Kan taksa peng pawimawh tak tak, thinlung, lung, thin, leh pum te hi kawng khata inrem a ni tih kan hre vek a. A tlangpuiin heng taksa peng hrang hrangte hi midang zawng zawng ang bawkin a sir khatah, a awm dan inangah an inrem a ni. Mahse, a tlem hle mai, mi taksa peng hrang hrangte chu darthlalang lem ang maiin a inthlak danglam vek thei tih i ngaihtuah ngai em? Vawiin hian chutiang dinhmun danglam tak, mahse a tam zawkah chuan hlauhawm lo tak chu kan sawi dawn a ni. Hei hi medical science-ah chuan (Situs Inversus) an ti a.
Hei hi eng nge ni (Situs Inversus)? A awlsam zawngin i hrethiam ang u.
A awlsam zawngin sawi ila, Situs Inversus hi genetic condition hmuh tur awm lo tak a ni a, i rilru leh i pum chhunga taksa peng hrang hrangte chu mihring taksa pangngaiah ni lovin, darthlalang lem ang maiin a inhmachhawn a ni.
Kan taksa peng hrang hrangte hi a pangngaia awm dan hi han en ila. Kan taksa peng zawng zawng deuhthaw hi veilam leh dinglam (left-right configuration)-ah an lo thang lian a. Hei hi dinhmun pangngai (Situs Solitus) kan ti a ni. Entirnan, thinlung tip chu vei lamah a tilt a, liver chu ding lamah a tilt a, pum leh spleen chu vei lamah a tilt a.
Mahse, hei hi (Situs Inversus) nei tan chuan a kalh zawng tak a ni. Chu chu:
- Thinlung veilam atrium leh veilam lung chu rilru dinglamah a awm thei.
- Pum i en chuan liver leh gallbladder chu dinglam ni lovin veilam lamah a awm thei.
- Pum leh ril chu veilam ni lovin dinglamah a awm thei.
Hetianga taksa peng pum pui hi kan inher chuan (Situs Inversus Totalis) an ti a ni. Hei hi harsatna dang awm lovin amah chauhvin a thleng thei a ni. Mahse, a châng chuan he natna hi piansualna dang emaw, symptoms inzawmkhawm (syndrome) engemaw zat nen emaw hmuh tur a ni. (Situs Inversus) hi (Primary Ciliary Dyskinesia) tih natna nei zingah a tam ber a ni. Tin, (Situs Inversus) vei zinga 5% atanga 10% vel chuan pianpui thinlung natna (Congenital Heart Defect) an nei thei bawk.
Situs Inversus chi hrang hrangte chu engte nge ni?
Situs Inversus hi chi hnih a awm a . Anni chu:
1. Dextrocardia with Situs Inversus: Hei hi i thinlung apex chu i rilru dinglam lam hawia a awm lai a ni. I taksa peng dang zawng zawng pawh chu kawng dang lam hawi a ni.
2. Levocardia with Situs Inversus: Hetiang chi ah hian thinlung apex chu a tlangpuiin veilam hawiin a awm thin. Mahse, pum chhunga taksa peng dangte chu a lehlamah an inher a. Hetiang chi hi a tlem deuh a, thinlung natna dang nen pawh a tel ve a rinawm zawk.
Hei bakah hian veilam emaw dinglam emaw lama taksa peng hrang hrangte lo thanglian danah thil danglam dang a awm chuan (Situs Ambiguous) an ti a ni.Hetiang dinhmunah hian thil thleng chu, taksa peng thenkhat chu kawng danglam takin awm mah se, a kalphung chiang tak a zui lo. Chu chu hmun thenkhatah chuan taksa peng hrang hrangte chu a buai deuh deuh thei tihna a ni.
Hetiang dinhmun hi engtiang chiahin nge a awm (Situs Inversus)?
Situs Inversus hi a awm fo lo. Mi 10,000 zinga pakhat velin a nghawng nia sawi a ni. Tin, he natna hi hmeichhia aiin mipaah a tam zawk deuh bawk.
Engtin nge hetiang (Situs Inversus) hi a lo awm?
Situs Inversus awm chhan ber chu genes inthlak danglamna a ni a, chu chu genetic mutation an ti a ni. Kan taksa peng hrang hrangte chu a sir dik takah a awm theih nan gene chi hrang hrang a awm a. Situs Inversus hi heng gene pakhat emaw a aia tam emaw a mutation avanga lo awm a ni. Tun thlengin scientist-te chuan taksa sir lehlamah chhiatna thlen thei gene 100 chuang an hmuchhuak tawh a ni. Entirnan, `(ANKS3)`, `(NODAL)`, `(DNAH9)` ang chi gene hming vuah theih a ni.
