Ke manaʻo nei ʻoe i kekahi manawa he manaʻo kaumaha kou i loko o kou umauma, he manaʻo paʻa i loko o kou umauma, a i ʻole he manaʻo palupalu ke piʻi ʻoe i luna o ke alapiʻi, holo no ke kaʻa, a i ʻole ke manaʻo nei ʻoe e aneane ana ʻoe e palupalu? Manaʻo paha ʻoe he luhi maʻamau kēia, akā i kekahi manawa he maʻi puʻuwai paha i kapa ʻia ʻo Hypertrophic Cardiomyopathy . Mai hopohopo, i kēia lā ke kamaʻilio nei mākou e pili ana i kahi ʻoki kino holomua loa i kapa ʻia ʻo Septal Myectomy , kahi i hana ʻia ma ke ʻano he lāʻau lapaʻau no kēia ʻano. E like me ka wehewehe ʻana i kahi hoaaloha, e kamaʻilio kākou e pili ana i nā mea āpau ma nā ʻōlelo maʻalahi.
ʻO ka mea mua, e nānā kākou i ke ʻano o kēia mea i kapa ʻia ʻo Hypertrophic Cardiomyopathy?
I mea e maʻalahi ai ke hoʻomaopopo ʻana i kēia, e hoʻohālikelike kākou i ko kākou puʻuwai me ka pamu wai. ʻO ka hana a ka pamu, ʻo ia ke huki i ka wai ma o nā paipu a hoʻouna iā ia i loko o ka hale. Pēlā ko kākou puʻuwai, ʻo kāna hana nui, ʻo ia ke pamu i ke koko ma loko o ko kākou kino.
ʻEhā keʻena nui i loko o ko kākou puʻuwai.
- Kāhea mākou i nā keʻena ʻelua o luna ʻo ka atria (ʻākau a me ka hema).
- Kāhea mākou i nā keʻena ʻelua ma lalo o nā ventricles o ka puʻuwai (ʻākau a me hema).
I mea e pololei ai, aia kahi pā o nā ʻiʻo e hoʻokaʻawale ana i nā keʻena hema a me ka ʻākau ma lalo. Kāhea mākou i kēia ʻo ka septum . I ka cardiomyopathy hypertrophic, ʻo kēia septum, ʻo ia hoʻi, kēia pā ma waenakonu o ka puʻuwai, e lilo i ʻoi aku ka mānoanoa ma mua o ka maʻamau.
E noʻonoʻo i ka mea e hana ʻia inā paʻa kahi paipu i loko o kēlā pamu wai? Ua emi ka hakahaka no ke kahe ʻana o ka wai, a pono ka pamu e hana ikaika loa e hoʻokuke i ka wai i waho. Pēlā nō hoʻi ka mea e hana ʻia ma ʻaneʻi. Mānoanoa kēia septum a puka i loko o ka ventricle hema. A laila ua ālai ʻia ke ala no ke kahe ʻana o ke koko mai ka ventricle hema, ke keʻena nui e pamu ana i ke koko mai ka puʻuwai a i ke kino. Ma muli o kēia, pono ka puʻuwai e hana ikaika loa (overwork) ma mua o ka maʻamau e pamu i ka nui o ke koko e pono ai ke kino holoʻokoʻa.
Hiki i kēia maʻi ke lilo i maʻi puʻuwai hānau no kekahi poʻe. ʻO ke ʻano kēia ua hānau ʻia lākou me kēia pilikia. No kekahi poʻe, hiki ke ulu aʻe ma hope o ke ola.
No laila he aha kēia ʻoki kino i kapa ʻia ʻo Septal Myectomy?
I ka ʻōlelo maʻalahi, ʻo Septal Myectomy kahi ʻoki puʻuwai hāmama kahi e ʻoki ai ke kauka puʻuwai a wehe i kahi ʻāpana mānoanoa o ka paia o ka puʻuwai (septum).
E like me ka hoʻomaʻemaʻe ʻana i ke alanui ma ka wehe ʻana i ka mea i ālai ʻia i loko o ka paipu wai, ma hope o kēia ʻoki kino, ua wehe ʻia ka mea i ālai ʻia i ke kahe koko i loko o ka puʻuwai. A laila hiki i ka puʻuwai ke pamu maʻalahi i ke koko ma ke kino holoʻokoʻa me ka ʻole o kekahi mea i ālai ʻia. ʻO kēia ke kumu nui o kēia ʻoki kino.
No wai kēia ʻoki kino i ʻōlelo ʻia?
