I chaw ei chu i pum hnuai lam pan ai chuan i rilruah a tlakbuak ang maiin i inhriat ngai em? A nih loh leh tui tlem i in hnuah pawh i rilruah a rawn lang leh zel ang tih i hre mai thei em? Hetiang thil hi a chang chuan thil awmdan pangngai a ni. Mahse a chhunzawm zel chuan kan ngaihthah theih tur thil a ni lo. Vawiin hian hetiang harsatna thlentu, mahse hriat lar vak lo dinhmun kan sawi dawn a ni. Chu chu Achalasia a ni.
A awlsam zawngin, Achalasia chu eng nge ni?
Achalasia hi natna awm lo tak a ni a, kan chaw kawng (esophagus) a nghawng nasa hle. Hei hi awlsam taka hriatthiam theih nan kan chaw kawng (esophagus) hian a tlangpuiin engtin nge hna a thawh tih hi han en hmasa ila.
Kan esophagus hi kan hmui atanga kan pum (stomach) thlenga kal muscle atanga siam tube a ni ang tih han ngaihtuah teh. Chaw kan ei hian he tube chhunga thau te hi a chung atanga a hnuai lam thlengin wave ang maiin a inzawm khawm a (hei hi damdawi lam tawng chuan peristalsis an ti a), ei tur ball chu a hnuai lamah a nawr thla a ni.
He chaw kawng hnuai ber, pum nena a inzawmna hmunah hian ring of muscle a awm a, chu chu valve ang maiin a thawk a ni. Hei hi Lower Esophageal Sphincter (LES) kan ti a. Kawngkhar ang mai a ni. He kawngkhar (LES) hi ei tur ball a lo chhuk chuan a hun takah a inhawng a, chaw chu pum chhunga a luh hnuah nghet takin a inkhar leh thin. Hetianga khar a nih avang hian stomach acids te chu esophagus ah a rawn chho leh tawh lo.
Tunah chuan Achalasia vei chuan he thil kalpui danah hian buaina pahnih a tawk a ni.
1. Esophagus chhunga muscle te hian hna an thawk tha lo: Wave ang maia chaw hnuai lam (peristalsis) ka sawi tawh kha a thleng tha lo hle. A thleng lo tak tak emaw, chak lo takin a thleng emaw pawh nise.
2. Lower esophageal sphincter (LES) a inhawng lo: Chaw chu lo tla thla mahse, pum chhunga lut tur valve ang deuh (LES) chu a inhawng tur angin a inhawng lo. A tight reng a ni.
Chuvangin han ngaihtuah teh, ei tur chu a nawr chho lo va, a hnuai lamah kawngkhar pawh a inhawng lo. Chuti a nih chuan eng nge thleng? Kan ei leh in zawng zawng hi chaw kawng chhungah a tang vek a ni. Pum chhungah a lut lo. Chu chu a bul berah chuan Achalasia-a thil thleng chu a ni.
Hetiang dinhmun hian United States ang ramah mi 100,000 zinga pakhat vel chauh a vei a ni. Chu chu a tlem hle tihna a ni. Kum 25 leh 60 inkar puitlingte a nghawng tlangpui a, mahse a chang chuan chu aia naupang zawkte a nghawng thei bawk.
Achalasia vei mi pakhatin eng symptoms nge a neih?
Achalasia symptoms hi vawi khatah a lang vek lo. Zawi zawiin an rawn lut a. Thla tam tak emaw, kum tam tak emaw pawh he natna hi i nei thei a, mahse danglamna lian tham i hmu lo mai thei. Hun kal zelah a symptoms hi a na zual zel chauh a ni.
