I vunah hmun pakhat chu a sen nghal a, a hring deuh a, a hring bawk em? Bacteria infection chi khat ang maiin a lang thei a, mahse a takah chuan infection a ni lo mai thei. Vawiin hian vun natna hmuh tur awm lo tak, mi tam takin an la hriat ngai loh, mahse hriat a pawimawh thu kan sawi dawn a ni. Wells’ Syndrome tih a ni. Eng nge a nih, engvangin nge a lo awm tih leh eng nge i tih theih tih hi han thlir ila.
A awlsam zawngin Wells-a Syndrome hi eng nge ni?
Wells’ Syndrome hi vun natna hmuh tur awm lo tak a ni. "Eosinophilic cellulitis" tia hriat a ni bawk. A hming i hriat chuan vun natna, cellulitis an tih ang maiin i ngai mai thei. Mahse a takah chuan infection a ni lo. Vun hmun khat emaw a aia tam emawa vun sen, hring, itchy, leh inflamed patches awm thei dinhmun a ni.
Tunah chuan zawhna i nei ta, heng "eosinophils" te hi eng nge ni? A awlsam khawp mai. Eosinophils hi kan thisena thisen var chi khat a ni. Kan taksaah sipai ang mai an ni. An hna ber chu hri kai dona a ni. Mahse a chang chuan heng eosinophil cell te hi taksaah hian a tul aia tam an siam chhuak a, a nih loh leh an thawk nasa lutuk bawk. Tichuan heng cell te hian inflammation an siam a, chu chuan keimahni vun ngei pawh a tichhe thin. Chu chu Wells’ Syndrome-ah chuan a thleng thin.
A awlsam zawngin Wells’ Syndrome hi natna hrik avanga lo awm a ni lo va, kan taksa ngeia immune cell chi khat overactive vang a ni.
Hetiang dinhmun hi khawvel pumah a tlem hle. Hri kai 100 aia tlem lo an awm tawh bawk. Puitlingte a nghawng tam ber a, naupangte pawh a nghawng thei bawk. Hmeichhia leh mipa pawh a nghawng vek a ni.
Engvangin nge hetiang thil hi a lo thlen?
Hei hi a chhan dik tak hriat a la ni lo a , mahse doctor te chuan autoimmune disorder a ni thei niin an ngai .
Hetiang hian han ngaihtuah teh: kan immune system hi ram venghimtu sipai ang a ni. A hna chu hnam dang rawn lut, hrik leh virus ang chi laka min humhim hi a ni. Mahse a chang chuan he system hian a kal a, kan cell hrisel tak takte chu "hmêlma" anga ngaihin a rawn bei tan thin. Chu chu ``autoimmune disorder'' kan tih chu a ni. Wells’ Syndrome hi chutiang bawka immune system malfunction vang nia rinhlelh a ni.
A tam zawkah chuan a thleng mai mai thin. Mahse, chhungkaw thenkhatah chuan he natna hi a kal zel avangin genetic component a awm thei. Chu bâkah, thil ṭhenkhat chuan chu dinhmun chu a tichhuak thei a, a tichhe thei bawk.
| Wells’ Syndrome lo awm theihna tura pui thei thilte | |
|---|---|
| Insect te hian an seh thin | A bik takin rulhut ang chi rannungin an seh hnuah. |
| Viral natna hrik kai te | Hetiang dinhmun hi virus infection thenkhat hnuah pawh a awm thei. |
| Vun natna te | Vun natna dang, dermatitis ang chi te. |
| Intestinal infection awm thei te | Intestinal infection, Giardiasis ang chi te pawh a awm thei. |
| Damdawi lam thil dang | Thisen cancer natna chi hrang hrang leukemia, fungal infection te. |
| Ruihhlo emaw, thir emaw nena inzawmna (reaction). | Damdawi emaw, thir emaw thenkhat avanga taksain a tihbuai angin. |
He natna lan chhuah dan engte nge ni?
He natna lan chhuah dan hi vun hmun khat emaw a aia tam emaw a kang emaw, a hring emaw atanga tan a ni tlangpui. Tichuan a hmunte chu a sen a, a hring bawk. Heng hmun hring te hi a na fo thin . Mi thenkhat tan chuan a chhinchhiahna hmasa ber chu blister thar emaw nodules emaw a ni thei.
Vun a thil langsar ber berte chu:
- Redness leh swelling: Hei hi a lan chhuahna ber a ni.
- Itching leh burning: A sen laiah hian na tak tak emaw, kang emaw a awm thei.
- Ring ang chi hmun hrang hrang:A châng chuan circular spot a lo lang thei bawk.
- Color change: Hun kal zelah heng red spot te hi rawng a inthlak thin. A hmasain, brown-red , chutah blue-gray , leh a tâwpah green-gray -ah an chang leh a ni. Hei hi he natna lan dan bik a ni.
