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So yɛbɛka akisikuru a ɛntaa nsi a wɔfrɛ no Pheochromocytoma no ho asɛm nnɛ?

So yɛbɛka akisikuru a ɛntaa nsi a wɔfrɛ no Pheochromocytoma no ho asɛm nnɛ?

So ɛtɔ mmere bi a wo mogya mmoroso mpofirim? Anaasɛ wo ho fifiri kɛkɛ? So wo ti yɛ wo yaw a wo koma rebɔ? Mma ntɛm nsusuw sɛ saa nneɛma yi mu kakraa bi yɛ yare a emu yɛ den. Nanso, sɛ saa sɛnkyerɛnne ahorow yi kɔ so, titiriw wɔ mogya mmoroso a ɛyɛ den sɛ wobedi so a, ɛbɛyɛ papa sɛ wobɛhaw wo ho kakra. Ɛnnɛ yɛrebɛka tebea bi a ɛntaa nsi kakra, nanso sɛ wohu no yiye a, wobetumi asa no yiye paa ho asɛm. Wɔfrɛ ɛno pheochromocytoma.

Dɛn ne Pheochromocytoma? Momma yɛnte ase tiawa.

Sɛ yɛbɛka no tiawa a, pheochromocytoma yɛ akisikuru a ɛba wɔ adrenal glands no mfinimfini fã, adrenal medulla. Nkwammoaa soronko bi a wɔfrɛ no chromaffin nkwammoaa na ɛyɛ saa akisikuru yi. Saa nkwammoaa yi yɛ na woyi nkwaadɔm a ɛho hia ma yɛn nipadua "ko anaa guan" mmuae kɔ mogya no mu. Susuw ho hwɛ, sɛ wosuro mpofirim anaasɛ wohyia adwennwen pii a, nsakrae a ɛba wo nipadua mu - wo koma bɔ kɔ soro, wo ho fifiri, wo nipadua wosow - saa hormone ahorow yi na ɛde eyi ba.

Pheochromocytoma taa ba wɔ adrenal gland biako pɛ mu. Nanso, ɛtɔ mmere bi a, ebetumi aba ntini abien no nyinaa mu. Ebetumi aba sɛ wobenya akisikuru bɛboro biako wɔ ntini biako mu.

Nea ɛho hia no, pheochromocytomas dodow no ara nyɛ nea asiane biara nni ho (ɛnyɛ nea ɛyɛ hu) . Eyi kyerɛ sɛ wɔntrɛw nkɔ nipadua no afã afoforo. Nanso, 10% kosi 15% betumi ayɛ kokoram. Sɛ eyi yɛ kokoram tebea a, wɔka ho asɛm wɔ akuw atitiriw pii mu, a egyina sɛnea atrɛw so:

  • Localized pheochromocytoma: Akisikuru no wɔ adrenal ntini biako anaa abien no nyinaa mu.
  • Regional pheochromocytoma: Kokoram no atrɛw akɔ ntini a ɛbɛn adrenal glands anaa ntini afoforo mu.
  • Metastatic pheochromocytoma: Kokoram no atrɛw akɔ akwaa a ɛwɔ akyirikyiri te sɛ mmerɛbo, ahurututu, anaa nnompe mu.
  • Pheochromocytoma a ɛsan ba bio: Kokoram no asan aba bio bere a wɔasa no yare akyi. Ebetumi ayɛ beae koro no ara a na ɛwɔ ansa na ɛreba no anaa baabi foforo.

Dɛn ne saa adrenal ntini ahorow yi a ɛwɔ yɛn nipadua mu? Dɛn ne wɔn dwumadi?

Yɛwɔ adrenal ntini abien. Wɔwɔ yɛn yafunu akyi, yɛn asaabo atifi, te sɛ kyɛw. Wɔyɛ yɛn endocrine nhyehyɛe no fã. Adrenal gland biara wɔ afã atitiriw abien. Wɔfrɛ akyi fã no adrenal cortex, na wɔfrɛ mfinimfini fã no adrenal medulla.

Yɛn adrenal medulla no yɛ nkwaadɔm kuw bi a wɔfrɛ no catecholamines. Saa nkwaadɔm yi di nneɛma pii a ɛho hia yiye so wɔ yɛn nipadua mu:

  • Koma a ɛbɔ
  • Mogya mmoroso
  • Mogya mu asikre dodow `(Mogya mu glucose)`
  • Sɛnea yɛn nipadua yɛ n’ade wɔ adwennwen ho ("ako anaa guankɔbea" mmuae) .

Catecholamine ahorow titiriw ne:

  • Dopamine a wɔde yɛ aduru
  • Epinephrine (Adrenaline) `(Nneɛma a ɛma obi nya ahoɔden / Adrenaline)`
  • Norepinephrine (Noradrenaline) `(Nor a wɔde hyɛ nipadua mu / Noradrenaline)`

Sɛ pheochromocytoma wɔ hɔ a, ebetumi ayi saa nkwaadɔm yi pii, adrenaline ne noradrenaline, akɔ mogya no mu sen sɛnea ɛho hia. Ɛno na sɛnkyerɛnne ahorow fi ase da adi.

Nsonsonoe bɛn na ɛda Pheochromocytoma ne Paraganglioma ntam?

Eyinom yɛ akisikuru ahorow abien a ɛne ne ho di nsɛ yiye, a wɔntaa nhu. Nneɛma abien no nyinaa fi chromaffin nkwammoaa koro no ara a yɛadi kan aka ho asɛm no mu. Nanso, pheochromocytoma sɔre wɔ adrenal gland (adrenal medulla) no mfinimfini, bere a paraganglioma sɔre wɔ mmeae afoforo a ɛwɔ adrenal gland no akyi .

Hena na ɛda adi kɛse sɛ obenya saa tebea yi? Ɛtaa ba dɛn?

Pheochromocytoma betumi aba wɔ mfeɛ biara mu, nanso ɛtaa ba nnipa a wɔadi fi mfeɛ aduasa kɔsi 50. Wɔbɔ amanneɛ sɛ bɛyɛ 10% wɔ mmofraberɛ mu.

Eyi yɛ akisikuru a ɛntaa nsi koraa . Ɛyɛ den sɛ yɛbɛka nnipa dodow pɔtee a wɔwɔ saa tebea yi. Esiane sɛ nnipa binom nkyerɛ yare no ho sɛnkyerɛnne biara nti, ebia wɔrenhu yare no. Wobu akontaa sɛ nnipa a wɔwɔ mogya mmoroso no mu nnu 1% na wɔwɔ pheochromocytoma.

Nsɛnkyerɛnne bɛn na obi a ɔwɔ pheochromocytoma da no adi?

Pheochromocytoma ho sɛnkyerɛnne ba bere a akisikuru no gyae nkwaadɔm a wɔfrɛ no adrenaline (epinephrine) anaa noradrenaline (norepinephrine) pii kɔ mogya no mu no. Nanso, akisikuru bi ntumi mma saa hormone ahorow yi pii mma na ebia enni sɛnkyerɛnne biara.