A hnuaia table-ah hian heng symptoms te hi eng nge ni tih i lo en ang u.
| Symptom a ni | A sawifiahna awlsam tak |
|---|---|
| Chaw ei harsa (Dysphagia) . | Hei hi a symptom ber leh langsar ber a ni. Chaw ei laiin rilru emaw, rilru emaw-ah blockage awm ang maiin a lang. A tirah chuan solid foods chauh a nghawng a, mahse a hnuah chuan liquid in pawhin he harsatna hi a awm thei a ni. |
| Regurgitation (chaw ei tur chu a rilruah a rawn chho leh) . | Chaw ei tawh, ei loh chu ka chhungah a rawn chho leh ta. Hei hi luak chhuak nen a inang lo. A thlum chu a thlum lo a, a chhan chu stomach acids nen a inhmeh loh vang a ni. Hei hi a bik takin mut laiin a thleng thei. |
| A rilru a na | Chest pain lo thleng leh kal lo chu a awm thei. Mi thenkhat phei chuan hei hi heart attack tiin an ngai sual mai thei. |
| Rihna tihtlem | A chhan chu chaw chu pum chhungah a lut tha lo a, ei a harsat avangin taksa chu chhan awm lovin a rihna a tlahniam tan thin. |
| Thil dang pawh a awm | Chaw ei harsa, thinlung natna, leh hiccups awm fo pawh a awm thei bawk. |
Engvangin nge hetiang hi a lo awm? Eng nge a chhan?
Dik tak chuan doctor-te chuan Achalasia hi eng nge a thlen tih hi 100% in an la chiang lo. Mahse theory lian ber pakhat chu autoimmune disease a ni tih hi a ni .
A awlsam zawngin kan taksa defence system (immune system) hian kan cell tha tak takte hi a rawn bei sual tihna a ni. Achalasia rama thil thleng nia rin chu hetiang hi a ni:
- Kan immune system hi virus infection ang chi thilin a tichak a ni.
- Tichuan he immune system hian kan chaw kawng chhunga thau hnathawh control tu nerve cell te chu a rawn bei sual tan ta a ni.
- He attack avang hian chu nerve cell te chu a chhe zauh zauh thin.
- Chu nerve cells te chu a bo chuan esophagus chhunga muscle te hian signal tha taka contract an hmu lo. Tin, lower esophageal sphincter (LES) hian relax turin signal a hmu lo bawk. Chu chu he harsatna thlentu a ni.
A pawimawh ber chu hei hi thlahtu leh hri kai theih natna a ni lo tih hi a ni. Chuvangin ngaihtuah buai a ngai lo.
Hetiang dinhmun avang hian eng harsatna nge awm thei?
Achalasia hi uluk taka enkawl a nih loh chuan harsatna lian tham engemaw zat a thlen thei a ni. Esophagus-a ei leh in tur awmkhawmte chu rilru chhungah a rawn chho leh thei a, thlipui hmangin lung chhungah a kal palh thei bawk. Chutiang a nih chuan hetiang ang harsatna hi a lo thleng thei a ni.
- Aspiration pneumonia: Ei emaw in tur emaw lung chhunga a luh avanga pneumonia na tak a ni.
- Lung infection leh bronchiectasis: Lung chhunga ei tur hip luh fo hian lung hi a tichhe reng thei hial a ni.
- Esophageal cancer vei theihna a sang: Achalasia hi rei tak a awm chuan esophagus cell-ah inthlak danglamna a awm a, esophageal cancer vei theihna hi mi pangngai aiin a pung tlem zawk.
- Malnutrition: Chaw ei hi taksain a hip lut tha tawk lo a, taksa chu a thau a, a tul angin ei leh in a dawng lo thei bawk.
Hei vang hian ei harsa i neih chuan ngaihthah la, a rang thei ang bera Doctor i pan tur a ni kan ti.
He natna hi engtin nge doctor hian a hriat theih ang?
