Loaʻa i kāu pēpē ka Short Bowel Syndrome (SBS)? E kamaʻilio maʻalahi kākou e pili ana.

Ke maʻi mau nei kāu keiki liʻiliʻi? Ke emi nei kona kaumaha me ka ʻike ʻole, ʻoiai ma hope o ka inu ʻana i ka waiū a i ʻole ka ʻai ʻana? ʻAʻole anei ʻo ia e piʻi iki ke kaumaha? Ma ke ʻano he makua, he mea maʻamau ke makaʻu nui a hopohopo ke ʻike ʻoe i nā mea e like me kēia. I kekahi manawa, aia paha kekahi maʻi ma hope o kēia mau hōʻailona i lohe ʻole ʻia e mākou. I kēia lā e kamaʻilio mākou e pili ana i kekahi o ia ʻano maʻi, ʻo "Short Bowel Syndrome".

He aha ka Short Bowel Syndrome (SBS)?

I ka ʻōlelo maʻalahi, ʻo ka Short Bowel Syndrome (SBS) kahi kūlana i hiki ʻole ai i ke kino o kāu keiki ke omo i nā meaʻai a me nā wai kūpono. ʻO kēia no ka mea ua nalowale kekahi hapa o ka ʻōpū liʻiliʻi o ke keiki a ʻaʻole paha e hana pono. ʻOi aku ka pololei, ʻaʻole lawa ka lōʻihi o ka ʻōpū. Hiki ke loaʻa kēia kūlana i ka wā hānau, a i ʻole hiki ke hana ma hope o ka wehe ʻia ʻana o kahi hapa nui o ka ʻōpū liʻiliʻi ma muli o kekahi kūlana olakino ʻē aʻe.

No ka hoʻomaopopo ʻana i kēia, e nānā mua kākou i ka mea e hana ʻia ana i loko o ko kākou ʻōpū liʻiliʻi.

Ke kuleana o ko kākou ʻōpū liʻiliʻi

E noʻonoʻo i ka ʻōpū liʻiliʻi e like me kahi 'laina hana' lōʻihi i loko o kahi hale hana. ʻO ka meaʻai a mākou e ʻai ai ua hoʻoheheʻe hapa ʻia i loko o ka ʻōpū a komo i loko o ka ʻōpū liʻiliʻi. A laila, i kona hele ʻana ma kēia ʻōpū lōʻihi, ʻo nā mea āpau e pono ai ke kino i loko o kēlā meaʻai - ʻo ia hoʻi, ka protein, nā carbohydrates (starch a me ke kō), ka momona, nā huaora, nā minelala e like me ka hao, ka calcium - ua komo i loko o ke kino. Hoʻokuʻu ʻia ke koena o ka ʻōpala ma o ka ʻōpū nui ma ke ʻano he feces.

ʻEkolu mau ʻāpana nui o ko kākou ʻōpū liʻiliʻi:

• Duodenum: ʻO ka ʻāpana pōkole loa ma hope o ka ʻōpū.
• Jejunum: ʻĀpana waena.
• ʻIleum: ʻO ka ʻāpana lōʻihi loa o ka ʻōpū nui.

I ke ʻano o SBS, ʻaʻole lawa ka lōʻihi o kēia 'laina hana'. E noʻonoʻo, he aha ka mea e hana ʻia inā e hoʻohana ʻia kahi alanui kilomika ka lōʻihi e omo i nā meaʻai, a hoʻopōkole koke ʻia kēlā alanui? E holo wikiwiki ke kaʻa i kapa ʻia ʻo ka meaʻai ma kēlā alanui pōkole a ʻaʻohe manawa e hoʻokuʻu i nā ukana āpau (nā meaʻai) i loko. Hana like ka mea ma SBS. No ka mea, he pōkole ka ʻōpū, haʻalele ka meaʻai i ke kino ma mua o ka ʻeli pono ʻia ʻana a omo ʻia nā meaʻai e ke kino. He kūlana koʻikoʻi kēia e hiki ai ke hoʻopilikia i ke ola o ke keiki inā ʻaʻole mālama ʻia.

Pehea ʻoe e ʻike ai inā loaʻa i kahi keiki ʻo SBS? He aha nā hōʻailona?

Hiki i kekahi keiki me SBS ke ʻike i hoʻokahi a ʻoi aku paha o kēia mau hōʻailona. ʻO ka hōʻailona maʻamau, ʻoi aku hoʻi i nā pēpē a me nā kamaliʻi liʻiliʻi, ʻo ia ka maʻi kahe wai.

No ke aha i loaʻa ai i kahi keiki ka Short Bowel Syndrome?

ʻElua mau ʻano kumu nui no kēia.

