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Koj puas muaj teeb meem roj ntau ntau hauv koj lub cev? Cia peb kawm txog Lipodystrophy!

Koj puas muaj teeb meem roj ntau ntau hauv koj lub cev? Cia peb kawm txog Lipodystrophy!

Koj puas tau pom, lossis tau ntsib, qhov poob rog sai sai hauv qee qhov chaw ntawm koj lub cev, lossis qhov nce rog tsis xav tau hauv lwm qhov chaw? Qhov no qee zaum yuav tsis xav txog. Hnub no peb yuav tham txog qhov mob no. Hauv kev kho mob, qhov no hu ua Lipodystrophy . Tsis txhob txhawj, txawm tias lub npe yuav zoo li txawv txawv, cia peb tham txog nws yooj yim.

Lipodystrophy yog dab tsi?

Hauv lwm lo lus, lipodystrophy yog qhov poob tag nrho lossis ib feem ntawm cov ntaub so ntswg adipose, qhov peb feem ntau hu ua "rog," hauv qee qhov chaw, lossis kev sib sau ua ke ntawm cov rog hauv ntau qhov chaw ntawm lub cev.

Xav txog tias koj poob phaus hauv qee qhov chaw ntawm koj lub cev, xws li koj txhais tes thiab ceg, thaum koj tau txais rog ntau dhau hauv thaj chaw xws li koj lub ntsej muag thiab caj dab. Qhov no yog qhov tshwm sim hauv Lipodystrophy. Muaj ntau hom mob no, qee qhov yog los ntawm caj ces (piv txwv li, qee yam uas peb yug los nrog), thaum lwm tus tshwm sim tom qab vim yog lwm yam mob. Txhua hom cuam tshuam rau tib neeg sib txawv thiab muaj cov tsos mob sib txawv.

Vim li cas cov rog (adipose tissue) thiaj li tseem ceeb rau peb lub cev?

Tam sim no koj yuav xav tias, "Cov rog tsawg dua koj muaj, qhov zoo dua." Tab sis qhov tseeb, cov ntaub so ntswg adipose ua ntau yam haujlwm tseem ceeb hauv peb lub cev. Saib seb:

  • Kev Khaws Cia Zog: Nws yog nyob rau hauv cov nqaij rog no uas cov calories ntxiv uas peb tau txais los ntawm cov khoom noj uas peb noj raug khaws cia ua lub zog.
  • Muab kev tiv thaiv: Nws muab kev tiv thaiv zoo li lub ncoo rau ntau yam kabmob hauv peb lub cev.
  • Tswj kom sov: Khaws lub cev kub thiab tiv thaiv peb ntawm qhov chaw txias.
  • Kev tso tawm cov tshuaj hormones: Muaj ntau cov tshuaj hormones tseem ceeb, xws li Leptin, raug tsim tawm thiab tso tawm rau hauv cov ntshav.
  • Tswj kev o: Nws kuj pab tswj kev o hauv lub cev.

Yog li, thaum cov nqaij rog no ploj lossis tso rau hauv qhov tsis zoo vim yog lipodystrophy, tsis yog peb qhov tsos xwb hloov pauv, tab sis cov haujlwm tseem ceeb hauv lub cev kuj raug cuam tshuam. Ntau tus neeg uas muaj lipodystrophy muaj feem yuav muaj kab mob xws li ntshav qab zib mellitus thiab muaj cov roj cholesterol tsis zoo.

Puas muaj hom lipodystrophy?

Yog lawm, Lipodystrophy tuaj yeem muab faib ua ob hom tseem ceeb: caj ces thiab tau txais.

Hom Kev Mob Lipodystrophy Genetic

Cov no yog cov uas tau txais los ntawm noob caj noob ces, uas yog, cov hom uas tshwm sim los ntawm kev hloov pauv caj ces.

  • Congenital Generalized Lipodystrophy (CGL): Qhov no yog Berardinelli-Seip syndrome.Kuj tseem hu ua. Qhov no yog ib qho mob tsis tshua muaj. Hauv qhov no, cov rog hauv lub cev yuav luag tag nrho lossis feem ntau ploj mus. Qhov no yog tshwm sim los ntawm qhov tsis zoo ntawm caj ces uas muaj thaum yug los. Feem ntau cov mob no tuaj yeem kuaj pom hauv thawj xyoo ntawm lub neej.
  • Kab mob Familial Partial Lipodystrophy (FPLD): Qhov no kuj yog ib qho mob caj ces. Txawm li cas los xij, feem ntau kuaj pom tias muaj mob tom qab hauv lub neej. Hauv qhov mob no, tus menyuam poob rog feem ntau ntawm ob txhais ceg thiab caj npab, thiab khaws cov rog ntau dua ntawm lub ntsej muag thiab caj dab.

Hom Kev Mob Lipodystrophy Uas Tau Txais

Cov no yog cov hom uas tshwm sim tom qab peb yug los thiab thaum peb tseem muaj sia nyob rau ntau yam laj thawj.

  • Kev Mob Lipodystrophy Dav Dav (AGL): Kuj hu ua Lawrence syndrome , qhov mob no ua rau poob rog, feem ntau yog nyob rau ntawm lub ntsej muag, caj dab, caj npab, thiab ceg. Qhov kev poob rog no tuaj yeem tshwm sim sai, dhau ob peb lub lis piam, lossis qeeb qeeb dhau ntau lub hlis lossis xyoo. Nws feem ntau pib thaum yau lossis hluas, tab sis nws tuaj yeem tshwm sim thaum twg los tau. Muaj ntau yam ua rau AGL.
  • Tau Txais Ib Nrab Lipodystrophy (APL): Kuj tseem hu ua Barraquer-Simons syndrome , qhov mob no ua rau maj mam poob rog ntawm lub ntsej muag, caj dab, caj npab, thiab hauv siab thaum yau. Ib txhia neeg kuj tseem yuav muaj rog ntau dhau ntawm thaj chaw xws li lub plab, ceg, thiab pob tw. APL feem ntau cuam tshuam nrog cov mob autoimmune .
  • Kev kho mob lipodystrophy uas siv tshuaj antiretroviral (HAART) ua rau muaj zog heev (LD-HIV): Hom kev kho mob lipodystrophy no tshwm sim rau cov neeg uas muaj tus kab mob HIV tom qab lawv tau txais kev kho mob antiretroviral uas siv tshuaj antiretroviral (HAART) uas suav nrog HIV-1 protease inhibitors . Qhov tshwm sim ntawm tus mob no nyob ntawm qhov mob hnyav thiab ntev npaum li cas ntawm kev kho mob. Cov neeg uas muaj LD-HIV feem ntau muaj kev poob rog maj mam los ntawm lawv txhais tes, ceg, thiab lub ntsej muag. Qee tus neeg kuj tseem yuav tau txais rog ntau dhau nyob ib puag ncig lawv lub ntsej muag, caj dab, nraub qaum sab saud, thiab duav.
  • Kev mob Lipodystrophy hauv zos: Qhov no yog thaum cov rog poob rau hauv ib cheeb tsam me me ntawm lub cev xwb. Piv txwv li, qhov mob no tuaj yeem tshwm sim thaum cov tshuaj (xws li insulin) raug txhaj rau hauv tib thaj chaw ntau zaus. Nws zoo li lub qhov me me, tab sis daim tawv nqaij uas nyob saum nws feem ntau tsis cuam tshuam.

