin kin gɛt?

Lɛk ɛni mɛrɛsin, Sodium Phenylbutyrate kin mek sɔm pipul dɛn gɛt sayd ɛfɛkt. Nɔto ɔlman kin gɛt dɛn, bɔt i fayn fɔ no di wan dɛn we pɔsin kin gɛt.

Di sayd ɛfɛkt dɛm we yu fɔ tɛl yu dɔktɔ wantɛm wantɛm:

If yu gɛt ɛni wan pan dɛn sayd ɛfɛkt ya, tɛl yu dɔktɔ ɔ di mɛdikal tim wantɛm wantɛm, bikɔs dɛn kin siriɔs :

• Alɛji: Skin de rɔsh, it, ayv, swel na yu fes, lip, tɔng, ɔ trot. If dis apin, i kin mek i nɔ izi fɔ blo, so ripɔt am wantɛm wantɛm.
• Diziz, nɔr de balans ɔr kɔdineshɔn, kɔnfyushɔn ɔr trɔbul fɔ tɔk: If yu fil diziz, nɔr de stedi we yu de waka, nɔr ebul fɔ pe atɛnshɔn, ɔr nɔr de tɔk fayn.
• Di potashɔm lɛvɛl smɔl: Di sayn dɛm na di mɔsul dɛm we de pen ɔ kramp, wik ɔ taya we nɔ kɔmɔn, at bit fast ɔr nɔr de bit ɔltɛm, ɛn kɔnstipɛshɔn.
• Di anklɛ, an, ɔ fut kin swel.

Sayd ɛfɛkt dɛm wae nɔr kin bi big tin, bɔt if dɛn kɔntinyu, yu fɔ tɛl yu dɔktɔ :

Di sayd ɛfɛkt dɛm wae de dɔŋ ya nɔr kin siriɔs. Bɔt if dɛn kɔntinyu fɔ de ɔ de mɔna yu, tɛl yu dɔktɔ bɔt dɛn:

• Bɔdi smel: Nɔto lɛk swet, bɔt na difrɛn kayn smel.
• Chenj in teist: Fɔ fil se di teist fɔ it dɔn chenj.
• uman dεm kin gεt mεnstral saykl we nכ de rεgulεr כ spat.
• I nɔ kin want fɔ it igen.

Dis list nɔto ɔl di sayd ɛfɛkt dɛn we pɔsin kin gɛt. If yu notis ɛni ɔda tin we nɔ kɔmɔn, nɔ fred fɔ aks yu dɔktɔ bɔt am.

Aw a fɔ kip dis mɛrɛsin fayn fayn wan?

I rili impɔtant bak fɔ kip di mɛrɛsin dɛn fayn fayn wan.

• Kip dis mɛrɛsin usay pikin ɛn animal dɛn we yu lɛk nɔ go ebul fɔ rich .
• Dɛn fɔ kip am na say we di ples kol bitwin 15 ɛn 30 digri sɛlshiɔs (59 ɛn 86 digri F. Dat min se, bɔt nɔmal rum tɛmpracha.
• Protɛkt am frɔm wet. Dat min se nɔ kip am na say dɛn we wet lɛk di bafa.
• Kip di mɔt fɔ di mɛrɛsin bɔtul/paket tayt tayt wan .
• Nɔ yuz di mɛrɛsin afta di de we i dɔn dɔn . Trowe ɛni mɛrɛsin we dɔn pas.

Aw yu kin trowe mɛrɛsin we i dɔn fɔ yuz am ɔ we i dɔn pas?

I nɔ fayn fɔ jɔs trowe mɛrɛsin dɛn we dɔn pas ɔ we yu nɔ want na dɔti ɔ dɔŋ di tɔylɛt. Dɛn kin dɔn na di envayrɔmɛnt. So, yu nid fɔ trowe dɛn mɛrɛsin ya fayn fayn wan.

Yu kin du dis tu we dɛn:

1. Gi to wan program fɔ tek mɛrɛsin bak: Sɔm famasi ɔ polis gɛt dɛn program ya. Chek fɔ si if wan de na yu eria.

2. If no we nɔ de fɔ gi am bak: Chek di mɛrɛsin paket ɔ di liflet we de insay fɔ si if dɛn kin trowe dis mɛrɛsin wit di dɔti ɔ flɔsh am dɔŋ di tɔylɛt. If yu nɔ shɔ, aks yu dɔktɔ ɔ fama.

If yu kin trowe am wit di dɔti, na so:

• Tek di mɛrɛsin kɔmɔt na di bɔtul ɔ paket we i kam insay.
• Miks di mɛrɛsin paoda wit pusi dɔti, dɔti, kɔfi grɔn, ɔ ɔda tin we nɔ gɛt yus.
• Put dis miksɔp insay bag ɔ kɔntena we yu kin sidɔm fayn fayn wan.
• Dɔn trowe am na di dɔti.

We yu trowe mɛrɛsin dis kayn we, yu go mek dɛn nɔ fɔdɔm na di rɔng an ɛn ambɔg di envayrɔmɛnt.

Di tin dɛn we impɔtant pas ɔl fɔ mɛmba insay shɔt tɛm

Okay, so wi don tok plenti boht Sodium Phenylbutyrate. Fɔ mek i izi fɔ yu fɔ mɛmba, lɛ wi tɔk bak bɔt di impɔtant pɔynt dɛn:

• Dɛn kin gi dis mɛrɛsin mɔ to pipul dɛn we gɛt yuria saykl disɔda (UCD) fɔ ridyus di amonia lɛvɛl na di bɔdi.
• Dis nɔ kin mɛn di sik ɔltogɛda, bɔt i kin ɛp fɔ kɔntrol di sayn dɛm.
• Mek shɔ se yu tɛl yu dɔktɔ bɔt ɛni ɔda mɛrɛsin we yu gɛt (espɛshali dayabitis, at sik, kidni/liva sik), ɔda mɛrɛsin dɛn we yu de tek, alɛji, ɛn bɛlɛ bifo yu tek di mɛrɛsin.
• Tek di mɛrɛsin di mɔnt we dɛn tɛl yu, di tɛm we dɛn tɛl yu, wit spɛshal spun, ɛn jɔs lɛk aw yu dɔktɔ tɛl yu . I impɔtant bak fɔ fala di it we nɔ gɛt bɔku prɔtin .
• If yu mis wan doz, tek am jɔs afta yu mɛmba. Bɔt if i dɔn lɛf smɔl fɔ lɛ yu tek yu nɛks doz, skip di doz we yu mis. Nɔ tek wan dɛbul doz.
• If yu gɛt siriɔs sayd ɛfɛkt (alɛji, i nɔ izi fɔ blo, yu ed de tɔn bad bad wan, yu an ɛn fut dɛn de swel) , tɛl yu dɔktɔ wantɛm wantɛm.
• Kip di mɛrɛsin na say we kol ɛn dray usay pikin ɛn animal nɔ go ebul fɔ rich. Trowe di mɛrɛsin we dɔn pas fayn fayn wan.
• Dis mɛrɛsin na fɔ yu nɔmɔ. Nɔ gi am to ɔda pipul dɛn.

If yu gɛt ɛni ɔda kwɛstyɔn ɔ wɔri bɔt dis mɛrɛsin, nɔ shek fɔ tɔk bɔt am wit yu dɔktɔ ɔ fama. Dɛn de de fɔ ɛp yu. Wi de wish yu fɔ wɛl kwik kwik wan!

` Sodium Phenylbutyrate, Yuria Saykl Dizayd, UCD, amonia, mεdikeshכn, sayd ifekt dεm