E aʻo kākou e pili ana i ke kumu aʻa maʻamau (Truncus Arteriosus) i loko o ka puʻuwai o kāu pēpē.

Ke nānā ʻoe i kāu pēpē hānau hou, ʻike paha ʻoe i kekahi manawa he uliuli iki kona mau lehelehe a me kona mau manamana lima? A i ʻole he paʻakikī iā ia ke inu i ka waiū? Hiki i kēia ke lilo i mau hōʻailona o ka maʻi puʻuwai hānau. He mea maʻamau no kekahi makuahine a makua paha ke makaʻu i ka ʻike ʻana i kahi mea e like me kēia. I kēia lā, ke kamaʻilio nei mākou e pili ana i kahi maʻi puʻuwai kakaʻikahi, akā he mea nui loa. ʻO ia ʻo Truncus Arteriosus.

I ka ʻōlelo maʻalahi, he aha kēia Truncus Arteriosus?

ʻAe, e hoʻomaopopo maʻalahi kākou i kēia. Loaʻa i kahi pēpē olakino ʻelua mau kīʻaha koko nui (nā aʻa) e puka mai ana mai loko mai o kona puʻuwai.

1. ʻAʻa Pulmonary: Lawe kēia i ke koko haumia a nele i ka oxygen mai ka puʻuwai a i nā māmā. I loko o nā māmā, hoʻomaʻemaʻe ʻia kēia koko ma ka hoʻohui ʻana i ka oxygen.

2. Aorta: Hoʻolaha kēia i ke koko waiwai i ka oxygen, i hoʻomaʻemaʻe ʻia i loko o nā māmā, mai ka puʻuwai a i ke kino holoʻokoʻa.

Akā i loko o kahi pēpē me Truncus Arteriosus , ma kahi o kēia mau kīʻaha koko ʻelua, hoʻokahi wale nō kīʻaha koko nui . E noʻonoʻo, hoʻokahi wale nō alanui kahi e pono ai ke loaʻa ʻelua alanui.

ʻO ka mea e hana ʻia ana, ʻo ia ka hui pū ʻana o ke koko waiwai i ka oxygen a me ke koko nele i ka oxygen. Ke kaʻapuni nei kēia koko i hui ʻia ma ke kino o ka pēpē. Hoʻokau kēia i kahi kaumaha hiki ʻole ke hoʻomanawanui ʻia ma ka puʻuwai a me nā māmā o ka pēpē. Pale pū ia i nā ʻōpū ʻē aʻe o ke kino mai ka loaʻa ʻana o ka oxygen a lākou e pono ai. Manaʻo nā kauka he kīnā puʻuwai hānau koʻikoʻi kēia. No laila, pono e mālama koke ʻia.

He aha nā hōʻailona e manaʻo ai au ua loaʻa i kaʻu pēpē kēia maʻi?

Hoʻomaka pinepine kēia mau hōʻailona e ʻike ʻia i loko o nā lā mua ma hope o ka hānau ʻana. E nānā e ʻike inā loaʻa i kāu pēpē kekahi o kēia mau hōʻailona.

No ke aha e hana ai kēia i nā pēpē?

ʻAʻole ʻike nā kānaka ʻepekema i ke kumu pololei o kēia. ʻO ka hapa nui o ka manawa, no ka mea ʻaʻole i ulu pono ka puʻuwai i ka wā e ulu ana ka pēpē i loko o ka ʻōpū. ʻO ka maʻamau, ʻo kēia ala hoʻokahi i kapa ʻia ʻo 'truncus' e kū nei i loko o ka embryo e māhele ʻia ma hope i ʻelua ʻāpana a hana i ʻelua mau aʻa. Akā i kekahi mau pēpē, ʻaʻole hana ʻia kēlā mahele ʻana.

Pili kēia me kekahi mau kūlana genetic. ʻO kahi laʻana ʻo DiGeorge syndrome . Eia kekahi, hiki ke hoʻonui ʻia kēia pilikia e kekahi mau mea e hoʻopilikia ana i ka makuahine i ka wā hāpai.

• Loaʻa i ka makuahine ka maʻi diabetes.
• nā maʻi viral e like me ka rubella.
• Ka hoʻohana ʻana i ka waiʻona a i ʻole nā ​​​​lāʻau lapaʻau ʻē aʻe.
• Ka ʻike ʻia ʻana i nā kemika ʻino e like me ke kēpau.

Nā pilikia puʻuwai ʻē aʻe e hiki ke hana me kēia ʻano

He nui nā pēpē me Truncus Arteriosus he mea ʻē aʻe ko lākou. He lua ia ma ka paia ma waena o nā keʻena haʻahaʻa ʻelua (atrium) o ka puʻuwai. Ua kapa nā kauka i kēia he Ventricular Septal Defect (VSD) . Hoʻoulu kēia lua i ka hui pū ʻana o ke koko maʻemaʻe a me ke koko lepo.

