Aia kekahi puka paʻa i loko o ka puʻuwai o kāu pēpē? E aʻo kākou e pili ana i ka Tricuspid Atresia ma nā ʻōlelo maʻalahi

Ma ke ʻano he makua, maopopo iaʻu ke kaumaha o kou puʻuwai ke haʻi aku kāu kauka iā ʻoe he kīnā puʻuwai hānau ko kāu keiki liʻiliʻi. ʻO ka lohe ʻana i kēlā mau ʻōlelo, e like paha me he mea lā ua hiolo kou honua holoʻokoʻa. Akā, mai hopohopo. E kamaʻilio kākou e pili ana i kēia maʻi i kapa ʻia ʻo Tricuspid Atresia me ka maʻalahi a me ka maopopo. E ʻike ʻoe i kahi manaʻo nui o ka hōʻoluʻolu ke maopopo iā ʻoe ke ʻano o ia mea, ke kumu e hana ʻia ai, a me nā mea hiki ke hana ʻia.

I ka ʻōlelo maʻalahi, he aha ka Tricuspid Atresia?

E noʻonoʻo i ko kākou puʻuwai me he hale liʻiliʻi me ʻehā lumi. Aia ʻelua lumi ma luna a ʻelua lumi ma lalo. Aia nā puka no ke kahe ʻana o ke koko ma waena o kēia mau lumi. ʻO ka Tricuspid Atresia kahi kīnā hānau ma ka Tricuspid Valve, ʻo ia ka valve ma waena o ke keʻena luna (Right Atrium) a me ke keʻena haʻahaʻa (Right Ventricle) ma ka ʻaoʻao ʻākau o ka puʻuwai.

Ma kahi o kēia puka, aia kahi pā i hana ʻia me nā ʻiʻo mānoanoa. Me he mea lā ua kūkulu kekahi i kahi pā ma kahi e pono ai ke puka. No laila, ʻo ke koko nele i ka oxygen e hele mai ana mai ke keʻena luna ma ka ʻākau, ʻaʻohe ala e hiki ai i ke keʻena haʻahaʻa. Pono kēia koko e hele i ke keʻena haʻahaʻa a hoʻokuʻu ʻia i nā māmā e loaʻa ai ka oxygen.

No laila, ʻo ka pani piha ʻana o kēia alanui e hoʻoulu ai i ʻelua mau pilikia nui:

1. Hoʻemi ʻia ke keʻena haʻahaʻa: ʻAʻole ulu pono ke keʻena haʻahaʻa ma ka ʻaoʻao ʻākau (Ventricle ʻĀkau) no ka mea ʻaʻole hiki ke koko i laila. Liʻiliʻi pinepine ia a nāwaliwali.

2. ʻAʻole kahe ke koko i nā māmā: Ua emi nui ka nui o ke koko e pono ai ke hele i nā māmā e loaʻa ai ka oxygen. ʻO ka hopena, ʻaʻole lawa ka oxygen e hāʻawi ʻia i ke kino holoʻokoʻa.

He mea hoʻoweliweli anei kēia i ke ola?

ʻAe. Manaʻo nā kauka ʻo Tricuspid Atresia he maʻi puʻuwai koʻikoʻi . I ka wā e hānau ai kahi pēpē me kēia maʻi, pono lākou e mālama ʻia i loko o kahi keʻena mālama koʻikoʻi (ICU) i loea i ka mālama ʻana i nā pēpē me nā maʻi puʻuwai paʻakikī. I nā hihia he nui, pono ka pēpē i ke ʻoki puʻuwai ulia pōpilikia ma mua o ko lākou hoʻi ʻana i ka home. Inā ʻaʻole ʻike ʻia a mālama ʻia kēia maʻi, hiki ke make. No laila, he mea nui ka nānā koke ʻana i ke kauka.

Aia kekahi mau ʻano nui o ka Tricuspid Atresia?

ʻAe, ua hoʻokaʻawale nā ​​kauka i kēia maʻi i kekahi mau ʻano nui. ʻO ke kumu o kēia, ʻokoʻa nā ʻano lapaʻau ma muli o nā kīnā puʻuwai ʻē aʻe e kū mai ana me kēia maʻi.

E haʻi pololei nā kauka iā ʻoe i ke ʻano o kāu pēpē ma hope o kahi echocardiogram.

He aha nā hōʻailona āu e ʻike ai ma ke ʻano he makua?

ʻO ka hapa nui o ka manawa, hoʻomaka kēia mau hōʻailona e ʻike ʻia i loko o ka pule mua ma hope o ka hānau ʻana o ke pēpē.