ʻO ka maʻamau, ʻaʻole ʻōlelo koke ke kauka i kēia ʻoki kino. Hoʻāʻo mua lākou e kāohi i nā hōʻailona ma ka hāʻawi ʻana i nā lāʻau lapaʻau. Eia naʻe,
- No ka poʻe i hiki ʻole ke kāohi ʻia ko lākou mau hōʻailona (e like me ka pōkole o ka hanu, ka ʻeha o ka umauma) me ka lāʻau lapaʻau.
- No ka poʻe nona ka paia mānoanoa loa ma ka ʻaoʻao hema o ka puʻuwai, e keakea nui ana i ke kahe koko .
- ʻO nā wahine me ka Hypertrophic Cardiomyopathy e hoʻolālā ana e hāpai (ʻoiai inā ʻaʻole koʻikoʻi nā hōʻailona, hiki ke ʻōlelo ʻia kēia ʻoki ʻana ma ke ʻano he mea pale aku no ka mea ua kau ʻia ka puʻuwai ma lalo o ke kaumaha keu i ka wā hāpai).
Ma nā hihia e like me kēia e kamaʻilio ai ke kauka me ʻoe a hoʻoholo ʻo kēia ʻoki kino ke koho maikaʻi loa.
He aha kāu e hana ai ma mua o ke ʻoki kino?
E hāʻawi aku kāu kauka iā ʻoe i nā kuhikuhi a pau āu e pono ai ma mua o ke ʻoki kino. ʻAʻohe mea nui loa e hana ai, akā aia kekahi mau mea āu e makaʻala ai.
- Inā ʻoe e lawe nei i kekahi mau lāʻau lapaʻau, e like me nā lāʻau hoʻokahe koko , e noi ʻia paha ʻoe e hoʻōki i ka lawe ʻana iā lākou i kekahi mau lā ma mua o ke ʻoki ʻana.
- Inā he mea puhi paka ʻoe , he mea nui loa e hoʻāʻo e haʻalele ma mua o ke ʻoki ʻana, no ka mea, ke hoʻopilikia nei ka puhi paka i ke kaʻina hana ho'ōla.
Eia kekahi, e hana ʻia kekahi mau hoʻokolohua e loiloi pololei i ke kūlana o kou puʻuwai. Hana ʻia kēia mau mea e ʻike ai i ka mākaukau o kou puʻuwai ma mua o ke ʻoki ʻana.
| Hoʻāʻo | I ka ʻōlelo maʻalahi, he aha kāu e hana ai me ia? |
|---|---|
| Nā hoʻāʻo koko | Nānā ʻia nā mea e like me kou olakino laulā, nā puʻupaʻa a me ka hana akepaʻa. |
| X-ray umauma | E nānā i ke ʻano a me ka nui o ka puʻuwai a me nā māmā. |
| ʻElectrocardiogram (ECG) | Nānā ʻia ka hana uila o ka puʻuwai, ʻo ia hoʻi, ke ʻano o ka puʻuwai. |
| ʻEchocardiogram (Echo) | Ua like kēia me ke scan puʻuwai. Hiki iā ia ke ʻike maopopo i ke ʻano o ka hana ʻana o nā keʻena, nā paia, a me nā valve o ka puʻuwai, pehea ka mānoanoa o nā paia, a inā paha he mau mea keakea i ke kahe koko. |
| MRI puʻuwai | Hana ʻia kēia hoʻāʻo e loaʻa ai nā kiʻi maopopo a kikoʻī loa o ka ʻiʻo puʻuwai. |
| Ka hoʻokomo ʻana o ka catheter cardiac | He hoʻokolohua kahi e hoʻokomo ʻia ai kahi ʻōmole liʻiliʻi ma o kahi aa koko ma ka lima a i ʻole ka wāwae i loko o ka puʻuwai e nānā ai no nā ālai ʻana i nā kīʻaha koko o ka puʻuwai a me ke kaomi i loko o ka puʻuwai. |
Pehea e hana ʻia ai ke ʻoki ʻana i kēlā me kēia ʻanuʻu
ʻOiai he ʻoki puʻuwai hāmama kēia, e hāʻawi ʻia ʻoe i ka anesthesia laulā. ʻO ke ʻano kēia, ʻaʻole ʻoe e ʻike i kekahi ʻeha, e hiamoe nui ʻoe. ʻAʻole ʻoe e ʻike i kekahi mea mai ka hoʻomaka ʻana o ke ʻoki a hiki i ka hopena.
Ma hope o kou hiamoe ʻana, e hahai ana ke kime hana i kēia mau hana:
1. Ke komo ʻana i ka puʻuwai: Hana ke kauka lapaʻau i kahi ʻoki kū pololei i waenakonu o kou umauma, e hoʻokaʻawale pono ana i ka iwi umauma (sternum) i ʻelua e komo ai i ka puʻuwai.
