A châng chuan i taksa pum puiah lump leh bumps te te i nei ṭhin a ni lawm ni? A tam zawkah chuan kan ngaihsak vak lo. "Hei hi cyst mai a ni thei" emaw, "Fatty tumor a ni thei" emaw tiin kan ngaihtuah thin. Mahse, a chang chuan hetiang thil hi tlem tal ngaihtuah a tha. Vawiin hian tumor chi khat, a tlem hle, mahse hriat tur pawimawh tak kan sawi dawn a ni. Hengte hi Solitary Fibrous Tumors (SFTs) kan ti a.
Solitary Fibrous Tumor (SFT) hi eng nge ni tak tak?
A awlsam zawngin sawi ila, SFT hi kan taksa soft tissue-a lo awm, tumor chi khat a ni. Taksa khawi hmunah pawh siam theih ni mah se, kan lung vel venhimna khuhnaah an awm tam ber.
Heng SFT nut hi chi hnih a awm a.
1. Ṭhenkhat chu an lo thang chak lo hle a, hmun dangah an darh lo (non-cancerous - benign) .
2. A chi dang chu cancer/malignant a ni a, a thang chak hle a, taksa hmun dangah a darh thei bawk .
A pawimawh ber chu heng SFT tumor tam zawk hi cancer an ni lo . Mahse, doctor-te chuan heng tumor te hi lakchhuah a tha ber tih an rawt a, chu chu operation emaw, enkawlna dang emaw hmangin a ni.
Hmanlai khan hei hi eng nge an tih?
Tun hma chuan doctor-te chuan heng tumor te hi rilru chhungah chauh a lo awm niin an ngai a. Chuvangin "benign fibrous tumors of the pleura" tia koh an ni. Hetah hian `(pleura)` tih hian kan rilru bang chhunga line siamtu leh kan lung venhimtu membrane te tak te a kawk a ni. He membrane hian kan thawk chhuah huna kan lungte awlsam taka a kal theihna tura a mamawh lubricant a siam chhuak bawk.
Mahse tunah chuan heng tumor te hi taksa khawi hmunah pawh a lo awm thei tih kan hria a, rilruah chauh ni lovin, thin, thluak leh kawr ah te pawh a lo awm thei a ni. Chuvangin chu hming hlui chu hman a ni tawh lo.
SFT leh Pleural Mesothelioma hi thil hrang hrang pahnih a ni em?
Ni e, hengte hi dinhmun hrang hrang pahnih a ni.
- Pleural Mesothelioma: Hei hi cancer a ni a, chu chu lung chhunga lining (pleura) a lo awm a ni. Hei hi a chhan ber chu asbestos inhalation vang a ni .
- Solitary Fibrous Tumor (SFT): Heng SFT te hian asbestos nen hian inzawmna an nei lo. Tin, cancer vei an tlem phah bawk. Tin, mesothelioma ang lo takin SFT hi taksa khawi hmunah pawh a lo awm thei bawk. SFTs awm chhan dik tak hi hriat a la ni lo .
Tute nge heng tumor te hi vei theihna chance sang zawk?
SFT hi kum eng pawhah a lo awm thei a, mahse kum 50 leh 60 inkar ah a awm tam ber.Kum upa lam zingah chuan naupang tê têah chuan he natna hi a tlem hle. Dik tak chuan soft tissue tumor report zinga 2% aia tlem chu SFT an ni.
Eng thilin nge SFT hi a thlen?
Hei hi a chhan dik tak hi hriat a la ni lo a, mahse zirchiangtute chuan kan gene pahnih , NAB2 leh STAT6 te hi an inzawm khawm niin an ngai. Tuna kan ngaihdan chu he gene danglam hian SFT vei theihna a tipung thei a ni.
SFT hian eng symptoms nge a thlen?
Heng SFT tumor te hi an lo thang zawi zawi hle fo thin. Chuvangin SFT vei zinga a chanve vel chuan symptom an nei lo . Tumor chu a bul hnaia taksa peng, ruh emaw, tissue dang emaw a nawr theih khawpa lian a nih hnuah chauh natna lan chhuah tan a ni.
Tumor awmna hmun azirin symptoms a inang lo. Chu chu engtin nge a thawh tih i en ang u.
| Tumor awmna hmun leh a lan chhuah theih dan | |
|---|---|
| A rilru chhungril (lungs, pleura) ah chuan . |
|
| Mit socket area ah chuan |
|
| Hnar leh sinus cavities chungchangah |
|
| Thluak nena inzawm |
|
| Spinal cord nena inzawm |
|
| Liver nena inzawm a ni |
|
| Thyroid nena inzawm a ni |
|
Engtin nge doctor chuan hei hi SFT a ni tih a hriat theih?
Test hi i symptoms leh tumor awmna ni rinhlelhna a zirin a inang lo. Test lian ber berte chu:
- Mit enfiah: Mit lama harsatna i neih chuan test bik Optical Coherence Tomography (OCT) te hian i mit harsatna chhan hriat theih nan a pui thei a ni.
