Ɛyɛ ade a ɛfata sɛ wobɛte ehu ne dadwen pii nka bere a wote komayare bi ho asɛm, sɛ́ ɛyɛ wo anaa wo ba no. Titiriw sɛ wote din te sɛ Eisenmenger Syndrome a, ebia wubesusuw ho sɛ, "Dɛn ne eyi?" Nanso mma ɛnhaw wo. Yɛbɛka tebea no, ne sɛnkyerɛnne ahorow, ne n’ayaresa ho asɛm wɔ ɔkwan tiawa a wubetumi ate ase so.
Ɔkwan bɛn so na tebea yi sɔre?
Sɛ yɛbɛka no tiawa a, Eisenmenger yare no yɛ nea efi koma mu yare a wɔde awo obi mu ba bere tenten . Nea ɛbɛyɛ na yɛate eyi ase no, ma yenni kan nhwɛ sɛnea yɛn koma yɛ adwuma.
Fa yɛn koma sɛ pɔmpɛ ketewaa bi nanso ahoɔden wom yiye a ɛwɔ adan anan. Afã anan na ɛwɔ hɔ: atifi adan abien (atria) ne abien a ɛwɔ fam (ventricles). Mpɛn pii no, eyi ne sɛnea ɛyɛ adwuma:
1. Mogya a oxygen nni mu a ɛnam nipadua no nyinaa mu no kɔ soro dan a ɛwɔ nifa so no mu.
2. Efi hɔ no, mogya no kɔ ɔdan a ɛwɔ fam a ɛwɔ nifa so no mu na wɔde kɔ ahurututu no mu.
3. Wɔ ahurututu mu no, oxygen wɔ mogya yi mu yiye.
4. Saa mogya a ɛho tew a oxygen wom yi san kɔ soro dan a ɛwɔ koma no benkum so no mu.
5. Fi hɔ kɔ dan a ɛwɔ fam a ɛwɔ benkum so no mu na pompa wo nipadua nyinaa.
Nanso, wɔ nnipa binom a wɔwoo wɔn koma mu dɛmdi bi mu no, ebia tokuru ketewaa bi bɛda koma no mu adan yi ntam, titiriw wɔ koma no mu adan abien a ɛwɔ fam (ventricles) no ntam . Eyi ne nea ɛba:
- Mogya a oxygen pii wom na ɛho tew wɔ benkum so no bi fa saa tokuru no mu kɔ nifa so na ɛsan kɔ ahurututu no mu.
- Sɛ mogya a ɛho nhia yi kɔ so kɔ ahurututu no mu a, mogya mmoroso a ɛwɔ ahurututu no mu no kɔ soro yiye . Yɛfrɛ eyi ``ahurututu mu mogya mmoroso``.
- Bere kɔ so no, esiane nhyɛso kɛse yi a ɛwɔ ahurututu mu nti, mogya no dan kɔ akyi. Ɛne sɛ, mogya a oxygen nni mu na ɛho ntew a ɛwɔ nifa so no sen fa saa tokuru no mu kɔ benkum so na efi ase di akɔneaba wɔ nipadua no nyinaa mu.
Eyi ne Eisenmenger yare no mu ade titiriw. Ɛne sɛ, nipadua no nnya mframa pa dodow a ɛho hia. Sɛ wɔanhu komayare a ɛwɔ awo mu no ntɛm na wɔansa no ntɛm a, saa tebea yi ba.
Dɛn ne eyi ho sɛnkyerɛnne atitiriw?
Mpɛn pii no, saa sɛnkyerɛnne ahorow yi fi ase da adi ansa na wɔadu mpanyin afe so. Ɛtɔ da bi mpo a, wotumi hu wɔn wɔ nkokoaabere mu. Nsɛnkyerɛnne a ɛyɛ mmerɛw sɛ wobehu no bi ni.