2. Hoʻohui i ka Mīkini Puʻuwai-Māmā: A laila, e hoʻopili ʻia ʻoe i kahi mīkini puʻuwai-māmā . He mīkini kupaianaha kēia. I ka wā o ke ʻoki kino, hana ʻia ka hana a kou puʻuwai a me kou māmā, ka mea e hoʻopuehu ana i ke koko a puni ke kino a hoʻohui i ka oxygen i ke koko, e kēia mīkini no kekahi manawa. ʻAe kēia i ke kauka ʻoki kino e hoʻōki i ka puʻuwai a hana i ke ʻoki kino ma kahi mālie a me ke koko ʻole.
3. Ke wehe ʻana i ka ʻāpana mānoanoa: I kēia manawa, e hiki mai ana ka ʻāpana nui. E ʻoki pono ke kauka lapaʻau i ka ʻāpana ʻiʻo keu o ka paia mānoanoa (septum) o ka puʻuwai. Hana ʻia kēia i ka nui e pono ai e wehe i ke ālai ʻana i ke kahe koko.
4. Ka Hoʻopau ʻana i ka Hana: Ma hope o ka pau ʻana o ke ʻoki kino, e hoʻokaʻawale ʻia ʻoe mai ka mīkini puʻuwai-māmā, a e hoʻomaka hou kou puʻuwai e hana ma kāna iho.
5. Ke pani ʻana i ka ʻoki ʻana:ʻO ka hope, ua hoʻopili hou ʻia ka sternum a ua pani ʻia ka ʻoki ʻana o ka umauma me nā humuhumu hiki ke hoʻoheheʻe ʻia.
ʻO ka maʻamau, ʻekolu a ʻehā paha hola ka lōʻihi o ke ʻoki kino holoʻokoʻa.
He aha ka mea e hana ʻia ma hope o ke ʻoki kino?
Ma hope o ke ʻoki kino, e hoʻokomo pololei ʻia ʻoe i ka Intensive Care Unit (ICU) , kahi e nānā pono ʻia ai kou puʻuwai a me ke koko.
- No nā hola 24-48 mua, loaʻa paha iā ʻoe kahi catheter mimi a me kahi paipu hoʻokahe umauma e hoʻokahe i ka wai keu. Mai hopohopo, he manawa pōkole kēia.
- Ma hope o 48 mau hola, e hoʻomaka ʻoe e hele mālie me ke kōkua o kahi mea hoʻoponopono kino.
- Noho ka hapa nui o ka poʻe ma ka haukapila no ka liʻiliʻi o ʻelima mau lā, a ma hope iho hiki iā lākou ke hoʻi i ka home.
He aha nā pōmaikaʻi a me nā pilikia o kēia ʻoki kino?
E like me nā ʻoki kino āpau, aia nā pono a me nā pilikia liʻiliʻi. Eia nō naʻe, he ʻoki kino holomua loa ʻo Septal Myectomy a haʻahaʻa ka pilikia.
| Nā pōmaikaʻi nui o ke ʻoki kino | |
|---|---|
| Ka nalo ʻana o nā hōʻailona | Ma hope o ke ʻoki ʻana, ʻaneʻane nalowale loa nā hōʻailona e like me ka pōkole o ka hanu (dyspnea), ka ʻeha o ka umauma (angina), a me ka nāwaliwali (syncope). E hiki iā ʻoe ke alakaʻi hou i kahi ola hana. |
| Loaʻa ka holomua kiʻekiʻe | He kiʻekiʻe loa ka holomua o kēia ʻoki kino. Wahi a kekahi noiʻi, ua ʻike ka 94% o ka poʻe i hana ʻia ke ʻoki kino i ka hōʻoluʻolu mai ko lākou mau hōʻailona. |
| Nā hopena lōʻihi | He lōʻihi ka hopena o kēia ʻoki kino. Ma hope o ke ʻoki kino, ua ʻike ʻia ua like ke ola o nā mea maʻi me ko ke kanaka olakino maʻamau. |
| Nā pilikia hiki ke loaʻa (Nā pilikia) - (ʻAʻole kēia mau mea maʻamau) | |
|---|---|
| Ka hōʻiliʻili ʻana o ka wai a puni ka puʻuwai a i ʻole nā māmā | I kekahi manawa hiki ke hōʻiliʻili ka wai a puni ka puʻuwai a i ʻole nā māmā. Hiki ke mālama ʻia kēia me ka lāʻau lapaʻau. |
| ʻO ka Fibrillation Atrial | He puʻuwai puʻuwai kūpono ʻole. Hiki ke hoʻomalu pinepine ʻia kēia me ka lāʻau lapaʻau. |
| Poloka Puʻuwai | Nā hoʻopilikia ʻana i nā hōʻailona uila o ka puʻuwai. Hiki i kēia ke hana i nā puʻuwai puʻuwai kūpono ʻole (arrhythmias). I kekahi mau hihia kakaikahi, pono paha e hoʻokomo ʻia kahi pacemaker ma ke ʻano he lāʻau lapaʻau. |
E hoʻomanaʻo, ua piʻi aʻe ka pilikia o kēia mau pilikia i ka poʻe me nā maʻi puʻuwai ʻē aʻe, nā mea puhi paka, a me ka poʻe ma luna o 65 mau makahiki. I ke kanaka olakino, ua haʻahaʻa loa kēia pilikia.