Hetiang dinhmun hi autosomal recessive pattern atanga inherit a ni . Chumi awmzia chu naupangin he natna hi a neih theih nan nu leh pa pahnih hian mutated gene hi an rochun a ngai tihna a ni. A awlsam zawngin sawi ila, nu leh pa pahnih hi he gene kengtu an ni ngei ang, mahse chutiang natna chu an nei lo mai thei (Situs Inversus) .
Engvangin nge Situs Inversus hi a lo awm? Risk factors te chu engte nge ni?
Situs Inversus lo awm chhan dik tak hi genetic ni mahse, a thlen theihna tur risk factor thenkhat a awm. Chungte chu:
- Chhungkaw history-a (biologically related) pianpui thinlung natna nei.
- Chhungkaw history-a (biologically related) nocardiac anomalies nei.
- Nu hian zunthlum natna a nei a .
- Naupai laiin khuh titawptu damdawi thenkhat hman.
- Naupai laiin zuk leh hmuam (e.g. cigarette) hman.
- Socioeconomic level hniam tak neih.
Situs Inversus natna lan chhuah dan chu engte nge ni?
Situs Inversus vei mi tam takin symptoms nei lo an tam hi a mak khawp mai! Ni e, i taksa peng hrang hrangte chu kawng dik lo lamah inher mah se, a thawk tha a nih chuan i nun pum pui chu danglamna leh harsatna nei lovin i kal thei a ni. Hetiang dinhmun hi i nei tih pawh i hre lo mai thei.
Mahse, Situs Inversus -a natna dang emaw, dinhmun dang emaw i neih chuan chu natna nena inzawm symptoms a awm thei. Entir nan:
- If you have cardiac defects , thinlung nena inzawm harsatna (thâwk harsa, rilru natna ang chi) i nei thei.
- Primary Ciliary Dyskinesia tih natna i neih chuan lungah mucus a lo awm thei a, chronic bronchitis a thlen thei bawk.Chronic bronchitis (khuh chhunzawm zel, phlegm) leh sinusitis ( sinus infection) te a awm thei.
Primary Ciliary Dyskinesia hi kan thawkna kawng chhunga sam ang chi (cilia) te hian hna a thawk tha lo tihna mai a ni. An hna chu mucus ang chi thilte chu lung atanga chhuak leh chhuah tir hi a ni. Hengte hian hna a thawh loh chuan mucus a lo pung a, natna hrik a thlen thin.
Engtin nge Situs Inversus hi hmuhchhuah a nih?
Vawi tam tak chu i doctor chuan natna dang enkawl i nih laiin Situs Inversus hi accident-in a hmuchhuak ang.
A châng chuan, i doctor-in i thinlung a ngaihthlâk hian (stethoscope hmanga) he natna hi a ringhlel thei a ni. Mi pangngai thinlung na hi a rilru veilam, thinlung hnuai ber hnaihah a lang chiang ber. Mahse Situs Inversus hmanga dextrocardia (thinlung dinglam hawi ) i neih chuan thinlung thawk chu i rilru dinglam lamah a lang chiang ber.
Doctor-te chuan imaging test hrang hrang hmangin a natna hmuhchhuah chu an finfiah a, eng taksa peng nge a nghawng tih chiang takin an hre thei bawk. Chung zingah chuan:
- X-ray hmanga enfiah (X-ray) .
- Ultrasound hmanga scan a ni
- CT scan (Computed Tomography - CT scan) hmanga tihchhuah a ni.
- MRI scan (Magnetic Resonance Imaging - MRI scan) hmanga tihchhuah a ni.
Heng test te hian taksa peng hrang hrangte dinhmun chiang takin a hmu thei a ni.
Situs Inversus hi engtin nge enkawl a nih?
Mi tam zawk chuan Situs Inversus , an vei tih pawh an hriat loh avangin, symptom leh complication engmah a thlen loh avangin enkawlna bik a ngai lo. I taksa peng hrang hrangte chu a sir dik lo lamah pawh awm mahse, a thawk tha a nih chuan dinglam hawia hruai kir leh turin operation i mamawh tawh lovang.
Mahse, he natna nena inzawm natna dang emaw, natna dang emaw i neih chuan i doctor chuan chutiang chhinchhiahnate chu a enkawl ang.
