He aha ka Wells' Syndrome? E aʻo kākou e pili ana i kēia mau kiko ʻē e kū mai ana ma ka ʻili

Ua lilo koke anei kahi kiko ma kou ʻili i ʻulaʻula, pehu iki, a ʻānai? Me he mea lā he maʻi bacteria, akā ʻaʻole paha he maʻi maoli. I kēia lā e kamaʻilio mākou e pili ana i kahi maʻi ʻili kakaikahi i lohe ʻole ʻia e ka poʻe he nui, akā he mea nui e ʻike. Ua kapa ʻia ʻo Wells' Syndrome . E nānā kākou i ke ʻano o ia mea, no ke aha e kū mai ai, a me kāu mea e hiki ai ke hana e pili ana i ia mea.

I ka ʻōlelo maʻalahi, he aha ka Wells' Syndrome?

He maʻi ʻili laha ʻole ka Wells' Syndrome. Ua kapa ʻia hoʻi ʻo "eosinophilic cellulitis." Ke lohe ʻoe i ka inoa, manaʻo paha ʻoe he maʻi ʻili ia i kapa ʻia ʻo cellulitis. Akā, ʻaʻole ia he maʻi maoli. He maʻi ia e hoʻoulu ai i nā ʻāpana ʻili ʻulaʻula, pehu, ʻāʻī, a me ka mumū ma kekahi a ʻoi aku paha mau wahi.

I kēia manawa, he nīnau kāu, he aha kēia mau "eosinophils"? He mea maʻalahi loa ia. ʻO nā Eosinophils kahi ʻano o nā hunaola koko keʻokeʻo i loko o ko kākou koko. Ua like lākou me nā koa i loko o ko kākou kino. ʻO kā lākou hana nui ke kaua ʻana i nā maʻi. Akā i kekahi manawa, hana ʻia kēia mau hunaola eosinophil i loko o ke kino ma nā nui he nui ma mua o ka mea e pono ai, a i ʻole lilo lākou i mea hana nui. A laila hoʻoulu kēia mau hunaola i ka mumū e hōʻino ai i ko kākou ʻili ponoʻī. ʻO ia ka mea e hana ʻia ma ka Wells' Syndrome.

He mea kākaʻikahi loa kēia maʻi ma ka honua holoʻokoʻa. ʻAʻole i hōʻike ʻia ma mua o 100 mau hihia. Hoʻopilikia nui ia i nā pākeke, akā hiki ke hoʻopilikia i nā keiki i kekahi manawa. Hoʻopilikia like ia i nā kāne a me nā wahine.

No ke aha lā e hana ʻia ai kekahi mea e like me kēia?

ʻAʻole ʻike ʻia ke kumu kikoʻī o kēia , akā manaʻoʻiʻo nā kauka he maʻi autoimmune paha ia.

E noʻonoʻo i kēia ʻano: ua like ko kākou ʻōnaehana pale kino me kahi pūʻali koa e pale ana i kahi ʻāina. ʻO kāna hana ka pale ʻana iā kākou mai nā mea komo hewa mai nā ʻāina ʻē e like me nā germs a me nā virus. Akā i kekahi manawa hele hewa kēia ʻōnaehana a hoʻomaka e hoʻouka i kā kākou mau cell olakino ponoʻī, me ka manaʻo he "ʻenemi" lākou. ʻO ia ka mea a mākou e kapa nei he "maʻi autoimmune". Ua manaʻo ʻia ua hana ʻia ka Wells' Syndrome e kahi hana hewa like o ka ʻōnaehana pale kino.

ʻO ka hapa nui o ka manawa, hiki wale mai ia. Eia nō naʻe, aia paha kahi ʻāpana genetic, ʻoiai ke holo nei ke ʻano i loko o kekahi mau ʻohana. Eia kekahi, hiki i kekahi mau mea ke hoʻoulu a hoʻonui paha i ke ʻano.

He aha nā hōʻailona o kēia maʻi?

Hoʻomaka pinepine nā hōʻailona o kēia maʻi me ka ʻā ʻana a i ʻole ka maneʻo ʻana ma kekahi a ʻoi aku paha o nā wahi o ka ʻili. A laila lilo nā wahi i ʻulaʻula a pehu. He ʻeha pinepine kēia mau wahi pehu. No kekahi poʻe, ʻo ka hōʻailona mua paha he mau pehu hou a i ʻole nā ​​​​nodules.

ʻO nā hiʻohiʻona nui i ʻike ʻia ma ka ʻili:

• ʻUlaʻula a me ka pehu: ʻO kēia ka hōʻailona nui.
• Ka maneʻo a me ke kuni ʻana: Hiki ke loaʻa ka maneʻo nui a i ʻole ke kuni ʻana ma kahi ʻulaʻula.
• Nā kiko ʻano apo:I kekahi manawa e ʻike ʻia paha nā kiko poepoe.
• Hoʻololi kala: I ka hala ʻana o ka manawa, loli ke kala o kēia mau kiko ʻulaʻula. ʻO ka mua, lilo lākou i ʻulaʻula-ʻeleʻele , a laila polū-hina , a ma hope he ʻōmaʻomaʻo-hina . He hiʻohiʻona kūikawā kēia o kēia maʻi.

