Yala aw den kɔnɔbara kurulen don i n’a fɔ jiribolo? An ka kuma Prune Belly Syndrome kan!

Ni an ye den bangenen kura kɔnɔbara lajɛ, a ka c’a la, an b’a ye ko a nɔgɔlen don kosɛbɛ ani a falen don, tiɲɛ tɛ? Nka miiri k’a filɛ, tuma dɔw la, an ma miiri min na, an b’a ye ko den kɔnɔbara fari bɛ kurukuru kosɛbɛ, i n’a fɔ jirisunba. Ni i y’o ye, i n’a fɔ ba walima fa, i bɛ se ka siran kosɛbɛ ani ka i kabakoya. "E, mun kɛra n den na?" I bɛ se ka miiri. Tiɲɛ na, nin ye bana ye min man ca kosɛbɛ. Bi an bɛ kuma bana dɔ kan min man teli ka kɛ min bɛ se ka kɛ sababu ye ka nin bana in bila mɔgɔ la, n’o ye Prune Belly Syndrome ye . Aw kana aw hakili ɲagami, an bɛna kuma fɛn bɛɛ kan cogo nɔgɔman na ani cogo jɛlen na.

N’an y’a fɔ cogo nɔgɔman na, Prune Belly Syndrome ye mun ye?

Prune Belly Syndrome ye bana ye min man teli ka sɔrɔ bangekɔlɔsi fɛɛrɛw fɛ. A tɔgɔ Sɔrɔla bari den kɔnɔbara fari bɛ i n’a fɔ jirisunba. A taamasiɲɛ kunbaba saba b’a la. O de y’a To a bɛ Weele tuma dɔw la ko ‘Syndrome Triad’. A bɛ fɔ fana ko ‘Eagle-Barrett Syndrome’ ka bonya da dɔgɔtɔrɔw kan minnu y’a sɔrɔ.

O fɛnba saba ninnu ye:

1. Kɔnɔbara fasaw barika ka dɔgɔn walima minnu tɛ yen : Farikolo dɔw bɛ an kɔnɔbara la minnu bɛ dɛmɛ ka a cogoya to a la ani ka kɔnɔna yɔrɔw lakana, i n’a fɔ banakɔtaa. Nin bana in bɛ denmisɛn minnu na, o fasaw tɛ yiriwa ka ɲɛ. Tuma dɔw la, u tɛ Dabɔ fewu. O de kama kɔnɔbara fari bɛ i ko a kurukurulen don ani a bɛ sɔgɔsɔgɔ.

2. Ɲɛgɛnɛsiraw minnu ma jigin : Den cɛman na, a ka ca a la, cɛya bɛ kɛ farikolo kɔkan cɛya la. Nka, nin bana in bɛ den minnu na, cɛya bɛ sɔrɔ kɔnɔbara kɔnɔ. U ma jigin.

3. Sugunɛ gɛlɛyaw : Nin ye bana in yɔrɔ jugumanba ye. Den ka sugunɛw, a sugunɛbaralabana, ani tubabufura minnu bɛ u siri ɲɔgɔn na (sɔgɔsɔgɔninjɛ) olu tɛ yiriwa ka ɲɛ. O bɛ se ka gɛlɛyabaw lase koli la.

Ka fara nin taamasiɲɛ kunbaba saba ninnu kan, den dɔw fana bɛ se ka gɛlɛya suguya caman sɔrɔ dusukun, fogonfogon, banakɔtaa ani kolotugudaw la.

Nin bana in ka ca cogo di?

Nin ye bana ye min man ca kosɛbɛ. A bɛ den kura 30 000 fo 40 000 la kelen ɲɔgɔn minɛ. Min kɛrɛnkɛrɛnnen don , o ye ko nin bana ninnu 95% bɛ sɔrɔ cɛdenw de la . O bɛ Kɛ k’a sababu Kɛ an ye cɛya-kɔnɔ-jiginbaliya gɛlɛya min Fɔ ka Tɛmɛ, o bɛ cɛdenw dɔrɔn de Sɔrɔ.

Taamasiɲɛ jumɛnw bɛ se ka aw dɛmɛ ka a dɔn ni nin bana in bɛ aw den na?

A fɔra ko Prune Belly Syndrome taamasiɲɛw ka ca ni 50 ye. Nka, o taamasiɲɛw bɛ se ka ɲɔgɔn ta den ni den cɛ. Den dɔw bɛ se ka juguya kosɛbɛ, ka sɔrɔ dɔw fana man jugu o cogo la. Aw ka dɔgɔtɔrɔ bɛna aw den sɛgɛsɛgɛ ani ka sɛgɛsɛgɛliw kɛ minnu ka kan ka kɛ walasa ka o dafa ka da a kan.

An ka tabali lajɛ min bɛ duguma walasa ka a dɔn bana taamasiɲɛ minnu ka teli ka ye.

Mun na o bɛ kɛ denw na?