• ʻIli polū a me nā lehelehe (Cyanosis): Lilo ka ʻili o ka pēpē, nā lehelehe, a ma lalo o nā kui lima i polū no ka mea ʻaʻole lawa ka oxygen i ke kino. ʻO kēia ka hōʻailona nui a maopopo loa.
• Paʻakikī ka hanu ʻana a me ka hanu wikiwiki: Paʻakikī paha ka pēpē i ka hanu ʻana a i ʻole e like paha me ka hanu wikiwiki ʻana, me he mea lā e hanu ana ʻo ia.
• Paʻakikī i ka inu ʻana a me ka luhi koke: Hiki i ka pēpē ke luhi ma hope o ka inu ʻana i kahi waiū liʻiliʻi. No laila, e hoʻōki i ka inu ʻana i ka hapalua, a i ʻole e hou paha ʻo ia i ka wā e inu ana.
• Ka Pōʻeleʻele o ke Keiki: Lohi loa ka piʻi ʻana o ke kaumaha a me ka ulu ʻana o ka pēpē ma muli o ka nele o ka meaʻai a me ka oxygen e pono ai.
• ʻŌhūhū Puʻuwai: Ke nānā ke kauka i ka puʻuwai me ka stethoscope, lohe paha ʻo ia i kahi kani puʻuwai kūpono ʻole.

Inā ʻike ʻoe i kekahi o kēia mau hōʻailona, ​​e ʻike koke i ke kauka me ka hoʻokaʻulua ʻole.

No ke aha e hana ai kēia i nā pēpē?

ʻo ia ke kumuʻAʻole ʻike ʻia ke kumu kikoʻī. Hiki mai kēia mau kīnā hānau i ka wā mua o ka ulu ʻana o ka pēpē i loko o ka ʻōpū, ʻoiai i nā pule 6-8 mua o ka hāpai ʻana i ka wā e hoʻokumu ʻia ai ka puʻuwai. Eia nō naʻe, ua ʻike ʻia kekahi mau mea e hoʻonui ai i ka pilikia o kēia maʻi.

Nā kumu pilikia

Hiki i kekahi mau kūlana e kū nei i ka makuahine i ka wā hāpai ke hoʻopilikia i kēia:

• Nā maʻi viral: Ke hoʻomohala nei i kahi maʻi viral i ka wā hāpai, ʻoi aku hoʻi kekahi e like me ka measles German.
• Maʻi diabetes: Loaʻa i ka makuahine ka maʻi diabetes a ʻaʻole i kaohi pono ʻia i ka wā hāpai.
• Ka hoʻohana ʻana i ka waiʻona: Ke inu ʻana i ka waiʻona i ka wā hāpai.
• Kekahi mau lāʻau lapaʻau: Ka hoʻohana ʻana i kekahi mau lāʻau lapaʻau no ka hopu ʻana a i ʻole ka ʻākena.
• Nā kumu hoʻoilina: Loaʻa i kekahi o nā mākua kahi maʻi puʻuwai hānau a i ʻole he maʻi hoʻoilina ko ka pēpē e like me Down syndrome.

Pehea e ʻike ai nā kauka i kēia maʻi?

Hiki ke ʻike ʻia ke tricuspid atresia ma mua a ma hope paha o ka hānau ʻana.

• Ma mua o ka hānau ʻana o ka pēpē: Inā loaʻa kahi ʻano ʻē i loko o ka puʻuwai o ka pēpē i ka wā o ka ultrasound scan i ka wā hāpai, e hana nā kauka i kahi scan kūikawā i kapa ʻia he fetal echocardiogram. ʻAe kēia i ka ʻike maopopo ʻia ʻana o ke ʻano o ka puʻuwai a me ke kahe o ke koko.
• Ma hope o ka hānau ʻana o ka pēpē: I ka wā o ka nānā mua ʻana ma hope o ka hānau ʻana o ka pēpē, lohe paha ke kauka i kahi leo puʻuwai ʻē (he `heart murmur`). Eia kekahi, inā uliuli ka pēpē, e hoʻohana ʻia kahi hoʻāʻo maʻalahi i kapa ʻia ʻo `pulse oximetry` e ana i ka pae oxygen i loko o ke koko. Inā hāpai kēia i nā kānalua, e hana ʻia kahi hoʻāʻo `echocardiogram` (echo) e ʻike pono ai i ka maʻi.

Hiki i kahi hoʻāʻo `Echo` ke hōʻike maopopo ua nalowale ka valve tricuspid, ua liʻiliʻi ka ventricle ʻākau, a inā he mau lua ʻē aʻe i loko o ka puʻuwai (`atrial septal defect` a i ʻole `ventricular septal defect`).

He aha nā lāʻau lapaʻau?

