A chang chuan chhan awm lovin i thinlung chu a na zual deuh niin i hria em? I tlanbo mai mai angin i inhria em? I rilru a na a, thawk a harsa a, i lu a buai a, i mit a sen vek ang tih i hria em? Heng thil tawn te hi i tawng tawh a nih chuan a chhan pakhat chu tuna kan sawi tak Wolff-Parkinson-White Syndrome tih hi a ni thei. A hming hi a buaithlak deuh a nih chuan hlau suh. Hemi chungchang hi awlsam takin, i hriatthiam theih angin i sawi ang u.
Wolff-Parkinson-White (WPW) Syndrome hi eng nge ni tak tak?
A awlsam zawngin WPW Syndrome hi kan thinlunga electrical signal kal dan inthlak danglamna tlemte a ni. Pian tirh atanga awm thin condition a ni.
Pump tlemte ang maiin han ngaihtuah teh. He pump hian rhythm dik taka hna a thawh theih nan electrical signal a dawng a ngai a ni. A tlangpuiin heng signal te hi thinlung chhunga kawng bik pakhatah chauh an kal thin. He kawngpui dungah hian junction te tak te AV node an tih a awm a . He junction hian thinlung chunglam (atria) leh hnuai lam (ventricular chambers) te chu a hnuaia mi ang hian a inzawm khawm theih nan a pui thin.
Mahse WPW Syndrome vei thinlungah chuan electrical pathway pangngai bakah hian accessory pathway a awm a. Hei hi khawpui chhunga kawngpui lian tak paltlang theihna tur "shortcut" ang mai a ni.
He extra pathway hian rate control tu AV node chu a bypass a, electrical signal te chu heart chamber hnuai lam, ventricles thlengin rang takin a kal thei a ni. Hei hian heart chambers te chu a pangngai aia hmain a contract tir thin. Damdawi lamah chuan hei hi preexcitation kan ti a ni. Heng signal rang leh pangngai lo tak takte hian thinlung chu a ti na nghal zual sauh sauh a ni. Heng thinlung thawk chak chi hrang hrangte hi ``supraventricular tachycardia - SVT'' emaw ``atrial fibrillation - AFib'' tih ang chi hming kan hmang thin.
WPW Syndrome hi i thinlunga chak lohna a ni lo tih hre reng ang che. Thinlung electrical system-a pianpui inthlak danglamna tenau tak mai a ni.
Hetiang dinhmun hi a tam vak lo. Khawvel puma mi 1,000 zinga 1 leh 3 inkar velin a vei a ni. Pianpui thinlung lama harsatna dang nei, Ebstein’s anomaly ang chite zingah a tam zawk.
WPW Syndrome natna lan chhuah dante chu engte nge ni?
WPW Syndrome vei zawng zawng hian symptom an nei vek dawn lo. Mi thenkhat chuan an dam chhung zawngin chutiang dinhmun chu an nei tih an hre lo mai thei. Mahse symptoms a awm tak tak a nih chuan heart rate a chak lutuk hian a awm tlangpui.
Engvangin nge hetiang hi a lo awm? Thinlung a thawk chak lutuk chuan a chamber-te hian thisen a khat turin hun an nei tlem hle. Chuvang chuan thinlung hian taksaah thisen a pump tling thei lo. Hei hi heng symptoms te hi a lo awm hun a ni.
A hnuaia table-ah hian eng symptoms ber berte nge ni tih i lo en ang u.
| Symptom a ni | Hrilhfiahna awlsam tak |
|---|---|
| Lungphun (Palpitations) a awm | I rilru a na nghal vat a, i thinlung chu i rilru atanga rawn chhuak ang maiin. Hei hi ṭhut mai mai, exercise lak lai, stress hnuaia awm emaw, coffee ang chi stimulant ei hnuah emaw a thleng thei a ni. |
| Luak chhuak thei | Lung a na hle tih a hriat. Hetiang dinhmun hi thluak hian thisen a dawn tlem chuan a thleng thei a ni. |
| Faint emaw, faint emaw tihna | Mit a sen, a rilru a buai emaw, a hriatna a bo emaw. |
| Chauhna emaw Chak lohna emaw | I taksain nunna nei lo anga inhriatna, chau reng reng anga inhriatna. |
| Thâwk a tawi | Thâwk khuh emaw, thawk harsa emaw tih hriat. |
| Chest pressure emaw tightness emaw a awm | A rilru a buai emaw, a rit emaw tih hriatna. |
WPW Syndrome hi eng thilin nge a thlen?
