Ua loaʻa anei iā ʻoe a i ʻole kekahi āu i ʻike ai kahi ʻike weliweli a koke i kahi o nā ʻāpana o kou kino, ʻoiai kou maka, lehelehe, alelo, a me ka puʻu, pehu koke a lilo i pehu iki? He ʻano ʻoluʻolu ʻole loa kēia a he ʻano koʻikoʻi i kekahi manawa. I ka lāʻau lapaʻau, kapa mākou i kēia he angioedema . ʻAʻole like kēia me kahi maʻi allergy maʻamau, akā hiki ke ʻokoʻa loa. No laila, ma kēia ʻatikala, e kamaʻilio mākou e pili ana i kahi lāʻau lapaʻau kikoʻī a ikaika e hiki ke kōkua i ka kaohi ʻana i kēia ʻano angioedema.
I ka ʻōlelo maʻalahi, he aha kēia lāʻau i kapa ʻia ʻo C1 Inhibitor?
ʻAe, kani iki paha ka inoa i kahi paʻakikī, akā he maʻalahi kāna hana. ʻO C1 Inhibitor (Human) kahi lāʻau lapaʻau i hāʻawi ʻia e kāohi i ka angioedema ke koʻikoʻi, ʻo ia hoʻi, ke loaʻa kahi hoʻouka kaua o ka pehu ʻana i loko o ke kino. ʻAʻole ia e hāʻawi ʻia ma ke ʻano he pila maʻamau, akā ma ke ʻano he infusion i loko o kahi vein .
Aia kekahi protein i kapa ʻia ʻo C1 inhibitor i loko o ko kākou koko. ʻO kēia ka mea e hana ai e kāohi i kekahi o nā hopena e hoʻoulu ai i ka pehu ʻana i loko o ko kākou kino. Hānau ʻia kekahi poʻe me ka nele o kēia protein, a i ʻole ʻaʻole ia e hana pono. ʻO ia ka manawa e loaʻa ai ka angioedema, ʻo ia ke ʻano e pehu koke ai nā ʻāpana o ke kino. No laila, ʻo ka hana a kēia lāʻau lapaʻau, ʻo ia ka hāʻawi ʻana i ke kino i kahi protein exogenous C1 inhibitor a kāohi koke i kēlā kaʻina hana pehu i kāohi ʻole ʻia.
ʻO ka mea nui, ʻaʻole kēia he lāʻau lapaʻau i kēlā me kēia lā. Hoʻohana wale ʻia ia i nā pilikia ke koʻikoʻi ka angioedema.
Hana ʻia kēia lāʻau lapaʻau mai ka plasma koko kanaka. Akā, mai hopohopo, ua hoʻokō ʻia ke koko i lawe ʻia mai nā mea hāʻawi i kahi kaʻina hoʻāʻo koʻikoʻi loa e hōʻoia i ka ʻole o nā maʻi. No laila, ua haʻahaʻa loa ka pilikia o ka hoʻoili ʻana i ka maʻi.
Nā mea e pono ai ʻoe e haʻi i kāu kauka ma mua o ka lawe ʻana i kēia lāʻau lapaʻau
He mea nui loa kēia. Ma mua o kou hoʻomaka ʻana i kēia lāʻau lapaʻau, he mea nui e ʻike kāu kauka i kou mōʻaukala olakino piha. E hōʻoia e haʻi iā ia e pili ana i kekahi o kēia mau mea, ʻoiai inā loaʻa iā ʻoe kekahi o kēia mau mea:
| Kūlana a maʻamau paha | No ke aha ʻoe e hōʻike ai? |
|---|---|
| Inā he moʻolelo kou o nā ʻōpū koko a i ʻole ka hahau ʻana | Hiki i kēia lāʻau lapaʻau ke hoʻonui iki i ka pilikia o nā ʻūpā koko, no laila he mea nui e nānā pono iā ʻoe. |
| Maʻi puʻuwai a maʻi aʻa koko paha | Pono e mālama pono ʻia i ka wā e hāʻawi ai i kekahi lāʻau lapaʻau intravenous i nā poʻe maʻi puʻuwai. |
| Inā he catheter noho i loko o kahi aa koko kou | Pono ke kauka e ʻike e pili pū ana paha ke alo o ia mau mea hana me ka pilikia o nā ʻūpā koko. |
| Inā hāpai ʻoe, e hoʻāʻo ana e hāpai, a he makuahine hānai paha | I kēia mau hihia, pono ʻoe e kamaʻilio me kāu kauka e pili ana i nā hopena o ka lāʻau lapaʻau a hana i ka hoʻoholo maikaʻi loa. |
| Inā loaʻa iā ʻoe nā maʻi allergies i nā lāʻau lapaʻau ʻē aʻe, nā meaʻai, a i ʻole nā mea ʻē aʻe | He mea nui kēia e loiloi ai inā he liʻiliʻi iki ka manawa kūpono o kahi maʻi allergy i ka lāʻau lapaʻau. |
Pehea e hoʻohana ai i ka lāʻau lapaʻau a me nā kuhikuhi kūikawā
No ka mea, ua hāʻawi ʻia kēia lāʻau lapaʻau ma ke ʻano he inikini i loko o ke aʻa, hāʻawi pinepine ʻia e nā limahana lapaʻau i aʻo ʻia ma kahi haukapila a i ʻole ke keʻena lapaʻau. Eia nō naʻe, ua aʻo ʻia kekahi mau maʻi, ma ke aʻo a kā lākou kauka, e hāʻawi i kēia lāʻau lapaʻau ma ka home. Inā loaʻa iā lākou kēlā ʻano aʻo, he mea nui loa ia e hoʻomākaukau a inikini i ka lāʻau lapaʻau e like me ke kuhikuhi ʻana.