Puas yog Lipodystrophy thiab Lipoatrophy zoo ib yam?

Lipodystrophy yog ib lo lus dav dav rau kev faib cov rog tsis zoo. Nws kuj tseem muaj feem cuam tshuam nrog Lipoatrophy , uas txhais tau tias poob rog. Qee cov kws tshawb fawb thiab kws kho mob siv ob lo lus los piav qhia tib yam mob. Hais yooj yim, Lipoatrophy yog ib feem ntawm Lipodystrophy.

Leej twg raug tus mob no ntau tshaj? Nws tshwm sim ntau npaum li cas?

Feem ntau hom lipodystrophy pib thaum yau, tab sis cov hom uas tau txais kuj tuaj yeem tshwm sim hauv cov neeg laus.

Tsuas yog HAART-induced lipodystrophy (LD-HIV) , lwm hom lipodystrophy uas tau txais feem ntau cuam tshuam rau cov poj niam. Vim tias tus kab mob HIV feem ntau tshwm sim rau cov txiv neej, LD-HIV kuj tshwm sim rau cov txiv neej.

Feem ntau, lipodystrophy tsis tshua muaj . Txawm li cas los xij, cov qauv lipodystrophy uas tau txais (mus tas li) tau dhau los ua ntau dua vim muaj cov kev phiv ntawm qee cov tshuaj.

Lipodystrophy cuam tshuam li cas rau kuv lub cev?

Txhua hom lipodystrophy cuam tshuam rau lub cev sib txawv, tab sis muaj ob qho tseem ceeb uas feem ntau tshwm sim: poob ntawm cov ntaub so ntswg adipose thiab tsis muaj cov tshuaj hormones leptin .

Cov nyhuv ntawm kev poob cov ntaub so ntswg adipose rau lub cev

Peb cov nqaij rog yog ua los ntawm cov hlwb hu ua adipocytes . Txhua lub hlwb adipocyte muaj li ntawm 90% cov roj lipid. Cov adipocytes no khaws cov rog (triglycerides). Thaum cov hlwb rog no puas tsuaj vim yog lipodystrophy, lawv tsis tuaj yeem khaws cov rog kom zoo.

Qee zaum ntawm Lipodystrophy, cov rog uas poob no tau tso rau hauv lwm cov nqaij ntawm peb lub cev tsis raug, piv txwv li, hauv daim siab, pancreas, lossis cov leeg nqaij. Qhov no tuaj yeem ua rau muaj teeb meem kev noj qab haus huv xws li:

  • Kab mob rog rog hauv siab / mob rog hauv siab
  • Kev tsis kam rau insulin thiab cov insulin ntau ntxiv hauv cov ntshav (hyperinsulinemia)
  • Kab mob ntshav qab zib (Diabetes Mellitus)
  • Cov theem ntawm triglycerides hauv cov ntshav nce siab (hypertriglyceridemia)
  • Mob Pancreatitis
  • Kab mob metabolic syndrome
  • Kab mob plawv

Tiam sis nco ntsoov, tsis yog txhua tus neeg uas muaj lipodystrophy yuav muaj cov mob no. Qee tus yuav muaj cov mob tsis hnyav heev, thaum lwm tus yuav muaj cov mob hnyav dua.

Cov teebmeem ntawm Leptin Deficiency rau lub cev

Thaum cov neeg uas muaj lipodystrophy poob cov nqaij rog, lawv kuj poob qee cov tshuaj hormones, tshwj xeeb tshaj yog cov tshuaj leptin .

Leptin yog ib yam tshuaj hormones uas peb cov nqaij rog tsim tawm. Nws pab peb kom peb lub cev hnyav ib txwm nyob rau lub sijhawm ntev. Koj puas paub yuav ua li cas? Los ntawm kev ua rau peb xav tias puv thiab tswj peb txoj kev tshaib plab. Cov kws tshawb fawb tseem tab tom tshawb nrhiav leptin. Lawv ntseeg tias leptin cuam tshuam rau peb cov metabolism , endocrine system ua haujlwm, thiab kev ua haujlwm ntawm lub cev tiv thaiv kab mob .

Cov neeg uas muaj lipodystrophy yuav muaj cov leptin txo qis, uas tuaj yeem ua rau muaj kev tshaib plab ntau dhau, tsis kam insulin, thiab lwm yam teeb meem kev noj qab haus huv.

Cov tsos mob ntawm lipodystrophy yog dab tsi?

Vim tias muaj ntau hom lipodystrophy, cov tsos mob kuj sib txawv heev.

Cov tsos mob feem ntau yog qhov pom tseeb thiab tsis tu ncua poob rog hauv qee qhov chaw ntawm lub cev, tib lub sijhawm, muaj cov rog tsis zoo lossis tsis xav tau ntau hauv lwm qhov chaw ntawm lub cev.

Piv txwv li, cov neeg uas muaj cov roj lipodystrophy (APL) maj mam poob rog ntawm lawv lub ntsej muag, caj dab, caj npab, thiab hauv siab thaum yau. Ib txhia neeg uas muaj APL kuj tseem yuav tau cov rog ntau dhau rau thaj chaw xws li lub plab, ceg, thiab pob tw.

Nyob ntawm seb koj muaj hom lipodystrophy thiab koj lub hnub nyoog li cas, tej zaum koj yuav tsis pom muaj teeb meem kev noj qab haus huv loj rau ntau xyoo. Txawm li cas los xij, ntau hom lipodystrophy ua rau cov roj cholesterol hauv cov ntshav siab, triglycerides, thiab qab zib (glucose). Koj tus kws kho mob tuaj yeem kuaj pom cov no nrog kev kuaj ntshav niaj hnub, xws li lipid panel thiab basic metabolic panel .

Qee hom lipodystrophy, tshwj xeeb tshaj yog ib feem lipodystrophy, yuav nyuaj rau kuaj mob. Yog li ntawd, nws yog ib qho tseem ceeb uas yuav tsum mus ntsib kws kho mob yog tias koj lossis koj tus menyuam muaj cov tsos mob tshiab lossis yog tias cov tsos mob uas twb muaj lawm hnyav zuj zus, tsis hais qhov ua rau yog dab tsi.

Dab tsi yog cov ua rau lipodystrophy?

Cov ua rau lipodystrophy sib txawv nyob ntawm seb nws yog caj ces lossis tau txais.

Ua rau muaj kev hloov pauv ntawm caj ces

Cov qauv caj ces ntawm lipodystrophy - uas yog congenital generalized lipodystrophy (CGL) thiab familial partial lipodystrophy (FPLD) - yog tshwm sim los ntawm qee qhov kev hloov pauv caj ces .

Kev hloov pauv ntawm cov noob caj noob ces yog kev hloov pauv hauv peb cov DNA. Peb cov DNA yog qhov muab cov ntaub ntawv rau peb cov hlwb kom ua lawv txoj haujlwm. Yog li, yog tias ib feem ntawm cov DNA no tsis tiav lossis puas lawm, peb yuav muaj cov tsos mob ntawm tus kab mob caj noob ces.