| Nsɛnkyerɛnne a ɛkyerɛ | Nkyerɛkyerɛmu a ɛnyɛ den |
|---|---|
| Honam ani kɔla a ɛsakra bruu (Cyanosis) . | Anofafa, nnadewa, ne honam ani hwɛbea yɛ bruu/kɔkɔɔ esiane mframa pa a enni nipadua no mu nti. |
| Clubbing a wɔbɔ | Nsateaa ne nansoaa ano yɛ kurukuruwa na nnadewa no te sɛ nea ahonhon. |
| Ɔhome a ɛyɛ den | Ɔbrɛ ne ɔbrɛ a wobɛte nka, titiriw bere a worebɔ mmɔden kakra no. |
| Nipadua mu ahonhon (Edema) . | Ɛhonhon, titiriw wɔ mmeae te sɛ nan, nansoaa, ne yafunu. |
| Koma a ɛbɔ a ɛnyɛ ne kwan so | Sɛ wote nka sɛ wo koma rebɔ ntɛmntɛm anaasɛ wo koma bɔ ntɛmntɛm. |
| Adwene a ɛyɛ basaa ne tiyɛ | Tebea a ebetumi afi oxygen a wonnya mu aba. |
| Koko mu yaw | Koko a ɛyɛ den anaa ɛyaw esiane nhyɛso a ɛba koma no so nti. |
Nea ɛka ho no, saa tebea yi betumi aka nipadua no mogya mu nkwammoaa kɔkɔɔ a wɔyɛ, mogya a ɛtwetwe, anaa mogya a ɛbɛtɔ dodo.
Ɔkwan bɛn so na oduruyɛfo no hu eyi? (Nyare a Wɔahu) .
Sɛ wo ba no wɔ saa sɛnkyerɛnne ahorow yi a, wo duruyɛfo bedi kan de wo akɔma mmofra komayare ho oduruyɛfo. Ebia obetumi ayɛ sɔhwɛ ahorow pii de asi tebea no so dua.
- Nipadua mu nhwehwɛmu: Ade a edi kan a ɛsɛ sɛ wohwehwɛ ne honam ani kɔla bruu, nsakrae a ɛba nsateaa mu, ne koma a wotie.
- Nhwehwɛmu titiriw: Wɔyɛ nhwehwɛmu ahorow yi de si so dua sɛ wɔahu yare no pɛpɛɛpɛ.
| Sɔhwɛ | Dɛn na wuhu wɔ eyi mu? |
|---|---|
| Echo Scan (Echocardiogram) . | Eyi yɛ koma no mu nhwehwɛmu. Etumi hu sɛnea wɔahyehyɛ koma no, sɛ ebia ntokuru wɔ adan no ntam, ne sɛnea mogya no sen no pefee. |
| ECG (Electrocardiogram) . | Eyi boa ma wɔhwɛ sɛnea koma no anyinam ahoɔden yɛ adwuma, kyerɛ sɛ, sɛnea koma no bɔ denneennen. |
| Mogya mu Nhwehwɛmu | Wɔrehwɛ nipadua no mogya mu nkwammoaa kɔkɔɔ dodow (a ebetumi akɔ soro esiane mframa pa a enni hɔ nti) ne nneɛma afoforo. |
| Koma mu Catheter a Wɔde Ma | Eyi yɛ sɔhwɛ titiriw. Wɔde afiri ketewaa bi (catheter) fa mogya ntini bi mu kɔ koma no mu, na ɛma wotumi susuw nhyɛso a ɛwɔ koma no mu adan mu ne mogya ntini a ɛkɔ ahurututu no mu no tẽẽ. |
Ɔkwan bɛn so na wɔsa?
Sɛ Eisenmenger yare no ba pɛ a, wontumi nyɛ oprehyɛn ntoto tokuru a ɛwɔ koma no mu a ɛde bae no mu efisɛ nhyɛso a ɛwɔ ahurututu no mu no akɔ soro kɛse dedaw. Enti, ayaresa botae titiriw ne sɛ wobedi yare no ho sɛnkyerɛnne ahorow so na ama asetra atu mpɔn.
Ebia ayaresa nhyehyɛe no bi ne:
- Nnuru ahorow a wɔde di dwuma:
- Nnuru a ɛma mogya ntini a ɛwɔ ahurututu mu no trɛw na ɛma mogya mmoroso so tew.
- Aduru a wɔde ma koma no bɔ denneennen.
- Nnuru a ɛmma mogya nkɔ (blood thinners).
- Siw nyarewa ano (nnuru a ekum ɔyare mmoawa).
- Ɛtɔ mmere bi a, nnuru a wɔde di dwuma a iron wom.
- Mogya a woyi fi hɔ: Sɛ wo mogya mu nkwammoaa kɔkɔɔ dodow dɔɔso dodo na wo mogya mu yɛ den a, ɛtɔ mmere bi a ebia ɛho behia sɛ woyi mogya bi fi wo nipadua mu (phlebotomy).