Nsɛnkyerɛnne a wɔtaa hu ne:

  • Mogya mmoroso (Hypertension): Eyi ne sɛnkyerɛnne titiriw. Ɛtɔ mmere bi a, ɛyɛ den sɛ wobedi so.
  • Tiyɛ: Ebetumi ayɛ tiyɛ a emu yɛ den a ɛba mpofirim.
  • Fifiri a ɛboro so a ntease biara nnim.
  • Sɛ obi bɔ ntɛmntɛm a, ɛyɛ koma a ɛbɔ ntɛmntɛm, ɛnyɛ nea ɛkɔ so daa, anaasɛ ɛbɔ denneennen.
  • Sɛ wote nka sɛ wo nipadua rewosow.

Nsɛnkyerɛnne a ɛntaa nsi:

  • Koko ne/anaa yafunu mu yaw.
  • Wora no yɛ fitaa mpofirim sen sɛnea ɛtaa ba.
  • Akisikuru ne/anaasɛ ɔfe.
  • Ayamtuo.
  • Ayamtim.
  • Orthostatic hypotension yɛ mogya mmoroso a ɛkɔ fam mpofirim bere a wosɔre no. Eyi kyerɛ sɛ, sɛ wugyina hɔ mpofirim fi baabi a wote a, wo ho yɛ wo yaw.
  • Mu duru a wɔtew so a ntease biara nnim.

Saa sɛnkyerɛnne ahorow yi betumi ada adi anaasɛ ayɛ kɛse wɔ nsɛm bi akyi. Nhwɛsoɔ:

  • Apɔw-mu-teɛteɛ a emu yɛ den.
  • Nipadua mu opira anaa adwene mu nhyɛso a emu yɛ den.
  • Awo a wɔwo.
  • Nnuru a wɔde kum nipadua no a wobenya.
  • Oprehyɛn a wɔreyɛ.
  • Nnuan a tyramine pii wom a wobedi (e.g. bobesa kɔkɔɔ, chocolate, kyiisi).

So sɛnkyerɛnne ahorow no wɔ hɔ bere nyinaa? Anaasɛ wɔba na wɔkɔ?

Obi a ɔwɔ pheochromocytoma betumi anya mogya mmoroso a ɛkɔ so, anaasɛ ebetumi aba na akɔ .

Nnipa binom betumi anya "paroxysmal attacks," anaasɛ yare no ho sɛnkyerɛnne ntua mpofirim. Eyi kyerɛ sɛ mogya mmoroso kɔ soro mpofirim, na sɛnkyerɛnne ahorow te sɛ tiyɛ a emu yɛ den, koma bɔ kɛse, ne fifiri a ɛboro so ka ho. Saa "ntua" yi betumi aba mpɛn pii da biara, anaasɛ pɛnkoro anaa mprenu mpo ɔsram biara.

Nea ɛho hia: Sɛ wowɔ saa sɛnkyerɛnne ahorow yi bi, titiriw mogya mmoroso mpofirim, tiyɛ, fifiri, ne koma a ɛbɔ a, ɛho hia yiye sɛ wohwehwɛ aduruyɛfo afotu.

Dɛn nti na pheochromocytoma nya nkɔso? Dɛn na ɛde ba?

Mpɛn pii no, wontumi nhu ade pɔtee biara a ɛde pheochromocytoma ba. Ɛba kwa.

Nanso, wɔ nsɛm 25% kosi 35% mu no, saa tebea yi ne awosu mu tebea horow wɔ abusuabɔ. Nneɛma atitiriw no bi ne:

  • Multiple endocrine neoplasia 2 yare, ahorow A ne B (MEN2A ne MEN2B) .
  • Von Hippel-Lindau (VHL) yare no
  • Ntini mu ntini mu yare a ɛto so 1 (NF1) .
  • Paraganglioma a efi awosu mu yare
  • Carney-Stratakis dyad [paraganglioma ne yafunu mu akisikuru (GIST)].
  • Carney triad (paraganglioma, GIST ne ahurututu mu ntini mu yare) .

Wɔ awosu mu tebea horow yi akyi no, pheochromocytoma nso betumi aba esiane anyɛ yiye koraa no awosu mu nkwaadɔm ahorow 10 mu nsakrae nti.

Ɔkwan bɛn so na wohu yare yi? (Nyare a Wɔahu) .

Ebetumi ayɛ den sɛ wobehu pheochromocytoma efisɛ ɛyɛ akisikuru a ɛntaa nsi na ɛtɔ mmere bi a ɛmma wonhu sɛnkyerɛnne biara. Ɛtɔ mmere bi a, wohu akisikuru no wɔ akwanhyia mu bere a wɔreyɛ nhwehwɛmu bi esiane biribi foforo nti.

Nneɛma pii nti na oduruyɛfo betumi asusuw sɛ saa yare yi:

  • Wo deɛAduruyɛ ho abakɔsɛm a ɛkɔ akyiri, titiriw sɛ ebia obi wɔ abusua no mu anya pheochromocytoma pɛn anaa.
  • Nipadua ne aduruyɛ mu nhwehwɛmu a edi mũ.
  • Some specific symptoms , sɛ nhwɛso no "paroxysmal attacks" a yɛkaa ho asɛm ne mogya mmoroso a ayaresa a ɛfata nni so.

Sɔhwɛ ahorow bɛn na wɔyɛ?

Ebia wo duruyɛfo bɛkamfo nhwehwɛmu a edidi so yi akyerɛ sɛ ebia wowɔ pheochromocytoma anaa:

  • Nnɔnhwerew 24 nsu mu nhwehwɛmu: Nea ɛka eyi ho ne sɛ wobɛboaboa wo nsu ano da mũ no nyinaa na woasusuw catecholamines dodow a ɛwɔ mu. Ɛsan nso susuw nneɛma a ɛba bere a saa hormone ahorow yi asɛe no. Sɛ saa dodow yi dɔɔso sen sɛnea ɛte daa a, ebetumi ayɛ pheochromocytoma ho sɛnkyerɛnne.
  • Mogya mu catecholamine nhwehwɛmu: Eyinom susuw catecholamine dodow a ɛwɔ mogya no mu. Te sɛ nsu mu nhwehwɛmu no, wɔhwehwɛ nneɛma a ɛnam hormone ahorow a ɛpaapae mu ba nso.
  • CT scan (Computer Tomography scan): Eyi gye X-ray ahorow a wɔde yɛ wo nipadua no mu mfonini a ɛkɔ akyiri. Ebia wo duruyɛfo bɛkamfo eyi akyerɛ sɛ wɔmfa nhwɛ wo adrenal glands.
  • MRI scan (MRI - Magnetic Resonance Imaging): Eyi de magnet, radio asorɔkye, ne kɔmputa na ɛyɛ nipadua no mu mfonini a ɛkɔ akyiri. Wɔde hwehwɛ adrenal ntini no nso mu.

Sɛ wosi yare no so dua wie a, wobetumi ayɛ nhwehwɛmu foforo de ahu sɛ ebia akisikuru no yɛ kokoram (ɛyɛ bɔne) anaasɛ ɛnyɛ bɔne (ɛnyɛ bɔne), ne sɛ ebia atrɛw akɔ nipadua no afã afoforo.

Dɛn nti na Awosu mu Nhwehwɛmu Ho Hia?