  • Ua rau muaj mob lipodystrophy (CGL) txij thaum yug los): CGL hom 1 txog 4 yog tshwm sim los ntawm kev hloov pauv hauv cov noob AGPAT2, BSCL2, CAV1 , thiab CAVIN1 . Cov noob no tseem ceeb rau kev loj hlob thiab kev ua haujlwm ntawm cov hlwb khaws rog (adipocytes) hauv peb cov nqaij rog. Kev hloov pauv hauv cov noob no cuam tshuam rau cov qauv thiab kev ua haujlwm ntawm adipocytes. Ib tug menyuam uas muaj CGL tau txais cov noob hloov pauv no los ntawm lawv niam lawv txiv. Txawm tias ob leeg niam txiv muaj ib daim qauv ntawm cov noob hloov pauv, feem ntau lawv tsis qhia cov tsos mob.
  • Ua rau muaj mob Familial Partial Lipodystrophy (FPLD): Kev hloov pauv hauv ntau hom noob caj ces tuaj yeem ua rau muaj FPLD. Feem ntau yog LMNA.Kev hloov pauv hauv ib lub noob hu ua LMNA. Lub noob LMNA thiab lwm cov noob uas koom nrog hauv FPLD qhia cov adipocytes kom khaws cov rog thiab ua ntau yam protein uas tseem ceeb rau kev khaws cov rog. Yog tias muaj kev hloov pauv tshwm sim hauv ib qho ntawm cov noob no, kev loj hlob, cov qauv, lossis kev ua haujlwm ntawm cov adipocytes raug cuam tshuam tsis zoo. Feem ntau ntawm FPLD yog tau txais los ntawm tus qauv autosomal dominant . Qhov no txhais tau tias muaj ib daim qauv ntawm cov noob hloov pauv hauv txhua lub cell txaus los ua rau muaj tus kab mob. Qee zaum, ib tus neeg uas muaj FPLD tau txais qhov kev hloov pauv los ntawm ib tus ntawm lawv niam lawv txiv uas raug cuam tshuam. Hauv lwm qhov xwm txheej, lawv yog tshwm sim los ntawm kev hloov pauv tshiab, random hauv cov noob, thiab tuaj yeem tshwm sim txawm tias tsis muaj leej twg hauv tsev neeg tau muaj tus kab mob ua ntej.

Cov ua rau mob Lipodystrophy

Kev mob lipodystrophy uas tau txais tuaj yeem tshwm sim los ntawm cov tshuaj, cov tshuaj tiv thaiv kab mob autoimmune , lossis cov ua rau idiopathic . Txawm hais tias tsis muaj lub hauv paus caj ces ncaj qha rau kev mob lipodystrophy uas tau txais, qee cov kws tshawb fawb ntseeg tias qee tus neeg yuav muaj kev mob caj ces uas yuav tsim kev mob lipodystrophy uas tau txais.

  • Cov Ua Rau Mob Pob Tawb (AGL): AGL tuaj yeem tshwm sim tom qab muaj kev kis kab mob lossis tom qab muaj kab mob ntawm lub cev tiv thaiv kab mob. Cov kab mob uas tau txuas nrog AGL suav nrog:
  • Kab mob qaib ntxhw (Chickenpox / varicella)
  • Kab mob qhua pias
  • Kab mob hnoos qhuav (pertussis)
  • Kab mob diphtheria
  • Mob ntsws o
  • Kab mob pob txha
  • Kab mob Mononucleosis (Mononucleosis / mono)

Nws tsis paub tseeb tias koj yuav muaj AGL tsuas yog vim koj muaj cov kab mob no.

Cov mob autoimmune cuam tshuam nrog AGL suav nrog:

  • Kab mob thyroid autoimmune
  • Kab mob siab autoimmune
  • Cov kab mob dermatomyositis rau cov menyuam yaus
  • Mob pob qij txha caj qaum
  • Kab mob Sjogren
  • Kab mob autoimmune hemolytic anemia

Yog koj muaj cov kab mob tiv thaiv kab mob no, nws tsis tuaj yeem hais tias koj yuav muaj AGL.

Feem ntau, qhov ua rau AGL tsis tuaj yeem txheeb xyuas tau (idiopathic).

  • Ua rau muaj qhov mob Acquired Partial Lipodystrophy (APL): Cov kws tshawb fawb ntseeg tias APL yog tshwm sim los ntawm peb lub cev tiv thaiv kab mob ua yuam kev rhuav tshem cov hlwb rog. Ntau tshaj 80% ntawm cov neeg uas muaj APL muaj Complement 3 hauv lawv cov ntshav.Muaj ib qho protein hu ua complement factor uas tsis tshua muaj. Cov protein no feem ntau koom nrog peb lub cev tiv thaiv kab mob. Cov neeg uas muaj APL feem ntau muaj ib qho autoantibody hu ua complement 3-nephritic factor hauv lawv cov ntshav. Ib qho autoantibody yog ib qho protein hauv lub cev tiv thaiv kab mob uas ua yuam kev tawm tsam thiab ua puas rau cov nqaij noj qab haus huv.
  • Cov ua rau muaj kev kho mob antiretroviral therapy (HAART)-induced lipodystrophy (LD-HIV): Cov kws tshawb fawb tseem tsis tau paub meej tias vim li cas HAART, uas muaj cov tshuaj tiv thaiv HIV-1 protease, ua rau muaj lipodystrophy.

Qhov xov xwm zoo yog tias feem ntau cov neeg uas pib kho tus kab mob HIV tam sim no tsis tas yuav txhawj ntau txog lipodystrophy, vim tias cov tshuaj HIV tshiab ua rau qhov mob no tsis tshua muaj tshwm sim.

Yuav ua li cas koj thiaj paub tias koj muaj lipodystrophy?

Yog tias koj muaj cov tsos mob ntawm lipodystrophy, koj tus kws kho mob yuav ua qhov kev kuaj mob lub cev, nug txog koj keeb kwm kev kho mob thiab keeb kwm kev kho mob hauv tsev neeg, thiab tom qab ntawd xaj qee qhov kev kuaj mob kom paub meej tias muaj mob thiab saib seb puas muaj lwm yam ua rau koj cov tsos mob.

Cov kev kuaj twg siv los kuaj mob lipodystrophy?

Koj tus kws kho mob yuav xaj ntau qhov kev kuaj mob kom paub tseeb tias koj cov lipodystrophy zoo li cas thiab/lossis seb puas muaj lwm yam ua rau koj cov tsos mob. Cov no suav nrog:

