Koj tus me nyuam puas muaj teeb meem plawv? Cia peb tham txog Hypoplastic Aortic Arch!

Koj tus me nyuam puas muaj teeb meem pub niam mis? Nws puas nkees dua li niaj zaus thaum ua pa? Los yog nws puas zoo li daj ntseg thiab hws? Nws yog ib qho ib txwm rau koj ua niam txiv kom txhawj xeeb heev thaum tej yam no tshwm sim rau koj tus me nyuam. Qee zaum qhov ua rau qhov no tuaj yeem yog mob plawv txij thaum yug los. Niaj hnub no, peb yuav tham txog ib qho mob uas tshwm sim hauv lub plawv ntawm cov menyuam mos, tab sis tuaj yeem kho tau yog tias paub thaum ntxov thiab kho kom zoo.

Dab tsi yog Hypoplastic Aortic Arch?

Hais yooj yim xwb, Hypoplastic Aortic Arch , qee zaum hu ua Aortic Arch Hypoplasia (AAH) , yog qhov teeb meem yug los uas tshwm sim hauv ib feem ntawm koj tus menyuam lub plawv , aorta . Xav txog nws li no, aorta zoo li ib txoj hlab ntsha loj uas nqa ntshav thoob plaws peb lub cev. Nws pib ntawm lub plawv thiab nqa cov ntshav oxygenated thoob plaws lub cev. Nws zoo li ib tug pas nrig, me ntsis nkhaus. Qhov nkhaus ntawm sab saum toj ntawm tus pas nrig hu ua aortic arch , uas txhais tau tias 'lub arch ntawm aorta.'

Lo lus 'hypoplastic' txhais tau tias 'tsis loj hlob zoo', 'me me'. Yog li, tus menyuam uas muaj hypoplastic aortic arch muaj lub aortic arch tsis loj hlob. Qhov ntawd yog, qhov qhib, lossis txoj kab uas hla, sab hauv qhov ntawd nqaim dua li nws yuav tsum yog. Ib yam li cov yeeb nkab dej raug thaiv, thaum lub aortic arch nqaim, nws nyuaj rau cov ntshav ntws los ntawm lub plawv mus rau qhov qis dua ntawm lub cev, los ntawm cov aorta nqis . Qhov no tuaj yeem txo cov ntshav uas mus txog tag nrho lub cev.

Leej twg raug kev txom nyem los ntawm tus mob no tshaj? Puas muaj kev sib txuas rau lwm yam kab mob plawv?

Aortic arch hypoplasia (AAH) tuaj yeem tshwm sim ntawm nws tus kheej. Txawm li cas los xij, nws feem ntau pom nrog lwm qhov teeb meem plawv yug los , hu ua coarctation ntawm aorta . Qhov no yog ib qho mob uas lwm qhov ntawm aorta, feem ntau nyob ze ntawm ductus arteriosus, ib txoj hlab ntsha tshwj xeeb uas feem ntau muaj nyob hauv plab, nqaim.

Yog li ntawd, koj tus menyuam tus kws kho mob yuav hais tias, "Koj tus menyuam muaj coagulopathy ntawm lub aorta nrog aortic arch hypoplasia." Qhov ntawd txhais tau tias muaj kev nqaim ntawm lub aorta, tsis yog nyob rau hauv ib qho chaw xwb, tab sis raws ib ntu ntev.