Sɛ wohu sɛ wowɔ pheochromocytoma a, ɛda adi sɛ wo duruyɛfo bɛkamfo akyerɛ sɛ fa awosu mu afotu ne nhwehwɛmu a wɔbɛyɛ de ahu sɛ ebia wowɔ yare bi a wonya fi awo mu a ɛde wo to asiane mu sɛ wubenya kokoram afoforo anaa.

Ebia wɔbɛkamfo awosu mu nhwehwɛmu akyerɛ wɔ nsɛm te sɛ eyinom mu:

  • Sɛ wo anaa obi a ɔwɔ w’abusua mu wɔ sɛnkyerɛnne ahorow a ɛfa awosu mu pheochromocytoma anaa paraganglioma syndrome ho a.
  • Sɛ wowɔ akisikuru wɔ wo adrenal glands abien no nyinaa mu a.
  • Sɛ akisikuru bɛboro biako wɔ adrenal gland biako mu a.
  • Sɛ sɛnkyerɛnne ahorow bi wɔ hɔ a ɛkyerɛ sɛ catecholamines dodow akɔ soro wɔ mogya no mu a.
  • Sɛ wohu pheochromocytoma ansa na wɔadi mfe 40 a.

Sɛ awosu mu nhwehwɛmu bi hu sɛ awosu mu nsakrae bi a, awosu mu ɔfotufo no betumi akamfo akyerɛ sɛ w’abusua mufo afoforo (wɔn a wonni sɛnkyerɛnne biara nanso wɔwɔ asiane mu) nso nyɛ nhwehwɛmu yi.

Dɛn ne ayaresa ahorow a wɔde sa Pheochromocytoma?

Eyi ho ayaresa a eye sen biara ne sɛ wɔbɛyɛ oprehyɛn ayi akisikuru no afi hɔ, sɛ ɛbɛyɛ yiye a .

Ayaresa a wɔpaw no gyina nneɛma pii so:

  • Sɛnea akisikuru no kɛse te.
  • Sɛ́ ebia akisikuru no yɛ kokoram (ɛyɛ bɔne) anaasɛ ɛnyɛ bɔne (ɛnyɛ bɔne).
  • Sɛ́ ebia sɛnkyerɛnne ahorow bi wɔ hɔ esiane catecholamine hormone a ɛkɔ soro nti.
  • So akisikuru no wɔ beae biako, anaasɛ atrɛw akɔ nipadua no afã afoforo? (Wɔde Metastasis) .
  • Sɛ́ ebia wohuu yare no nea edi kan, anaasɛ asan aba bio wɔ ayaresa a atwam akyi.

Sɛ wowɔ sɛnkyerɛnne ahorow esiane adrenal hormone a ɛkɔ soro nti a, ebia wo duruyɛfo bɛkyerɛw nnuru a wode bedi saa sɛnkyerɛnne ahorow no so. Nhwɛsoɔ:

  • Nnuru a wɔde ma mogya mmoroso yɛ nea ɛfata, te sɛ alpha-blockers.
  • Nnuru a wɔde ma koma no bɔ ntɛmntɛm te sɛ beta-blockers.
  • Nnuru a esiw hormone ahorow a adrenal gland no gyae boro so no nkɛntɛnso ano.

Ayaresa atitiriw a wobetumi apaw ama pheochromocytoma ne:

  • Sɛɛgyiri
  • Mframa a wɔde sa yare
  • Nnuru a wɔde sa yare
  • Ablation ayaresa
  • Embolization ayaresa
  • Ayaresa a wɔde wɔn ani asi so

Wo ne w’aduruyɛ kuw no bom bɛkyerɛ ayaresa nhyehyɛe a eye ma wo.

Akwan titiriw a wɔfa so sa yare

  • Sɛɛgyiri:

Eyi ne pheochromocytoma ayaresa titiriw. Wobetumi de oprehyɛn ayi akisikuru bɛyɛ 90% afi hɔ yiye .

Ebia wo duruyɛfo bɛkamfo akyerɛ sɛ wɔnyɛ oprehyɛn nyi wo adrenal glands no biako anaa abien no nyinaa (adrenalectomy). Bere a wɔreyɛ oprehyɛn no, oduruyɛfo a ɔyɛ oprehyɛn no bɛhwehwɛ ntini ne ntini a atwa ho ahyia no mu ahwɛ sɛ akisikuru no atrɛw anaa. Sɛ ayɛ saa a, sɛ ɛbɛyɛ yiye a, wobeyi saa ntini no afi hɔ.

Sɛ wɔyɛ oprehyɛn wie a, wɔbɛsɔ wo mogya anaa wo nsu mu ahwɛ sɛ catecholamine dodow wɔ mu anaa. Sɛ dodow no san kɔ sɛnea na ɛte kan no a, ɛkyerɛ sɛ wɔayi pheochromocytoma nkwammoaa no nyinaa afi hɔ.

Sɛ woyi adrenal ntini abien no nyinaa fi hɔ a, ɛsɛ sɛ wofa hormone therapy wo nkwa nna nyinaa de si hormone a adrenal glands no yɛ no ananmu.

  • Mframa a wɔde sa yare:

Eyi yɛ aduru a wɔde kum kokoram nkwammoaa anaasɛ wɔmma ɛnnyin. Wɔyɛ eyi wɔ ɔkwan a ɛrempira ntini a ɛwɔ apɔwmuden sɛnea ɛbɛyɛ yiye biara so.

Mframa a wɔde sa yare no gu ahorow abien:

  • Abɔnten mframa a wɔde sa yare: Wɔde mframa fi afiri bi a ɛwɔ nipadua no akyi mu kɔ baabi a kokoram no wɔ.
  • Mframa a wɔde sa yare a ɛwɔ nipadua no mu: Wɔde aduru bi a ɛma mframa bɔne hyehyɛ nnade, aba, nhama, anaa afiri a wɔde fa nsu mu na oduruyɛfo de hyɛ baabi a kokoram no wɔ anaa baabi a ɛbɛn hɔ.

Mframa a wɔde sa yare no gyina sɛ ebia kokoram no wɔ baabi, ɔmantam, ɛtrɛw kɔ mmeae afoforo, anaasɛ ɛsan ba bio so. Wɔtaa de abɔnten so mframa a wɔde sa yare ne/anaasɛ 131I-MIBG ayaresa na ɛsa pheochromocytoma a ɛyɛ hu. 131I-MIBG yɛ ade a ɛma anyinam ahoɔden a ɛbata kokoram nkwammoaa bi ho na ekum wɔn.

  • Nnuru a wɔde sa yare:

Eyi de nnuru di dwuma de kunkum kokoram nkwammoaa, siw wɔn mpaepae na ɛnnɔɔso, anaasɛ wogyae kokoram nyin. Wɔtaa de nnuru yi fa ntini mu. Ɛwom sɛ eyi yɛ ayaresa a edi mu de, nanso ebetumi de ɔhaw ahorow aba.

  • Ablation ayaresa:

Eyi yɛ ayaresa a ɛnyɛ den pii. Ɛde ɔhyew a ano yɛ den anaa awɔw a ano yɛ den di dwuma de sɛe akisikuru no.