  • Kev Ntsuas MRI Tag Nrho Lub Cev (Magnetic Resonance Imaging): Kev ntsuas MRI siv lub hlau nplaum loj, cov nthwv dej xov tooj cua, thiab lub khoos phis tawj los ua cov duab ntxaws ntxaws ntawm cov kabmob thiab lwm yam qauv hauv koj lub cev. Koj tus kws kho mob yuav hais kom ua qhov kev kuaj no los ntsuas qhov sib xyaw thiab kev faib tawm ntawm cov rog hauv koj lub cev.
  • Kev Ntsuam Xyuas Txog Kev Hloov Pauv Txhua Yam: Qhov no yog kev kuaj ntshav uas ntsuas 14 yam khoom sib txawv hauv koj cov ntshav. Nws muab cov ntaub ntawv tseem ceeb txog kev sib npaug ntawm cov tshuaj lom neeg thiab kev hloov pauv ntawm koj lub cev. Tus kws kho mob yuav saib xyuas koj cov piam thaj hauv cov ntshav (glucose) thiab cov enzymes hauv siab .
  • Panel Lipid: Qhov no kuj yog kev kuaj ntshav. Nws ntsuas qhov ntau ntawm cov rog hu ua lipids hauv koj cov ntshav. Kev kuaj no feem ntau suav nrog plaub qhov kev ntsuas roj cholesterol thiab kev ntsuas triglyceride. Lipodystrophy feem ntau ua rau cov roj cholesterol tsis zoo.
  • Kev Ntsuas Leptin: Qhov no ntsuas qib ntawm leptin hauv koj cov ntshav. Yog tias koj muaj lipodystrophy thiab koj cov qib leptin qis dua li qub, qhov no tuaj yeem muab qee lub tswv yim rau koj txog li cas koj lub cev yuav teb rau kev kho mob hloov leptin.
  • Kev Kuaj Mob Genetic: Yog tias koj tus kws kho mob xav tias koj muaj hom Lipodystrophy uas tau txais los ntawm noob caj noob ces, lawv yuav pom zoo kom kuaj mob genetic los xyuas kom meej qhov kev kuaj mob.
  • Kev kuaj mob raum:Qhov no suav nrog kev phais tshem tawm ib qho qauv ntawm cov nqaij ntawm lub raum thiab kuaj nws hauv qab lub tshuab microscope. Koj tus kws kho mob yuav hais kom kuaj qhov no kom pom tias koj lub raum puas tau raug cuam tshuam los ntawm lipodystrophy.

Cov kev kho mob rau lipodystrophy yog dab tsi?

Kev kho mob thiab kev tswj hwm ntawm lipodystrophy nyob ntawm hom tshwj xeeb uas koj muaj, thiab seb koj puas muaj lwm yam mob cuam tshuam, xws li ntshav qab zib lossis cov roj cholesterol tsis zoo.

Cov kev kho mob uas siv ntau tshaj plaws rau lipodystrophy yog:

  • Tshuaj hloov Leptin: Koj tus kws kho mob yuav sau ntawv kom siv cov tshuaj hormones leptin hu ua metreleptin . Cov neeg uas muaj lipodystrophy feem ntau muaj qhov tsis txaus ntawm leptin. Cov tshuaj hormones no pab tswj lub cev cov metabolism thiab tseem tuaj yeem txo cov roj cholesterol thiab triglyceride ntau.
  • Kev Kho Mob Ntshav Qab Zib thiab Kev Tsis Haum Insulin: Yog tias koj muaj kev tsis haum insulin thiab/lossis ntshav qab zib vim yog lipodystrophy, koj tus kws kho mob yuav sau ntawv kom noj tshuaj xws li pioglitazone, metformin, sulfonylureas , lossis thiazolidinediones los kho nws. Qee tus neeg uas muaj lipodystrophy kuj tseem yuav tsum tau noj insulin los kho lawv tus kab mob ntshav qab zib. Koj kuj tseem yuav tsum tau kuaj xyuas koj cov ntshav qab zib tsis tu ncua hauv tsev nrog lub glucometer .
  • Tswj cov roj triglyceride thiab cov roj cholesterol: Cov tshuaj noj uas tau hais ua ntej uas pab kho mob ntshav qab zib feem ntau tuaj yeem pab tswj cov roj cholesterol. Koj tus kws kho mob kuj tseem yuav sau ntawv kom noj cov tshuaj statins , xws li rosuvastatin thiab pravastatin . Cov neeg uas muaj cov roj triglyceride ntau yuav tsum tau noj cov tshuaj ntxiv ntawm cov roj fibric acid lossis n-3 polyunsaturated fatty acids , xws li cov uas pom muaj nyob rau hauv roj ntses.
  • Kev phais kom zoo nkauj thiab cov txheej txheem: Cov neeg uas muaj lipodystrophy nyob rau hauv cov cheeb tsam uas rhiab heev rau kev zoo nkauj, xws li lub ntsej muag, hauv siab, thiab qhov chaw mos, yuav raug phais kom zoo nkauj kom zoo dua qub thiab muaj kev ntseeg siab rau lawv tus kheej. Cov kws phais yas yuav ua kev hloov pauv cov nqaij adipose, kev tsim kho lub ntsej muag siv cov flaps dawb, thiab silicone lossis lwm yam kev cog rau hauv. Lawv kuj tseem siv tau liposuction lossis kev phais tshem tawm cov txheej txheem kom tshem tawm cov rog tsis xav tau hauv cov cheeb tsam xws li lub puab tsaig lossis nraub qaum ntawm lub caj dab (feem ntau hu ua "buffalo hump" ).

Cov kws tshawb fawb tseem muaj ntau yam yuav tsum kawm txog kev kho thiab tswj cov teeb meem lipodystrophy. Thaum lawv tshawb pom ntau ntxiv txog qhov nyuaj ntawm cov txheej txheem metabolic, ntau txoj kev kho mob yuav muaj.

Puas tuaj yeem tiv thaiv lipodystrophy?

Feem ntau, lipodystrophy tsis tuaj yeem tiv thaiv tau.

Cov qauv caj ces ntawm lipodystrophy tsis tuaj yeem tiv thaiv tau, vim tias lawv yog qhov tshwm sim ntawm kev hloov pauv caj ces. Yog tias koj tab tom npaj yuav muaj menyuam, nkag siab txog qhov kev pheej hmoo ntawm kev muaj menyuam uas muaj mob caj ces thiab tham nrog koj tus kws kho mob txog kev kuaj caj ces.

Feem ntau cov kab mob lipodystrophy uas tau txais los ntawm kev kis kab mob lossis cov kab mob ntawm lub cev tiv thaiv kab mob. Txawm hais tias qee cov kab mob, xws li mob qaib ntxhw thiab hnoos qhuav, tuaj yeem tiv thaiv tau los ntawm kev txhaj tshuaj tiv thaiv kab mob, lwm cov kab mob thiab cov kab mob ntawm lub cev tiv thaiv kab mob uas cuam tshuam nrog cov kab mob lipodystrophy uas tau txais los ntawm kev kis kab mob tsis tuaj yeem tiv thaiv tau.

Yuav ua li cas thiaj paub tias lipodystrophy yog dab tsi?

Qhov kev cia siab rau lipodystrophy feem ntau nyob ntawm seb koj muaj hom lipodystrophy twg, thiab seb koj puas muaj lwm yam mob lossis teeb meem cuam tshuam, xws li ntshav qab zib, teeb meem siab lossis raum.

Kev kho kom zoo nkauj ntawm cov cheeb tsam uas muaj roj tsawg thiab cov cheeb tsam uas muaj roj ntau dhau pab txhim kho lub neej zoo rau cov neeg uas muaj lipodystrophy.

Yog tias koj lossis koj tus menyuam raug kuaj pom tias muaj lipodystrophy, nrog koj tus kws kho mob tham txog yam yuav tshwm sim thiab yuav ua li cas thiaj tswj tau qhov mob zoo tshaj plaws.

Thaum twg koj yuav tsum mus ntsib kws kho mob txog lipodystrophy?

Yog koj pom tias koj lossis koj tus menyuam cov rog hauv lub cev pheej poob qis hauv qee qhov chaw, lossis cov rog nce ntxiv hauv qee qhov chaw, nrog koj tus kws kho mob tham.