Ntxiv rau, cov menyuam mos uas muaj AAH tej zaum yuav muaj lwm yam mob plawv. Piv txwv li:

• Atrial Septal Defect (ASD) : Ib lub qhov nyob rau hauv phab ntsa ntawm ob lub chav sab saud ntawm lub plawv.
• Atrioventricular Septal Defect : Ib qho teeb meem nyuaj hauv phab ntsa ntawm cov chav ntawm lub plawv.
• Bicuspid Aortic Valve thiab Aortic Valve Stenosis : Qhov tsis zoo thiab kev nqaim ntawm lub aortic valve.
• Hypoplastic Left Heart Syndrome (HLHS) : Sab laug ntawm lub plawv tsis loj hlob zoo.
• Patent Ductus Arteriosus (PDA) : Ib txoj hlab ntshav hu ua ductus arteriosus uas yuav tsum kaw tom qab yug los tseem qhib.
• Shone's Syndrome : Kev sib xyaw ua ke ntawm ntau yam teeb meem uas cuam tshuam rau kev ntws ntshav mus rau sab laug ntawm lub plawv.
• Kab Mob Ventricular Septal Defect (VSD) : Ib lub qhov hauv phab ntsa ntawm ob lub chav hauv qab ntawm lub plawv.

Muaj ntau tshaj ib yam mob plawv zoo li no yog ib qho tseem ceeb heev thaum npaj kev kho mob. Vim tias xav tau kev phais lossis kev kho mob uas tsim los rau qhov nyuaj, tshwj xeeb hauv lub plawv ntawm tus menyuam.

Yog tias ib tug me nyuam muaj tus mob no, cov tsos mob yuav zoo li cas?

Cov menyuam mos uas muaj coarctation ntawm lub aorta thiab aortic arch hypoplasia feem ntau pib qhia cov tsos mob tsis ntev tom qab yug los . Xav txog koj tus menyuam mos, uas nkees tom qab haus dej ob peb zaug, zoo li ua pa nyuaj. Qee zaum lawv hws thiab hloov mus ua xim xiav-dawb. Yuav ua li cas txaus ntshai rau ib leej niam pom ib yam dab tsi zoo li no, puas yog?

Cov tsos mob tseem ceeb uas pom tau yog:

• Lub plawv dhia ceev : Lub plawv dhia ceev dhau.
• Qaug zog : Tus menyuam yuav nkees sai sai, tshwj xeeb tshaj yog thaum pub niam mis.
• Tawv nqaij xim grey los yog dawb : Qee zaum tawv nqaij kuj tuaj yeem tshwm xiav.
• Hws noo heev .
• Quaj ntau zaus, chim siab .
• Ua pa sai los yog ua pa nyuaj .
• Teeb meem nrog kev pub mis: Tsis kam haus mis nyuj, lossis tsum tom qab haus me ntsis.
• Lub plawv dhia tsis muaj zog hauv qhov qis ntawm lub cev : Tshwj xeeb tshaj yog nyob rau hauv ob txhais ceg, lub plawv dhia hauv cov hlab ntsha femoral tsis muaj zog heev thaum palpated.

Yog tias koj tus menyuam muaj ib lossis ntau yam ntawm cov tsos mob no, nws yog ib qho tseem ceeb heev uas yuav tsum nrhiav kev pab kho mob tam sim ntawd .

Vim li cas qhov no thiaj tshwm sim? Yog vim li cas?

AAH yog ib qho teeb meem plawv uas muaj txij thaum yug los . Nws yog ib yam dab tsi uas tshwm sim thaum tus menyuam tseem nyob hauv plab. Cov kws tshawb fawb tseem tab tom sim nrhiav seb qhov ua rau muaj hom teeb meem plawv no yog dab tsi.

Tab sis qhov paub yog tias qhov mob no tuaj yeem tshwm sim yog tias tus menyuam lub aortic arch tsis loj hlob zoo thaum ob peb lub lis piam thawj zaug ntawm cev xeeb tub .

Koj nrhiav tau qhov no li cas? Cov kev xeem yog dab tsi?

Cov kws kho mob siv qhov no los kuaj mob.Kev kuaj duab tshwj xeeb. Cov kev kuaj no feem ntau ua tom qab tus menyuam yug los.

