I ruh na, i hring, leh zing lamah i ke ruh a na deuh pawh a awm thei bawk, a dik em? A tam zawkah chuan hengte hi rheumatoid arthritis vang a ni thei. Mahse, he arthritis natna nen hian harsatna dang a awm thei tih i hria em, mahse chutiang chuan hriat lar a ni lo a, mahse hriat a pawimawh hle? Chu chu Felty Syndrome a ni. Hemi chungchang hi vawiinah hian chipchiar deuhin han sawi ila.
Felty Syndrome hi eng nge ni tak tak?
A awlsam zawngin sawi ila, Felty Syndrome hi thil pathum awmkhawm, a inzawmkhawm a ni. Anni chu:
- Rheumatoid Arthritis - Mi tam takin in hriat chian em em, ruh natna (joint inflammation) a ni.
- Neutropenia - Hei hi thisen a thisen var chi khat, neutrophils awm zat tlahniam tihna a ni.
- Splenomegaly - Hei hian taksa peng pakhat, spleen chu a pangngai aia lian a lo ni tihna a ni.
Rheumatoid arthritis (RA) atanga tan a ni fo. Condition dang pahnih hi RA complication angin a thleng thin. Doctor-te chuan hengte hi ‘extra-articular manifestations’ an ti a. Chu chu arthritis hi ruhroah chauh a awm lo va, a pawn lam ruhte a nghawng tihna a ni. Hei hi arthritis thlentu inflammatory process vang a ni. RA vei hian heng thil chi hrang hrangte hi ruhkawr pawnah a awm fo laiin, Felty Syndrome hi a awm lo deuh a ni.
Hei hian engtin nge a nghawng che?
Felty’s syndrome hi Rheumatoid Arthritis atanga tan a ni. Tichuan i ruhteah natna nasa tak leh hliam na tak i nei ta a ni. Tichuan, Neutropenia leh Splenomegaly ang chi natna a lo awm chuan i immune system a nghawng a ni . Neutropenia hi thisen var chi khat, neutrophils an tih tlahniam a ni. Heng neutrophils te hi kan taksa natna laka vengtu cell chi pawimawh tak a ni. Chuvangin an tlahniam chuan natna vei theihna chance a sang chho zel a ni. Spleen lian lutuk hi neutrophils tlahniam chhan dang a ni thei bawk.
Hetiang dinhmun hi engtiang chiahin nge a awm?
Felty’s syndrome hi rheumatoid arthritis vei zinga 2% vel ah a awm thin. RA ang bawkin Felty’s syndrome hi mipa aiin hmeichhiaah a let thum velin a tam zawk a ni. Ngaihven awm tak chu RA vei Felty’s syndrome vei zawng zawng deuhthaw hi ‘seropositive’ an ni. Chumi awmzia chu test-na chuan an thisenah rheumatoid factor antibodies an tih thil pakhat an nei tih a nemnghet tihna a ni. ‘seronegative’ mi, chu antibodies nei lote tihna a ni a, Felty’s syndrome hi an vei tlem hle.
Hei hi eng symptoms nge ni?
Vawi tam tak chu a lan chhuah hmasak ber chu rheumatoid arthritis a ni. Chung zingah chuan:
- Joint natna
- Joint swelling a awm
- Joint stiffness, a bik takin zing lamah
Mi thenkhat chuan an ruhkawr ah RA bakah symptom dang an nei thei bawk. Entir nan:
- Vun hnuaia ruhkawr bul hnaia lo awm (hengte hi rheumatoid nodules an ti) .
- Kawng leh kawrfual ang chi hmunah lymph node a hring
- Liver a hring thei a, khawih pawhin a na thei bawk.
- Mit leh hmui a vawt (hei hi Sjogren’s syndrome an ti) .
- Mit sen, hring (hei hi episcleritis an ti) .
- Vun natna, a bik takin keah
- Vun hnuaia thisen chhuak chhinchhiahna
- Lung natna avanga thawk harsa
- Thinlung vel a hring chhuak avanga rilru natna
- Khawsik
- Chauhna leh rilru hahna
- Chaw ei duh lohna emaw, sawifiah theih loha taksa rihna tlahniam emaw
Heng bakah hian Felty Syndrome hian symptom dang a nei bawk. A châng chuan heng symptoms te hi RA symptoms lo awm hmain a lo lang thei bawk.
- Infection tam tak, rei tak awm thei. Entirnan, khawsik, pum na, vun natna te hi a ni.
- Spleen a hring chhuak. Kut a hriat theih a, a na thei bawk.
- Vun rawng a danglam (spot ang chi).
Mahse mak tak mai chu, a chang chuan Felty Syndrome natna lanchhuahna awm lovin hriatchhuah theih a ni. Thisen test leh scan-ah pawh symptoms i hriat hmain condition pathumte hi i nei vek tih a hriat theih.