Yog tias koj lossis koj tus menyuam raug kuaj pom tias muaj Lipodystrophy, koj yuav tsum ntsib nrog koj pab neeg kho mob tsis tu ncua kom paub tseeb tias koj txoj kev kho mob ua haujlwm zoo rau koj.

Thaum kawg, tej yam uas yuav tsum nco ntsoov

Lipodystrophy yog ib qho mob uas tsis tshua muaj tab sis loj heev. Txawm hais tias tsis muaj kev kho mob los xij, qee qhov kev kho mob tuaj yeem pab tswj nws cov tsos mob thiab cov mob cuam tshuam, xws li ntshav qab zib thiab cov roj cholesterol tsis zoo.

Kev kho mob txawv ntawm ib tus neeg mus rau ib tus neeg. Yog li ntawd, koj pab neeg kho mob yuav ua haujlwm nrog koj los tsim ib txoj kev npaj uas zoo tshaj plaws rau koj. Tsis txhob ntshai nug koj tus kws kho mob cov lus nug. Lawv nyob ntawd los pab koj. Cov kev paub no yuav pab koj ua neej noj qab nyob zoo!


lipodystrophy , cov nqaij adipose, leptin, genetic, acquired, ntshav qab zib, cholesterol, triglyceride, HIV, cov kab mob metabolic

Frequently Asked Questions (FAQ)

Cov kev kuaj twg siv los kuaj mob lipodystrophy?

Koj tus kws kho mob yuav xaj ntau qhov kev kuaj mob kom paub tseeb tias koj cov lipodystrophy zoo li cas thiab/lossis seb puas muaj lwm yam ua rau koj cov tsos mob. Cov no suav nrog:

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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Tsis muaj lus teb tau muab tso tawm. Ntxiv koj cov lus tawm ntawm no thawj zaug.

Ntxiv koj cov lus

Thov xam: 3 + 3 =
Koj puas muaj teeb meem roj ntau ntau hauv koj lub cev? Cia peb kawm txog Lipodystrophy!

Koj puas muaj teeb meem roj ntau ntau hauv koj lub cev? Cia peb kawm txog Lipodystrophy!

Koj puas tau pom, lossis tau ntsib, qhov poob rog sai sai hauv qee qhov chaw ntawm koj lub cev, lossis qhov nce rog tsis xav tau hauv lwm qhov chaw? Qhov no qee zaum yuav tsis xav txog. Hnub no peb yuav tham txog qhov mob no. Hauv kev kho mob, qhov no hu ua Lipodystrophy . Tsis txhob txhawj, txawm tias lub npe yuav zoo li txawv txawv, cia peb tham txog nws yooj yim.

Lipodystrophy yog dab tsi?

Hauv lwm lo lus, lipodystrophy yog qhov poob tag nrho lossis ib feem ntawm cov ntaub so ntswg adipose, qhov peb feem ntau hu ua "rog," hauv qee qhov chaw, lossis kev sib sau ua ke ntawm cov rog hauv ntau qhov chaw ntawm lub cev.

Xav txog tias koj poob phaus hauv qee qhov chaw ntawm koj lub cev, xws li koj txhais tes thiab ceg, thaum koj tau txais rog ntau dhau hauv thaj chaw xws li koj lub ntsej muag thiab caj dab. Qhov no yog qhov tshwm sim hauv Lipodystrophy. Muaj ntau hom mob no, qee qhov yog los ntawm caj ces (piv txwv li, qee yam uas peb yug los nrog), thaum lwm tus tshwm sim tom qab vim yog lwm yam mob. Txhua hom cuam tshuam rau tib neeg sib txawv thiab muaj cov tsos mob sib txawv.

Vim li cas cov rog (adipose tissue) thiaj li tseem ceeb rau peb lub cev?

Tam sim no koj yuav xav tias, "Cov rog tsawg dua koj muaj, qhov zoo dua." Tab sis qhov tseeb, cov ntaub so ntswg adipose ua ntau yam haujlwm tseem ceeb hauv peb lub cev. Saib seb:

  • Kev Khaws Cia Zog: Nws yog nyob rau hauv cov nqaij rog no uas cov calories ntxiv uas peb tau txais los ntawm cov khoom noj uas peb noj raug khaws cia ua lub zog.
  • Muab kev tiv thaiv: Nws muab kev tiv thaiv zoo li lub ncoo rau ntau yam kabmob hauv peb lub cev.
  • Tswj kom sov: Khaws lub cev kub thiab tiv thaiv peb ntawm qhov chaw txias.
  • Kev tso tawm cov tshuaj hormones: Muaj ntau cov tshuaj hormones tseem ceeb, xws li Leptin, raug tsim tawm thiab tso tawm rau hauv cov ntshav.
  • Tswj kev o: Nws kuj pab tswj kev o hauv lub cev.

Yog li, thaum cov nqaij rog no ploj lossis tso rau hauv qhov tsis zoo vim yog lipodystrophy, tsis yog peb qhov tsos xwb hloov pauv, tab sis cov haujlwm tseem ceeb hauv lub cev kuj raug cuam tshuam. Ntau tus neeg uas muaj lipodystrophy muaj feem yuav muaj kab mob xws li ntshav qab zib mellitus thiab muaj cov roj cholesterol tsis zoo.

Puas muaj hom lipodystrophy?

Yog lawm, Lipodystrophy tuaj yeem muab faib ua ob hom tseem ceeb: caj ces thiab tau txais.

Hom Kev Mob Lipodystrophy Genetic

Cov no yog cov uas tau txais los ntawm noob caj noob ces, uas yog, cov hom uas tshwm sim los ntawm kev hloov pauv caj ces.

  • Congenital Generalized Lipodystrophy (CGL): Qhov no yog Berardinelli-Seip syndrome.Kuj tseem hu ua. Qhov no yog ib qho mob tsis tshua muaj. Hauv qhov no, cov rog hauv lub cev yuav luag tag nrho lossis feem ntau ploj mus. Qhov no yog tshwm sim los ntawm qhov tsis zoo ntawm caj ces uas muaj thaum yug los. Feem ntau cov mob no tuaj yeem kuaj pom hauv thawj xyoo ntawm lub neej.
  • Kab mob Familial Partial Lipodystrophy (FPLD): Qhov no kuj yog ib qho mob caj ces. Txawm li cas los xij, feem ntau kuaj pom tias muaj mob tom qab hauv lub neej. Hauv qhov mob no, tus menyuam poob rog feem ntau ntawm ob txhais ceg thiab caj npab, thiab khaws cov rog ntau dua ntawm lub ntsej muag thiab caj dab.

Hom Kev Mob Lipodystrophy Uas Tau Txais

Cov no yog cov hom uas tshwm sim tom qab peb yug los thiab thaum peb tseem muaj sia nyob rau ntau yam laj thawj.