ʻAʻole hiki ke ho'ōla piha ʻia kēia maʻi. Akā, ʻo ka pahuhopu o ka mālama ʻana, ʻo ia ka mālama ʻana i ka hana o ka puʻuwai ma ka pae maikaʻi loa a me ka hoʻomaikaʻi ʻana i ke kahe koko i loaʻa i ke kino ka oxygen e pono ai. Hiki ke hoʻokaʻawale ʻia nā ʻano mālama i ʻelua mau māhele: ka lāʻau lapaʻau a me ke ʻoki kino.

Lāʻau lapaʻau

Ma mua o ke ʻoki ʻana, hāʻawi ʻia ka pēpē i ka lāʻau lapaʻau e hoʻopaʻa i ke kūlana. ʻO ka lāʻau lapaʻau nui he lāʻau i kapa ʻia ʻo 'Alprostadil'. Mālama kēia i kahi kīʻaha koko liʻiliʻi ('ductus arteriosus') i loko o ka puʻuwai o ka pēpē, ka mea maʻamau e pani ʻia i ka wā hānau. Hoʻokumu kēia i kahi ala hou no ke kahe ʻana o ke koko i nā māmā.

Nā ʻoki kino

He mea nui ke ʻoki kino no ke ola ʻana o kahi pēpē me Tricuspid Atresia. ʻAʻole hana pinepine ʻia kēia ma ke ʻano he ʻoki kino hoʻokahi. Ma muli o ka makahiki o ke pēpē, pono kekahi mau ʻoki kino ma nā pae he nui.

Ma hope o kēia mau ʻoki kino, pono ke pēpē e noho ma ka haukapila no hoʻokahi a ʻelua paha pule. ʻO ka mea mua ma ka ʻāpana mālama koʻikoʻi, a laila hoʻoneʻe ʻia i kahi keʻena maʻamau. Inā ʻaʻole holomua kēia mau ʻoki kino a inā nāwaliwali ka puʻuwai i ka hala ʻana o ka manawa, hiki ke noʻonoʻo ʻia kahi hoʻoili puʻuwai.

Pehea lā ke ola o ke keiki ma hope o ka lāʻau lapaʻau?

Hiki i kēia mau ʻoki kino ke hoʻokokoke aku i ke keiki i kahi ola maʻamau. Eia nō naʻe, pono lākou e noho ma lalo o ka nānā ʻana a ke kauka puʻuwai no ke koena o ko lākou ola.

• Nā nānā kino maʻamau: ʻO ka makahiki o ke keiki a me ke kahua o ka mālama ʻana e hoʻoholo i ka pinepine o ka pono o ke kauka e ʻike iā ia. Ma hope o ke ʻoki ʻana o Fontan, pono ʻoe e hele no nā nānā kino ma ka liʻiliʻi hoʻokahi manawa i ka makahiki.
• Ka nānā ʻana ma ka home: I kekahi manawa e noi paha kāu kauka iā ʻoe e nānā mau a hoʻopaʻa i nā mea e like me ke kaumaha o kāu pēpē a me nā pae oxygen ma ka home.
• Nā lāʻau lapaʻau: Pono paha ʻoe e lawe i nā lāʻau lapaʻau pale e pale aku i ka maʻi ma mua o ka hana ʻana i nā mea e like me nā mālama niho.
• Hana kino:Pono paha ʻoe e kaupalena i nā haʻuki a me nā hana ikaika. E kamaʻilio me kāu kauka e pili ana i kēia a e kiʻi i ka ʻōlelo aʻoaʻo.
• Nā pilikia aʻo: Loaʻa i kekahi mau keiki me Tricuspid Atresia kahi pilikia iki o ka loaʻa ʻana o nā pilikia aʻo a i ʻole ka maʻi hyperactivity deficit attention (ADHD). He mea nui hoʻi kēia e makaʻala.

He aha kāu e ʻōlelo ai e pili ana i ke ola o kēia mau keiki?

He mea koʻikoʻi loa kēia. ʻO ka ʻoiaʻiʻo, inā ʻaʻole mālama ʻia, nui nā pēpē me Tricuspid Atresia e hiki ʻole ke hoʻolauleʻa i ko lākou lā hānau mua.

Eia naʻe, me ke ʻoki ʻana, ua loli loa kēia kūlana. Me ka holomua o ka ʻenehana lapaʻau i kēia lā, ʻo ka hapa nui o nā keiki i hana ʻia i ke ʻoki ʻana e ola a hiki i ka wā makua. Wahi a kekahi mau noiʻi, ʻo ka hapa nui o ka poʻe i hana ʻia i ke ʻoki ʻana e ola ma mua o 20 mau makahiki. Manaʻo ʻia e hiki i kahi keiki i hana ʻia i ke ʻoki ʻana ʻo `Fontan` ke ola no 35-40 mau makahiki a ʻoi aku paha.