I doctor-in i fate chu pianpui thinlung natna avanga Fontan Procedure neih a ngai tih a hrilh che chuan hlauhna leh hlauhna nasa tak i nei thei a ni. Zawhna sangkhat chu rilruah a lo lang nghal mai thei. "Chu chu eng ang surgery nge ni?", "Engvangin nge ka fa hian hetiang hi a paltlang?", "Hei hnu hian a dam tha ang em?" Lungngai suh. Hemi chungchang hi thlamuang tak leh chiang takin sawi ila. He thuziakah hian hemi chungchanga i zawhnate chu a awlsam zawngin chhan ka tum ang.
A awlsam zawngin Fontan Procedure chu eng nge ni?
Hei hi hrethiam tur chuan kan thinlung hnathawh dan hi tlem han hrechhuak hmasa ila. Thinlung hrisel chuan chamber lian pali a nei a. A chung lamah pahnih leh a hnuai lamah pahnih. Heng ventricle hnuaia chamber lian leh chak tak pahnih hi kan ti a ni . Chamber pakhat chuan taksa thisen oxygen tlachham, "bawlhhlawh" chu a khawlkhawm a, chu chu lungah a pump lut a, oxygen a hmu thei a ni. Chamber dang chuan oxygen tamna, "thianghlim" thisen chu lung atanga lakkhawmin taksa dang zawng zawngah a pump chhuak thin. Heng pahnih hian tui motor pahnih angin hna an thawk a.
Amaherawhchu, naupang thenkhat an lo pian chuan heng cell pahnih zinga pakhat hi a lo thanglian kim lo. Tichuan, cell tha awmchhun chuan heng hna pahnih hi a thawk tur a ni. Chu chu lungah leh taksa pum puiah thisen a pump chhuah a ngai tihna a ni. Chu motor chuan motor pakhat hmanga in pahnih tui a pump a ngaih hunah engzat nge a rit tih hi han ngaihtuah teh. Chuvangin, he cell pakhat hian phurrit rit tak hnuaiah hna a thawk a ngai a ni.
Fontan procedure hian a tih dan chu hetiang hi a ni : Surgeon te chuan thinlung lam panna tur "shortcut" te tak te an siam thin. Hei hian taksa hnuai lam atanga oxygen tlachham thisen chu lungah direct-in a luang lut thei a, thinlung chu a paltlang thei a ni. A bul berah chuan thinlung chhunga lirthei tlan tam tak thenkhat chu a bypass a ni.
Hetiang shortcut siam hian chu cell pakhat, thawkrim em em lai phurrit chu nasa takin a tlahniam a ni. Tichuan, chu cell chuan a chakna zawng zawng hmangin thisen thianghlim, oxygen tamna chauh taksaah a pump thei a ni. Hei hian nausen taksain oxygen a dawn zat a tipung a, a rilru a hahdam zawk thin.
He surgery hi eng naupang nge an tih?
Fontan operation hi vawi khata tih tur a ni lo. Naupang single-chamber heart defect nei tan surgery hrang hranga step pathumna leh hnuhnung ber atan tih a ni tlangpui. Chumi hma chuan naupang kum leh dinhmun a zirin surgery dang pakhat emaw a aia tam emaw neih a ngai thei a ni.
| Surgery hmasa chi hrang hrang | A awlsam zawngin, eng nge thleng? |
|---|---|
| Norwood kalphung a ni | Thinlung dinglam hian taksa leh lungah thisen pump turin a pui a ni. Hei hi naute pian hnu kar hmasa berah tih a ni tlangpui. |
| Glenn kalphung a ni | Taksa chunglam a oxygen tlachham thisen chu lung lam pan nghal a ni. Hei hi a tlangpuiin stage hnihna a ni. |
| BTT shunt (Blalock-Taussig-Thomas-a shunt) hmanga tihchhuah a ni. | Artificial tube hmangin lungah thisen kal a tipung a. |
| Pulmonary artery band a ni | Lung lama thisen kal dan a control a, taksa peng dangah thisen tam zawk a kal tir bawk. |
Fontan surgery neih ngai condition lian ber berte
He surgery hi pian tirh atanga thinlung siam that lohna hmun tlemteah a ngai ber a ni. Chungte chu:
- Hypoplastic left heart syndrome: Hei hi a chhan tam ber a ni. Hetiang dinhmunah hian thinlung veilam hi a lo thang tha lo.
- Hypoplastic right heart syndrome: Hetiang dinhmunah hian thinlung dinglam hi a lo thang tha lo.