  • Radiofrequency ablation: Radiofrequency ablation de radio asorɔkye di dwuma de ma kokoram nkwammoaa ne nkwammoaa a ɛnyɛ ne kwan so yɛ hyew na ɛsɛe.
  • Cryoablation: Ɛde nitrogen a ɛyɛ nsu anaa carbon dioxide a ɛyɛ nsu di dwuma de ma kokoram nkwammoaa ne nkwammoaa a ɛnyɛ ne kwan so yɛ nwini na ɛsɛe.
  • Embolization ayaresa:

Wɔ eyi mu no, ntini a ɛde mogya kɔ adrenal gland no mu no siw. Eyi ma mogya nkɔ ntini no mu, na ekunkum kokoram nkwammoaa a enyin wɔ hɔ no.

  • Ayaresa a wɔde asi wɔn ani so:

Eyi de nnuru anaa nneɛma afoforo a ɛtow hyɛ kokoram nkwammoaa nkutoo so pɔtee a ɛnpira nkwammoaa a ɛte apɔw di dwuma. Wɔde saa ayaresa yi di dwuma ma pheochromocytoma a ɛkɔ mmeae afoforo ne nea ɛsan ba bio.

Wɔreyɛ aduru bi a esiw tyrosine kinase ano a wɔfrɛ no sunitinib ho nhwehwɛmu wɔ pheochromocytoma a ɛkɔ mmeae afoforo ho. Saa nnuru yi siw akisikuru no nyin ano.

So wobetumi asiw yare yi ano?

Nea ɛyɛ awerɛhow no, ɔkwan biara nni hɔ a wɔbɛfa so asiw pheochromocytoma ano. Nanso, sɛ wowɔ asiane mu sɛ wubenya yare yi esiane awosu mu yare ne awosu mu nkwaadɔm nti a, awosu mu afotu betumi aboa ma woayɛ nhwehwɛmu na woahu ntɛm.

Sɛ w’abusua mufo a wɔbɛn wo no mu biara (anuanom, awofo) anya pheochromocytoma, anaasɛ wowɔ awosu mu tebea bi te sɛ nea yɛadi kan aka ho asɛm no (Multiple endocrine neoplasia 2 syndrome, Von Hippel-Lindau (VHL) yare, Neurofibromatosis type 1 (NF1), Hereditary paraganglioma syndrome, Carney-Stratakis dyad, Carney triad), ɛho hia yiye sɛ wo ne wo duruyɛfo kasa fa ho.

Hokwan bɛn na ɛwɔ hɔ sɛ ne ho bɛtɔ no bere a wɔasa no yare awie no? (Nkɔmhyɛ) .

Mpɛn pii no, sɛ wɔsa pheochromocytoma ho anidaso no ye yiye .Yɛaka dedaw sɛ wobetumi ayi akisikuru bɛyɛ 90% afi hɔ yiye wɔ oprehyɛn mu.

Nanso, sɛ wɔansa tebea yi a, ebetumi de ɔhaw ahorow a emu yɛ den a ɛde nkwa to asiane mu mpo aba . Nhwɛsoɔ:

  • Koma ne ntini mu yare
  • Myocarditis a ɛyɛ mmerɛw
  • Mogya a ɛba amemene no mu a wontumi nni so (Cerebral hemorrhaging) .
  • Nsu a ɛboaboa ano wɔ ahurututu mu (Pulmonary edema) .

Ayarefo binom a wɔwɔ pheochromocytoma nso wɔ asiane mu sɛ wobenya akisikuru anaasɛ koma mu ntini a ɛyɛ mmerɛw.

Bere bɛn na ɛsɛ sɛ mekɔ oduruyɛfo nkyɛn?

  • Sɛ wohu sɛ wowɔ pheochromocytoma na wunya sɛnkyerɛnne biara a ɛhaw adwene a, kɔ wo duruyɛfo nkyɛn ntɛm ara.
  • Sɛ wowɔ pheochromocytoma ho sɛnkyerɛnne te sɛ mogya mmoroso ne tiyɛ a, wo ne wo duruyɛfo nkasa. Ɛwom sɛ pheochromocytoma ntaa mma de, nanso ɛho hia sɛ wɔsa mogya mmoroso.
  • Sɛ wunim sɛ w’abusuafo a wɔbɛn wo no mu biako (nuanom, awofo) wɔ awosu mu tebea bi te sɛ `Multiple endocrine neoplasia 2 syndrome` anaa `Von Hippel-Lindau (VHL) disease` a, ebia wo nso wobɛkɔ asiane kɛse mu sɛ wubenya pheochromocytoma, enti kɔ oduruyɛfo nkyɛn kɔka awosu mu nhwehwɛmu ho nkɔmmɔ.

Nsɛm bɛn na ɛsɛ sɛ mibisa oduruyɛfo no?

Sɛ wohu sɛ wowɔ pheochromocytoma a, ebia ɛbɛyɛ papa sɛ wubebisa wo duruyɛfo nsɛm yi:

  • Dɛn nti na minyaa pheochromocytoma?
  • So me mma ne/anaasɛ me abusuafo betumi anya pheochromocytoma?
  • Ayaresa ahorow bɛn na mewɔ?
  • Dɛn ne nneɛma bɔne a efi ayaresa ahorow mu ba?
  • Mɛyɛ dɛn atumi adi me yare no ho sɛnkyerɛnne ahorow ho dwuma?

Nea etwa to no, nneɛma a ɛho hia sen biara a ɛsɛ sɛ wokae (Take-Home Message) .

Okay, enti, ɛwom sɛ pheochromocytoma yɛ akisikuru a ɛntaa nsi de, nanso ɛtaa yɛ nea ɛnyɛ hu na wotumi sa . Afei nso, ebetumi atu mmirika wɔ mmusua mu, enti sɛ wohu sɛ wo anaa w’abusua mu obi anya saa tebea yi a, ɛho hia sɛ woyɛ awosu mu nhwehwɛmu. Eyi nso betumi aboa ma woahu sɛ ebia wowɔ asiane mu sɛ wubenya akwahosan ho haw afoforo anaa.

Kae sɛ, sɛ wowɔ nsɛmmisa bi fa asiane a ɛwɔ hɔ sɛ wubenya pheochromocytoma anaa yare yi ho a, nsuro sɛ wo ne wo duruyɛfo bɛkasa. Wɔwɔ ha sɛ wɔrebɛboa wo. Kɔ so nya apɔwmuden!


Pheochromocytoma , adrenal gland, catecholamines, mogya mmoroso, tiyɛ, fifiri, akisikuru, endocrine nhyehyɛe

Frequently Asked Questions (FAQ)

Sɔhwɛ ahorow bɛn na wɔyɛ?

Ebia wo duruyɛfo bɛkamfo nhwehwɛmu a edidi so yi akyerɛ sɛ ebia wowɔ pheochromocytoma anaa:

Dɛn nti na Awosu mu Nhwehwɛmu Ho Hia?

Sɛ wohu sɛ wowɔ pheochromocytoma a, ɛda adi sɛ wo duruyɛfo bɛkamfo akyerɛ sɛ fa awosu mu afotu ne nhwehwɛmu a wɔbɛyɛ de ahu sɛ ebia wowɔ yare bi a wonya fi awo mu a ɛde wo to asiane mu sɛ wubenya kokoram afoforo anaa.