Cov kev kuaj mob tseem ceeb uas siv los kuaj mob AAH yog:

• Kev Siv Computer Tomography (CT scan) Rau Lub Plawv
• Kev Siv Lub Tshuab Xam Xaj Magnetic Resonance Angiogram (MRA)
• Transthoracic Echocardiogram (TTE) : Qhov no zoo li kev ntsuas ultrasound ntawm lub plawv.
• Kev Siv Catheter Rau Lub Plawv : Qee zaum qhov kev kuaj no kuj yuav tsum tau ua.

Cov kev kuaj no tuaj yeem saib xyuas lub plawv ntawm tus menyuam, uas yog, seb cov khoom sab hauv tau teeb tsa li cas, kom meej meej. Lawv kuj tuaj yeem nrhiav tau seb tus menyuam puas muaj lwm yam teeb meem plawv. Yog los ntawm kev sau tag nrho cov ntaub ntawv no uas cov kws kho mob npaj txoj kev kho mob zoo tshaj plaws rau tus menyuam.

Yuav kom paub tseeb tias muaj AAH, cov kws kho mob yuav tsum saib qhov loj ntawm tus menyuam lub aortic arch. Tshwj xeeb, lawv ntsuas nws txoj kab uas hla , uas yog qhov dav ntawm qhov qhib sab hauv. Qhov kev ntsuas no piv rau txoj kab uas hla ntawm lwm qhov ntawm tus menyuam lub aorta (piv txwv li, lub ascending aorta lossis lub descending aorta). Cov nqi no yog siv los txiav txim siab seb txoj kab uas hla ntawm lub aortic arch puas nqaim dhau.

Cia peb kawm me ntsis txog ntau qhov ntawm lub aotic arch.

Thaum koj tus menyuam tus kws kho mob tham txog qhov mob no, nws yuav tham txog cov feem sib txawv ntawm lub aortic arch. Tej zaum koj yuav xav tsis thoob, "Puas yog lub aortic arch faib ua lwm qhov? Qhov ntawd puas yog ib feem ntawm lub aorta loj dua?" Yog, qhov ntawd yog qhov tseeb. Lub aortic arch yog ib feem me me, "zoo li tus pas nrig" ntawm lub aorta. Tab sis, zoo li txhua qhov ntawm lub aorta, lub aortic arch muaj cov hlab ntsha (arteries) uas ceg tawm mus rau ntau qhov kev taw qhia. Ib yam li txoj kev loj muaj cov kev sab. Cov kws kho mob siv cov hlab ntsha sib txawv no ua ciam teb, cim qhov twg ib feem ntawm lub aortic arch pib thiab xaus. Daim "daim ntawv qhia" no pab tau zoo heev rau kev kuaj mob AAH thiab npaj kev kho mob.

Nov yog qee qhov ntawm lub pob ntseg uas koj tus menyuam tus kws kho mob yuav tham txog:

• Proximal Transverse Arch : Qhov no nyob nruab nrab ntawm tus menyuam lub Brachiocephalic Artery (qee zaum hu ua Innominate Artery) thiab Left Common Carotid Artery . Qhov no yog qhov ze tshaj plaws rau lub plawv.
• Distal Transverse Arch : Qhov no nyob nruab nrab ntawm sab laug carotid artery thiab sab laug subclavian artery .
• Aortic Isthmus : Qhov no nyob nruab nrab ntawm sab laug subclavian artery thiab cov hlab ntsha uas tau hais ua ntej hu ua Ductus Arteriosus .

Koj tus menyuam tus kws kho mob yuav txiav txim siab seb qhov twg ntawm qhov nqaim ntawm koj tus menyuam lub pob ntseg, thiab qhov dav ntawm qhov nqaim. Cov ntaub ntawv no yuav coj kev npaj kho mob.

Cov kev kho mob rau qhov no yog dab tsi?