Ni an b’a fɛ ka tiɲɛ fɔ, dɔgɔtɔrɔw ma o sababu tigitigi sɔrɔ hali bi, nka hakilina damadɔ bɛ yen.

Dɔ wɛrɛw dalen b’a la ko nin gɛlɛya in bɛ sɔrɔ barisa kɔnɔbara fasaw tɛ yiriwa ka ɲɛ fɔlɔ. Dɔ wɛrɛw b’a fɔ ko a bɛ se ka kɛ sababu ye ka bɔ jamu dɔ la. O bana in fana fɔra balimakɛw cɛ. Ani fana, denmisɛn dɔw minnu ka kolosinsinnanw tɛ kelen ye i n’a fɔ `Trisomy 18 (Edwards Syndrome)` ani `Trisomy 21 (Down Syndrome)` fana bɛ nin Prune Belly Syndrome in sɔrɔ.

Gɛlɛya jumɛnw bɛ se ka sɔrɔ nin bana in fɛ?

Prune Belly Syndrome juguya bɛ bɔ gɛlɛya wɛrɛw la minnu bɛ sɔrɔ a la, kɛrɛnkɛrɛnnenya la sugunɛbaralabana tiɲɛni hakɛ.

Gɛlɛya minnu ka teli ka sɔrɔ olu ye:

• Kɔnɔboli : Kɔnɔbara fanga dɔgɔyali bɛ a to a ka gɛlɛn ka a gɛrɛntɛ kosɛbɛ fo ka se ka banakɔtaa tɛmɛ.
• Kolotugudaw : fɛn minnu bɛ i n’a fɔ kɔkiliw bɔli, tɛgɛw, bolokɔniw walima senkɔniw bɔgɔbɔgɔli.
• Sugunɛbilenni ka teli: Banakisɛw bɛ se ka sɔrɔ nɔgɔya la barisa sugunɛ tɛ bɔ ka ɲɛ. Nin bana ninnu bɛ se ka sugunɛ tiɲɛ.
• Den sɔrɔbaliya : Ni cɛya tɛ se ka jigin, o bɛ se ka nɔ bila den sɔrɔli seko la don nataw la. Farati bɛ cɛya kansɛri fana na.
• Fogonfogon la sɔgɔsɔgɔninjɛ : Fogonfogonw bɛ se ka yiriwa ka ɲɛ ka a sababu kɛ yɔrɔ dɛsɛ ye kɔnɔbara la.
• Sugunɛbilenni basigilen: O de ye gɛlɛya jugumanba ye. Gɛlɛya minnu bɛ to ka sɔrɔ sugunɛbaralabana na, olu bɛ se ka kɛ sababu ye ka sugunɛbaralabana dɔɔni dɔɔni.

Nin bana in bɛ dɔn cogo di?

A ka ca a la, nin bana in bɛ se ka dɔn joona i ka kɔnɔmaya waati la ni den ka ultrasound scan ye.Dɔgɔtɔrɔw bɛna sigasiga o la ni sɛgɛsɛgɛli y’a jira ko den ka sugunɛ ka bon kosɛbɛ walima ni sugunɛ fununen don. Sɛgɛsɛgɛli bɛ se k’a jira fana ko den kɔnɔbara fasaw tɛ a la.

Den bangenen kɔfɛ, dɔgɔtɔrɔ bɛ se ka sigasiga o la ka da den kɛnɛma cogoya kan, o kɔrɔ ye ko kɔnɔbara kurulen don. O kɔ, sɛgɛsɛgɛli suguya caman bɛ kɛ walasa ka bana in sɛgɛsɛgɛ ani ka farikolo yɔrɔw tiɲɛni hakɛ dɔn.

Sɛgɛsɛgɛli jumɛnw bɛ kɛ?

• Joli sɛgɛsɛgɛliw: Aw bɛ a dɔn sugunɛ baaracogo kan.
• Ultrasound Scan : Aw bɛ kɔnɔbara kɔnɔna yɔrɔw cogoya lajɛ, i n’a fɔ sugunɛ ni sugunɛ.
• X-ray : Walasa ka gɛlɛya dɔw lajɛ kolotugudaw la.
• CT Scan walima MRI Scan: Aw bɛ farikolo yɔrɔw ja jɛlen ni fɛn caman sɔrɔ.
• VCUG (Voiding Cystourethrogram): Nin ye sɛgɛsɛgɛli kɛrɛnkɛrɛnnen ye min bɛ kɛ ni rezow ye. O ye ka ji kɛrɛnkɛrɛnnen dɔ pikiri kɛ sugunɛ na ani ka ji bɛ tɛmɛ a kɔnɔ ni den bɛ koli kɛ. O bɛ dɛmɛ ka a dɔn ni sugunɛ bɛ ka woyo kɔfɛ (reflux).

O furakɛcogo jumɛnw bɛ yen?