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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Yɛsrɛ wo bu akontaa: 8 + 1 =
So yɛbɛka akisikuru a ɛntaa nsi a wɔfrɛ no Pheochromocytoma no ho asɛm nnɛ?
Nyarewa ne Tebea Ahorow5, Kutawonsa, 2026

So yɛbɛka akisikuru a ɛntaa nsi a wɔfrɛ no Pheochromocytoma no ho asɛm nnɛ?

So ɛtɔ mmere bi a wo mogya mmoroso mpofirim? Anaasɛ wo ho fifiri kɛkɛ? So wo ti yɛ wo yaw a wo koma rebɔ? Mma ntɛm nsusuw sɛ saa nneɛma yi mu kakraa bi yɛ yare a emu yɛ den. Nanso, sɛ saa sɛnkyerɛnne ahorow yi kɔ so, titiriw wɔ mogya mmoroso a ɛyɛ den sɛ wobedi so a, ɛbɛyɛ papa sɛ wobɛhaw wo ho kakra. Ɛnnɛ yɛrebɛka tebea bi a ɛntaa nsi kakra, nanso sɛ wohu no yiye a, wobetumi asa no yiye paa ho asɛm. Wɔfrɛ ɛno pheochromocytoma.

Dɛn ne Pheochromocytoma? Momma yɛnte ase tiawa.

Sɛ yɛbɛka no tiawa a, pheochromocytoma yɛ akisikuru a ɛba wɔ adrenal glands no mfinimfini fã, adrenal medulla. Nkwammoaa soronko bi a wɔfrɛ no chromaffin nkwammoaa na ɛyɛ saa akisikuru yi. Saa nkwammoaa yi yɛ na woyi nkwaadɔm a ɛho hia ma yɛn nipadua "ko anaa guan" mmuae kɔ mogya no mu. Susuw ho hwɛ, sɛ wosuro mpofirim anaasɛ wohyia adwennwen pii a, nsakrae a ɛba wo nipadua mu - wo koma bɔ kɔ soro, wo ho fifiri, wo nipadua wosow - saa hormone ahorow yi na ɛde eyi ba.

Pheochromocytoma taa ba wɔ adrenal gland biako pɛ mu. Nanso, ɛtɔ mmere bi a, ebetumi aba ntini abien no nyinaa mu. Ebetumi aba sɛ wobenya akisikuru bɛboro biako wɔ ntini biako mu.

Nea ɛho hia no, pheochromocytomas dodow no ara nyɛ nea asiane biara nni ho (ɛnyɛ nea ɛyɛ hu) . Eyi kyerɛ sɛ wɔntrɛw nkɔ nipadua no afã afoforo. Nanso, 10% kosi 15% betumi ayɛ kokoram. Sɛ eyi yɛ kokoram tebea a, wɔka ho asɛm wɔ akuw atitiriw pii mu, a egyina sɛnea atrɛw so:

  • Localized pheochromocytoma: Akisikuru no wɔ adrenal ntini biako anaa abien no nyinaa mu.
  • Regional pheochromocytoma: Kokoram no atrɛw akɔ ntini a ɛbɛn adrenal glands anaa ntini afoforo mu.
  • Metastatic pheochromocytoma: Kokoram no atrɛw akɔ akwaa a ɛwɔ akyirikyiri te sɛ mmerɛbo, ahurututu, anaa nnompe mu.
  • Pheochromocytoma a ɛsan ba bio: Kokoram no asan aba bio bere a wɔasa no yare akyi. Ebetumi ayɛ beae koro no ara a na ɛwɔ ansa na ɛreba no anaa baabi foforo.

Dɛn ne saa adrenal ntini ahorow yi a ɛwɔ yɛn nipadua mu? Dɛn ne wɔn dwumadi?

Yɛwɔ adrenal ntini abien. Wɔwɔ yɛn yafunu akyi, yɛn asaabo atifi, te sɛ kyɛw. Wɔyɛ yɛn endocrine nhyehyɛe no fã. Adrenal gland biara wɔ afã atitiriw abien. Wɔfrɛ akyi fã no adrenal cortex, na wɔfrɛ mfinimfini fã no adrenal medulla.

Yɛn adrenal medulla no yɛ nkwaadɔm kuw bi a wɔfrɛ no catecholamines. Saa nkwaadɔm yi di nneɛma pii a ɛho hia yiye so wɔ yɛn nipadua mu:

  • Koma a ɛbɔ
  • Mogya mmoroso
  • Mogya mu asikre dodow `(Mogya mu glucose)`
  • Sɛnea yɛn nipadua yɛ n’ade wɔ adwennwen ho ("ako anaa guankɔbea" mmuae) .

Catecholamine ahorow titiriw ne:

  • Dopamine a wɔde yɛ aduru
  • Epinephrine (Adrenaline) `(Nneɛma a ɛma obi nya ahoɔden / Adrenaline)`
  • Norepinephrine (Noradrenaline) `(Nor a wɔde hyɛ nipadua mu / Noradrenaline)`

Sɛ pheochromocytoma wɔ hɔ a, ebetumi ayi saa nkwaadɔm yi pii, adrenaline ne noradrenaline, akɔ mogya no mu sen sɛnea ɛho hia. Ɛno na sɛnkyerɛnne ahorow fi ase da adi.

Nsonsonoe bɛn na ɛda Pheochromocytoma ne Paraganglioma ntam?

Eyinom yɛ akisikuru ahorow abien a ɛne ne ho di nsɛ yiye, a wɔntaa nhu. Nneɛma abien no nyinaa fi chromaffin nkwammoaa koro no ara a yɛadi kan aka ho asɛm no mu. Nanso, pheochromocytoma sɔre wɔ adrenal gland (adrenal medulla) no mfinimfini, bere a paraganglioma sɔre wɔ mmeae afoforo a ɛwɔ adrenal gland no akyi .

Hena na ɛda adi kɛse sɛ obenya saa tebea yi? Ɛtaa ba dɛn?

Pheochromocytoma betumi aba wɔ mfeɛ biara mu, nanso ɛtaa ba nnipa a wɔadi fi mfeɛ aduasa kɔsi 50. Wɔbɔ amanneɛ sɛ bɛyɛ 10% wɔ mmofraberɛ mu.

Eyi yɛ akisikuru a ɛntaa nsi koraa . Ɛyɛ den sɛ yɛbɛka nnipa dodow pɔtee a wɔwɔ saa tebea yi. Esiane sɛ nnipa binom nkyerɛ yare no ho sɛnkyerɛnne biara nti, ebia wɔrenhu yare no. Wobu akontaa sɛ nnipa a wɔwɔ mogya mmoroso no mu nnu 1% na wɔwɔ pheochromocytoma.

Nsɛnkyerɛnne bɛn na obi a ɔwɔ pheochromocytoma da no adi?

Pheochromocytoma ho sɛnkyerɛnne ba bere a akisikuru no gyae nkwaadɔm a wɔfrɛ no adrenaline (epinephrine) anaa noradrenaline (norepinephrine) pii kɔ mogya no mu no. Nanso, akisikuru bi ntumi mma saa hormone ahorow yi pii mma na ebia enni sɛnkyerɛnne biara.