Mi tam zawk tan chuan WPW Syndrome hi a chhan chiang tak hmuh a la ni lo. Hei hian random takin a thleng mai tihna a ni. Mahse mi tlemte tan chuan he natna hi genetic factors avanga lo awm a ni thei. A chhan pakhat chu PRKAG2 tih gene a inthlak danglam vang a ni. Heng genetic changes te hi thlah khat atanga thlah dangah pawh a kal zel thei bawk.
Hetiang dinhmun avang hian eng harsatna nge awm thei?
WPW Syndrome vei tam zawk hi chu nun pangngaiin an hmang thin. Mahse, enkawl loh chuan a chang chuan harsatna a awm thei. Ngaihtuah buai suh , hengte hi a tlem hle. Tin, tûn laiah hian an veng thei damdawi ṭha tak tak a awm bawk.
- Thil hriatna hloh vanga accident: I hriatna hloh thut chuan i tlu thei a, i hliam thei bawk.
- Heart rhythm dik lo dang: Heart rhythm dik lo dang, atrial fibrillation ang chi te hi a lo awm thei a ni.
- Heart rhythm mumal lo hlauhawm tak: A tlem hle a, ``Ventricular fibrillation'' tih hming pu natna hlauhawm tak a awm thei.
- Sudden cardiac death: Hei hi WPW syndrome natna khirh ber leh awm lo ber a ni. Enkawlna tum ber pakhat chu he hlauhawmna hi tihbo vek hi a ni.
He natna hi Doctor ten engtin nge an hriat chian?
A chunga kan sawi tak symptoms i neih chuan i doctor-in a tih hmasak ber tur chu ECG (electrocardiogram) tih a ni ang. Hei hi test awlsam tak, hrehawm lo tak a ni.
ECG hian thinlung electrical activity a record thei a ni. WPW syndrome vei ECG-ah chuan extra electrical pathway avanga pattern bik a awm tih a lang. He pattern hi "WPW pattern" kan ti a.
- WPW pattern: I ECG-ah he pattern bik hi nei mah la, symptom i neih loh chuan i doctor chuan WPW pattern i nei tih chauh a sawi ang.
- WPW Syndrome: I ECG-ah hian he pattern nen hian rilru natna ang chi symptoms i neih chuan i doctor chuan WPW Syndrome i nei tih a hre mai ang.
ECG bakah hian i doctor chuan test dang engemaw zat tih a rawt thei bawk.
- Echocardiogram (Echo): Hei hi thinlung ultrasound scan a ni. Thinlung insiam dan, chamber leh valve te chu a thawk tha em tih hriat nan a pui thin.
- Electrophysiology study: Hei hi test buaithlak deuh a ni. Hetah hian wire te tak te (catheter) te chu thinlung chhungah dahin, thinlunga electrical pathways te chu map a ni a, extra pathway awmna dik tak chu hriat chian a ni.
- Exercise stress test: Treadmill-a tlan tir i ni a, exercise i tih laiin i thinlung hnathawh leh rhythm a inthlak dan enfiah nan ECG hman a ni.
- Ambulatory monitoring (Holter monitor) hmanga enkawlna: 1.1.I taksaah hian device te tak te i bun a, chu chuan darkar 24 emaw a aia rei emaw chhung i heart rate a record thin. Hei hian nitin hnathawh pangngai i tih laiin i thinlung rhythm inthlak danglamna hriatchhuahna kawngah a pui a ni.
WPW Syndrome hi eng enkawlna nge ni?
WPW Syndrome hi enkawlna tha tak tak a awm a. I doctor chuan i natna lan chhuah dan te, a lo awm fo dan te, leh i test result te a zirin i tana enkawlna tha ber tur a ruat ang.
| Enkawl dan tur | Hrilhfiahna |
|---|---|
| Antiarrhythmic damdawi hman tur | Thinlung thawk chakna control thei damdawi hian natna lan chhuah tamna a ti tlem thei a ni. |
| Vagal Maneuver hmanga tih theih a ni | I heart rate a chak chuan a pangngaia a lo kir leh theih nan in lamah thil awlsam tak tak i tih theih a awm. Entirnan, khuh nasa emaw, towel lum hmanga hmai phih emaw. I doctor chuan hengte tih dan tur a zirtir ang che. |
| Cardioversion tih hi a ni | Emergency-ah, chu chu heartbeat a rang chhunzawm zel chuan damdawi inah electric shock te tak te chu a rilruah thlentirna a ni. |
| Catheter hmanga tihbo a ni | Hei hi WPW Syndrome enkawlna tha ber leh nghet ber a ni. Hetah hian wire te tak te (catheter) chu thinlungah hian groin chhunga thisen kalna kaltlangin dah a ni a, extra electrical pathway chu a awm a, radiofrequency energy emaw cryoablation hmangin a deactivate a ni. Hei hi enkawlna 94% aia tam hlawhtling a ni. Hemi hnu hian natna hi a dam kim thei a ni. |
| Surgery hmanga Ablation tih a ni | Catheter ablation method a hlawhchham emaw, heart surgery dang neih a ngai emaw chauha hman thin method. |
Engtikah nge Doctor ka hmuh ang?
