Hliam te tak te atang pawhin thisen a chhuak nasa em? Von Willebrand Disease chungchang hi han sawi ila

Hun rei tak chhung thisen chhuah khap theih loh khawpa cut te tak te i nei tawh em? A nih loh leh, a bump tlem hnuah pawh blue bruise lian tak tak i nei em? A châng chuan hengte hi thil pangngaiah kan ngai a, mahse kan thisen lama harsatna tlem a awm tih chhinchhiahna a ni thei. Vawiin hian thisen zam tichhe thei, sawi hlawh lo mahse tlanglawn tak tak kan sawi dawn a ni. Chu chu von Willebrand natna a ni.

A awlsam zawngin, von Willebrand natna (VWD) hi eng nge ni?

von Willebrand disease (VWD) hi kan thisen zam (blood clotting process) a thawk tha lo a nih chuan a lo awm thin a ni. Natna aiin kan taksa chak lohna rochun a ni zawk.

Ngaihtuah teh, kan thisen kalna kawng pakhata hliam kan neih chuan kan taksaa cell (platelet) chi khat te tak te chu thisen chhuahna titawp turin a lo kal a, hliam chu a seal ta a ni. Bang chhunga khur pakhat chu brick hmanga khat ang mai a ni. Heng platelet te hi an inzawm khawm a, kan thisenah hian "gum" ang chi protein bik an nei a, chu chuan clot chak tak siam turin a pui a ni. Chu chu von Willebrand factor (VWF) kan tih chu a ni.

VWD vei chuan he VWF protein hi an taksaah a nei tlem thei a, a nih loh leh protein an neih hian hna a thawk tha lo thei bawk. Tichuan, thisen zam chu a lo insiam tha tawk lo a, hliam tenau a\anga thisen chhuah a reh theih nan hun rei tak a ngai a ni.

VWD chi hrang hrangte chu engte nge ni?

He dinhmun hi chi thum ah then a ni ber. Tin, pianpui ni lo mahse a hnu lama lo piang chhuak chi khat a awm bawk.

Hetiang natna lan chhuah dan hi engte nge ni?

VWD i neih chi hrang hrang a zirin symptoms a inang lo.

Type 1 leh 2-a symptoms na lo leh na lo tak tak a awm

• Hliam tenau tak pawh hian hliam lian tak blue a thlen thei: I taksa chu hmun thenkhatah blue a lo ni tih i hmu em?
• Hnar thisen chhuak fo: Mi thenkhat chuan hnar thisen an nei fo thin a, tihtawp a harsa thin.
• Operation emaw ha lakchhuah hnua thisen chhuak tam lutuk: Ha lakchhuah hnu darkar tam tak chhung thisen chhuak chu a tawp lo em ni?
• Hmeichhia hian an period laiin thisen chhuak nasa tak an nei thin: Thisen a chhuak nasa lutuk a, darkar khatah vawi khat tal i pad thlak a ngai em? Clots nen a lo thleng em? Hun a kal zel a, hei hian iron tlakchhamna thisen tlakchhamna a thlen thei a ni .
• Thisen chu bawlhhlawh emaw zun emaw ah a awm.

Type 3 a symptom na tak tak a awm

Hetiang chi ah hian a chunga kan sawi zawng zawng hi a na thei hle. Chubakah chuan,

• Chhan awm lovin thisen chhuak nghal, na tak.
• Thisen hi ruh leh soft tissue-ah a luang lut a, chu chuan a hring a, a na hle bawk.

Engtin nge hei hi i hriat chian?

I doctor chuan i symptoms leh chhungkaw medical history te a zawt hmasa ang. Hei hi thlahtute atanga lo piang a nih avangin i chhungte zingah hian hetiang thisen chhuahna lama harsatna nei tawh an awm em tih hriat a pawimawh hle.

Tichuan, i thisen a inzawm theih nan eng chen nge a duh tih leh a tha tih hriat nan special test engemaw zat an ti ang. A bik takin, .

• Thisen a VWF protein awm zat tehna (Antigen test).
• Chu protein hnathawh dan test.

A châng chuan, stress leh exercise ang chi thilte hian VWF level a tidanglam thei a, chuvangin result dik ber hmuh theih nan heng test te hi vawi khat aia tam tih a ngai mai thei.

Enkawlnate chu engte nge ni? Engtin nge kan enkawl ang?

VWD hi tihdam theih ni lo mah se, nun pangngaia hman theih turin control theih leh enkawl theih a ni . A pawimawh ber chu thisen chhuah theihna tihziaawm hi a ni.

1. Damdawi thenkhat ei loh

Thisen tithianghlim thei damdawi thenkhat ei loh tur a ni. I doctor chuan aspirin leh NSAID (ibuprofen leh naproxen ang chi) ei lo turin a hrilh fo ang che. Acetaminophen hi natna emaw, khawsik emaw tan chuan a him zawk. Mahse damdawi engmah i ei hmain doctor zawt hmasa phawt ang che.

2. Enkawlna bik

Enkawlna chu i natna lan chhuah dan nasat dan leh chi hrang hrangah a innghat a ni.

• Desmopressin Acetate (DDAVP): Hei hi damdawi hman tam ber a ni. Hnar spray angin emaw, injection angin emaw pek theih a ni. Kan cell-a VWF protein dahkhawm chu thisenah a chhuah tir a, hei hian hna a thawk a ni. He damdawi hian taksaah tui a tikhawlo thei a, chuvangin i doctor chuan i tui ei tlem turin a rawt mai thei.
• Clotting Factor Concentrates: VWF protein awmna concentrate, thisen kal tlanga pek (IV). Hei hi natna khirh takah leh operation hmaa hman a ni tlangpui.
• Damdawi dang: Ha lakchhuah ang chiah hian thisen zam a hmin loh nan pill emaw, damdawi tui tak aminocaproic acid emaw tranexamic acid emaw pek theih a ni.
• Hmeichhia tana enkawlna bik: Hmeichhe period nasat tan chuan birth control pill hian VWF level a tisang thei a ni. Hormone awmna loop (levonorgestrel intrauterine device) bun emaw, nausen pum chhunga lining lakchhuah emaw (endometrial ablation) tih ang chi pawh a awm bawk.

A tawp berah chuan Type 3 ang natna khirh tak i neih chuan thisen chhuak i neih chuan emergency a ni. Damdawi in pakhat Emergency Department (ETU) ah i kal nghal tur a ni. Tikhawtlai hi nunna atana hlauhawm tak a ni thei.