He kiko e pono ai ka nānā kūikawā!
Inā loaʻa iā ʻoe kahi hoʻouka ʻana o ka larynx, he kūlana koʻikoʻi ia e hiki ai ke pilikia i ka hanu ʻana. I kēlā hihia, ʻoiai inā ua mālama ʻoe i ka lāʻau lapaʻau ma ka home, pono ʻoe e hele i ka Emergency Department (ETU) o ka haukapila kokoke loa ma hope o ka loaʻa ʻana o ka lāʻau lapaʻau.
Mai hoʻolei i nā nila a me nā syringe i hoʻohana ʻia i loko o ka ʻōpala. Pono e waiho ʻia i loko o kahi pahu kūikawā ('pahu ʻoi') no kēia kumu. Inā ʻaʻohe āu, hiki iā ʻoe ke kiʻi i hoʻokahi mai kāu kauka a i ʻole ka haukapila.
Inā makemake kahi keiki ʻōpiopio i kēia lāʻau lapaʻau, e kūkākūkā pono me ke kauka pediatric a hahai i kā lākou ʻōlelo aʻo.
He aha kāu e hana ai inā lawe nui ʻoe i ka lāʻau lapaʻau?
He lāʻau lapaʻau ulia pōpilikia kēia, no laila haʻahaʻa ka manawa e hiki ai kēia. Eia nō naʻe, inā manaʻo ʻoe ua overdose ʻoe, e hele koke i ka Emergency Department (ETU) kokoke loa. Inā pono, hiki iā ʻoe ke kelepona i ke National Poisons Information Centre ma ka Colombo National Hospital no ka ʻōlelo aʻoaʻo.
Nā hopena ʻaoʻao e hiki mai ana ma hope o ka lawe ʻana i ka lāʻau lapaʻau
E like me nā lāʻau lapaʻau āpau, hiki i kēia ke hana i nā hopena ʻaoʻao i kekahi poʻe. Hiki i kekahi o lākou ke koʻikoʻi a pono e mālama koke ʻia.
| Nā hopena ʻaoʻao koʻikoʻi e pono e hōʻike koke ʻia i ke kauka | |
|---|---|
| 🔴 | Nā hopena maʻi ʻaleka koʻikoʻi (hives, maneʻo, pehu o ka maka, lehelehe, alelo) |
| 🔴 | Nā Hōʻailona o ka hahau ʻana: Ka mae koke ʻana a i ʻole ka nāwaliwali ma ka maka, ka lima, a i ʻole ka wāwae, ka paʻakikī i ka ʻōlelo ʻana a i ʻole ka hoʻomaopopo ʻana, ka paʻakikī i ka hele wāwae, ka poniuniu, a me nā loli o ka ʻike. |
| 🔴 | Nā Hōʻailona o ke Koko Paʻa: Paʻakikī ka hanu ʻana, ʻeha ka umauma, ʻeha ka wāwae, ka pehu ʻana, a me ka mehana. |
| 🔴 | Ka puʻuwai wikiwiki, ka ʻeha poʻo nui. |
| Nā hopena ʻaoʻao ʻaʻole i koʻikoʻi pinepine, akā pono e hōʻike ʻia i ke kauka inā hoʻomau lākou | |
|---|---|
| 🟢 | ʻEha poʻo |
| 🟢 | Ka loli ʻana o ka ʻono i loko o ka waha |
ʻAʻole i loko o kēia papa inoa nā hopena ʻaoʻao āpau. Inā loaʻa iā ʻoe kekahi mea ʻē, e kamaʻilio me kāu kauka e pili ana i ia mea.
Leka Lawe-Home
- He lāʻau lapaʻau kūikawā ka mea hoʻopaʻa C1 no ka angioedema. He inikini ia i hāʻawi ʻia i loko o kahi aʻa koko.
- He mea nui e haʻi i kāu kauka i kou mōʻaukala olakino piha, ʻoiai kekahi mōʻaukala o nā ʻōpū koko a i ʻole nā maʻi puʻuwai.
- Inā paha ʻoe e lawe i ka lāʻau lapaʻau no ka hoʻouka ʻana o ka larynx, e hele koke i ka lumi pilikia o ka haukapila (ETU) ma hope o ka lawe ʻana. He hana hoʻōla ola kēia.
- E makaʻala i nā hopena ʻino koʻikoʻi, e like me nā hōʻailona o ka hahau ʻana a i ʻole ke koko ʻūlū. Inā ʻike ʻoe i kekahi o kēia mau mea, e ʻimi koke i ke kōkua lapaʻau.
- Inā he mau nīnau kāu e pili ana i kēia lāʻau lapaʻau, mai makaʻu e kūkākūkā me kāu kauka.











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