- Koma ne ahurututu a wɔde ma:Wɔyɛ eyi wɔ tebea horow a emu yɛ den sen biara mu nkutoo, bere a koma ne ahurututu no nyinaa adi nkogu no. Eyi yɛ oprehyɛn a ɛyɛ den yiye, kɛse.
Ɔkwan bɛn so na wobɛtra ase ne tebea yi?
Ɛyɛ nokware sɛ eyi yɛ nkwa nna nyinaa tebea, nanso sɛ wodi ho dwuma yiye na wodi aduruyɛ mu afotu akyi a, nnipa pii betumi atra ase a ɛbɛn sɛnea ɛte daa.
Ade a ɛho hia sen biara ne sɛ wo ne wo duruyɛfo bɛkɔ so adi nkitaho daa na woadi n’akwankyerɛ akyi pɛpɛɛpɛ.
Suban ahorow bi a ɛho hia a ɛsɛ sɛ wode ka w’asetra ho:
- Kwati sɛ wobɛkɔ mmeae a ɛkorɔn na wo ho ayɛ wo hyew.
- Wɔnkamfo apɔw-mu-teɛteɛ ne agumadi a emu yɛ den nkyerɛ, nanso bisa wo duruyɛfo apɔw-mu-teɛteɛ ko a wubetumi ayɛ.
- Di aduan a nkyene nnim . Kwati sigaretnom koraa.
- Mma nnnom nnuru a wɔtɔn wɔ aduruyɛdan mu, nea wonom ma wo ti yɛ wo yaw mpo, a wunni kan nkɔ wo duruyɛfo nkyɛn.
- Nya wo vaccinations wɔ bere ano. Hohoro akuru nketewa mpo ho yiye na ama woabɔ wo ho ban afi ɔyare mmoawa ho.
- Mfa nsu a ɛyɛ hyew anaa sauna nni dwuma. Wobetumi ama mogya mmoroso akɔ fam mpofirim.
- Sɛ worehyia oprehyɛn foforo anaa biribi te sɛ wo sẽ a woyi a, hwɛ hu sɛ wubebisa wo koma ho ɔyaresafo sɛ ɛsɛ sɛ wudi kan nom nnuru a ekum ɔyare mmoawa anaa.
Nyinsɛn ho nimdeɛ titiriw
Sɛ woyɛ ɔbea a wowɔ saa tebea yi a, nyinsɛn yɛ asiane kɛse ma wo ne wo ba nkwa nyinaa . Esiane sɛ nyinsɛn de ɔhaw kɛse ba koma no so nti, mpɛn pii no nnuruyɛfo nkamfo nkyerɛ. Ɛho hia sɛ wo ne wo duruyɛfo bɔ eyi ho nkɔmmɔ pefee.
Saa tebea yi a wobɛtra ase no betumi ayɛ nkate fam asɛnnennen. Bisa wo duruyɛfoɔ fa afotuo dwumadie anaa mmoa akuo a ɛbɛtumi aboa wo ne w’abusua ho.
Nkrasɛm a Wɔde Kɔ Fie
- Eisenmenger syndrome yɛ tebea a emu yɛ den a efi komayare a wɔde awo obi mu ba, nanso wobetumi adi ho dwuma yiye.
- Wobetumi asiw tebea yi ano denam komayare a ɛda adi no a wobehu na wɔasa wɔ mmofraase no so.
- Ɛho hia sɛ wudi ayaresa nhyehyɛe a wo duruyɛfo de ma wo no akyi pɛpɛɛpɛ. Mma w’ankasa mfi ase nni nnuru biara ase anaasɛ nnyae.
- Nsakrae a wɔyɛ wɔ asetra mu (aduan a nkyene nnim, sigaretnom a wogyae, apɔw-mu-teɛteɛ a ɛfata) boa kɛse wɔ sɛnkyerɛnne ahorow a wodi so no mu.
- Nyinsɛn yɛ asiane kɛse ma ɔbea a ɔwɔ saa tebea yi, enti ɛho hia sɛ wo ne wo duruyɛfo bɛka ho asɛm pefee.
- Ɛnyɛ wo nko ara na woretu kwan yi. Nsuro sɛ wobɛsrɛ mmoa afi nnuruyɛfo, abusua, ne sɛ ɛho hia a, ɔfotufo bi hɔ.











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