Pehea kou manaʻo i ka wā e hoʻōla ai?
E hoʻomaka ʻoe e ʻoi aku ka maikaʻi i loko o kekahi mau lā a i ʻole mau pule ma hope o ke ʻoki ʻana. E ʻike ʻoe i ka ʻokoʻa i ka nalo ʻana o nā mea e like me ka pōkole o ka hanu.
- I ka hoʻomaka ʻana, hiki paha iā ʻoe ke manaʻo i kahi ʻeha iki a i ʻole ka paʻa i loko o kou umauma, akā ʻaʻole pono e hoʻomanawanui ʻole ʻia.
- He mea maʻamau ke manaʻo i ka luhi iki a me ka nele o ka ikaika ma hope o ke ʻoki ʻana, akā e hoʻi hou kou ikaika i ka maʻamau i loko o kekahi mau pule.
Āhea ʻoe e ʻike ai i ke kauka?
He mea nui loa ia e nānā i kou ho'ōla ʻana ma hope o kou hoʻi ʻana i ka home. Inā ʻike ʻoe i kekahi o kēia mau hōʻailona, pono ʻoe e kelepona koke aku i kāu kauka .
| Nā hōʻailona e makaʻala ai | |
|---|---|
| Nā pilikia e pili ana i ka ʻoki ʻana | Inā he ʻulaʻula ʻē, pehu, a mehana paha a puni ke kahua ʻoki (incision). |
| kuni | Inā piʻi ka mahana o ke kino ma luna o 100.4 Fahrenheit (38 Celsius) . |
| Piʻi ke kaumaha | Inā piʻi koke kou kaumaha ma mua o 2.5 kg (5 paona) i hoʻokahi pule (he hōʻailona paha kēia o ka paʻa ʻana o ka wai). |
| Paʻakikī ka hanu ʻana | Inā loaʻa koke iā ʻoe ka pilikia hanu a i ʻole ka ʻeha o ka umauma. |
He ʻoki kino nui ka Septal Myectomy. Akā he lāʻau lapaʻau holomua loa ia a hoʻololi i ke ola no ka Hypertrophic Cardiomyopathy. Ma hope o kēia ʻoki kino, hiki iā ʻoe ke ola i kahi ola maʻamau me ka makaʻu ʻole, me ka luhi ʻole. Inā loaʻa iā ʻoe kēia mau hōʻailona, mai kānalua e kamaʻilio me kāu kauka, e hana i nā hoʻokolohua e pono ai, a nīnau hou e pili ana i kēia.
Leka Lawe-Home
- ʻO ka Septal Myectomy kahi ʻoki puʻuwai hāmama i hana ʻia no ke ʻano Hypertrophic Cardiomyopathy , kahi i mānoanoa ai ka paia o ka puʻuwai.
- ʻO kēia ʻoki kino e pili ana i ka ʻoki ʻana i kahi ʻāpana keu o ka paia puʻuwai mānoanoa, e wehe ana i ke ālai ʻana i ke kahe koko i loko o ka puʻuwai.
- ʻO ka maʻamau, paipai ʻia kēia ʻoki kino no ka poʻe i hiki ʻole ke kāohi ʻia ko lākou mau hōʻailona me ka lāʻau lapaʻau.
- He hana holomua loa kēia a haʻahaʻa ka pilikia. Loaʻa i ka hapa nui o ka poʻe ka hōʻoluʻolu piha mai nā hōʻailona ma hope o ke kaʻina hana.
- He mau pule ka lōʻihi o ka hoʻōla ʻana ma hope o ke ʻoki ʻana, a he mea nui loa e hahai i nā ʻōlelo aʻoaʻo lapaʻau i loko o ia manawa.
- Inā loaʻa iā ʻoe kekahi mau hōʻailona ʻē, e like me ka pehu ʻana o ka ʻoki, ke kuni, a i ʻole ka piʻi koke ʻana o ke kaumaha, e hoʻomaopopo koke i kāu kauka.











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