Ke paʻakikī nei ʻoe i ka hanu ʻana i kekahi manawa, ke kaumaha o kou umauma, a i ʻole ke nāwaliwali nei ʻoiai ua luhi iki ʻoe? ʻOiai he nui nā kumu no kēia, i kekahi manawa hiki i ke kumu ke piʻi aʻe o ke kaomi i loko o nā kīʻaha koko i loko o nā māmā. I kēia lā e kamaʻilio mākou e pili ana i kahi lāʻau lapaʻau i hoʻohana ʻia e mālama i ia ʻano maʻi.
He aha ka Treprostinil?
I ka ʻōlelo maʻalahi, he lāʻau lapaʻau ʻo Treprostinil i hoʻohana ʻia e mālama i kahi maʻi i kapa ʻia ʻo Pulmonary Arterial Hypertension (PAH). He lāʻau lapaʻau wai ia e hanu ʻia ma ke ʻano he mahu.
I kēia manawa, ke noʻonoʻo nei paha ʻoe i ke ʻano o ka hypertension arterial pulmonary (PAH), he ʻokoʻa anei ia mai ke koko maʻamau? ʻAe, he ʻokoʻa ia. E noʻonoʻo ua paʻa a ua haiki nā paipu wai i loko o kou hale. Pehea ka paʻakikī o ka pamu wai e pamu i ka wai ma o nā paipu? Pono ka pamu e hāpai i ka nui o ke kaumaha, ʻeā? Ma ke ʻano like, i ka wā e haiki ai nā kīʻaha koko e lawe ana i ke koko mai ko kākou puʻuwai a i nā māmā, pono ka puʻuwai e hana ikaika e pamu i ke koko i nā māmā. ʻO kēia ka mea a mākou e kapa nei ʻo 'Pulmonary Arterial Hypertension (PAH)'.
Hana ʻo Treprostinil ma ka hoʻomaha ʻana a me ka hoʻonui ʻana i nā kīʻaha koko i haiki ʻia i loko o nā māmā. Hoʻemi kēia i ke kaomi i loko o nā māmā. Hoʻemi kēia i ka ukana hana ma ka puʻuwai, e ʻae ana iā ia e pamu i ke koko i ke koena o ke kino me ka maʻalahi. ʻO kēia ka mea e maʻalahi ai iā ʻoe ke hanu a e maʻalahi ai ka hana ʻana i kāu mau hana o kēlā me kēia lā. Loaʻa kēia lāʻau lapaʻau ma lalo o nā inoa inoa ʻo Tyvaso a me nā mea ʻē aʻe.
Nā mea e pono ai ʻoe e haʻi i kāu kauka ma mua o ka lawe ʻana i kēia lāʻau lapaʻau
Ma mua o ka hoʻomaka ʻana i kēia lāʻau lapaʻau, he mea nui loa ia e hāʻawi i kāu kauka i kahi wehewehe piha o kou kūlana olakino. E hōʻoia e haʻi i kēia mau mea:
- Maʻi akepaʻa: Inā loaʻa iā ʻoe kekahi maʻi akepaʻa, e hōʻoia e haʻi aku, no ka mea, pili pono ke akepaʻa i ke kaʻina hana o ka hoʻopau ʻana i kēia lāʻau mai ke kino.
- Ke koko haʻahaʻa: Inā he haʻahaʻa kou koko, hiki i kēia lāʻau lapaʻau ke hoʻohaʻahaʻa hou aku. Hiki i kēia ke hoʻoulu i ka poniuniu. E haʻi i kāu kauka e pili ana i ia mea.
- Nā maʻi hanu ʻē aʻe: Inā loaʻa iā ʻoe nā maʻi hanu ʻē aʻe e like me ka hānō a i ʻole COPD, e haʻi mai iā mākou e pili ana iā lākou.
- ʻUmiʻumi: Inā lohe ʻoe i kahi leo hūʻū ke hanu ʻoe, he hōʻailona paha ia o kahi ālai ʻia i kou ala ea. E haʻi pū i kāu kauka e pili ana i kēlā.
- Nā maʻi ʻaleka: Inā he maʻi ʻaleka kou i kēia lāʻau lapaʻau, Treprostinil, a i ʻole kekahi lāʻau lapaʻau ʻē aʻe, meaʻai, a mea hoʻoluʻu paha, e ʻoluʻolu e haʻi mai iā mākou e pili ana.
- Ka hāpai ʻana a me ka hānai ʻana i ka waiū:Inā hāpai ʻoe, e hoʻāʻo ana e hāpai, a hānai waiū paha, he mea nui e hoʻomaopopo i kāu kauka ma mua o ka hoʻomaka ʻana i kēia lāʻau.
