I naute hmai chu triangle ang maiin a lang em? Metopic Craniosynostosis chungchang hi i zir dawn nia.

I fa naupang lu pianziaah hian thil danglam tak i hmu em, a bik takin a hmai, a pianzia chu triangular a ni mai thei? Nu emaw pa emaw chuan chutiang thil an hmuh chuan tlemin an lungkham deuh hi thil pangngai a ni. Chutiang huna i rilruah zawhna lo awm thinte chhanna atan vawiin hian Metopic Craniosynostosis tih natna chungchang kan sawi dawn a ni. A chang chuan hei hi Trigonocephaly an ti bawk.

Metopic Craniosynostosis hi eng nge ni?

A awlsam zawngin, metopic craniosynostosis hi piansualna a ni . Naute lu emaw, luruh emawa hmalam ruh pahnih chu a hun hmaa (premature fusion) an inzawm khawm hian a thleng thin a, chu chu nausen pum chhungah emaw, nau piang lai emaw pawhin a ni. Ngaihtuah teh, kan luruh hi ruh pakhat atanga siam a ni lo va, ruh chi hrang hrang atanga siam a ni zawk. Heng ruh chi hrang hrangte hi "sutures" an tih hian an inzawm khawm a ni. Heng sutures te hi ruh lo thang lianna hmun ang mai a ni. Naute thluak a lo thanglian zel chuan heng suture te hian luruh chu a awm theih nan a lo thang lian thin.

Tunah chuan metopic craniosynostosis-ah chuan naute thluak a lo thanglian kim hmain hmalam ruh pahnih inkar seam, "metopic suture" tia koh chu a khar ta a ni. Hei hi naute hmai chu triangular shape a neih hun a ni. Hei hi trigonocephaly an ti bawk.

Hetiang dinhmun hi engtiang chiahin nge a awm?

Tun hnaia zirchianna hrang hrangah chuan metopic craniosynostosis hi craniosynostosis chi hnihna a ni thei tih a tarlang. Mahse, ram hrang hrangah a vei dan a inang lo. United States ang ramah chuan he natna hian nau piang thar 700 zinga pakhat atanga 15,000 zinga pakhat thlengin khawi hmunah pawh a nghawng niin an chhut.

Hei hi eng symptoms nge ni?

Naute metopic craniosynostosis vei chuan a hnuaia symptoms te hi a nei thei a ni:

• Naute lu leh hmai ruh te a lo thang dan pangngai lo .
• Naute luruh chhungah thluak chu an nawr lut a, chu chu intracranial pressure tihsan tihna a ni .
• Mit hmuhna lama harsatna a awm .

Engtin nge naute hmel a danglam?

Hetiang dinhmun hian naute hmel lan dan a nghawng a ni. Hetiang hian a lang thei:

• A hmai chu a sei, a zungpui, a sir pathum ang mai a ni .
• Mit chu a inhnaih hle niin a lang .
• Ka mitmeng chu a sang hle niin a lang .
• Lu hnunglam chu a zau takin a lang .

Ngaihtuah teh, naute hmai chu a lai atanga rawn chhuak ang maiin a lang.

Engvangin nge hetiang hi a lo awm? A chhan engte nge ni?

Metopic craniosynostosis thlentu ber chu thluak a lo thanglian kim hmaa hmalam ruh inzawmkhawm vang a ni .. Chu chu a fuse hmasa tihna a ni. Mahse doctor-te chuan heng ruhte hi an inzawm rang lutuk chhan chiang tak an la hmu lo. Mahse, zirchianna chuan thil engemaw zatin chanvo a nei thei tih a tarlang a:

• Genetic changes (entir nan, FREM1 leh SMAD6 genes te genetic mutations).
• Naupai laiin nuin a ei damdawi thenkhat (e.g., valproic acid leh clomiphene citrate ang chi damdawi) avanga side effect angin.
• Nu hian thyroid natna a nei a .
• Nausen nausen awmna uterus chhunga awm dan .
• Genetic condition dang, Williams syndrome ang chi symptom angin .