Hei hi eng kum atang nge a intan tlangpui?
Felty Syndrome hi kum upa lam, kum 50 leh 70 inkar ah a awm tlangpui a, mi tam zawk tan chuan Felty Syndrome hi kum 10 atanga kum 15 vel chhunga rheumatoid arthritis symptoms an neih hnuah a lo lang thin.
Engvangin nge Felty Syndrome hi a lo awm?
Rheumatoid arthritis hi ‘autoimmune natna’ a ni. Chumi awmzia chu keimahni taksa peng hrang hrangte chu hmelma ang maiin a bei thin tihna a ni. Scientist tam tak chuan Felty Syndrome hi RA natna khirh tak a ni an ti. Heng autoimmune natnaah hian kan taksa hian protein thenkhat lakah ‘antibodies’ a siam chhuak thin. Heng antibodies te hian kal a, chu protein te chu an man a, tihchhiat an nih thu an signal thin. Hei hi inflammation a pun dan a ni.
Heng antibodies te hi RA ah hian a awm reng lo mai thei. Mahse, Felty Syndrome vei tan chuan heng antibodies te hi a awm ngei ang. Heng antibodies awm hi RA a nasat chhan leh ruh pawn lama nghawng dang (extra-articular manifestations) a pun chhan a ni. Antibody nei RA hi ‘seropositive RA’ an ti a. Research atanga a lan dan chuan seropositive RA leh Felty Syndrome te hi ‘genetic factors’ thenkhat nen an inzawm a ni. Chumi awmzia chu eng emaw chen chu thlah kal zelah an inthleng thei tihna a ni.
Engtin nge rheumatoid arthritis (RA) hian neutropenia leh splenomegaly a thlen?
Neutropenia Lo awm Dan
Neutropenia hi thisen var (white blood cells) neutrophils an tih tlem a ni. Hei hi chhan lian tak pahnih a awm a. Pakhat chu i ruhro hian neutrophils a siam tling lo tih hi a ni. A nih loh leh, i taksaa neutrophils awmte chu a chhe vek tawh a ni. Felty Syndrome-ah chuan heng pahnih hi a thleng thei a ni. A hmaa kan sawi tawh angin autoimmune process hian ruh marrow-a neutrophils siam chhuahna a tibuai thei a, neutrophils siam tawhte chu a tichhia thei bawk. Tin, spleen lian lutuk hi neutrophils tlahniam chhan dang a ni bawk.
Splenomegaly a lo awm dan
I spleen hna chu i thisen atanga thisen cell hlui, tangkai lo tak takte filter chhuah hi a ni. Mahse i spleen a lian lutuk (splenomegaly) chuan a overactive a, thisen cell tha tam lutuk a paih chhuak tan thin. Rheumatoid arthritis hian a chang chuan spleen a ti lian thei bawk. A chhan dik tak erawh hriat chian a la ni lo. Neutropenia tel lovin spleen pawh a lian thei bawk. Tin, a tlem hle bawk, Felty Syndrome hi spleen lian lo a awm thei bawk.
Felty Syndrome natna hlauhawm tak takte chu engte nge ni?
Felty Syndrome hian i taksa hriselna a tichak lo a, natna khirh tak tak, natna khirh tak tak i vei fo theihna chance a sang zawk a ni . Natna tenau, enkawl awlsam tak i nei tlangpui a nih pawhin, he natna hi a nasat phah thei a, a awm reng thei a, a chang chuan nunna atana hlauhawm tak a ni thei bawk. Bacteria infection thunun loh chuan natna hlauhawm tak sepsis an tih chu a thlen thei a ni. Felty Syndrome vei te pawh hi cancer chi hrang hrang, lymphoma ang chi te an vei theihna a sang zawk bawk.
Mahse heng thu i hriat hian hlau suh. Heng hlauhawmnate hi a awm a, mahse enkawlna leh ngaihvenna dik tak nen chuan thunun theih a ni.
Engtin nge hei hi kan hriat theih ang?
Doctor-te chuan Felty Syndrome hi an hmuchhuak a, chu chu rheumatoid arthritis, neutropenia, leh splenomegaly te a awm vek tih an hriat chuan a ni. (A tlem berah chuan diagnosis hi spleen lian lovin tih theih a ni.)
Test tih tlangpui chu:
- Thisen test: Thisen chhiar kimchang, a bik takin neutrophils awm zat enfiahna atan.
- X-ray of joint: Arthritis a awm leh awm loh enfiah thin ang che.
- Spleen scan: Entirnan, ultrasound emaw CT scan emaw.
- Bone marrow biopsy hmanga lak chhuah: 1.1.Hei hian damdawi lam thil dang a awm loh nan a pui a ni.
Hei hi eng enkawl dan nge ni ang?
Felty Syndrome enkawlnaah hian thil tum lian tak pathum a awm a, chungte chu:
- Rheumatoid Arthritis natna hnuaia awmte control.