1. Nā kumu hānau: Hiki ke hānau ʻia kekahi mau keiki me kahi ʻōpū liʻiliʻi pōkole. A i ʻole e nalowale ana kekahi ʻāpana o ka ʻōpū, a i ʻole ʻaʻole paha i ulu piha ka ʻōpū i ka wā e ulu ana i loko o ka ʻōpū o ka makuahine. Ua kapa ʻia kēia maʻi ʻo `(Intestinal Atresia)`.

2. Ma ke ʻano he hopena ʻaoʻao o ke ʻoki kino: Pono kekahi mau keiki e wehe ʻia kekahi hapa o ko lākou ʻōpū liʻiliʻi ma ke ʻoki kino ma muli o nā kūlana olakino ʻē aʻe. ʻO kekahi o nā kumu maʻamau no kēia ʻano ʻoki kino:

• ʻO ka necrotizing enterocolitis: He maʻi koʻikoʻi, ʻoi aku hoʻi i nā pēpē hānau mua ʻia, kahi e make ai nā ʻāpana o ka ʻōpū ma muli o ka emi ʻana o ke kahe koko.
• Gastroschisis: ʻO ke ʻano kahi e puka ai nā ʻōpū ma waho o ke kino i ka wā e ulu ana ke pēpē i loko o ka ʻōpū.
• Volvulus: ʻO kahi kūlana kahi e wili ai nā ʻōpū a nalowale ke kahe o ke koko.
• ʻO ka maʻi o Crohn:He ʻano mumū lōʻihi o ka ʻōnaehana hoʻoheheʻe ʻana.
• Intussusception: ʻO ke ʻano kahi i paʻa ai kekahi ʻāpana o ka ʻōpū i loko o kekahi ʻāpana ʻē aʻe.

He aha nā pilikia e hiki ke loaʻa mai ka SBS?

ʻAʻole he maʻi maʻalahi ka SBS. Inā ʻaʻole mālama pono ʻia, hiki i ke keiki ke loaʻa i nā pilikia like ʻole.

• Ka maloʻo ʻana: Hiki i ke kino ke mālama mau i ka wai no ka mea ʻaʻole hiki iā ia ke omo i ka nui o ka wai e pono ai.
• ʻAi ʻole: Ka pohō kaumaha a me ka ulu ʻana o ka mea kanu ma muli o ka nele o ka meaʻai e pono ai.
• Ka nele o nā wikamina a me nā minelala: Ka nele o nā wikamina koʻikoʻi (A, D, E, K, B12) a me nā minelala (calcium, magnesium, zinc) no ke kino.
• ʻEha nui o ka diaper: ʻO nā ʻōpala waikawa pinepine e hiki ke hoʻolilo i ka ʻili ma kahi diaper i ʻulaʻula nui a ʻeha.
• Maʻi ʻāʻī: Hiki ke hoʻopilikia ʻia ke akepaʻa, ʻoiai inā loaʻa iā ʻoe ka meaʻai parenteral (TPN) no ka manawa lōʻihi.
• Nā pōhaku puʻupaʻa: Ma muli o ke kaulike ʻole o ka omo ʻana o nā mea e like me ka calcium.
• Ka ulu nui ʻana o ka bacteria ma ka ʻōpū liʻiliʻi: ʻO ka hana ʻōpū i hōʻino ʻia e hiki ke alakaʻi i ka ulu nui ʻana o nā bacteria ʻino.

No laila, inā loaʻa i kāu keiki nā hōʻailona o SBS, ʻoi aku hoʻi ma hope o ke ʻoki ʻana i ka ʻōpū, he mea nui loa ia e ʻike koke i kāu kauka .

He aha nā lāʻau lapaʻau no SBS?

He hana hui ka mālama ʻana i kahi keiki me SBS. He nui ka poʻe, me nā kauka keiki, nā kauka ʻokiʻoki, a me nā meaʻai, e hana pū ana e hoʻomohala i ka hoʻolālā lapaʻau maikaʻi loa no kāu keiki. ʻO ka pahuhopu nui o ka mālama ʻana, ʻo ia ke kāohi i nā hōʻailona me ka hāʻawi ʻana i ke keiki i ka meaʻai e pono ai.

1. Nā Hoʻololi Meaʻai

ʻO kēia ka ʻāpana koʻikoʻi loa o ka lāʻau lapaʻau.