Hemi atan hian tute nge hlauhawm ber?

Metopic craniosynostosis natna vei fa neih theihna i neih theihna a sang thei a, chu chu:

• Twins i beisei a nih chuan .
• I hriselna dinhmun hnuaia awm thyroid natna emaw zunthlum emaw i neih chuan .
• Epilepsy ang chi natna damdawi thenkhat i ei chuan.
• Zuk leh hmuam thil i hman chuan .

Nausen piangsual nei neih theihna tur hlauhawmna hriat belh duh chuan i doctor hnenah preconception counseling dil rawh. Nausen piangsual nei i neih theihna tur a tihziaawm thei tur thurawn i dawng thei ang .

Hei hian eng harsatna nge a thlen theih?

Naupang a lo puitlin a, sikul a kal tan hma chuan metopic craniosynostosis avanga harsatna awm thei chu a lang lo thei. Harsatna awm tam ber chu:

• Hmasawnna tlai (thusawi leh tawng emaw motor thiamna emaw).
• Cognitive development lama harsatna awm thei .
• Nungchang inthlak danglamna (irritability ang chi).
• Intracranial pressure sang zawk chhinchhiahna ( lu na leh mit lama harsatna te pawh a tel ).
• Lu hi taksa peng dang nena khaikhin chuan a thang zawi zawi a .

Engtin nge doctor-te hian hei hi an hriat chian?

A châng chuan, naupai kum hnihna leh thla thumnaah nau neih hmaa ultrasound scan- naah doctor chuan hei hi a ringhlel thei a ni. Mahse, a tam zawkah chuan naute pian hnua nausen piang thar taksa enfiahnaah he natna hi hriat chhuah a ni .

Doctor chuan naute lu chu a chung lam (vertex) atanga hmai sir lam thlengin uluk takin a enfiah ang. Vawk mit atanga thlir chuan naute lu chu a zungbun ang ni lovin triangular emaw conical emaw angin a awm a nih chuan trigonocephaly an tih natna a ni tih hriat theih a ni.

Naute ruh ruh pianzia hriat chian nan X-ray emaw CT scan (Computed Tomography - CT scan) ang chi test te pawh an ti thin. Heng test atanga information kan hmuh te hian enkawlna ruahmanna siamnaah a pui thin.

He dinhmun hi engtiang chiahin nge a pawi thei ang?

Metopic craniosynostosis nasat dan hi mi hrang hrangah a inang lo thei. A nasat dan chu luruh ruhte inzawmkhawm chak lutuk avanga angle lian leh te a zirin a ni. Entir nan:

• Mild case-ah chuan hmai pianziaah hian a danglamna tlemte chauh a awm.
• A nasat chuan a hmai chu a hrual nasa hle a, triangular emaw conical emaw angin a awm ta a ni.
• Heng pahnih inkarah hian hun remchang tlemte a awm a ni.

Hei hi engtin nge enkawl a nih?

Metopic craniosynostosis a na lo a nih chuan , emaw, hmaiah natna lian tham nei lo metopic ridge chhuak chauh a awm a nih chuan, damdawi lam enkawlna a ngai lo mai thei

Mahse, trigonocephaly chu a hniam emaw, a na emaw a nih chuan, naute lu chu siam danglamin, thluak chu a ṭhanlenna tûr hmun a neih theih nân operation tih theih a ni A tul chuan surgery hian thluaka pressure a tihziaawm thei bawk.

Metopic craniosynostosis enkawlna atan hian surgery chi hnih a awm a, chungte chu:

1. Endoscopic hmanga operation tih tur:

• He surgery hi naute naupang, a tlangpuiin thla 4 an tlin hmain tih a ni a, a tam berah thla 6 .
• Surgeon chuan naute hmaiah hian incision te tak te a siam a, chuta tang chuan hairline a intan a ni.
• Tichuan, endoscope (camera nei tube te tak te) hmangin metopic suture chunga ruh strip pakhat chu lakchhuah a ni. He endoscope hmang hian surgeon chuan luruh chhung chu a hmu thei a, incision lian tak siam lovin surgery chu a ti thei a ni.