Nsɛnkyerɛnne a wɔtaa hu ne:

  • Mogya mmoroso (Hypertension): Eyi ne sɛnkyerɛnne titiriw. Ɛtɔ mmere bi a, ɛyɛ den sɛ wobedi so.
  • Tiyɛ: Ebetumi ayɛ tiyɛ a emu yɛ den a ɛba mpofirim.
  • Fifiri a ɛboro so a ntease biara nnim.
  • Sɛ obi bɔ ntɛmntɛm a, ɛyɛ koma a ɛbɔ ntɛmntɛm, ɛnyɛ nea ɛkɔ so daa, anaasɛ ɛbɔ denneennen.
  • Sɛ wote nka sɛ wo nipadua rewosow.

Nsɛnkyerɛnne a ɛntaa nsi:

  • Koko ne/anaa yafunu mu yaw.
  • Wora no yɛ fitaa mpofirim sen sɛnea ɛtaa ba.
  • Akisikuru ne/anaasɛ ɔfe.
  • Ayamtuo.
  • Ayamtim.
  • Orthostatic hypotension yɛ mogya mmoroso a ɛkɔ fam mpofirim bere a wosɔre no. Eyi kyerɛ sɛ, sɛ wugyina hɔ mpofirim fi baabi a wote a, wo ho yɛ wo yaw.
  • Mu duru a wɔtew so a ntease biara nnim.

Saa sɛnkyerɛnne ahorow yi betumi ada adi anaasɛ ayɛ kɛse wɔ nsɛm bi akyi. Nhwɛsoɔ:

  • Apɔw-mu-teɛteɛ a emu yɛ den.
  • Nipadua mu opira anaa adwene mu nhyɛso a emu yɛ den.
  • Awo a wɔwo.
  • Nnuru a wɔde kum nipadua no a wobenya.
  • Oprehyɛn a wɔreyɛ.
  • Nnuan a tyramine pii wom a wobedi (e.g. bobesa kɔkɔɔ, chocolate, kyiisi).

So sɛnkyerɛnne ahorow no wɔ hɔ bere nyinaa? Anaasɛ wɔba na wɔkɔ?

Obi a ɔwɔ pheochromocytoma betumi anya mogya mmoroso a ɛkɔ so, anaasɛ ebetumi aba na akɔ .

Nnipa binom betumi anya "paroxysmal attacks," anaasɛ yare no ho sɛnkyerɛnne ntua mpofirim. Eyi kyerɛ sɛ mogya mmoroso kɔ soro mpofirim, na sɛnkyerɛnne ahorow te sɛ tiyɛ a emu yɛ den, koma bɔ kɛse, ne fifiri a ɛboro so ka ho. Saa "ntua" yi betumi aba mpɛn pii da biara, anaasɛ pɛnkoro anaa mprenu mpo ɔsram biara.

Nea ɛho hia: Sɛ wowɔ saa sɛnkyerɛnne ahorow yi bi, titiriw mogya mmoroso mpofirim, tiyɛ, fifiri, ne koma a ɛbɔ a, ɛho hia yiye sɛ wohwehwɛ aduruyɛfo afotu.

Dɛn nti na pheochromocytoma nya nkɔso? Dɛn na ɛde ba?

Mpɛn pii no, wontumi nhu ade pɔtee biara a ɛde pheochromocytoma ba. Ɛba kwa.

Nanso, wɔ nsɛm 25% kosi 35% mu no, saa tebea yi ne awosu mu tebea horow wɔ abusuabɔ. Nneɛma atitiriw no bi ne:

  • Multiple endocrine neoplasia 2 yare, ahorow A ne B (MEN2A ne MEN2B) .
  • Von Hippel-Lindau (VHL) yare no
  • Ntini mu ntini mu yare a ɛto so 1 (NF1) .
  • Paraganglioma a efi awosu mu yare
  • Carney-Stratakis dyad [paraganglioma ne yafunu mu akisikuru (GIST)].
  • Carney triad (paraganglioma, GIST ne ahurututu mu ntini mu yare) .

Wɔ awosu mu tebea horow yi akyi no, pheochromocytoma nso betumi aba esiane anyɛ yiye koraa no awosu mu nkwaadɔm ahorow 10 mu nsakrae nti.

Ɔkwan bɛn so na wohu yare yi? (Nyare a Wɔahu) .

Ebetumi ayɛ den sɛ wobehu pheochromocytoma efisɛ ɛyɛ akisikuru a ɛntaa nsi na ɛtɔ mmere bi a ɛmma wonhu sɛnkyerɛnne biara. Ɛtɔ mmere bi a, wohu akisikuru no wɔ akwanhyia mu bere a wɔreyɛ nhwehwɛmu bi esiane biribi foforo nti.

Nneɛma pii nti na oduruyɛfo betumi asusuw sɛ saa yare yi:

  • Wo deɛAduruyɛ ho abakɔsɛm a ɛkɔ akyiri, titiriw sɛ ebia obi wɔ abusua no mu anya pheochromocytoma pɛn anaa.
  • Nipadua ne aduruyɛ mu nhwehwɛmu a edi mũ.
  • Some specific symptoms , sɛ nhwɛso no "paroxysmal attacks" a yɛkaa ho asɛm ne mogya mmoroso a ayaresa a ɛfata nni so.

Sɔhwɛ ahorow bɛn na wɔyɛ?

Ebia wo duruyɛfo bɛkamfo nhwehwɛmu a edidi so yi akyerɛ sɛ ebia wowɔ pheochromocytoma anaa:

  • Nnɔnhwerew 24 nsu mu nhwehwɛmu: Nea ɛka eyi ho ne sɛ wobɛboaboa wo nsu ano da mũ no nyinaa na woasusuw catecholamines dodow a ɛwɔ mu. Ɛsan nso susuw nneɛma a ɛba bere a saa hormone ahorow yi asɛe no. Sɛ saa dodow yi dɔɔso sen sɛnea ɛte daa a, ebetumi ayɛ pheochromocytoma ho sɛnkyerɛnne.
  • Mogya mu catecholamine nhwehwɛmu: Eyinom susuw catecholamine dodow a ɛwɔ mogya no mu. Te sɛ nsu mu nhwehwɛmu no, wɔhwehwɛ nneɛma a ɛnam hormone ahorow a ɛpaapae mu ba nso.
  • CT scan (Computer Tomography scan): Eyi gye X-ray ahorow a wɔde yɛ wo nipadua no mu mfonini a ɛkɔ akyiri. Ebia wo duruyɛfo bɛkamfo eyi akyerɛ sɛ wɔmfa nhwɛ wo adrenal glands.
  • MRI scan (MRI - Magnetic Resonance Imaging): Eyi de magnet, radio asorɔkye, ne kɔmputa na ɛyɛ nipadua no mu mfonini a ɛkɔ akyiri. Wɔde hwehwɛ adrenal ntini no nso mu.

Sɛ wosi yare no so dua wie a, wobetumi ayɛ nhwehwɛmu foforo de ahu sɛ ebia akisikuru no yɛ kokoram (ɛyɛ bɔne) anaasɛ ɛnyɛ bɔne (ɛnyɛ bɔne), ne sɛ ebia atrɛw akɔ nipadua no afã afoforo.

Dɛn nti na Awosu mu Nhwehwɛmu Ho Hia?