  • Kev Mob Lipodystrophy Dav Dav (AGL): Kuj hu ua Lawrence syndrome , qhov mob no ua rau poob rog, feem ntau yog nyob rau ntawm lub ntsej muag, caj dab, caj npab, thiab ceg. Qhov kev poob rog no tuaj yeem tshwm sim sai, dhau ob peb lub lis piam, lossis qeeb qeeb dhau ntau lub hlis lossis xyoo. Nws feem ntau pib thaum yau lossis hluas, tab sis nws tuaj yeem tshwm sim thaum twg los tau. Muaj ntau yam ua rau AGL.
  • Tau Txais Ib Nrab Lipodystrophy (APL): Kuj tseem hu ua Barraquer-Simons syndrome , qhov mob no ua rau maj mam poob rog ntawm lub ntsej muag, caj dab, caj npab, thiab hauv siab thaum yau. Ib txhia neeg kuj tseem yuav muaj rog ntau dhau ntawm thaj chaw xws li lub plab, ceg, thiab pob tw. APL feem ntau cuam tshuam nrog cov mob autoimmune .
  • Kev kho mob lipodystrophy uas siv tshuaj antiretroviral (HAART) ua rau muaj zog heev (LD-HIV): Hom kev kho mob lipodystrophy no tshwm sim rau cov neeg uas muaj tus kab mob HIV tom qab lawv tau txais kev kho mob antiretroviral uas siv tshuaj antiretroviral (HAART) uas suav nrog HIV-1 protease inhibitors . Qhov tshwm sim ntawm tus mob no nyob ntawm qhov mob hnyav thiab ntev npaum li cas ntawm kev kho mob. Cov neeg uas muaj LD-HIV feem ntau muaj kev poob rog maj mam los ntawm lawv txhais tes, ceg, thiab lub ntsej muag. Qee tus neeg kuj tseem yuav tau txais rog ntau dhau nyob ib puag ncig lawv lub ntsej muag, caj dab, nraub qaum sab saud, thiab duav.
  • Kev mob Lipodystrophy hauv zos: Qhov no yog thaum cov rog poob rau hauv ib cheeb tsam me me ntawm lub cev xwb. Piv txwv li, qhov mob no tuaj yeem tshwm sim thaum cov tshuaj (xws li insulin) raug txhaj rau hauv tib thaj chaw ntau zaus. Nws zoo li lub qhov me me, tab sis daim tawv nqaij uas nyob saum nws feem ntau tsis cuam tshuam.

Puas yog Lipodystrophy thiab Lipoatrophy zoo ib yam?

Lipodystrophy yog ib lo lus dav dav rau kev faib cov rog tsis zoo. Nws kuj tseem muaj feem cuam tshuam nrog Lipoatrophy , uas txhais tau tias poob rog. Qee cov kws tshawb fawb thiab kws kho mob siv ob lo lus los piav qhia tib yam mob. Hais yooj yim, Lipoatrophy yog ib feem ntawm Lipodystrophy.

Leej twg raug tus mob no ntau tshaj? Nws tshwm sim ntau npaum li cas?

Feem ntau hom lipodystrophy pib thaum yau, tab sis cov hom uas tau txais kuj tuaj yeem tshwm sim hauv cov neeg laus.

Tsuas yog HAART-induced lipodystrophy (LD-HIV) , lwm hom lipodystrophy uas tau txais feem ntau cuam tshuam rau cov poj niam. Vim tias tus kab mob HIV feem ntau tshwm sim rau cov txiv neej, LD-HIV kuj tshwm sim rau cov txiv neej.

Feem ntau, lipodystrophy tsis tshua muaj . Txawm li cas los xij, cov qauv lipodystrophy uas tau txais (mus tas li) tau dhau los ua ntau dua vim muaj cov kev phiv ntawm qee cov tshuaj.

Lipodystrophy cuam tshuam li cas rau kuv lub cev?

Txhua hom lipodystrophy cuam tshuam rau lub cev sib txawv, tab sis muaj ob qho tseem ceeb uas feem ntau tshwm sim: poob ntawm cov ntaub so ntswg adipose thiab tsis muaj cov tshuaj hormones leptin .

Cov nyhuv ntawm kev poob cov ntaub so ntswg adipose rau lub cev

Peb cov nqaij rog yog ua los ntawm cov hlwb hu ua adipocytes . Txhua lub hlwb adipocyte muaj li ntawm 90% cov roj lipid. Cov adipocytes no khaws cov rog (triglycerides). Thaum cov hlwb rog no puas tsuaj vim yog lipodystrophy, lawv tsis tuaj yeem khaws cov rog kom zoo.

Qee zaum ntawm Lipodystrophy, cov rog uas poob no tau tso rau hauv lwm cov nqaij ntawm peb lub cev tsis raug, piv txwv li, hauv daim siab, pancreas, lossis cov leeg nqaij. Qhov no tuaj yeem ua rau muaj teeb meem kev noj qab haus huv xws li:

  • Kab mob rog rog hauv siab / mob rog hauv siab
  • Kev tsis kam rau insulin thiab cov insulin ntau ntxiv hauv cov ntshav (hyperinsulinemia)
  • Kab mob ntshav qab zib (Diabetes Mellitus)
  • Cov theem ntawm triglycerides hauv cov ntshav nce siab (hypertriglyceridemia)
  • Mob Pancreatitis
  • Kab mob metabolic syndrome
  • Kab mob plawv

Tiam sis nco ntsoov, tsis yog txhua tus neeg uas muaj lipodystrophy yuav muaj cov mob no. Qee tus yuav muaj cov mob tsis hnyav heev, thaum lwm tus yuav muaj cov mob hnyav dua.

Cov teebmeem ntawm Leptin Deficiency rau lub cev

Thaum cov neeg uas muaj lipodystrophy poob cov nqaij rog, lawv kuj poob qee cov tshuaj hormones, tshwj xeeb tshaj yog cov tshuaj leptin .

Leptin yog ib yam tshuaj hormones uas peb cov nqaij rog tsim tawm. Nws pab peb kom peb lub cev hnyav ib txwm nyob rau lub sijhawm ntev. Koj puas paub yuav ua li cas? Los ntawm kev ua rau peb xav tias puv thiab tswj peb txoj kev tshaib plab. Cov kws tshawb fawb tseem tab tom tshawb nrhiav leptin. Lawv ntseeg tias leptin cuam tshuam rau peb cov metabolism , endocrine system ua haujlwm, thiab kev ua haujlwm ntawm lub cev tiv thaiv kab mob .

Cov neeg uas muaj lipodystrophy yuav muaj cov leptin txo qis, uas tuaj yeem ua rau muaj kev tshaib plab ntau dhau, tsis kam insulin, thiab lwm yam teeb meem kev noj qab haus huv.

Cov tsos mob ntawm lipodystrophy yog dab tsi?

Vim tias muaj ntau hom lipodystrophy, cov tsos mob kuj sib txawv heev.

Cov tsos mob feem ntau yog qhov pom tseeb thiab tsis tu ncua poob rog hauv qee qhov chaw ntawm lub cev, tib lub sijhawm, muaj cov rog tsis zoo lossis tsis xav tau ntau hauv lwm qhov chaw ntawm lub cev.

Piv txwv li, cov neeg uas muaj cov roj lipodystrophy (APL) maj mam poob rog ntawm lawv lub ntsej muag, caj dab, caj npab, thiab hauv siab thaum yau. Ib txhia neeg uas muaj APL kuj tseem yuav tau cov rog ntau dhau rau thaj chaw xws li lub plab, ceg, thiab pob tw.

Nyob ntawm seb koj muaj hom lipodystrophy thiab koj lub hnub nyoog li cas, tej zaum koj yuav tsis pom muaj teeb meem kev noj qab haus huv loj rau ntau xyoo. Txawm li cas los xij, ntau hom lipodystrophy ua rau cov roj cholesterol hauv cov ntshav siab, triglycerides, thiab qab zib (glucose). Koj tus kws kho mob tuaj yeem kuaj pom cov no nrog kev kuaj ntshav niaj hnub, xws li lipid panel thiab basic metabolic panel .

