Loaʻa iā ʻoe a i ʻole kekahi āu i ʻike ai kahi maʻi koko e like me ka hemophilia? I ia mau hihia, hiki i kahi ʻeha liʻiliʻi ke hoʻoulu i ke kahe koko nui. No laila i kēia lā e kamaʻilio mākou e pili ana i kahi lāʻau pale kūikawā koʻikoʻi i hoʻohana ʻia e kāohi a pale aku paha i ke kahe koko i ia mau hihia koʻikoʻi. Ua kapa ʻia kēia ʻo Recombinant Factor VIIa. E nānā kākou i kāu mea e pono ai e ʻike e pili ana i kēia lāʻau lapaʻau.
I ka ʻōlelo maʻalahi, he aha ka Factor VIIa?
He ʻano maoli kēia o "Factor VII", kahi protein kūlohelohe e kōkua ana i ke kāpili ʻana o ke koko o ko mākou kino, i hana ʻia ma ke ʻano hana i loko o kahi keʻena hoʻokolohua. ʻO ka ʻōlelo pololei, ʻaʻole kēia he mea i lawe ʻia mai nā kānaka.
Hoʻohana pinepine ʻia kēia lāʻau lapaʻau:
- E kāohi i ke kahe koko i nā poʻe maʻi me ka hemophilia A a i ʻole hemophilia B i pane ʻole i nā lāʻau lapaʻau maʻamau (loaʻa nā mea hoʻopaʻa).
- E mālama i ke kahe koko ʻana i nā poʻe me ke ʻano i kapa ʻia ʻo Factor VII deficiency .
- Hiki i nā kauka ke ʻōlelo aku i kēia no nā maʻi me kekahi mau maʻi kahe koko ʻē aʻe.
Nā mea e pono ai ʻoe e haʻi i kāu kauka ma mua o ka lawe ʻana i kēia lāʻau lapaʻau:
Ma mua o ka hoʻomaka ʻana i kēia lāʻau lapaʻau, he mea nui loa ia e hāʻawi i kāu kauka i kahi kiʻi piha o kou olakino. ʻOiai inā loaʻa iā ʻoe kekahi o kēia mau mea, e hōʻoia e haʻi iā lākou e pili ana i ia mea.
- Inā loaʻa iā ʻoe ka atherosclerosis .
- Inā he moʻolelo kou a i ʻole ka pilikia o nā ʻōpū koko (thrombosis) i loko o kou mau kīʻaha koko .
- Inā he mau pilikia ʻē aʻe o ke kāpili ʻana o ke koko ma waho aʻe o kēia.
- Inā loaʻa iā ʻoe kahi hopena maʻi i nā protein kanaka a holoholona paha (no ka laʻana, bipi, hamster, ʻiole) .
- Inā he maʻi ʻoe i nā lāʻau lapaʻau ʻē aʻe, nā meaʻai, nā mea mālama, a i ʻole nā mea hoʻoluʻu .
- Inā ʻoe e hāpai ana, e hoʻāʻo ana e hāpai, a e hānai waiū ana paha .
He mea nui loa ia no kou palekana e kamaʻilio me ke kauka me ka hūnā ʻole i kēia ʻike.
Pehea e hoʻohana ʻia ai kēia lāʻau pale?
He inikini kēia i loko o kahi aa koko. Hāʻawi pinepine ʻia kēia lāʻau pale e kekahi loea mālama ola ma kahi haukapila a i ʻole ke keʻena lapaʻau.
Eia nō naʻe, i kekahi manawa e haʻi aku paha kāu kauka iā ʻoe e hoʻohana ia mea ma ka home. Inā pēlā, pono ʻoe e hahai pololei i kēia mau kuhikuhi.
E hoʻomanaʻo i kēia mau mea inā ʻoe e hoʻohana ia mea ma ka home.
- Hoʻomākaukau:Ma mua o ka hoʻomākaukau ʻana i ka lāʻau pale, e ʻae i ka pauka lāʻau a me ka wai hoʻonā e hōʻea i ka mahana o ka lumi.
- Ke kāwili ʻana: I ke kāwili ʻana i ka lāʻau lapaʻau, e hahai pono i nā kuhikuhi ma ka ʻōmole. Mai lūlū ikaika i ka ʻōmole, no ka mea hiki i kēia ke hana i ka huʻa. Akā, e hoʻowali wale i ka ʻōmole.
- Hoʻohana: Mai hoʻohana hou i kekahi lāʻau lapaʻau i koe, e hoʻolei aku. E lawe wale i ka nui i kuhikuhi ʻia, i ka manawa i kuhikuhi ʻia, e like me ke kauoha a kāu kauka. Mai lawe ʻoi aku ma mua o ka nui i kuhikuhi ʻia.
- Ke hoʻolei ʻana i nā nila: He mea nui loa kēia. Mai hoʻolei i nā nila a i ʻole nā syringe i hoʻohana ʻia i loko o ka ʻōpala. E waiho iā lākou i loko o kahi pahu ʻoi. Inā ʻaʻohe āu, e nīnau i kāu kauka pehea e loaʻa ai.