2. Open surgery (Open surgery - Cranial Vault Remodeling) tih tur a ni:

• He surgery hi naute thla 6 leh thla 12 inkar te hi tih thin a ni .
• A tam zawkah chuan hei hi neurosurgeon leh plastic surgeon te thawhhonain an ti thin.
• Surgeon chuan naute lu vunah hian endoscopic surgery aiin incision lian zawk a siam thin .
• Tichuan, lu ruh peng hrang hrang, a pianzia danglam tak takte chu lakchhuah a ni. A dawtah chuan ruhte chu an tan a, an siam thar a, an inzawm leh a, chu chuan lu lem dik tak siam a ni.Hei hian naute thluak chu hmasawnna tur hmun a pe tam zawk a ni.

Naute hian operation hnuah helmet a bun a ngai em?

Endoscopic surgery hnuah i naute hian thla 12 vel a tlin hma chuan helmet bik a bun a ngai dawn a ni. He helmet hian naute luruh chu zungbun ang maia siam turin a pui thin. Helmet hi open surgery hnuah a ngai lo tlangpui , mahse i surgeon chuan chutiang lam chu a fuih ang che.

Enkawlna hrang hrangte hian side effect a nei em?

Surgery dang ang bawkin, heng surgery pahnih hmang hian risk leh side effect engemaw zat a awm thei a:

• Thisen tlakchhamna .
• Kaichhawng .
• Thluak thisen chhuak (Hematoma) .

I fa surgeon chuan operation hmain heng side effects te hi a hrilhfiah ang che. Open surgery hian endoscopic surgery aiin risk a keng tel zawk a ni . Tin, operation leh damna hun a rei zawk bawk.

A châng chuan, operation hnua thisen chhuak a awm chuan, naupang chu thisen pek a ngai mai thei . Hei hi open surgery-ah hmuh tur a tam ber.

Trigonocephaly hian a natna siamthat nan operation dang neih belh a ngai hi thil awm lo tak a ni a , mahse a ngai mai thei.

Operation hnuah a dam leh theih nan eng chen nge a duh?

I fa chu operation a nih atanga kar tlemte chhungin a dam tha hle mai thei. Mahse, a dam kim theih nân thla hnih aṭanga thla thum a la ngai thei . Ruh dam leh lo thang leh hian kum khat vel a daih thei. I fa surgeon chuan a dam hun tur leh operation hmaa i beisei tur chungchang a sawipui ang che.

Ka fa hian metopic craniosynostosis a vei a nih chuan eng nge ka beisei ang?

Metopic craniosynostosis hi thil awm lo tak ni mahse, naupang tinte a nghawng dan chu a inang lo thei hle. Naupang thenkhat chuan lu pianziaah danglamna tenau tak tak chauh an nei thei a , enkawl an ngai lo mai thei . Mi dangte chuan lu pianzia siam\hat nan operation an mamawh thei a, an hmasawnna tihkhawtlai ang chi harsatna awmte enkawl an ngai thei bawk.

Surgery hmanga enkawlna hi a hlawhtling a, a side effect pawh a tlem hle. Endoscopic surgery an neih hnuah naupang chu damdawi inah zan khat dahin uluk takin an enfiah thin. Ni khat emaw ni hnih emaw chhungin an haw thei tlangpui. Open surgery hmangin naupang hi darkar 24 chhung intensive care unit-ah dah a ni a, darkar tin doctor-te chuan an enkawl zui zel a ni. Chumi hnuah chuan damdawi in ward dangah ni engemaw zat emaw, kar khat emaw chhung chu an dam leh dan enfiah turin an sawn a ni.

Damdawi ina a awm chhung hian naupang lu leh hmai a na thei. Hei hi thil pangngai a ni. Mit a hring thei a, ni hnih atanga ni thum chhung a khar thei bawk. Chumi hnuah chuan a hring chu a tlahniam zauh zauh ang.