- Tricuspid atresia: Thinlung dinglamah valve a awm tha lo.
- Pulmonary atresia: Pulmonary atresia: Lung chhunga thisen phurtu valve chu a block a.
- Double inlet left ventricle: Thinlung chunglam chamber pahnih atanga thisen lo chhuak chu left ventricle-ah chauh a lut thin.
- Congenital heart condition dang engemaw zat a awm bawk.
Heng hmingte hian hlauhna a tizual thei che a ni. Mahse hengte hi doctor-te’n i hriat theihna tura an hman hmingte chauh a ni. A pawimawh ber chu heng dinhmun zawng zawngah hian heart valve pakhat chauh hi a buai lutuk a ni. Fontan procedure hian chu strain chu tihziaawm a tum a ni.
Surgery neih hmain eng nge thleng?
Fontan surgery hi naupangte tih a ni tlangpui.Kum 2 leh 5 inkar.A chang chuan kum 15 vel an tlin thlengin hei hi tihkhawtlai theih a ni. Mahse he surgery hi mi zawng zawng tan tih theih a ni lo. Doctor-te chuan test thenkhat an ti hmasa ang a, i fa chu he surgery atan hian a tling em tih an enfiah ang.
Entirnan, naupang hnathawk single cell chu pump tha thei tur khawpa chak a ni tur a ni. Tin, lungte tanpuina tel lova thisen lo lut chu direct-a pawm thei khawpa hrisel a ngai bawk.
Operation hmain a hnuaia test te hi tih thin a ni:
- Transthoracic echocardiogram (TTE): Hei hi thinlung scan ang mai a ni. Thinlung pindan, valve leh thisen kal dan te chiang takin a hmu thei a ni.
- Electrocardiogram (EKG): Hei hian thinlung electrical activity a test a, chu chu heartbeat pattern a ni.
- Heart catheterization: Tube (catheter) te tak te tak mai chu ke emaw, kut emaw chhunga thisen kalna kawng kaltlangin thinlungah an kal a, thinlung chhunga pressure leh oxygen level an teh thin. Hei hian operation hmaa thinlung dinhmun dik tak a pe thei a ni.
- Thâwk leh oxygen level enfiah.
- A châng chuan CT emaw MRI scan emaw pawh a awm ṭhin.
Heng test zawng zawng hi a him thei ang bera surgery leh hlawhtling thei tura tih a ni.
Surgery neih chhung hian eng nge thleng?
Operation room-ah chuan naupang chu a mut tir turin anesthesia pek hmasak a ni a, chutiang chuan a natna engmah a hriat loh nan. Surgery neih chhung hian heart-lung machine hmangin lung leh lung hnathawh chu hun eng emaw chen atan an thawk thin.
Chumi hnuah chuan surgeon chuan taksa hnuai lam atanga oxygen tlachham thisen phurtu thisen kalna bulpui inferior vena cava chu conduit hmangin lung lama thisen phurtu pulmonary artery-ah a thlunzawm a ni. Hei hi a hmaa kan sawi tawh "shortcut" siam dan chu a ni.
A châng chuan, he surgery neih rual hian siamthatna tenau dang, heart valve siamthat ang chi te pawh hi tih theih a ni.
Surgery pumpui hi darkar li atanga darkar nga vel a ni thei tlangpui . Chumi chhung chuan medical team te chuan an be fo ang che a, i fa dinhmun update an pe ang che.
Surgery hian eng hlawkna leh hlauhawmna nge a neih?
Surgery dang ang bawkin Fontan surgery hian hlawkna a neih bakah hlauhawmna engemaw zat a nei bawk.
A thatna ber chu thinlunga hnathawh tur a tihtlem avangin a hna a awlsam phah hle. Tin, oxygen tamna leh oxygen tlem thisen inzawmkhawm a tlem avangin taksain oxygen a dawn zat a pung bawk. Naupang hmui leh kut zungtang chu a sen (cyanosis) a tlem a, a thawkrim zawk theih nan chakna a nei tam zawk bawk.
| Operation hnua harsatna awm thei te | |
|---|---|
| Hun rei lote chhunga harsatna awm thei | Hun rei tak chhunga harsatna awm thei |
| Kidney a chhiat phah | Protein hloh enteropathy (protein ei harsa) 1.1. |
| Lung lam chak lohna | Thisen zam (embolism) 1.1. |
| Lungphun mumal lo | Liver natna (Fontan nena inzawm thin natna - FALD) . |
| Liver hnathawh danah nghawng a nei | Mucus thick (plastic bronchitis) avanga thawkna kawng tihkhawtlai . |
| Lung vel a tui awmkhawm (pleural effusions) . | |
Heng thilte hi hmuh a hlauhawm thei a, mahse hre reng ang che, medical team hian heng hlauhawm zawng zawng hi an hre vek a ni. An lo thlen chuan ven leh enkawl turin an inpeih reng a ni.