Sɛ wohu sɛ wowɔ pheochromocytoma a, ɛda adi sɛ wo duruyɛfo bɛkamfo akyerɛ sɛ fa awosu mu afotu ne nhwehwɛmu a wɔbɛyɛ de ahu sɛ ebia wowɔ yare bi a wonya fi awo mu a ɛde wo to asiane mu sɛ wubenya kokoram afoforo anaa.

Ebia wɔbɛkamfo awosu mu nhwehwɛmu akyerɛ wɔ nsɛm te sɛ eyinom mu:

  • Sɛ wo anaa obi a ɔwɔ w’abusua mu wɔ sɛnkyerɛnne ahorow a ɛfa awosu mu pheochromocytoma anaa paraganglioma syndrome ho a.
  • Sɛ wowɔ akisikuru wɔ wo adrenal glands abien no nyinaa mu a.
  • Sɛ akisikuru bɛboro biako wɔ adrenal gland biako mu a.
  • Sɛ sɛnkyerɛnne ahorow bi wɔ hɔ a ɛkyerɛ sɛ catecholamines dodow akɔ soro wɔ mogya no mu a.
  • Sɛ wohu pheochromocytoma ansa na wɔadi mfe 40 a.

Sɛ awosu mu nhwehwɛmu bi hu sɛ awosu mu nsakrae bi a, awosu mu ɔfotufo no betumi akamfo akyerɛ sɛ w’abusua mufo afoforo (wɔn a wonni sɛnkyerɛnne biara nanso wɔwɔ asiane mu) nso nyɛ nhwehwɛmu yi.

Dɛn ne ayaresa ahorow a wɔde sa Pheochromocytoma?

Eyi ho ayaresa a eye sen biara ne sɛ wɔbɛyɛ oprehyɛn ayi akisikuru no afi hɔ, sɛ ɛbɛyɛ yiye a .

Ayaresa a wɔpaw no gyina nneɛma pii so:

  • Sɛnea akisikuru no kɛse te.
  • Sɛ́ ebia akisikuru no yɛ kokoram (ɛyɛ bɔne) anaasɛ ɛnyɛ bɔne (ɛnyɛ bɔne).
  • Sɛ́ ebia sɛnkyerɛnne ahorow bi wɔ hɔ esiane catecholamine hormone a ɛkɔ soro nti.
  • So akisikuru no wɔ beae biako, anaasɛ atrɛw akɔ nipadua no afã afoforo? (Wɔde Metastasis) .
  • Sɛ́ ebia wohuu yare no nea edi kan, anaasɛ asan aba bio wɔ ayaresa a atwam akyi.

Sɛ wowɔ sɛnkyerɛnne ahorow esiane adrenal hormone a ɛkɔ soro nti a, ebia wo duruyɛfo bɛkyerɛw nnuru a wode bedi saa sɛnkyerɛnne ahorow no so. Nhwɛsoɔ:

  • Nnuru a wɔde ma mogya mmoroso yɛ nea ɛfata, te sɛ alpha-blockers.
  • Nnuru a wɔde ma koma no bɔ ntɛmntɛm te sɛ beta-blockers.
  • Nnuru a esiw hormone ahorow a adrenal gland no gyae boro so no nkɛntɛnso ano.

Ayaresa atitiriw a wobetumi apaw ama pheochromocytoma ne:

  • Sɛɛgyiri
  • Mframa a wɔde sa yare
  • Nnuru a wɔde sa yare
  • Ablation ayaresa
  • Embolization ayaresa
  • Ayaresa a wɔde wɔn ani asi so

Wo ne w’aduruyɛ kuw no bom bɛkyerɛ ayaresa nhyehyɛe a eye ma wo.

Akwan titiriw a wɔfa so sa yare

  • Sɛɛgyiri:

Eyi ne pheochromocytoma ayaresa titiriw. Wobetumi de oprehyɛn ayi akisikuru bɛyɛ 90% afi hɔ yiye .

Ebia wo duruyɛfo bɛkamfo akyerɛ sɛ wɔnyɛ oprehyɛn nyi wo adrenal glands no biako anaa abien no nyinaa (adrenalectomy). Bere a wɔreyɛ oprehyɛn no, oduruyɛfo a ɔyɛ oprehyɛn no bɛhwehwɛ ntini ne ntini a atwa ho ahyia no mu ahwɛ sɛ akisikuru no atrɛw anaa. Sɛ ayɛ saa a, sɛ ɛbɛyɛ yiye a, wobeyi saa ntini no afi hɔ.

Sɛ wɔyɛ oprehyɛn wie a, wɔbɛsɔ wo mogya anaa wo nsu mu ahwɛ sɛ catecholamine dodow wɔ mu anaa. Sɛ dodow no san kɔ sɛnea na ɛte kan no a, ɛkyerɛ sɛ wɔayi pheochromocytoma nkwammoaa no nyinaa afi hɔ.

Sɛ woyi adrenal ntini abien no nyinaa fi hɔ a, ɛsɛ sɛ wofa hormone therapy wo nkwa nna nyinaa de si hormone a adrenal glands no yɛ no ananmu.

  • Mframa a wɔde sa yare:

Eyi yɛ aduru a wɔde kum kokoram nkwammoaa anaasɛ wɔmma ɛnnyin. Wɔyɛ eyi wɔ ɔkwan a ɛrempira ntini a ɛwɔ apɔwmuden sɛnea ɛbɛyɛ yiye biara so.

Mframa a wɔde sa yare no gu ahorow abien:

  • Abɔnten mframa a wɔde sa yare: Wɔde mframa fi afiri bi a ɛwɔ nipadua no akyi mu kɔ baabi a kokoram no wɔ.
  • Mframa a wɔde sa yare a ɛwɔ nipadua no mu: Wɔde aduru bi a ɛma mframa bɔne hyehyɛ nnade, aba, nhama, anaa afiri a wɔde fa nsu mu na oduruyɛfo de hyɛ baabi a kokoram no wɔ anaa baabi a ɛbɛn hɔ.

Mframa a wɔde sa yare no gyina sɛ ebia kokoram no wɔ baabi, ɔmantam, ɛtrɛw kɔ mmeae afoforo, anaasɛ ɛsan ba bio so. Wɔtaa de abɔnten so mframa a wɔde sa yare ne/anaasɛ 131I-MIBG ayaresa na ɛsa pheochromocytoma a ɛyɛ hu. 131I-MIBG yɛ ade a ɛma anyinam ahoɔden a ɛbata kokoram nkwammoaa bi ho na ekum wɔn.

  • Nnuru a wɔde sa yare:

Eyi de nnuru di dwuma de kunkum kokoram nkwammoaa, siw wɔn mpaepae na ɛnnɔɔso, anaasɛ wogyae kokoram nyin. Wɔtaa de nnuru yi fa ntini mu. Ɛwom sɛ eyi yɛ ayaresa a edi mu de, nanso ebetumi de ɔhaw ahorow aba.

  • Ablation ayaresa:

Eyi yɛ ayaresa a ɛnyɛ den pii. Ɛde ɔhyew a ano yɛ den anaa awɔw a ano yɛ den di dwuma de sɛe akisikuru no.