Cov menyuam mos uas muaj hypoplastic aortic arch yuav tsum tau phais plawv kom kho qhov mob. Koj tus menyuam tus kws phais plawv yuav piav qhia rau koj seb koj tus menyuam yuav tsum tau phais hom twg. Cov txheej txheem phais yuav txawv nyob ntawm lwm yam teeb meem thiab cov qauv ntawm koj tus menyuam lub plawv. Tej zaum koj yuav tsum tau muaj thoracotomy , uas yog ib qho kev phais me me ua rau sab laug ntawm koj tus menyuam lub hauv siab, lossis sternotomy, uas yog ib qho kev phais ua rau nruab nrab ntawm lub hauv siab.

Ib txoj kev phais mob uas feem ntau hu ua resection nrog rau kev anastomosis ntev mus txog rau thaum kawg . Txoj kev phais mob no pab tau zoo heev rau cov menyuam mos uas muaj coarctation ntawm lub aorta thiab aortic arch hypoplasia. Hauv txoj kev phais mob no, tus kws phais mob tshem tawm qhov nqaim ntawm lub aorta, coj qhov qis ntawm lub aorta (lub descending aorta), thiab txuas nws rau qhov phais ntev me ntsis hauv lub aortic arch.

Qhov kev cia siab ntawm qhov kev phais no yog los txhim kho cov ntshav ntws los ntawm tus menyuam lub aorta, kom ntseeg tau tias tus menyuam lub cev thiab cov nqaij tau txais cov ntshav txaus oxygen.

Muaj kev cia siab li cas rau kuv tus menyuam txoj kev rov zoo?

Cov lus teb zoo tshaj plaws rau lo lus nug no yog tus kws kho mob ntawm koj tus menyuam. Vim tias tus menyuam txoj kev noj qab haus huv nyob ntawm ntau yam. Tshwj xeeb, seb puas muaj lwm yam teeb meem plawv uas yug los muaj feem cuam tshuam loj heev.

Feem ntau, cov menyuam mos uas tau kho rau tus mob hu ua aotic arch hypoplasia muaj feem ntau dua los tsim cov teeb meem hauv qab no tom qab hauv lub neej:

• Kev nqaim ntawm lawv cov aorta rov qab los .
• Ntshav siab (Hypertension) .
• Nyuaj noj mov lossis nqos : Qhov no tuaj yeem tshwm sim yog tias cov hlab ntsha raug puas tsuaj thaum lub sijhawm phais (qhov no tsis tshua muaj).

Tham nrog koj tus menyuam tus kws kho mob txog cov kev pheej hmoo no thiab yuav ua li cas tswj hwm lawv.

Puas tiv thaiv tau qhov teeb meem no?

Cov teeb meem plawv uas muaj txij thaum yug los xws li hypoplastic aortic arch tej zaum yuav tsis tiv thaiv tau tag nrho . Txawm li cas los xij, kev ua raws li koj tus kws kho mob cov lus qhia kom muaj kev xeeb tub noj qab haus huv tuaj yeem pab txo koj txoj kev pheej hmoo ntawm kev muaj tus mob no lossis lwm yam teeb meem.

Feem ntau, cov no yuav tsum tau zam thaum cev xeeb tub:

• Cawv .
• Tsis txhob haus luam yeeb, haus luam yeeb hluav taws xob thiab txhua yam khoom haus luam yeeb . Tsis tas li ntawd, tsis txhob haus luam yeeb ntawm lwm tus .
• Cov tshuaj yeeb tsis raug cai, tshwj xeeb yog cocaine .

Thiab tseem, koj li.Nws tseem ceeb heev uas yuav tsum mus kuaj mob ua ntej yug menyuam tsis tu ncua. Yog tias koj muaj lwm yam mob nkeeg, nrhiav kev pab kho mob kom tswj tau cov mob ntawd ua ntej thiab thaum cev xeeb tub.

Yuav ua li cas saib xyuas tus menyuam tom qab phais?

