Gaucher’s Disease pawh i nei ve em? Taliglucerase Alfa damdawi chungchang hi han sawi ila?

A chang chuan kan ngaihtuah phak loh natna kan vei thin a ni lawm ni? Gaucher natna pawh hi a tlem hle a, mahse uluk taka enkawl a ngai a ni. Chuvangin nangmah emaw i hnaih ber emaw hian he natna hi i neih chuan vawiin hian damdawi Taliglucerase alfa chungchang kan sawi dawn a, chu chu a enkawlna a ni. Eng nge a nih, engtin nge a thawh tih leh fimkhur tur chu i hrethiam mai ang u.

Gaucher-a natna hi eng nge a nih i lo en hmasa ang u.

A awlsam zawngin sawi ila, Gaucher natna hi kan taksaa genetic factor thenkhat avanga lo awm a ni. Kan taksaah hian hna pawimawh tak thawk thei enzyme chi hrang hrang a awm a. He natnaah hian enzyme pakhat glucocerebrosidase an tih chu kan taksa cell-ah a siam tha lo a, a nih loh leh a hnathawh a tlahniam bawk. He enzyme hian kan taksaa thau thenkhat a tichhia a, chuta tang chuan thil tangkai tak tak a siam chhuak thin. Chuvângin, he enzyme hi a tlahniam chuan, chu thau tak takte chu kan taksa hmun ṭhenkhatah, entîr nân , ruhro, ruhro, leh thin An pungkhawm chuan symptom hrang hrang a lo lang thin. Chu chu mi ṭhenkhat chuan ruh na, thisen tlakchhamna, leh rilṭâm lian tak an nei thei tihna a ni. Hei hi thil buaithlak deuh angin lang mahse, hriatthiam dan dik a nih chuan thil lian tak a ni lo.

Chuti a nih chuan he damdawi hi eng nge Taliglucerase Alfa an tih?

Taliglucerase alfa hi Gaucher natna vei, kan sawi tawh ang khan an taksaa an tlakchham enzyme chu artificial-a siamin an pe thin a ni. A dik tak chuan hei hi mihring siam enzyme chi khat a ni . Gaucher natna lan chhuah dan control nan hman a ni. Mahse hei hi natna tidam vek thei damdawi a ni lo tih pawh i hre reng tur a ni . Mahse a symptoms control nan a pui a, nun a ti awlsam hle.

A chang chuan doctor ten he damdawi hi thil dang atan an hmang mai thei a, chuvangin zawhna i neih chuan i doctor emaw pharmacist emaw zawh a tha ber.

He damdawi hi brand name ELELYSO hmangin i hmu tlangpui ang.

He damdawi hi ka hman hmain medical team te hnenah eng nge ka hrilh ang?

He damdawi, Taliglucerase alfa pek i nih hma hian i medical team (care team) te hian thil engemaw zat an hriat a ngai a ni. A chhan chu, chu thu hriat a\ang chuan him takin enkawlna chu an pe thei che a ni. Eng nge an nih i en ang u:

• Taliglucerase alfa, damdawi dang, ei tur, food dyes, emaw preservatives emaw avanga allergy reaction danglam tak i neih tawh chuan min hrilh ngei ang. Hei hi thil tenawm tak angin a lang thei a, mahse a pawimawh hle.
• Naupai i nih chuan, a nih loh leh nakin lawka naupai i tum a nih chuan i doctor hnenah pawh hrilh bawk ang che.
• Nu hnute pe thin i nih chuan chu pawh chu sawi theihnghilh suh.

Heng thilte hi dik taka i tih theih chuan medical team chuan i tana tha ber leh him ber tur enkawlna tur ruahmanna an siam thei a ni.

Engtin nge he damdawi hi ka pek theih ang che?

He damdawi hi vein pakhatah infusion hmanga pek a ni . A awlsam zawngin, vein-ah pek a ni. Hei hi damdawi in emaw, clinic setting emaw-ah health care professional, pe tura zirtirna neiin a ti tlangpui. Hei hian in lamah i hmang thei lo tihna a ni. Chu pawh chu invenna chi khat a ni.

He damdawi hi naupang te te hnenah pek tur em ni?

I fain he damdawi, Taliglucerase alfa hi a hmang a nih chuan i pediatrician nen pawh he thu hi i sawipui ngei tur a ni. A chhan chu a chang chuan hetiang damdawi hi naupang tê tête hnena pek dawnin fimkhur bik a ngai ṭhin. Dosage leh schedule of administration ang chi thilte chu a inmil theih nan siamrem a ngai a ni.

Damdawi i ei tam lutuk chuan eng nge thleng ang?

He damdawi hi pek tam lutuk che nia i hriat chuan, emaw, pek i rinhlelh chuan poison control center emaw, damdawi in emergency room hnai ber emaw i biak nghal tur a ni tih hre reng ang che Hetiang thilah hian rang taka hmalak hi a pawimawh ber a ni.

Khawngaihin hre reng ang che: He damdawi hi nangmah tan chauh pek a ni. I thian emaw, chhungte emaw hnenah pe suh, symptom inang an nei a nih pawhin. Damdawi dik leh hman dan dik chu mi tin tan a inang lo thei.

Damdawi dose i ei loh chuan engtin nge i tih ang?

He damdawi hi a hun taka ei a pawimawh hle a, a dose skip lo. Hei hi a chhan chu damdawi i ei hunah chauh hlawkna tam ber i hmu dawn a ni. Ni ruat saah damdawi in/clinic-ah enkawl i kal thei lo a nih chuan i doctor emaw health professional emaw ko nghal la, hriattir rawh . Chumi hnuah chuan i tih tur chu an hrilh ang che.