Hei hi a pawimawh hle: Situs Inversus i vei tih i hriat chuan i doctor zawng zawngte hriattir vek a pawimawh hle.
Hetiang hian han ngaihtuah teh. Appendicitis hian i pum dinglam hnuai lam a ti na tlangpui. Mahse i appendix chu a sir lehlamah a awm chuan i pum veilam hnuai lam a na thei. I doctor hian i Situs Inversus dinhmun a hriat loh chuan i veilam natna chu appendicitis a ni lo niin a ngai thei a, emergency treatment pawh a tikhawtlai thei bawk. Hei hi harsatna lian tak a ni thei.
Chuvangin, nakin lawkah natna eng emaw i neih chuan, he thu hi doctor-te tan dik taka hriat theihna turin a pawimawh hle. Tin, eng surgery emaw, damdawi lam thil dang emaw an tih hmain doctor zawng zawngin i dinhmun an hriat hmasak a pawimawh hle bawk. (Situs Inversus) nei mi pakhat surgery an tih hian surgeon-te chuan hun rei zawk an mamawh emaw, ruahmanna danglam tak an siam emaw a ngai mai thei.
Situs Inversus hi a veng thei ang em?
Situs Inversus hi genetic mutation hmuh tur awm lo tak avanga lo awm a ni. Chuvangin tun dinhmunah hian he dinhmun hi lo awm lo turin kan tih theih a la awm lo.
(Situs Inversus) vei mi pakhat dam rei zawng chu engzat nge ni?
Situs Inversus vei tam zawk chuan nun pangngaia nun an beisei thei. He natna hi i nei tih pawh i hre lo mai thei a, symptom leh complication engmah nei lovin i nung thei bawk. Mahse, i dinhmun hi hriselna lama harsatna dang emaw, chhiatna dang emaw nena inzawm a nih chuan i prognosis chu a hnuaia awm leh a enkawl danah a innghat ang.
Situs Inversus vei te hian nau an pai thei em?
Ni e, Situs Inversus vei hmeichhiate chu a pangngaiin nau an pai thei a, thil thleng bik awm lovin an naupai zo thei bawk. Hetiang dinhmun hian naupai a tibuai lo.
Doctor hnenah eng zawhna nge ka zawh ang?
Situs Inversus i nei tih i hriat chuan zawhna tam tak i nei mai thei. Chu chu thil pangngai a ni. I doctor hnenah zawhna i zawt thei ang:
- "Engvangin nge ka taksa pengte hi hetiang lam a inher?"
- " Situs Inversus Totalis nge Situs Inversus Ambiguous ka nei em ?"
- "Ka dinhmun (Situs Inversus) hi natna dang emaw, chhiatna dang emaw nen a inzawm em?"
- "Hemi atan hian enkawlna bik ka mamawh em?"
- "Nakin lawkah eng thil nge ka fimkhur bik ang?"
A tawp berah chuan hriat reng tur (Take-Home Message) .
Chuvangin, (Situs Inversus) hi genetic condition hmuh tur awm lo tak a ni a, kan taksa chhunga taksa peng hrang hrang, rilru leh pum chhunga awm te chu an awmna pangngai atanga a kalh zawnga awm, mirror image ang maia awm a ni. He thu i hriat hian i hlauthawng deuh mai thei, "Aw, ka taksa pengte hi an awmna tur hmunah a awm lo?" Mahse, a tam zawkah chuan hei hian harsatna a thlen lo.
Symptoms i nei lo mai thei a, i taksa peng hrang hrangte pawh a pangngaiin hna a thawk thei bawk. A châng chuan he natna hi hriselna lama harsatna dang nen pawh a inzawm thei bawk. Chutiang a nih chuan i doctor chuan chu natna chu a enkawl ang. Mahse, chu natna tak tak tan chuan enkawlna bik a ngai lo tlangpui a, chu chu Situs Inversus an ti a ni.
A pawimawh ber chu i doctor leh healthcare provider zawng zawngte hnenah Situs Inversus i nei tih hriattir hi a ni. He thu hi dik taka hriat theihna leh him taka enkawlna atan a pawimawh thei hle.
Hei hi kan hriat chian a pawimawh hle a ni. Hemi chungchanga zawhna dang i neih chuan doctor nen inbiakna neih hreh suh.
` Situs Inversus, Situs Inversus, Organs lehlamah, Genetic diseases, Dinglamah Heart, Dextrocardia, Levocardia, Primary Ciliary Dyskinesia, Congenital heart diseases











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