Doctor i pan hunah i symptoms te a zawt ang che a, physical exam a ti ang che. Chumi hnuah chuan Achalasia i vei em tih finfiah nan test eng emaw zat neih a rawt ang. Test hman tlanglawn ber pathumte chu:
1. Esophagram (Barium Swallow) Test: He test-ah hian tui bik barium an tih chu in tur i pe a. He liquid hi X-ray-ah chuan a var a ni. I ei lai chuan X-ray thlalak hrang hrang lak a ni. Hei hian tui chu esophagus kal tlanga a kal dan te, khawi hmunah pawh a block em tih te, esophagus a zau em tih te, a hnuai lam a zim em tih te chiang takin a hmu thei a (hei hi ‘bird’s beak’ sign an ti bawk).
2. Esophageal Manometry: Hei hi Achalasia hriat theihna atana test tha ber leh dik ber a ni. Hetah hian i hnar kaltlangin i chaw kawng (esophagus) chhungah tube te tak te, flexible tak tak a lut a. Tui tlemte ei tura tih i nih laiin, tube-a sensor-te chuan i chaw kawng chhunga taksa ruh inzawmkhawmte pressure dik takin an teh thei a, wave ang maia chetna (peristalsis) a awm leh awm loh leh lower esophageal sphincter (LES) chu a relax tha em tih te a teh thei bawk.
3. Upper Endoscopy: He test -ah hian camera dahna flexible tube (endoscope) chu ka kaltlangin esophagus-ah dahin a chhung lam chu screen-ah direct-in en a ni. Hei hian chaw kawng a block em tih te, ei tur a tlakbuak em tih te, cancer ang chi natna dang a awm em tih emaw a nemnghet thei a ni.
Achalasia natna enkawl dan tur chu engte nge ni?
Achalasia enkawlna tum ber chu tight lower esophageal sphincter (LES) tih hahdam a ni a, chu chuan ei tur chu awlsam zawkin pum chhungah a kal thei a ni.
A pawimawh ber chu heng enkawlnate hian Achalasia hi a tidam kim thei lo a, nerve cell bo tawhte chu siam thar leh theih a nih loh avangin. Mahse, heng enkawlnate hian i natna lan chhuah dan thunun theiin nun pangngai i neih theih nan a pui thei che a ni .
Enkawlna kawng hrang hrang hi chi hnih ah then theih a ni a, non-surgical leh surgical te an ni. I doctor chuan i dinhmun, kum leh i duhzawng a zirin enkawlna dik ber tur a sawipui ang che.
| Enkawlna chi hrang hrang | Tih dan leh sawifiahna |
|---|---|
| Nonsurgical Treatment te pawh a awm bawk | |
| Balloon tihzauh a ni | Endoscopy an tih lai hian balloon chu tube hmangin esophagus hmun zau takah dahin an inflated a. Muscle tawi tawh chu a relax a, a hawnna chu a lian deuh hlek a ni. Hei hi light anesthesia hmanga tih a ni. He enkawlna hi vawi tam tak tih a ngai mai thei. |
| Damdawi ei tur | Damdawi hmang hian LES muscle tih hahdam theih a ni. Kawng khat chu Botox® (botulinum toxin) chu taksa ruh chhungah inject hi a ni. Pill nifedipine leh isosorbide te pawh a awm bawk. Mahse, hengte hian nghawng a neih chu rei lo te chauh a ni. |
| Surgery hmanga enkawl dan tur | |
| Laparoscopic hmanga Heller Myotomy hmanga tih a ni | Hei hi surgery neih tam ber leh hlawhtling ber a ni. Pum chhungah hian incision tenau tak tak tlemte siam a ni a, camera leh hmanraw nalh tak tak dah a ni a, chaw kawng hnuai lama muscle fibers nghet tak takte chu zawi zawiin an tan a, pawn lam atanga then a ni. Chumi hnuah chuan tightness chu a thlah a, kawngkhar chu a tizau ta a ni. |
| A rilru a buai em em a, a rilru a hah em em bawk a. . | Hei hi technique thar a ni. Taksa pawn lamah engmah incision siam lovin ka chhungah endoscope dahin, esophagus chhung atangin tight muscle chu an tan a ni. |
A tlem hle a, symptoms a nasat em em a, enkawlna dang a hlawhtlin loh chuan esophagus pumpui (esophagectomy) lakchhuahna tur operation (esophagectomy) neih a ngai mai thei.