• ʻO ka ʻai ʻana i ka ʻōpū (TPN): Ma hope o ke ʻoki ʻana i ka ʻōpū a i ʻole ke hiki ʻole i nā ʻōpū ke omo i nā meaʻai, hāʻawi ʻia nā meaʻai a pau e pono ai ke keiki (protein, momona, carbohydrates, vitamins, a me nā minelala) i ke keiki ma o kahi wai kūikawā, e like me ka saline, ma o kahi aa koko. Hoʻopau loa kēia i ka ʻōnaehana hoʻoheheʻe a hoʻohui pololei i ka meaʻai i ke koko. He lāʻau lapaʻau ola kēia no ke keiki.
• ʻAi ʻai ʻōpū / Hānai ʻana i ka paipu:Inā hana iki nā ʻōpū o ke keiki, hāʻawi ʻia nā meaʻai wai kūikawā ma o kahi paipu i kau ʻia ma ka ihu i loko o ka ʻōpū a i ʻole ma o kahi paipu i hoʻopili pololei ʻia i ka ʻōpū. Hiki i kēia ke hāʻawi i ke keiki i ka meaʻai hou aʻe ma waho aʻe o ka meaʻai a lākou e ʻai ai ma ka waha.
• Nā loli i ka ʻai: Ke hoʻomaka mālie nei ka pēpē e ʻai ma ka waha, e hāʻawi ke kauka a me ka meaʻai meaʻai i kahi hoʻolālā ʻai kūikawā. I loko,
• Ma kahi liʻiliʻi, e noi lākou iā ʻoe e hānai iā lākou i nā manawa he nui i ka lā.
• ʻŌlelo ʻia e hōʻemi i nā meaʻai kiʻekiʻe i ka momona, ke kō, a me ka fiber.
• Ua ʻōlelo ʻia e hāʻawi i nā meaʻai waiwai i ka protein a me nā carbohydrates.
• Manaʻo ʻia e hāʻawi i nā huaora a me nā minelala e pono ai ma ke ʻano he mea hoʻohui.

2. Nā lāʻau lapaʻau

Hoʻohana ʻia nā lāʻau lapaʻau like ʻole e kāohi i nā hōʻailona a hoʻomaikaʻi i ka hoʻopili ʻana i ka meaʻai.

• Nā lāʻau lapaʻau e hoʻemi i ka waikawa o ka ʻōpū ('Nā mea hoʻopaʻa pump Proton').
• Hoʻopilikia nā lāʻau antibiotic i ka ulu ʻana o ka bacteria i loko o ka ʻōpū.
• Nā lāʻau lapaʻau e hōʻemi ai i ka maʻi pākī a hoʻolohi i ka wikiwiki o ka neʻe ʻana o ka meaʻai ma o nā ʻōpū.
• Nā ʻano hormones e hoʻomaikaʻi ai i ka omo ʻana o nā meaʻai.

3. ʻoki kino

I kekahi mau hihia koʻikoʻi, pono paha ke ʻoki kino hou aʻe e hoʻomaikaʻi i ka hana o nā ʻōpū o ke keiki. Eia kekahi laʻana, aia nā kaʻina hana hoʻolōʻihi ʻōpū. I nā hihia koʻikoʻi loa, kahi ʻaʻohe lāʻau ʻē aʻe e pono ai, pono paha kahi hoʻoili ʻōpū.

ʻO ka manaʻolana maikaʻi o ka hoʻololi ʻana o ka ʻōpū

ʻO kēia ka manaʻolana nui loa no nā keiki a me nā mākua me SBS. He mea kupaianaha ko mākou kino. Ma hope o ka wehe ʻia ʻana o kahi ʻāpana o ka ʻōpū, hoʻomaka ke koena o ka ʻōpū e loli i ka hala ʻana o ka manawa. Ua kapa ʻia kēia ʻo 'Intestinal Adaptation'.

Eia ka mea e hana ʻia:

• Hoʻonui ʻia ka ʻili o ka paia o loko o ka ʻōpū i koe.
• ʻO nā ʻāpana liʻiliʻi e like me ka manamana lima (villi) e omo ana i nā meaola e hoʻolōʻihi a mānoanoa.
• Hoʻonui ʻia ke anawaena o ka ʻōpū.
• Hoʻolohi ka wikiwiki o ka neʻe ʻana o ka meaʻai, e hāʻawi ana i ka manawa hou aʻe no ka omo ʻana i nā meaola.

Ma muli o kēia kaʻina hana hoʻololi, hiki i nā keiki he nui ke neʻe mālie mai ka meaʻai parenteral (TPN) i ka hānai waha. Loaʻa nā lāʻau lapaʻau hou, e like me ka teduglutide, i hiki ke hoʻolalelale i kēia hoʻololi.

He huakaʻi paʻakikī ʻo SBS. Akā me ka mālama lapaʻau kūpono, ka mālama pono ʻana i ka meaʻai, a me ke aloha a me ka hoʻolaʻa ʻana o nā mākua, hiki i kēia mau keiki ke ola i nā ola maikaʻi a hauʻoli. He mea nui loa ia e hoʻomau i ka launa pū ʻana me kāu kauka a me ka hui lapaʻau a hahai i kā lākou ʻōlelo aʻo.