Surgery hnua nun chu engtin nge a awm?
Surgery zawhah naupang chu intensive care unit (ICU)-ah dahin uluk taka enkawl a ni. Ni engemaw zat hnuah an dinhmun a ṭhat chuan general ward-ah sawn an ni. Naupang pakhat chu damdawi inah a vaiin ni 7 atanga ni 13 chhung a awm thei .
In lama i haw hmain doctor leh nursing staff te chuan i naute enkawl dan tur te, damdawi pek tur te leh a natna lan chhuah dan fimkhur tur te chipchiar takin an hrilhfiah ang che.
Engtikah nge doctor nen inbiakna neih a ngaih?
In lama i haw hnuah heng symptoms te hi i hriat chuan doctor i ko nghal tur a ni:
- Surgery hliam atanga thisen emaw tui dang emaw a luang chhuak a nih chuan.
- Khawsik emaw, hri kai chhinchhiahna dang (khawsik, hring, sen hring) i neih chuan.
- Thâwk harsa a pun chuan.
Naupang Fontan operation nei tawh chuan dam chhung damdawi lam enkawlna a mamawh dawn a ni. Thla 6 atanga thla 12 danah doctor an pan a ngai tlangpui ang . Tin, an thinlung leh thin (liver) dinhmun enfiah nan test neih reng a ngai dawn bawk a ni.
A pawimawh ber chu Fontan procedure hi "damdawi" a ni lo. Naupang thinlung hnathawh thatna tur a ni. Chuvangin hun rei tak chhung enkawl zui a pawimawh hle.
Nun rei zawng chungchangah eng nge i sawi theih ang?
Hei hi nu leh pa tam tak tan chuan zawhna lian tak a ni. Fontan operation hnua dam rei zawng chu naupangin pianpui thinlung natna a neih nasat danah a innghat a ni.
Mahse, tunlai hian damdawi lam hian hma a sawn nasa hle. Mi tam zawk chu operation hnu kum 10 vel an dam. Mi sawm zinga pariat chu kum 30 aia rei an dam . Dik tak chuan Fontan operation nei tawh tam tak chu tunah chuan kum 40 hnuai lam thlengin an dam tawh a ni.
Hun a kal zel a, mi thenkhat thinlung pump theihna a chak lo thei a, a nih loh leh thin (liver) a nghawng thei bawk. Hei hi "Fontan hlawhchham" an ti. Chutiang hunah chuan , thinlung thlak a ngai mai thei. Mahse hei hi mi zawng zawngin kan mamawh vek lo.
I fa hian thinlung natna khirh tak a nei tih leh zai a nih dawn tih i hriat chuan rilru natna nasa tak i nei thei a ni. Hlauhna te, lungkhamna te, leh hmalam hun hriat chian lohna te hi thil pangngai a ni vek. Mahse hriat tur pawimawh ber chu nangmah chauh i ni lo tih hi a ni .
He surgery zawh hian i fa chu naupang dang ang bawkin a khel thei a, a zir thei a, a thang lian thei a, nun a hlim thei bawk. An chau thuai mai thei a, damdawi lam test dang pawh an mamawh thei bawk. Mahse, damdawi lam thurawn dik tak leh i hmangaihna leh i ngaihsakna nen chuan nun famkim, hlim tak an hmang thei a ni.
Take-Home Thuchah a ni
- Fontan Procedure hi nausen piang, ventricle hnathawk pakhat chauh neia piangte thinlung surgery bik a ni.
- Hei hian thinlunga thisen kalna tur "shortcut" a siam a, chu chuan single working cell-a hnathawh tur a tihtlem phah a ni.
- Hei hi surgery hrang hranga stage hnuhnung ber a ni tlangpui a, naupang kum 2 leh kum 5 inkar chu tih thin a ni.
- Fontan surgery hian natna hi a "tidam" kim lo nain, naupang chu nun tha zawk, active zawka nung turin nasa takin a pui thei a ni.
- Operation hnuah doctor nena enkawl reng reng hi i dam chhung atan a pawimawh hle.
- Damdawi lam enkawlna leh enkawlna dik tak an neih chuan he surgery nei naupang tam tak hi hlawhtling tak leh nun famkim tak an hmang thin.











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