Nā ʻano kino ʻē aʻe:

Hiki ke ʻike ʻia nā hōʻailona e like me ka hānō, ka ʻeha o nā hono, a me ke kuni, akā ʻaʻole pinepine lākou e ʻike ʻia . Aia nā hōʻailona nui ma ka ʻili.

ʻO ka mea maikaʻi loa, ʻo ia ka hoʻōla pinepine ʻana o kēia mau kiko me ka waiho ʻole ʻana i nā ʻeha i loko o kekahi mau pule a i ʻole mau mahina. Eia nō naʻe, hiki iā lākou ke hana hou ma kahi lā ma hope.

Pehea e ʻike ai ke kauka i kēia?

Inā loaʻa iā ʻoe kēia mau hōʻailona, ​​​​pono ʻoe e ʻike i ke kauka. E nānā ʻo ia iā ʻoe a hana i kekahi mau hoʻokolohua e hoʻoholo ai inā he Wells' Syndrome kēia a i ʻole kekahi maʻi ʻē aʻe.

1. Biopsy ʻili: ʻO kēia ke ala maikaʻi loa e hōʻoia i ka hōʻailona. E lawe ke kauka i kahi ʻāpana ʻili liʻiliʻi mai ka wahi i hoʻopilikia ʻia ma lalo o ka anesthesia a hoʻouna iā ia i kahi keʻena hoʻokolohua no ka hoʻāʻo ʻana. E nānā kēia hoʻāʻo i ka nui o nā eosinophils a mākou i kamaʻilio ai ma mua i loko o ka ʻili a me nā ʻiʻo ma lalo. Hiki iā ia ke kōkua i ka hōʻoia ʻaʻole kēia he allergy, he parasite, dermatitis, he nahu pepeke, a i ʻole kekahi ʻano ʻē aʻe e like me ka Churg-Strauss syndrome.

2. Helu Koko Piha: ʻO kēia hoʻāʻo, i hana ʻia ma ka lawe ʻana i kahi hāpana koko, hiki ke nānā inā ua piʻi ka helu o nā eosinophils i loko o ke koko.

He aha nā lāʻau lapaʻau no kēia?

Na kāu kauka e hoʻoholo i ka lāʻau no ka Wells' Syndrome. Aia kekahi mau lāʻau lapaʻau kūpono loa no kēia.

• Nā Steroid Systemic: ʻO ka lāʻau lapaʻau maʻamau a maikaʻi loa, ʻo ia nā steroid waha a i ʻole nā ​​steroid injectable e like me prednisone . Loaʻa i kēia mau mea kahi hopena immunosuppressant. ʻO ke ʻano kēia e kāohi lākou i ka ʻōnaehana pale mai ka hoʻouka ʻana i kona mau ʻiʻo ponoʻī. ʻO Prednisone kahi mana synthetic o ka hormone steroid cortisol, ka mea i hana maoli ʻia i loko o ke kino. Hoʻomaka pinepine nā hōʻailona e hoʻomaikaʻi i loko o kekahi mau lā o ka lawe ʻana i kēia lāʻau. Hiki ke hoʻemi mālie ʻia ka nui o ka lāʻau ma kahi o hoʻokahi mahina, e like me ka ʻōlelo a kāu kauka.

• Nā lāʻau lapaʻau ʻē aʻe: I kekahi mau hihia, hiki ke hoʻohana ʻia nā antifungals (e.g., griseofulvin) a i ʻole nā ​​​​​​antibiotics (e.g., dapsone) ma ke ʻano he lāʻau lapaʻau.

• Nā kirīmi:Inā ʻaʻole koʻikoʻi loa ke ʻano, ʻo ka hoʻopili wale ʻana i kahi kirīmi steroid e like me ka hydrocortisone i ka wahi i hoʻopilikia ʻia e hāʻawi i ka hōʻoluʻolu.

He aha ka manaʻo? (Wānana)

He maikaʻi loa ka nānā ʻana no kekahi me Wells' Syndrome. ʻO ke ʻano kēia, ʻaʻole ia he kūlana e hoʻoweliweli i ke ola.

• Hoʻōla loa nā ʻeha i loko o kekahi mau pule a i ʻole mau mahina.
• ʻAʻole pinepine e koe nā ʻōpala .
• I kekahi manawa, aia paha kahi loli iki o ke kala o ka ʻili ma kahi o nā kiko. Akā nalo pinepine kēlā i ka hala ʻana o ka manawa.
• Hiki i kēia maʻi ke hoʻi hou mai. I ia mau hihia, hiki ke hala kekahi mau makahiki e kāohi piha ai. Akā hiki nō hoʻi ke mālama maikaʻi ʻia me ka lāʻau lapaʻau.

ʻOiai ʻaʻole i loaʻa ke kumu kikoʻī o kēia maʻi, ʻaʻohe ala kikoʻī e pale aku ai. Eia nō naʻe, inā ʻike ʻoe i kēia mau hōʻailona, ​​ʻo ka mea maikaʻi loa e hana ai, ʻaʻole e hopohopo a ʻike koke i ke kauka no ka ʻōlelo aʻoaʻo.