Enkawl zawhah eng thilah nge fimkhur tur?
Achalasia symptoms hi enkawl hnuah a lo lang leh thei bawk. Chuvangin doctor nen hian rei tak in inbiak reng a ngai dawn a ni. A hnuaia mite hi a enfiah fo ang:
- I esophagus kaltlangin ei leh in tur tling tak chu i pum chhungah i pass thei em?
- Kawngkhar hnuai lam a tihzauh avangin pum chhunga acids te chu chaw kawng (GERD) -ah a luang kir leh theihna tur dinhmun a lo awm ta a ni.
- Esophageal cancer vei theihna a awm em?
He natna hian i dam chhung a nghawng dawn lo va, mahse enkawl dan dik leh enkawl zui a ngai ngei ang .
Achalasia nena kan awm chhung hian eng nge ka tih ang?
Enkawlna rual hian i nunphung leh ei leh in lama inthlak danglamna tenau te siam hian heng harsatnate hi nasa takin a tihziaawm thei a ni.
- I ei dan thlak danglam: I ei laiin i chaw chu a te tein then la, i ei tha la, ei la. I chaw ei rualin tui tam tak in thin ang che. Hei hian chaw chu a hnim reng ang a, awlsam zawkin a tlahniam ang.
- Thut ding chungin chaw ei rawh: Chaw ei laiin ding takin thu rawh. Chaw ei zawhah darkar khat emaw darkar hnih emaw chhung muhil suh. Hei hian gravity chu chaw chu a hnuai lam pan turin a pui ang.
- Mut hmain ei loh tur: Mut hma darkar 3-4 tal chu solid foods ei kha bansan rawh. Hei hian i pumin i mut hmain chaw chu a ei theih nan hun a pe ang.
- Lu chawi sangin mu rawh: Mut laiin extra pillow hmangin i lu chu sang deuhin dah la. Hei hian chaw kawng chhunga ei tur chu thlipui chhunga a luh theihna a ti tlem ang.
Eng ei tur nge ka ei loh tur?
Achalasia vei chuan ei tur thenkhat ei harsa a ti thei. A bik takin heng ei tur chi hrang hrangah hian fimkhur hle ang che.
- Chaw ei tur kawngkhar chhunga tang thei: apple hnah hring, grape, thlai raw, sa hrui hring emaw, sa hring emaw.
- Esophagus-a solid lo thei ei tur: Chhang, buhfai, potato, chips, leh pasta ang chi thilte chu esophagus-ah a inzawm khawm thei a, solid a lo ni thei.
- Esophagus ti na thei thil: ei tur tui tak tak, carbonated drinks (soda ang chi), zu.
Heng ei tur te hi i bansan vek a ngai lova, mahse i rilru hahdam loh chuan i hlat a tha ber.
Take-Home Thuchah a ni
- Achalasia hi chaw kawng ruh leh lower esophageal sphincter (LES) hnathawh that loh vang a ni.
- Chaw ei harsa, regurgitation, leh rilru natna te hi a lan chhuah dan ber a ni.
- Heng symptoms te hi a chang chuan a awm thin a, chuvangin ei harsa tlemte pawh ngaihthah suh.
- Dam kim theih ni lo mah se, zai leh enkawlna dang hmangin a natna lan chhuah dan chu hlawhtling takin a thunun thei a, mite chu nun pangngaia an nun theih nan a pui thei a ni.
- Heng symptoms te hi i neih chuan a rang thei ang bera chhungkaw doctor pan a, thurawn lak a pawimawh hle.











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