Taksa pianphung dangte: 1.1.
Asthma, ruh natna, leh khawsik ang chi natna lan chhuahna a awm thei a, mahse a langsar lo fo . A lan chhuah dan ber chu vunah a ni.
A tha ber chu heng spot te hi kar tlemte emaw thla engemaw zat chhungin hliam engmah awm lovin an dam tlangpui thin. Mahse, nakin lawkah an lo lang leh thei a ni.
Engtin nge doctor hian hei hi a hriat theih?
Heng symptoms te hi i neih chuan doctor pan ngei ngei tur a ni. A enfiah ang che a, test thenkhat a kalpui ang a, hei hi Wells’ Syndrome emaw, natna dang emaw a ni em tih a hriat theih nan.
1. Skin biopsy: Hei hi a natna hriat chian dan tha ber a ni. Doctor chuan a natna hmun atanga vun te tak te chu anesthesia hmangin a la ang a, laboratory-ah test turin a thawn ang. He test hian a hmaa kan sawi tawh eosinophils tam tak chu vun leh a hnuaia tissue-ah te a zawng dawn a ni. Hei hi allergy, parasite, dermatitis, insect seh emaw, Churg-Strauss syndrome ang chi natna dang emaw a ni lo tih finfiah nan a pui thei bawk.
2. Complete Blood Count: He test hi thisen sample lak atanga tih a ni a, thisenah eosinophils a pung em tih enfiah theih a ni.
Hei hi eng enkawlna nge ni?
I doctor chuan Wells’ Syndrome enkawl dan tur a ruat ang. Hemi atan hian enkawlna tha tak tak a awm tlangpui.
- Systemic Steroids: Enkawlna hman tlanglawn leh tangkai ber chu oral emaw injectable steroids prednisone te hi a ni. Hengte hian immunosuppressant effect an nei a. Chumi awmzia chu immune system chu a tissue te a beih loh nan an titawp tihna a ni. Prednisone hi steroid hormone cortisol synthetic version a ni a, taksaa pianphung atanga siam a ni. He damdawi hi ei a nih atanga ni engemaw zat chhungin a natna lan chhuah dan a tha chho tan tlangpui. Dosage hi thla khat vel chhungin zawi zawiin tihhniam theih a ni a, i doctor-in a thurawn angin.
- Damdawi dang: A then phei chuan antifungals (e.g., griseofulvin) emaw antibiotics (e.g., dapsone) emaw pawh enkawlna atan hman theih a ni.
- Cream hrang hrang:A natna hi a na lutuk lo a nih chuan a natna hmunah hydrocortisone ang chi steroid cream hnawih mai mai hian a ti hahdam thei a ni.
A pawimawh ber chu, heng damdawi te hi i duh angin hmang ngai suh . Doctor pan ngei ngei tur a ni a, a thurawn angin chauh, a zat tur angin, hun bituk chhung atan ei thin ang che.
Eng ang thlirna nge ni ang? (Prognosis) tih a ni.
Wells' Syndrome vei tan chuan hmalam hun a tha hle . Chumi awmzia chu nunna atana hlauhawm tak a ni lo tihna a ni.
- A tlangpuiin kar tlemte emaw thla engemaw zat emaw chhungin a hliamte chu a dam vek thin.
- Vawi tam tak chu hliam a awm lo .
- A châng chuan, a hrualna hmunah chuan vun rawng a danglam deuh thei bawk. Mahse chu chu hun kal zelah a bo fo thin.
- He natna hi a lo awm leh thei a ni. Chutiang hunah chuan a thunun vek theih nân kum engemaw zât a la ngai thei a ni. Mahse enkawlna hmangin a enkawl tha thei bawk.
He natna thlentu dik tak hi hmuh chhuah a la nih loh avangin inven dan tur chiang tak a awm lo. Mahse, heng symptoms te hi i tawn chuan a tha ber chu hlauthawng lo la, a rang thei ang bera doctor pan la, thurawn la rawh.
Take-Home Thuchah a ni
- Wells’ Syndrome hi vun natna hrik kai lo, natna hrik awm lo a ni. Bacteria infection cellulitis an tih nen chuan a danglam vek a ni.
- Hei hi keimahni immune system-a ‘eosinophils’ an tih cells te overactivity vang a ni.
- A lan chhuah dan ber chu vun sen, hring, hring, leh vun natna te hi a ni. Heng patch te hi hun kal zelah rawng a inthlak thin.
- Natna dik taka hriat theih nan vun biopsy tih a pawimawh hle.
- He natna hi steroid damdawi ang chi enkawlna hmangin hlawhtling takin a control theih a ni.
- Hei hi natna hlauhawm tak a ni lo. A tlangpuiin hliam awm lovin a dam thin.
- I vunah hian hetiang chiah hian hmun danglam emaw, a hring emaw i neih chuan doctor pan nghal rawh.











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