Txhua tus menyuam yaus tej kev xav tau yuav txawv tom qab phais, yog li nws yog qhov zoo tshaj plaws los nug koj tus menyuam pab pawg kho mob seb yuav saib xyuas koj tus menyuam li cas rau lub sijhawm luv luv thiab ntev.

Nov yog qee cov lus nug uas koj tuaj yeem nug koj tus kws kho mob:

• Kuv yuav tsum saib xyuas kuv tus menyuam li cas thaum kuv mus tsev?
• Kuv yuav tsum muab tshuaj dab tsi rau kuv tus menyuam? Kuv yuav tsum muab nws ntev npaum li cas?
• Puas xav tau kev kho mob los pab tus menyuam lub cev lossis lub paj hlwb ua haujlwm tau zoo?
• Puas muaj kev txwv rau tus menyuam txoj kev ua ub ua no?
• Thaum twg thiaj muaj kev nyab xeeb xa kuv tus menyuam mus rau chaw zov menyuam? Kuv yuav tsum muab cov lus qhia tshwj xeeb dab tsi rau lawv?
• Puas yog kuv tus menyuam yuav tsum tau kev kho mob ntxiv lossis phais?

Ua niam txiv yeej ib txwm nyuaj. Tab sis nyob nrog ib tug me nyuam uas muaj mob plawv xws li hypoplastic aortic arch (AAH) tuaj yeem coj cov teeb meem tshiab txhua hnub. Qee cov lus uas cov kws kho mob hais thiab cov phiaj xwm kho mob yuav zoo li nyuaj rau nkag siab. Qhov ntawd yog qhov ib txwm muaj, thiab koj tsis nyob ib leeg. Nug koj tus menyuam tus kws kho mob txog cov peev txheej thiab cov pab pawg txhawb nqa uas tuaj yeem pab koj. Kev tsim kom muaj zej zog txhawb nqa rau koj thiab koj tsev neeg tuaj yeem pab txo kev ntxhov siab thiab muab lub zog rau koj kom txav mus tom ntej nrog koj tus menyuam cov kev xav tau.

Cia peb nco ntsoov txog yam peb tau tham txog (Cov Lus Coj Mus Tsev)

• Hypoplastic Aortic Arch (AAH) yog ib qho mob uas lub arch ntawm aorta, ib txoj hlab ntsha loj hauv lub plawv ntawm tus menyuam, tsis loj hlob zoo, ua rau lub arch nqaim.
• Qhov no ua rau nws nyuaj rau cov ntshav ntws los ntawm lub plawv mus rau lwm qhov ntawm lub cev.
• Tus mob no feem ntau pom ua ke nrog lwm yam kab mob plawv hu ua Coarctation of the Aorta .
• Cov tsos mob xws li qaug zog, ua pa nyuaj, thiab tawv nqaij dawb yuav tshwm sim thaum ntxov ntawm tus menyuam lub neej.
• Tus mob no tuaj yeem kuaj pom los ntawm kev siv cov kev ntsuas tshwj xeeb.
• Kev kho mob yog phais plawv .
• Ua raws li cov lus qhia kho mob raws nraim thiab ua raws li kev soj ntsuam mus sij hawm ntev tom qab phais mob yog qhov tseem ceeb heev.
• Kev ua raws li cov cwj pwm noj qab haus huv thaum cev xeeb tub tuaj yeem txo qhov kev pheej hmoo ntawm qee qhov teeb meem yug los.
• Koj tsis yog tib leeg xwb. Nrhiav kev pab los ntawm cov kws kho mob thiab cov pab pawg txhawb nqa.

Peb vam tias cov ntaub ntawv no yuav pab tau koj. Peb xav kom koj tus me nyuam zoo sai sai!

` Hypoplastic Aortic Arch, Aorta Arch Hypoplasia, qhov teeb meem plawv txij thaum yug los, phais plawv menyuam yaus, coarctation ntawm aorta, cov kab mob plawv menyuam yaus, phais plawv