Pehea e ʻike ai nā kauka i kēia?

I ka manawa pinepine, kānalua nā kauka i kēia ke hōʻike kahi pēpē i nā hōʻailona i luna i kekahi mau lā ma hope o ka hānau ʻana. A laila, no ka hōʻoia ʻana i ka maʻi, ʻo ka mea nui ka hana ʻana i kahi hoʻāʻo echocardiogram (echo) . Ua like kēia me kahi scan ultrasound o ka puʻuwai. Hiki i kēia ke ʻike maopopo i ke ʻano o ka puʻuwai, nā kīʻaha koko, a me ke ʻano o ke kahe ʻana o ke koko.

I kekahi manawa, ma mua o ka ʻike ʻia ʻana o nā hōʻailona, ​​hiki ke kānalua ʻia kēia inā hōʻike ka hoʻāʻo pulse oximetry (kahi e ana i ka pae oxygen i loko o ke koko ma ke kau ʻana i kahi clip liʻiliʻi i ka manamana lima) i hana ʻia ma nā pēpē āpau ma ka haukapila i nā pae oxygen haʻahaʻa.

He mea kākaʻikahi loa, hiki ke ʻike ʻia kēia ʻano i ka wā o nā scan ultrasound ma mua o ka hānau ʻana o ke pēpē.

He aha nā lāʻau lapaʻau no kēia?

He mea weliweli paha kēia, akā ʻo ka ʻoiaʻiʻo, pono nā pēpē me kēia maʻi i ke ʻoki puʻuwai i loko o nā pule mua o ka hānau ʻana. ʻO kēia wale nō ka lāʻau lapaʻau. Hana kēia ʻoki ma ka hoʻoponopono ʻana i ke ʻano o ka puʻuwai e like me ka hiki.

Ma ke kaʻina hana i kapa ʻia he hoʻoponopono Rastelli , ka mea a nā kauka e hana mau ai, hana nui ke kauka ʻoki i kēia mau mea:

• Ua pani ʻia ka lua ma ka puʻuwai (VSD) me kahi mea e like me kahi ʻāpana.
• ʻO ke kīʻaha koko nui wale nō (truncus) e kū nei ke hana ʻia nei ma ke ʻano he aorta hou.
• Ma ka hoʻohana ʻana i kahi conduit a me ka valve hana, hana ʻia kahi aʻa pulmonary hou e lawe i ke koko i nā māmā.

E pono anei ke ʻoki kino i ka wā e hiki mai ana?

ʻAe. He mea nui loa kēia e ʻike. ʻAʻole ulu pū ka ʻauwai hana i kau ʻia i ka wā o ke ʻoki mua me ka pēpē. No laila, i ka ulu ʻana o ka pēpē, e pono ai kekahi a ʻoi aku paha nā ʻoki i ka wā e hiki mai ana e pani i ke ʻauwai. E wehewehe kāu kauka i kēia iā ʻoe i kēlā me kēia manawa.

Pehea e mālama ai i kaʻu pēpē ma hope o ke ʻoki kino?

Ma hope o ke ʻoki ʻana, pono kāu keiki e kipa aku i ke keʻena o ka cardiologist no ke koena o kona ola.

• I ka wā kamaliʻi, pono ʻoe e loaʻa i ka lāʻau lapaʻau ma lalo o ke alakaʻi ʻana o kahi cardiologist pediatric .
• Ke hiki ʻoe i ka makahiki 18, e hoʻouna ʻia ʻoe i kahi kauka maʻi puʻuwai makua hānau.

He mea koi ʻia ke hele ʻana i kēia mau keʻena lapaʻau no ka mea ʻo lākou ka poʻe e nānā mau i ka hana o ka puʻuwai o ke keiki, e hana i nā hoʻokolohua e pono ai, a e hoʻoholo i ka wā e hana ai i ke ʻoki kino aʻe.

Hiki i kahi pēpē ke ola me kēia maʻi? Hiki iā lākou ke ola i kahi ola maʻamau?

ʻO kēia ka nīnau nui loa ma ka noʻonoʻo o kēlā me kēia mākua.

He ʻokoʻa ke 'ola maʻamau' no kēlā me kēia kanaka. Hiki i kekahi mau keiki ke holo a pāʻani e like me nā keiki ʻē aʻe. Hiki i kekahi ke luhi iki i ka wā e hoʻoikaika kino ai. Akā me ka nānā pono ʻana o ke kauka, hiki i ka hapa nui o ka poʻe ke hele i ke kula, e aʻo, e hana, a e ola i kahi ʻohana.

He mea paʻakikī kēia huakaʻi, akā, ʻaʻole ʻoe hoʻokahi. E lilo ana kāu mau kauka, nā kahu maʻi, a me kou ʻohana i kumu ikaika nui nou.