Pehea e hoʻohana ai i ka lāʻau lapaʻau?
Hana ʻia kēia me ka hoʻohana ʻana i kahi nebulizer , kahi mea hana e hana ai i ka noe. Hoʻololi ka nebulizer i ka lāʻau lapaʻau wai i noe liʻiliʻi (aerosol). A laila hiki iā ʻoe ke hanu i ka noe ma kou waha a i ʻole ka ihu a hoʻouna pololei i loko o kou mau māmā.
He mea nui loa: Pono e hoʻohana wale ʻia kēia lāʻau lapaʻau me ka ʻōnaehana hanu Tyvaso kikoʻī. Mai hoʻohuihui i kēia lāʻau lapaʻau me nā lāʻau lapaʻau ʻē aʻe i loko o ka Nebulizer.
E hoʻohana i kēia lāʻau lapaʻau e like me ke kuhikuhi a kāu kauka, no ka manawa i kuhikuhi ʻia. Mai hoʻōki i ka lawe ʻana i kēia lāʻau lapaʻau me ka ʻole o ke aʻo ʻana a kāu kauka. E heluhelu pono i nā kuhikuhi e hele pū me kēia lāʻau lapaʻau. Inā he mea āu i maopopo ʻole ai, e nīnau i kāu kauka e hōʻoia ua maopopo iā ʻoe.
He aha inā ua hoʻonui ʻia a poina paha ka nui ?
Inā ua lawe hewa ʻoe ma mua o ka nui i kuhikuhi ʻia, e kelepona koke i ke Kikowaena ʻIke Poisons National ma ka Halemai Lahui ʻo Colombo , a i ʻole e hele i ka ʻOihana Pilikia (ETU) o ka haukapila kokoke loa.
Inā poina iā ʻoe ke lawe i kahi lāʻau, e lawe koke iā ia i kou hoʻomanaʻo ʻana. Akā inā kokoke ka manawa no kāu lāʻau aʻe, e kāpae i ka lāʻau i poina a lawe i kāu lāʻau aʻe i ka manawa i hoʻonohonoho ʻia. Mai lawe i kahi lāʻau pālua e hoʻopiha ai i kahi lāʻau i poina.
Nā mea ʻē aʻe e launa pū me kēia lāʻau lapaʻau
Hiki i kekahi mau lāʻau lapaʻau ke launa pū me Treprostinil, no laila e haʻi i kāu kauka e pili ana i nā mea āpau āu e lawe nei.
- ʻO kekahi mau lāʻau lapaʻau no ke koko kiʻekiʻe a i ʻole ka maʻi puʻuwai
- ʻO Gemfibrozil (he lāʻau hoʻohaʻahaʻa cholesterol)
- ʻO Rifampin (he lāʻau antibiotic i hāʻawi ʻia no ka maʻi puʻupuʻu)
ʻAʻole i piha kēia papa inoa. No laila e hāʻawi i kāu kauka i kahi papa inoa piha o nā lāʻau lapaʻau āpau (i kauoha ʻia a me nā lāʻau lapaʻau ma luna o ke kūʻai aku), nā mea kanu, nā huaora, a me nā mea hoʻohui āu e lawe ai. Eia kekahi, e haʻi i kāu kauka inā ʻoe e puhipaka a inu waiʻona paha.
Nā hopena ʻaoʻao a me nā mea e pono ai ke ʻike
He mea nui e hoʻolohe i nā loli i kou kino i ka wā e lawe ana i kēia lāʻau.
Nā mea e ʻike ai ma ke ʻano laulā
- Nā nānā kino maʻamau: Mai hōʻole i nā manawa i koho ʻia e kāu kauka. He mea nui kēia e ʻike ai pehea ʻoe e hana nei me kāu lāʻau lapaʻau.
- Hōʻike ʻana i nā hōʻailona:Inā ʻaʻole e hoʻomaikaʻi kāu mau ʻōuli a i ʻole e ʻoi aku ka ʻino, e haʻi koke aku i kāu kauka.
- Ka pilikia o ke kahe koko: Hiki i kēia lāʻau lapaʻau ke hoʻonui iki i ka pilikia o ka palapū a me ke kahe ʻana o ke koko. No laila, inā ʻike ʻoe i ka palapū ʻē, ke kahe ʻana o nā ʻāʻī i ka wā e palaki ai i kou mau niho, a i ʻole ke kahe ʻana o ke koko me ka makemake ʻole, e hoʻomaopopo i kāu kauka.