- Imaging Scans: X-ray, CT scan, MRI scan, Ultrasound scan , emaw PET scan hmangin tumor awmna leh a lian leh te dik tak hriat theih a ni.
- Biopsy: Hei hi test pawimawh ber leh chiang ber a ni . Tumor atang hian tissue te tak te tak te chu lakchhuah a ni a, microscope hmangin an enfiah thin. Hei hian tumor hi cancer a nih leh nih loh 100% in a nemnghet thei a ni.
World Health Organization (WHO)-in a thliar hranna
World Health Organization (WHO) chuan SFT tumor hi a nasat dan a zirin grade hrang hrangah a thliar hrang a. He grade hian tumor a lo thang chak dan a kawk a, chu chu microscope hmanga cell te an lan dan atanga chhut a ni. Hei hi cancer stage nen a danglam hle.
- Grade I (Low-grade): Hengte hi a aggressive lo ber chi an ni. Cell te hi a tam zawk chu cell pangngai ang an ni. An thang zawi zawi hle. Anni hian symptom engmah an nei lo mai thei.
- Grade II (Intermediate-grade): He grade-a cell-te hi Grade I-a cell-te aiin a pangngai lo deuhin an lang a, chuvangin an than chakna chu a sang deuh hlek a ni. Cancer vei theihna chance pawh a sang zawk.
- Grade III (High-grade): Heng zingah hian cell pangngai lo ber ber a awm a. Heng tumor te hi a nasat em em a, a thang chak hle a, enkawl hnuah a lo let leh a, cancer a lo ni a, taksa peng dangah pawh a darh zau zawk a ni.
SFT enkawlna tur engte nge ni?
SFT tumor enkawlna ber leh tha ber chu surgery a ni . Doctor chuan a tumor pumpui chu surgery hmangin lakchhuah a tum ang.
A then phei chuan tumor awmna hmun azirin operation tih theih a ni lo thei bawk. Chutiang hunah chuan radiation therapy hmangin tumor chu tihtlem leh tihchhiat a ni. A châng chuan operation hmain radiation therapy an pe bawk a, chu chuan tumor chu a tikehsawm a, a chhuah awlsam phah a ni.
SFT avanga harsatna awm thei te chu engte nge ni?
SFT vei tan chuan hlauhthawnna lian ber chu cancer a nih dawn nge hmun dangah a darh dawn (metastatic cancer) tih hi a ni. He hlauhawmna hi nasa takin a tihziaawm thei a, chu chu tumor lakchhuahna tur operation neih a ni.
Mahse, enkawl hnuah pawh a chang chuan SFT tumor hi `recur` thei a ni . Hetiang tumor chi hi cancer a nih theihna chance a sang zawk.
Tumor awmna hmun a zirin harsatna dang pawh a awm thei bawk.
- Taksa peng hrang hrang paralysis
- Pleural effusion (lung chhunga tui awmkhawm) .
- Mit atanga thluak thlenga thuchah phurtu nerve te chhiatna (Optic atrophy) .
Outlook leh engtikah nge doctor hmuh tur?
Mi tam tak chu tumor lakchhuah nan operation an neih hnuah an dam chhuak vek a ni. Mahse, a hmaa kan sawi tawh ang khan tumor lo kir lehin cancer a lo awm hi a tlem hle. Chuvangin, i doctor chuan a lo lang leh tawh em tih enfiah turin scan mumal tak a nei ang.
Heng symptoms te hi i neih chuan doctor pan ngei ngei tur a ni:
- A rilru a na
- Thâwk harsa
- Chhan awm lova hah lutuk
- Mit hmuhna lama harsatna a awm
Doctor i hmuh hunah heng zawhnate hi zawh theihnghilh suh:
- Khawiah nge tumor chu a awm?
- Hei hi operation hmangin lakchhuah theih a ni em?
- Tumor a lo awm leh theihna tur chhinchhiahna engte nge ni?
- Engzat nge scan ka neih ang?
- Eng harsatna dang nge ka ngaihtuah tur?
Tumor i nei tih i hriat chuan hlauhna i neih hi thil pangngai a ni. Mahse hre reng ang che, SFT hi natna hlauhawm tak ni mahse, enkawl dan dik tak chuan a dam kim thei a ni. A pawimawh ber chu a natna lan chhuah dan thliar lovin, a rang thei ang bera damdawi lam pan hi a ni.
Take-Home Thuchah a ni
- Solitary Fibrous Tumors (SFTs) hi taksa peng nem tak takah a lo piang chhuak a, hei hi a tlem hle a ni.
- Chung zinga a tam zawk chu cancer (benign) an ni lo va, a then chu cancer (malignant) an ni thei.
- A tam zawkah chuan a tir lamah chuan symptom a awm lo. Symptoms lo lang chu tumor awmna hmunah a innghat a ni.
- Enkawlna ber chu operation hmanga tumor chu paih vek a ni.
- Enkawlna hnuah pawh tumor lo kir leh theihna a tlem avangin doctor thurawn angin checkup neih fo a pawimawh hle.
- I taksaah lump, natna, symptom dang danglam tak i neih chuan ngaihthah suh la, doctor pan nghal rawh.











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