- Neutropenia a nasat chuan direct-in enkawl tur a ni.
- Infection ven leh a lo awm chuan enkawl.
Felty Syndrome hi enkawl loh emaw, control tha lo emaw, rheumatoid arthritis (RA) avanga lo awm a ni thei. Mi tam tak tan chuan neutropenia pawh hi an RA a that chhoh zel chuan a tha chho zel bawk. Chuvangin doctor-te chuan RA tan natna tidanglam thei antirheumatic drugs (DMARDs) tha tak tak thlan chhuah an tum hmasa thin. Tin, a theih ang anga immunosuppressant ei loh an tum bawk.
Felty Syndrome natna atan hian DMARD chi hrang hrang hman theih a awm a:
- Methotrexate leh folic acid (methotrexate natna tha lo tihziaawmna) .
- Abatacept tih hi a ni
- Rituximab a ni
- Leflunomide hmanga siam a ni
Mahse heng DMARDs hmang hian i neutropenia a lo tha lo a nih chuan, emaw, i neutropenia a na hle a nih chuan, emaw, natna hrik i neih tawh chuan, i doctor chuan i neutrophil count tihpun nan enkawlna dang a lo enchhin ang. Chûng zîngah chuan:
- Vaccine pakhat G-CSF (granulocyte colony-stimulating factor) tih a ni.
- Hun rei lote chhunga corticosteroid damdawi hman tur.
- ‘Splenectomy’ - Hei hian surgery hmanga overactive spleen lakchhuah tihna a ni.
Tin, doctor-te chuan natna hrik laka venhimna atan hma bik an la ang a, a bik takin i enkawlnain i taksa hriselna a nghawng a nih chuan. Anni chuan hetiang hi an rawt mai thei:
- Broad-spectrum antibiotics ei thin.
- Vaccine mamawh tur lak chhuah.
- I hmui leh ha hriselna hi a bik takin ngaihven rawh.
Felty Syndrome vei miin infection a neih chuan doctor-te chuan an ngai pawimawh hle. Hei hi i chungah a lo thleng a nih chuan enkawlna i lak nghal a ngai a ni . I doctor chuan damdawi chak tak a pe ang che.
Felty Syndrome natna vei hian engzat nge dam rei zawng?
Tunah hian Felty Syndrome vei te dam rei zawng statistics a la awm lo. Mahse, a tlangpuiin tun hnaiah enkawlna kawngah hmasawnna nasa tak a awm a. Chuvangin eng enkawlna pawh i tan a hlawhtling theihna chance tha tak a awm. Felty Syndrome natna avanga thihna hlauhawm ber chu natna khirh tak tak avanga thihna a la ni . Chuvangin, natna hrik laka invenna tura hma lak hian hun rei tak chhung hriselna atan danglamna nasa tak a thlen thei a ni.
Felty Syndrome hi rheumatoid arthritis (RA) natna hlauhawm tak leh ngaihthah fo thin a ni. Hun rei tak chhung RA control loh i neih chuan, emaw, i damdawi te chu a hma angin a thawk tha tawh lo a nih chuan Felty Syndrome i nei thei a ni. Mi thenkhat chuan symptom nei lovin an nei thin. I ruh natnain i thisen cell a nghawng thei tih hriat chu a buaithlak deuh thei.
RA i hmachhawn tawh a, leh symptom dang pawh a awm thei a nih chuan, diagnosis thar hmuh chu a buaithlak thei hle. Mahse Felty Syndrome hian symptom thar tam tak a thlen lo va, enkawlna dang a mamawh lo mai thei bawk. A pawimawh ber chu a hlauhawmna hriat chian a ni. I doctor nen thawhhona tha tak neiin i RA enkawlna leh natna kai laka invenna hmang hian Felty Syndrome hi i enkawl thei ang.
A tawp berah chuan thil hriat reng tur
Felty Syndrome hi Rheumatoid arthritis (RA) vei thenkhatah a awm thei a, a natna hi a ni. I thisenah thisen var neutrophils an tih zat a tlahniam (neutropenia) leh spleen a lian (splenomegaly) a ni.
- A hlauhawm ber chu hri kai fo hi a ni a, chuvangin hri kai laka inven a pawimawh hle.
- Hei hi hlauhawm deuh angin lang mah se, he natna hi damdawi lam enkawlna leh thurawn dik tak hmangin control theih a ni .
- RA i neih chuan heng symptom dangte hi lo thlir reng ang che. If you have any concerns , i doctor nen inbiakna neihpui ngei ang che. Anni chuan an pui thei ang che.
` Felty Syndrome, Rheumatoid Arthritis, Neutropenia, Splenomegaly, Arthritis, Joint Inflammation, Neutrophils, Spleen, Immunity te hi a awm thei lo











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