Nā hopena ʻaoʻao
E hoʻokaʻawale kākou i nā hopena ʻaoʻao o kēia lāʻau lapaʻau i ʻelua mau ʻāpana. He koʻikoʻi kekahi a pono e mālama koke ʻia e ke kauka. He mea maʻamau kekahi, akā pono e hōʻike ʻia inā hoʻomau lākou.
| Ka hopena ʻaoʻao | Wehewehena |
|---|---|
| Nā hopena ʻaoʻao koʻikoʻi e pono e hōʻike koke ʻia i ke kauka | |
| Nā hopena alerika | ʻŌhūhū ʻili, maneʻo, pehu o ka maka, nā lehelehe, ke alelo a i ʻole ka puʻu. |
| Ke kahe koko ʻano ʻē | Koko i loko o ka ʻōpala a i ʻole nā ʻōpala ʻeleʻele, luaʻi e like me ke ʻano o ka lepo kofe, mimi ʻulaʻula/ʻeleʻele ʻeleʻele, nā kiko liʻiliʻi ʻulaʻula/poni ma ka ʻili, nā palapū ʻē. |
| Ke koko haʻahaʻa | Pōniuniu nui, poʻo māmā, ʻike pōwehiwehi. |
| ʻŌhūhū a pilikia paha ka hanu ʻana | Ka hū ʻana a i ʻole ka paʻakikī o ka hanu ʻana. |
| Nā hopena ʻaoʻao i maʻa mau, akā pono e hōʻike ʻia i ke kauka inā hoʻomau lākou | |
| Kuke | ʻŪhū iki i hoʻokumu ʻia ma ka hanu ʻana i ka lāʻau. |
| Ka maʻi pākī | Ka hoʻonui ʻana o ka ʻōpū. |
| ʻEha poʻo a me ka poniuniu | ʻEha iki ka ʻeha a i ʻole ka poniuniu. |
| ʻO ka ʻulaʻula o ka maka | Wela a ʻulaʻula ka maka. |
| ʻO ka ʻeha o ka puʻu a me ka ihu | ʻO ka ʻāʻī ʻeha, ka ihu wai, a i ʻole ka ʻāʻī ʻeha. |
| Ka luaʻi | Manaʻo e luaʻi ana. |
Pehea ʻoe e mālama ai a hoʻolei aku i ka lāʻau lapaʻau?
- Mālama: E mālama ʻia mai ka hiki ʻana aku o nā keiki a me nā holoholona. E mālama i ka ʻeke ampoule i wehe ʻole ʻia ma ka mahana o ka lumi (20-25 kekelē Celsius). Ke wehe ʻia ka ʻeke ampoule, pono e hoʻohana ʻia nā ampoule i loko o 7 lā. E pale mai ka mālamalama. Mai wehe i ka ampoule a hiki i ka wā e hoʻohana ai.
- Lāʻau lapaʻau i loko o ka Nebulizer: Ke kau ʻia ka lāʻau lapaʻau i loko o ka Nebulizer, mai waiho iā ia i loko o ka mīkini no nā hola he 24. E wehe i nā lāʻau lapaʻau i koe i loko o ka mīkini i ka hopena o ka lā.
- Ka Hoʻolei ʻana: ʻO ke ala maikaʻi loa e hoʻolei aku ai i nā lāʻau lapaʻau i pau ka manawa a i ʻole nā lāʻau lapaʻau ʻaʻole pono hou ʻia, ʻo ia ke hāʻawi aku iā lākou i nā papahana lawe-hoʻihoʻi lāʻau i loaʻa ma nā haukapila a i ʻole kekahi mau hale kūʻai lāʻau. E nīnau i kāu kauka a haukapila paha e pili ana i kēia. Inā ʻaʻole hiki kēia, e nīnau i kāu kauka pehea e hoʻolei palekana ai i kēia lāʻau.
Leka Lawe-Home
- He lāʻau lapaʻau kūikawā ʻo Treprostinil no ke koko kiʻekiʻe o ke aʻa pulmonary (PAH). Hoʻoheheʻe ʻia ia ma o kahi vaporizer.
- Pono e hoʻohana wale ʻia kēia lāʻau lapaʻau me ka Tyvaso Inhalation System i kuhikuhi ʻia no ia. Mai hoʻohuihui me nā lāʻau lapaʻau ʻē aʻe.
- E haʻi i kāu kauka e pili ana i nā lāʻau lapaʻau ʻē aʻe, nā huaora, a me nā mea hoʻopihapiha āu e lawe nei.
- Inā loaʻa iā ʻoe ke kahe koko ʻē, ka dizziness koʻikoʻi, a i ʻole nā hōʻailona maʻi, e hoʻomaopopo koke i kāu kauka.
- Ua kuhikuhi ʻia kēia lāʻau lapaʻau nou wale nō. Mai kaʻana like me nā poʻe ʻē aʻe.
- Inā he mau hopohopo a kānalua paha kāu, e kamaʻilio koke me kāu kauka.











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