Naupang endoscopic surgery nei tawhte chuan thla 12 an tlin thlengin helmet an vuah a ngai a, hei hi nu leh pa thar tan chuan a harsa deuh thei a ni. A chhan chu an fa chu a dam hma loh chuan midang aiin a lang danglam dawn a ni. Nu leh pa tam tak chuan an fate mizia nena inmil turin stickers mawi tak tak hmangin helmet hi an chei thin.

I naute chu a hmel a danglam avângin, miten chumi chungchângah zawhna an zawt mai thei. Heng thu chipchiar tak takte hi mi zawng zawng hnena sawi chhuah chu i harsat mai thei. Chhungkaw tam tak chuan hetiang hunah hian rilru lam hriselna lama mithiamte biak hian thlamuanna an hmu a ni.

Hetiang dinhmun hi ven theih a ni em?

Tunah hian metopic craniosynostosis ven dan tur a la awm lo . Mahse, naupai hma leh naupai laia hrisel taka awm dan tur leh nau piangsual laka inven dan tur chungchang doctor nen inbiakna hmangin i hlauhawmna chu i tihtlem thei a ni.

Engtikah nge ka fa hian doctor a hmuh ang?

I fa chu a dam kim tawh chuan specialist team (craniofacial team) chuan a puitlin thlengin an enkawl ang.

I fa chu an kum nena inmil developmental milestone a thlen tlai a nih chuan doctor pan nghal rawh. Entirnan, kea kal emaw, an thu hmasa ber sawi emaw. Metopic craniosynostosis vei naupang tam zawk chu an lo thanglian tlangpui a, mahse naupang thenkhat chu an thanlenna a tlai thei hle. Midang aiin hun tlem an mamawh zawk mai thei. Doctor chuan i fa chu an thil tum a thlen theih nan a pui thei a ni.

Operation hnuah i surgeon chuan fimkhur tur thil, infection ang chi te information a pe ang che. Thil danglam bik i hriat chuan doctor rawn nghal tur a ni.

Ka fa doctor hnenah eng zawhna nge ka zawh ang?

• Ka fa hian operation a mamawh em?
• Eng ang surgery nge i rawt?
• Enkawlna hian side effect a nei em?
• Engtikah nge operation zawhah check-up turin ka lo haw leh ang?
• Ka fa hian hmasawnna kawng hrang hrang a thlen tlai a nih chuan engtin nge ka tih ang?

I naute piang thar lu pianzia chu beisei aia danglamin a lang tih hmuh chu thil mak tak a ni thei. Mahse, lungngai suh. I naute a pian veleh i medical team chuan metopic craniosynostosis an hmuchhuak ang a, i naute thanlenna leh thanlenna tichhe thei tur harsatna awm lo turin an enkawl ang. Surgery hian i naute thluak leh luruh a lo thanglian tha hle ang.

Thupui tawi (Take-Home Message) 1.1.

I naute hmai chu triangular angin a awm tih i hmuh chuan metopic suture chu a hun hmaa khar a nih thu chhinchhiahna a ni thei. Hei hi metopic craniosynostosis emaw trigonocephaly emaw an ti a .

Hlau suh!A natna a na lo a nih chuan enkawl a ngai lo mai thei. A na zawk a nih chuan lu pianzia siamthat nan leh thluak tha taka a than theih nan surgery tih theih a ni. Surgery hi a hlawhtling a, naupangte pawh an dam thuai thin. Surgery zawhah hian hun engemaw chen chu helmet bik i bun a ngai mai thei.

A pawimawh ber chu doctor thupek uluk taka zawm a, i fate hmasawnna nena inzawmna nei reng hi a ni . Zawhna emaw rinhlelhna emaw i neih chuan Doctor hnenah zawh hreh suh. I fa chu hrisel leh hlim taka seilian turin kan duh vek!

` Metopic craniosynostosis, trigonocephaly, nausen luruh, hmai pianzia, piansualna, thluak thanlenna, surgery