  • Radiofrequency ablation: Radiofrequency ablation de radio asorɔkye di dwuma de ma kokoram nkwammoaa ne nkwammoaa a ɛnyɛ ne kwan so yɛ hyew na ɛsɛe.
  • Cryoablation: Ɛde nitrogen a ɛyɛ nsu anaa carbon dioxide a ɛyɛ nsu di dwuma de ma kokoram nkwammoaa ne nkwammoaa a ɛnyɛ ne kwan so yɛ nwini na ɛsɛe.
  • Embolization ayaresa:

Wɔ eyi mu no, ntini a ɛde mogya kɔ adrenal gland no mu no siw. Eyi ma mogya nkɔ ntini no mu, na ekunkum kokoram nkwammoaa a enyin wɔ hɔ no.

  • Ayaresa a wɔde asi wɔn ani so:

Eyi de nnuru anaa nneɛma afoforo a ɛtow hyɛ kokoram nkwammoaa nkutoo so pɔtee a ɛnpira nkwammoaa a ɛte apɔw di dwuma. Wɔde saa ayaresa yi di dwuma ma pheochromocytoma a ɛkɔ mmeae afoforo ne nea ɛsan ba bio.

Wɔreyɛ aduru bi a esiw tyrosine kinase ano a wɔfrɛ no sunitinib ho nhwehwɛmu wɔ pheochromocytoma a ɛkɔ mmeae afoforo ho. Saa nnuru yi siw akisikuru no nyin ano.

So wobetumi asiw yare yi ano?

Nea ɛyɛ awerɛhow no, ɔkwan biara nni hɔ a wɔbɛfa so asiw pheochromocytoma ano. Nanso, sɛ wowɔ asiane mu sɛ wubenya yare yi esiane awosu mu yare ne awosu mu nkwaadɔm nti a, awosu mu afotu betumi aboa ma woayɛ nhwehwɛmu na woahu ntɛm.

Sɛ w’abusua mufo a wɔbɛn wo no mu biara (anuanom, awofo) anya pheochromocytoma, anaasɛ wowɔ awosu mu tebea bi te sɛ nea yɛadi kan aka ho asɛm no (Multiple endocrine neoplasia 2 syndrome, Von Hippel-Lindau (VHL) yare, Neurofibromatosis type 1 (NF1), Hereditary paraganglioma syndrome, Carney-Stratakis dyad, Carney triad), ɛho hia yiye sɛ wo ne wo duruyɛfo kasa fa ho.

Hokwan bɛn na ɛwɔ hɔ sɛ ne ho bɛtɔ no bere a wɔasa no yare awie no? (Nkɔmhyɛ) .

Mpɛn pii no, sɛ wɔsa pheochromocytoma ho anidaso no ye yiye .Yɛaka dedaw sɛ wobetumi ayi akisikuru bɛyɛ 90% afi hɔ yiye wɔ oprehyɛn mu.

Nanso, sɛ wɔansa tebea yi a, ebetumi de ɔhaw ahorow a emu yɛ den a ɛde nkwa to asiane mu mpo aba . Nhwɛsoɔ:

  • Koma ne ntini mu yare
  • Myocarditis a ɛyɛ mmerɛw
  • Mogya a ɛba amemene no mu a wontumi nni so (Cerebral hemorrhaging) .
  • Nsu a ɛboaboa ano wɔ ahurututu mu (Pulmonary edema) .

Ayarefo binom a wɔwɔ pheochromocytoma nso wɔ asiane mu sɛ wobenya akisikuru anaasɛ koma mu ntini a ɛyɛ mmerɛw.

Bere bɛn na ɛsɛ sɛ mekɔ oduruyɛfo nkyɛn?

  • Sɛ wohu sɛ wowɔ pheochromocytoma na wunya sɛnkyerɛnne biara a ɛhaw adwene a, kɔ wo duruyɛfo nkyɛn ntɛm ara.
  • Sɛ wowɔ pheochromocytoma ho sɛnkyerɛnne te sɛ mogya mmoroso ne tiyɛ a, wo ne wo duruyɛfo nkasa. Ɛwom sɛ pheochromocytoma ntaa mma de, nanso ɛho hia sɛ wɔsa mogya mmoroso.
  • Sɛ wunim sɛ w’abusuafo a wɔbɛn wo no mu biako (nuanom, awofo) wɔ awosu mu tebea bi te sɛ `Multiple endocrine neoplasia 2 syndrome` anaa `Von Hippel-Lindau (VHL) disease` a, ebia wo nso wobɛkɔ asiane kɛse mu sɛ wubenya pheochromocytoma, enti kɔ oduruyɛfo nkyɛn kɔka awosu mu nhwehwɛmu ho nkɔmmɔ.

Nsɛm bɛn na ɛsɛ sɛ mibisa oduruyɛfo no?

Sɛ wohu sɛ wowɔ pheochromocytoma a, ebia ɛbɛyɛ papa sɛ wubebisa wo duruyɛfo nsɛm yi:

  • Dɛn nti na minyaa pheochromocytoma?
  • So me mma ne/anaasɛ me abusuafo betumi anya pheochromocytoma?
  • Ayaresa ahorow bɛn na mewɔ?
  • Dɛn ne nneɛma bɔne a efi ayaresa ahorow mu ba?
  • Mɛyɛ dɛn atumi adi me yare no ho sɛnkyerɛnne ahorow ho dwuma?

Nea etwa to no, nneɛma a ɛho hia sen biara a ɛsɛ sɛ wokae (Take-Home Message) .

Okay, enti, ɛwom sɛ pheochromocytoma yɛ akisikuru a ɛntaa nsi de, nanso ɛtaa yɛ nea ɛnyɛ hu na wotumi sa . Afei nso, ebetumi atu mmirika wɔ mmusua mu, enti sɛ wohu sɛ wo anaa w’abusua mu obi anya saa tebea yi a, ɛho hia sɛ woyɛ awosu mu nhwehwɛmu. Eyi nso betumi aboa ma woahu sɛ ebia wowɔ asiane mu sɛ wubenya akwahosan ho haw afoforo anaa.

Kae sɛ, sɛ wowɔ nsɛmmisa bi fa asiane a ɛwɔ hɔ sɛ wubenya pheochromocytoma anaa yare yi ho a, nsuro sɛ wo ne wo duruyɛfo bɛkasa. Wɔwɔ ha sɛ wɔrebɛboa wo. Kɔ so nya apɔwmuden!


Pheochromocytoma , adrenal gland, catecholamines, mogya mmoroso, tiyɛ, fifiri, akisikuru, endocrine nhyehyɛe

Frequently Asked Questions (FAQ)

Sɔhwɛ ahorow bɛn na wɔyɛ?

Ebia wo duruyɛfo bɛkamfo nhwehwɛmu a edidi so yi akyerɛ sɛ ebia wowɔ pheochromocytoma anaa:

Dɛn nti na Awosu mu Nhwehwɛmu Ho Hia?

Sɛ wohu sɛ wowɔ pheochromocytoma a, ɛda adi sɛ wo duruyɛfo bɛkamfo akyerɛ sɛ fa awosu mu afotu ne nhwehwɛmu a wɔbɛyɛ de ahu sɛ ebia wowɔ yare bi a wonya fi awo mu a ɛde wo to asiane mu sɛ wubenya kokoram afoforo anaa.

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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