Qee hom lipodystrophy, tshwj xeeb tshaj yog ib feem lipodystrophy, yuav nyuaj rau kuaj mob. Yog li ntawd, nws yog ib qho tseem ceeb uas yuav tsum mus ntsib kws kho mob yog tias koj lossis koj tus menyuam muaj cov tsos mob tshiab lossis yog tias cov tsos mob uas twb muaj lawm hnyav zuj zus, tsis hais qhov ua rau yog dab tsi.

Dab tsi yog cov ua rau lipodystrophy?

Cov ua rau lipodystrophy sib txawv nyob ntawm seb nws yog caj ces lossis tau txais.

Ua rau muaj kev hloov pauv ntawm caj ces

Cov qauv caj ces ntawm lipodystrophy - uas yog congenital generalized lipodystrophy (CGL) thiab familial partial lipodystrophy (FPLD) - yog tshwm sim los ntawm qee qhov kev hloov pauv caj ces .

Kev hloov pauv ntawm cov noob caj noob ces yog kev hloov pauv hauv peb cov DNA. Peb cov DNA yog qhov muab cov ntaub ntawv rau peb cov hlwb kom ua lawv txoj haujlwm. Yog li, yog tias ib feem ntawm cov DNA no tsis tiav lossis puas lawm, peb yuav muaj cov tsos mob ntawm tus kab mob caj noob ces.

  • Ua rau muaj mob lipodystrophy (CGL) txij thaum yug los): CGL hom 1 txog 4 yog tshwm sim los ntawm kev hloov pauv hauv cov noob AGPAT2, BSCL2, CAV1 , thiab CAVIN1 . Cov noob no tseem ceeb rau kev loj hlob thiab kev ua haujlwm ntawm cov hlwb khaws rog (adipocytes) hauv peb cov nqaij rog. Kev hloov pauv hauv cov noob no cuam tshuam rau cov qauv thiab kev ua haujlwm ntawm adipocytes. Ib tug menyuam uas muaj CGL tau txais cov noob hloov pauv no los ntawm lawv niam lawv txiv. Txawm tias ob leeg niam txiv muaj ib daim qauv ntawm cov noob hloov pauv, feem ntau lawv tsis qhia cov tsos mob.
  • Ua rau muaj mob Familial Partial Lipodystrophy (FPLD): Kev hloov pauv hauv ntau hom noob caj ces tuaj yeem ua rau muaj FPLD. Feem ntau yog LMNA.Kev hloov pauv hauv ib lub noob hu ua LMNA. Lub noob LMNA thiab lwm cov noob uas koom nrog hauv FPLD qhia cov adipocytes kom khaws cov rog thiab ua ntau yam protein uas tseem ceeb rau kev khaws cov rog. Yog tias muaj kev hloov pauv tshwm sim hauv ib qho ntawm cov noob no, kev loj hlob, cov qauv, lossis kev ua haujlwm ntawm cov adipocytes raug cuam tshuam tsis zoo. Feem ntau ntawm FPLD yog tau txais los ntawm tus qauv autosomal dominant . Qhov no txhais tau tias muaj ib daim qauv ntawm cov noob hloov pauv hauv txhua lub cell txaus los ua rau muaj tus kab mob. Qee zaum, ib tus neeg uas muaj FPLD tau txais qhov kev hloov pauv los ntawm ib tus ntawm lawv niam lawv txiv uas raug cuam tshuam. Hauv lwm qhov xwm txheej, lawv yog tshwm sim los ntawm kev hloov pauv tshiab, random hauv cov noob, thiab tuaj yeem tshwm sim txawm tias tsis muaj leej twg hauv tsev neeg tau muaj tus kab mob ua ntej.

Cov ua rau mob Lipodystrophy

Kev mob lipodystrophy uas tau txais tuaj yeem tshwm sim los ntawm cov tshuaj, cov tshuaj tiv thaiv kab mob autoimmune , lossis cov ua rau idiopathic . Txawm hais tias tsis muaj lub hauv paus caj ces ncaj qha rau kev mob lipodystrophy uas tau txais, qee cov kws tshawb fawb ntseeg tias qee tus neeg yuav muaj kev mob caj ces uas yuav tsim kev mob lipodystrophy uas tau txais.

  • Cov Ua Rau Mob Pob Tawb (AGL): AGL tuaj yeem tshwm sim tom qab muaj kev kis kab mob lossis tom qab muaj kab mob ntawm lub cev tiv thaiv kab mob. Cov kab mob uas tau txuas nrog AGL suav nrog:
  • Kab mob qaib ntxhw (Chickenpox / varicella)
  • Kab mob qhua pias
  • Kab mob hnoos qhuav (pertussis)
  • Kab mob diphtheria
  • Mob ntsws o
  • Kab mob pob txha
  • Kab mob Mononucleosis (Mononucleosis / mono)

Nws tsis paub tseeb tias koj yuav muaj AGL tsuas yog vim koj muaj cov kab mob no.

Cov mob autoimmune cuam tshuam nrog AGL suav nrog:

  • Kab mob thyroid autoimmune
  • Kab mob siab autoimmune
  • Cov kab mob dermatomyositis rau cov menyuam yaus
  • Mob pob qij txha caj qaum
  • Kab mob Sjogren
  • Kab mob autoimmune hemolytic anemia

Yog koj muaj cov kab mob tiv thaiv kab mob no, nws tsis tuaj yeem hais tias koj yuav muaj AGL.

Feem ntau, qhov ua rau AGL tsis tuaj yeem txheeb xyuas tau (idiopathic).

  • Ua rau muaj qhov mob Acquired Partial Lipodystrophy (APL): Cov kws tshawb fawb ntseeg tias APL yog tshwm sim los ntawm peb lub cev tiv thaiv kab mob ua yuam kev rhuav tshem cov hlwb rog. Ntau tshaj 80% ntawm cov neeg uas muaj APL muaj Complement 3 hauv lawv cov ntshav.Muaj ib qho protein hu ua complement factor uas tsis tshua muaj. Cov protein no feem ntau koom nrog peb lub cev tiv thaiv kab mob. Cov neeg uas muaj APL feem ntau muaj ib qho autoantibody hu ua complement 3-nephritic factor hauv lawv cov ntshav. Ib qho autoantibody yog ib qho protein hauv lub cev tiv thaiv kab mob uas ua yuam kev tawm tsam thiab ua puas rau cov nqaij noj qab haus huv.
  • Cov ua rau muaj kev kho mob antiretroviral therapy (HAART)-induced lipodystrophy (LD-HIV): Cov kws tshawb fawb tseem tsis tau paub meej tias vim li cas HAART, uas muaj cov tshuaj tiv thaiv HIV-1 protease, ua rau muaj lipodystrophy.

Qhov xov xwm zoo yog tias feem ntau cov neeg uas pib kho tus kab mob HIV tam sim no tsis tas yuav txhawj ntau txog lipodystrophy, vim tias cov tshuaj HIV tshiab ua rau qhov mob no tsis tshua muaj tshwm sim.

Yuav ua li cas koj thiaj paub tias koj muaj lipodystrophy?