He damdawi nen hian eng thil dang nge inzawm thei?

A tlangpuiin he Taliglucerase alfa damdawi leh damdawi dangte inkarah hian inzawmna lian tham a awm beisei a ni lo tih an sawi. Mahse, chu chu engmah nen a inzawm dawn lo tihna erawh a ni lo. A châng chuan, side effect tenau te a awm thei bawk.

Chuvangin, i doctor hnenah damdawi i ei zawng zawng list kimchang pe rawh – doctor-in a pek chauh ni lovin, herb eng pawh, non-prescription drugs, emaw, vitamin ang chi dietary supplement eng pawh. Tin, zu i in emaw, zu i in emaw, dan loa ruihhlo i hman chuan.Chu pawh chu rinawm takin sawi rawh, a chhan chu thil ṭhenkhat chu i damdawi nena inkawp chuan nghawng ṭha lo a nei thei a ni.

He damdawi hi i ei dawnin eng nge i fimkhur tur?

I enkawlna a kal zel dan tur enfiah turin i doctor tlawh fo ang che . Hei hi a pawimawh hle. I doctor chuan damdawi hian hna a thawk em tih leh i symptoms a that lehzual em tih a enfiah ang che. I symptoms a lo tha lo a nih chuan, emaw a na zual a nih chuan , i doctor emaw healthcare professional emaw hnenah hrilh rawh. Nangmah ah engmah dah suh.

He damdawi hian eng side effect nge a neih theih?

Damdawi dang ang bawkin Taliglucerase alfa hian side effect engemaw zat a nei thei a ni. Mi zawng zawngin kan hmu vek lo a, mahse fimkhur a tha. Ṭhenkhat chu a na hle a, damdawi lam pan vat a ngai a ni. A dangte chu a awm fo a, ni rei lote hnuah a bo vek ang. Anni hi han thlir ila.

Doctor emaw health professional emaw hnena hriattir nghal tur side effects:

Heng symptoms zinga pakhat tal i neih chuan a rang thei ang bera doctor thurawn lak a pawimawh a, hengte hi a chang chuan natna khirh zawk chhinchhiahna a ni thei a ni:

• Allergic reactions : Chungte chu vun rawng chhuak nghal, vun na tak emaw, hive emaw, hmai, hmui emaw lei emaw a hring chhuak te a ni. Hengte hian thawk harsatna a thlen thei bawk.
• Blue fingernail emaw hmui emaw .
• Thâwk lama harsatna , thawk hah ang maia inhriatna.
• Chhuak na emaw, rilru a tight tih hriatna emaw.
• Khuh chu tihtawp theih loh.
• Thinlung thawk chak tak emaw, a mumal lo emaw rang tak .
• Hmai sen, taksa lum leh thawk hah (flushing) .
• Thisen sang hniam , chu chu luak chhuak leh lu hah tihna a ni.
• Injection pekna hmunah natna, sen, emaw, thinrimna , a chang chuan a hring pawh a awm thei bawk.
• Ke ruh, ke, kut a hring .

Side effects, a tlangpuiin damdawi lam enkawl ngai lo, mahse a awm reng emaw, a buaithlak emaw a nih chuan doctor hnenah hriattir tur a ni:

Hengte hi ni engemaw zat hnuah a bo tlangpui a, mahse a awm reng a nih chuan, emaw, nitin hnathawh tur i tih theih lohna tur khawpa buaithlak a nih chuan i doctor hnenah hrilh rawh:

• Khua a vawt, khur (chills) .
• Kawthalo .
• Khawsik .
• Lu na .
• Nausea, luak chhuak .
• Tuar theih loh khawpinChau lutuk nia inhria.
• Pum natna, chaw ei loh ang chi .

He list hi side effect awm thei zawng zawng a ni lo. I taksaah thil danglam emaw, danglamna emaw i hmuh chuan doctor rawn la. Engmah ngai pawimawh suh.

He damdawi hi khawiah nge i dah?

He damdawi hi damdawi in emaw, damdawi in emaw-ah pek a nih dawn avangin in lamah i dah a ngai tawh lo vang . Chumi awmzia chu damdawi chu a chhe dawn em tih emaw, a dah that dawn em tih emaw ngaihtuah a ngai lo tihna a ni. Chu mawhphurhna chu damdawi in emaw, clinic emaw thawktute kutah a awm a ni.

A tawp berah chuan i hriat reng tur thil tlemte:

Taliglucerase alfa hi damdawi pawimawh tak a ni a, Gaucher natna lanchhuahna control nan a pui a ni. Hei hian taksaa enzyme awm lo chu artificial-a thlak danglam a huam a ni. He damdawi hi vein-ah injection angin an pe a, damdawi inah an pe thin. Allergy i neih chuan, nau i pai a, damdawi dang i ei a nih chuan doctor hnenah hrilh ngei ang che. Side effects a awm thei a, chuvangin symptom na tak i neih chuan doctor thurawn zawng nghal rawh . A hun taka enkawl leh doctor nena inbiak reng a pawimawh hle.

Zawhna emaw, ngaihtuahna emaw i neih chuan i doctor, pharmacist, emaw health care provider emaw zawh hlau suh. I tanpui turin an awm reng a ni. I hriselna pawh an tan a pawimawh hle.

` Taliglucerase alfa, Gaucher natna, enzyme, damdawi, side effects te