WPW Syndrome i nei a nih chuan doctor pan a, regular check-up (follow-up) neih a pawimawh hle. I doctor chuan eng chen nge i luh tur tih a hrilh ang che.Tin, i natna lan chhuah danah danglamna i hmuh emaw, natna thar i neih chuan i doctor hnenah hriattir nghal rawh.
Hetiang dinhmun nena nun dun hian a chang chuan hlauhna leh lungkhamna tlem i nei thei. Chu chu thil pangngai tak a ni. Hetiang hunah hian a chhunga bottle-a dah ai chuan i rintlak tak emaw, counselor emaw pawh biak hi i rilru hriselna atan a tha hle thei a ni.
ETU-a emergency treatment neih hun tur
A hnuaia symptoms te hi i neih chuan damdawi in hnai ber Emergency Treatment Unit (ETU) ah kal nghal rawh .
- I rilru natna nasa tak i neih chuan .
- Fainting a ni.
- I thinlung thawk chak tak chu minute engemaw zat aia rei a awm reng a, i doctor-in a tih Vagal Maneuvers i tih hnuah pawh a reh lo a nih chuan .
Hriat lohna i neih chuan i in tanpui thei lo mai thei. Chuvangin i chhungte leh i thiante i hun hmanpui thinte hnenah i dinhmun hi hriattir a pawimawh hle. Chutiang chuan emergency-a tih tur an hre thei ang.
Hetiang dinhmun karah hian ka hmalam hun chu eng ang nge ni ang?
WPW Syndrome vei tam zawk, enkawlna dik dawngte chuan nun pangngai, hrisel takin an hmang thei a ni . A bik takin Catheter Ablation hian he natna hi a tidam vek thei a, cardiac death nghal theihna lakah a venghim thei bawk.
I nitin nunah thil engemaw takah i fimkhur a ngai mai thei. Entirnan, i thinlung ti na thei thilte chu pumpelh a tha ber.
- Zu
- Caffeine (coffee, tea thenkhat, soft drink thenkhat) .
- Nicotine (meizial zuk) ang chi thil tichaktu .
- Exercise hahthlak, hahthlak tak (i doctor hnenah eng exercise nge i tan a him tih zawt rawh) .
I fain WPW Syndrome a neih chuan...
Nu leh pa i nih angin i fain he natna hi a nei tih i hriat chuan i hlau hle mai thei. Chu chu thil pangngai a ni. A pawimawh ber chu i fa doctor nen zalen taka inbia a, i zawhna zawng zawng zawh hi a ni.
Entirnan, i fate tan infiamna khelh a him em tih emaw, sikulah an heart rate a san chuan eng nge an tih tur tih emaw chungchangah thupek chiang tak dawng rawh. Doctor chuan i fain a hriatthiam theih ṭawngkam hmanga thil awmdan sawifiah turin a pui thei bawk che a ni.
WPW Syndrome tih hming hi a hlauhawm thei hle. Mahse, enkawl theih, a tam zawkah chuan tihdam theih vek dinhmun a ni tih hre reng ang che. I doctor leh medical team te chu tanpui turin an awm a ni. Chuvangin zawhna i neih apiang zawt hreh suh.
Take-Home Thuchah a ni
- Wolff-Parkinson-White (WPW) Syndrome hi pianpui atanga lo piang a ni a, chu chu thinlungah extra electrical pathway a awm vang a ni.
- Lung na lutuk, luak chhuak, leh hriatna hloh ang chi symptoms te chu a lo lang nghal thei a ni. Mahse, mi zawng zawng hian symptom an nei vek lo.
- He natna hriat theihna atana test ber chu ECG a ni.
- Lungngai suh! Hemi atan hian enkawlna tha tak tak a awm a. Catheter Ablation tih damdawi hian he natna hi 94% aia tam a tidam vek thei a ni.
- I rilru na, i rilru a buai emaw, i thinlung a na reng a nih chuan damdawi in ETU- ah kal nghal rawh.
- I natna lan chhuah dan leh i enkawl dan tur chu i doctor nen zalen takin sawipui rawh. Enkawlna dik leh nunphung thlak danglam chuan nun hrisel tak i hmang thei ang.











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