Prune Belly Syndrome furakɛcogo bɛ danfara don den ni den cɛ. Sabula den bɛɛ tɛ bana in sɔrɔ cogo kelen na. A ka ca a la, dɔgɔtɔrɔ kɛrɛnkɛrɛnnenw ka kulu dɔ, i n’a fɔ denmisɛnw ka dɔgɔtɔrɔw, denmisɛnw ka sugunɛbilennikɛlaw ani sugunɛbilennikɛlaw, olu bɛ jɛ ka furakɛli fɛɛrɛ ɲuman labɛn aw den ye.

Ni aw bɛ furakɛli latigɛ, aw bɛ jateminɛ kɛ nin ko ninnu na:

• Den ka kɛnɛya bɛɛ lajɛlen.
• Den si hakɛ.
• Bana juguya ni farikolo yɔrɔ minnu tiɲɛna.
• Den ka se ka opereli ni furakɛli muɲu.
• Aw ka hakilinaw n’aw negew i n’a fɔ bangebagaw.

Nka, den caman bɛna opereli caman kɛ. Nin opereli ninnu kun ye ka kɔnɔbara kogo barika bonya, ka cɛya jigin, ani ka sugunɛbaralabana gɛlɛyaw latilen.

Opereli suguya caman bɛ kɛ minnu bɛ kɛ:

• Vesicostomie : O bɛ kɛ ni opereli ye ka da fitini dɔ kɛ kɔnɔbara dugumayanfan na ka don sugunɛ na. O bɛ a to sugunɛ bɛ bɔ ka ɲɛ. O bɛ se ka dɔ bɔ sugunɛ tiɲɛni na.
• Orchiopexy (Orchiopexy): O bɛ kɛ ni opereli ye ka cɛya, minnu bɛ kɔnɔbara kɔnɔ, ka jigin ka don cɛya la ka u labɛn.
• Sistɔplasti : Nin ye opereli ye min ka gɛlɛn dɔɔni. O bɛ kɛ sababu ye ka sugunɛbaralabana labɛn kokura pewu.

A jugumanba dɔw la, ni sugunɛw dɛsɛra pewu, .Sugunɛbilenni fana bɛ se ka kɛ wajibi ye.

O denmisɛnw ka siniɲɛsigi bɛna kɛ cogo di?

N b’a dɔn ko nin mɛnni ka gɛlɛn dɔɔnin. Nka a nafa ka bon ka tiɲɛ dɔn. Denmisɛn ninnu si hakɛ bɛ bɔ bana juguya hakɛ la. A ka c’a la, den 10% ni 25% cɛ bɛ sa kɔnɔbara la walima u bɛ sa gɛlɛyaw fɛ u bangenen dɔgɔkun fɔlɔ kɔnɔ.

Nka, fan dɔ bɛ yen min ka kɛnɛ. Prune Belly Syndrome bɛ denmisɛn minnu na, olu 40% ɲɔgɔn, hali ni gɛlɛya misɛnniw bɛ u ka sugunɛ kɛcogo la, u bɛ sugunɛ kɛcogo ɲuman mara ani ka ɲɛnamaya kɛcogo ɲuman na.

30% wɛrɛw bɛ se ka mago don sugunɛbilenni na waati dɔ la u ka ɲɛnamaya kɔnɔ. Min nafa ka bon kosɛbɛ, o ye ko nin bana in bɛ mɔgɔ o mɔgɔ la, o tigi ka kan ka kɛ dɔgɔtɔrɔ ka kɔlɔsili kɔnɔ a si bɛɛ la. Ka to ka sugunɛ kɛcogo kɔlɔsi, o nafa ka bon walasa ka sugunɛ tiɲɛni fɛn o fɛn dɔgɔya.

Aw bɛ se ka aw den ladon cogo di ani aw ka kan ka taa dɔgɔtɔrɔso la tuma min na?

Ni a sɔrɔla ko Prune Belly Syndrome (Prune Belly Syndrome) bɛ aw den na, a nafa ka bon kosɛbɛ ka dɔgɔtɔrɔ dɔ ɲini min bɛ se ka bana in dɔn. A bɛna fɛn bɛɛ ɲɛfɔ i ye ani k’i bilasira i den ladoncogo la.

Sugunɛbilenni (UTI) farati ka bon kosɛbɛ o denmisɛnniw ma. O la, ni aw ye sugunɛbilenni taamasiɲɛ fitini yɛrɛ kɔlɔsi, aw ka kan ka dɔgɔtɔrɔ wele joona.

Ni aw ye nin taamasiɲɛ ninnu dɔ kɔlɔsi, aw kana mɛn. Aw bɛ dɔgɔtɔrɔ ka ladilikan ɲini joona. Ani fana, a nafa ka bon ka taa dɔgɔtɔrɔsow la waati latigɛlenw na ani ka den lajɛ, i n’a fɔ dɔgɔtɔrɔ y’a fɔ cogo min na.