Inā ʻoe e hāʻawi ana i kēia lāʻau lapaʻau i nā keiki, pono ʻoe e kamaʻilio me ke kauka pediatric e pili ana i ia mea a hahai i kāna ʻōlelo aʻo.
He aha kāu e hana ai inā lawe nui ʻoe i ka lāʻau lapaʻau?
Inā manaʻo ʻoe ua overdose ʻoe, mai hopohopo. Akā, pono ʻoe e hana koke. E kelepona koke aku i ke Kikowaena ʻIke Poisons Lahui ma ka Halemai Lahui ma Colombo. A i ʻole, e hele i ka Emergency Treatment Unit (ETU) o ka haukapila kokoke loa.
Nā hopena ʻaoʻao hiki ke hoʻohana ʻia i ka lāʻau lapaʻau
E like me nā lāʻau lapaʻau āpau, hiki i kēia ke loaʻa kekahi mau hopena ʻaoʻao. He koʻikoʻi kekahi, he mea maʻamau kekahi. He mea nui e makaʻala i kēia mau mea.
| Ka hopena ʻaoʻao | Ka wehewehe a me nā mea e hana ai |
|---|---|
| Nā hopena ʻaoʻao e pono e hōʻike koke ʻia i ke kauka | |
| Ka hopena maʻi ʻaleka koʻikoʻi | Nā hōʻailona e like me ka paʻakikī o ka hanu ʻana, ka ʻū ʻana o ka umauma, ka ʻulaʻula o ka ʻili a i ʻole ka maneʻo. Inā loaʻa kekahi o kēia mau mea, he pilikia ia. E ʻimi koke i ke kōkua lapaʻau. |
| ʻO ka palapū maʻamau ʻole a i ʻole ke kahe mau ʻana o ke koko | Inā ʻaʻole i kaohi ʻia ke kahe ʻana o ke koko ma hope o ka lawe ʻana i ka lāʻau lapaʻau a inā paha he ʻeha hou, e haʻi i kāu kauka. |
| Nā hōʻailona o ka maʻi | Hiki i ke kuni, ke anu, a me ke kuʻi ke lilo i mau hōʻailona o kahi maʻi. |
| ʻEha, pehu, ʻulaʻula ma kahi i hoʻokomo ʻia | Inā ʻeha loa a pehu paha kahi i inikini ʻia. |
| Pehu wāwae | Inā pehu kekahi a i ʻole nā wāwae ʻelua i kahi ʻano ʻē, he hōʻailona paha ia o kahi ʻūpā koko. E hōʻike koke aku. |
| Nā mea i maʻa mau ʻole i ka nui, akā pono e hōʻike ʻia i ke kauka inā hoʻomau lākou | |
| ʻEha poʻo | Hiki ke loaʻa kahi ʻeha poʻo maʻamau. |
| Ka luaʻi ʻana | Hiki ke luaʻi. |
Nā mea nui ʻē aʻe
- Kāleka hōʻoia: Inā he hemophilia kou, e lawe mau i kahi kāleka me ʻoe e komo pū ana me kou inoa, ka inoa a me ka nui o ka lāʻau lapaʻau āu e lawe nei, ka inoa a me ka helu kelepona o kāu kauka, a me nā kikoʻī o kekahi e hoʻokaʻaʻike aku ai inā he pilikia.
- Nā lāʻau lapaʻau ʻē aʻe: Hiki i kēia lāʻau lapaʻau ke launa pū me nā huahana coagulation koko ʻē aʻe (nā huahana coagulation factor). No laila, e hōʻoia e haʻi i kāu kauka e pili ana i nā lāʻau lapaʻau āpau āu e lawe nei, me nā huaora, nā lāʻau lapaʻau lāʻau, a me nā mea hoʻohui, a me ka puhipaka ʻana, inu waiʻona, a hoʻohana paha i nā lāʻau lapaʻau ʻē aʻe.
Leka Lawe-Home
- He lāʻau pale ola ka Recombinant Factor VIIa i hoʻohana ʻia no kekahi mau maʻi kahe koko, e like me ka hemophilia.
- Ma mua o ka hoʻomaka ʻana i ka lāʻau lapaʻau, he mea nui e haʻi i kāu kauka e pili ana i kou mōʻaukala olakino piha a me nā lāʻau lapaʻau a pau āu e lawe nei.
- Inā ʻoe e hoʻohana ana i kēia lāʻau lapaʻau ma ka home, e aʻo pehea e kāwili ai a hoʻokomo pololei iā ia. E hoʻolei pono i nā nila i hoʻohana ʻia.
- E ʻimi koke i ke kōkua lapaʻau inā loaʻa iā ʻoe kekahi mau hopena koʻikoʻi e like me ka paʻakikī o ka hanu ʻana, ka ʻū ʻana o ka umauma, a i ʻole ka pehu ʻana ma ke ʻano ʻē.
- Nou wale nō kēia lāʻau lapaʻau. Mai kaʻana like me kekahi.











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