Yog tias koj muaj cov tsos mob ntawm lipodystrophy, koj tus kws kho mob yuav ua qhov kev kuaj mob lub cev, nug txog koj keeb kwm kev kho mob thiab keeb kwm kev kho mob hauv tsev neeg, thiab tom qab ntawd xaj qee qhov kev kuaj mob kom paub meej tias muaj mob thiab saib seb puas muaj lwm yam ua rau koj cov tsos mob.

Cov kev kuaj twg siv los kuaj mob lipodystrophy?

Koj tus kws kho mob yuav xaj ntau qhov kev kuaj mob kom paub tseeb tias koj cov lipodystrophy zoo li cas thiab/lossis seb puas muaj lwm yam ua rau koj cov tsos mob. Cov no suav nrog:

  • Kev Ntsuas MRI Tag Nrho Lub Cev (Magnetic Resonance Imaging): Kev ntsuas MRI siv lub hlau nplaum loj, cov nthwv dej xov tooj cua, thiab lub khoos phis tawj los ua cov duab ntxaws ntxaws ntawm cov kabmob thiab lwm yam qauv hauv koj lub cev. Koj tus kws kho mob yuav hais kom ua qhov kev kuaj no los ntsuas qhov sib xyaw thiab kev faib tawm ntawm cov rog hauv koj lub cev.
  • Kev Ntsuam Xyuas Txog Kev Hloov Pauv Txhua Yam: Qhov no yog kev kuaj ntshav uas ntsuas 14 yam khoom sib txawv hauv koj cov ntshav. Nws muab cov ntaub ntawv tseem ceeb txog kev sib npaug ntawm cov tshuaj lom neeg thiab kev hloov pauv ntawm koj lub cev. Tus kws kho mob yuav saib xyuas koj cov piam thaj hauv cov ntshav (glucose) thiab cov enzymes hauv siab .
  • Panel Lipid: Qhov no kuj yog kev kuaj ntshav. Nws ntsuas qhov ntau ntawm cov rog hu ua lipids hauv koj cov ntshav. Kev kuaj no feem ntau suav nrog plaub qhov kev ntsuas roj cholesterol thiab kev ntsuas triglyceride. Lipodystrophy feem ntau ua rau cov roj cholesterol tsis zoo.
  • Kev Ntsuas Leptin: Qhov no ntsuas qib ntawm leptin hauv koj cov ntshav. Yog tias koj muaj lipodystrophy thiab koj cov qib leptin qis dua li qub, qhov no tuaj yeem muab qee lub tswv yim rau koj txog li cas koj lub cev yuav teb rau kev kho mob hloov leptin.
  • Kev Kuaj Mob Genetic: Yog tias koj tus kws kho mob xav tias koj muaj hom Lipodystrophy uas tau txais los ntawm noob caj noob ces, lawv yuav pom zoo kom kuaj mob genetic los xyuas kom meej qhov kev kuaj mob.
  • Kev kuaj mob raum:Qhov no suav nrog kev phais tshem tawm ib qho qauv ntawm cov nqaij ntawm lub raum thiab kuaj nws hauv qab lub tshuab microscope. Koj tus kws kho mob yuav hais kom kuaj qhov no kom pom tias koj lub raum puas tau raug cuam tshuam los ntawm lipodystrophy.

Cov kev kho mob rau lipodystrophy yog dab tsi?

Kev kho mob thiab kev tswj hwm ntawm lipodystrophy nyob ntawm hom tshwj xeeb uas koj muaj, thiab seb koj puas muaj lwm yam mob cuam tshuam, xws li ntshav qab zib lossis cov roj cholesterol tsis zoo.

Cov kev kho mob uas siv ntau tshaj plaws rau lipodystrophy yog:

  • Tshuaj hloov Leptin: Koj tus kws kho mob yuav sau ntawv kom siv cov tshuaj hormones leptin hu ua metreleptin . Cov neeg uas muaj lipodystrophy feem ntau muaj qhov tsis txaus ntawm leptin. Cov tshuaj hormones no pab tswj lub cev cov metabolism thiab tseem tuaj yeem txo cov roj cholesterol thiab triglyceride ntau.
  • Kev Kho Mob Ntshav Qab Zib thiab Kev Tsis Haum Insulin: Yog tias koj muaj kev tsis haum insulin thiab/lossis ntshav qab zib vim yog lipodystrophy, koj tus kws kho mob yuav sau ntawv kom noj tshuaj xws li pioglitazone, metformin, sulfonylureas , lossis thiazolidinediones los kho nws. Qee tus neeg uas muaj lipodystrophy kuj tseem yuav tsum tau noj insulin los kho lawv tus kab mob ntshav qab zib. Koj kuj tseem yuav tsum tau kuaj xyuas koj cov ntshav qab zib tsis tu ncua hauv tsev nrog lub glucometer .
  • Tswj cov roj triglyceride thiab cov roj cholesterol: Cov tshuaj noj uas tau hais ua ntej uas pab kho mob ntshav qab zib feem ntau tuaj yeem pab tswj cov roj cholesterol. Koj tus kws kho mob kuj tseem yuav sau ntawv kom noj cov tshuaj statins , xws li rosuvastatin thiab pravastatin . Cov neeg uas muaj cov roj triglyceride ntau yuav tsum tau noj cov tshuaj ntxiv ntawm cov roj fibric acid lossis n-3 polyunsaturated fatty acids , xws li cov uas pom muaj nyob rau hauv roj ntses.
  • Kev phais kom zoo nkauj thiab cov txheej txheem: Cov neeg uas muaj lipodystrophy nyob rau hauv cov cheeb tsam uas rhiab heev rau kev zoo nkauj, xws li lub ntsej muag, hauv siab, thiab qhov chaw mos, yuav raug phais kom zoo nkauj kom zoo dua qub thiab muaj kev ntseeg siab rau lawv tus kheej. Cov kws phais yas yuav ua kev hloov pauv cov nqaij adipose, kev tsim kho lub ntsej muag siv cov flaps dawb, thiab silicone lossis lwm yam kev cog rau hauv. Lawv kuj tseem siv tau liposuction lossis kev phais tshem tawm cov txheej txheem kom tshem tawm cov rog tsis xav tau hauv cov cheeb tsam xws li lub puab tsaig lossis nraub qaum ntawm lub caj dab (feem ntau hu ua "buffalo hump" ).

Cov kws tshawb fawb tseem muaj ntau yam yuav tsum kawm txog kev kho thiab tswj cov teeb meem lipodystrophy. Thaum lawv tshawb pom ntau ntxiv txog qhov nyuaj ntawm cov txheej txheem metabolic, ntau txoj kev kho mob yuav muaj.

Puas tuaj yeem tiv thaiv lipodystrophy?

Feem ntau, lipodystrophy tsis tuaj yeem tiv thaiv tau.

Cov qauv caj ces ntawm lipodystrophy tsis tuaj yeem tiv thaiv tau, vim tias lawv yog qhov tshwm sim ntawm kev hloov pauv caj ces. Yog tias koj tab tom npaj yuav muaj menyuam, nkag siab txog qhov kev pheej hmoo ntawm kev muaj menyuam uas muaj mob caj ces thiab tham nrog koj tus kws kho mob txog kev kuaj caj ces.

Feem ntau cov kab mob lipodystrophy uas tau txais los ntawm kev kis kab mob lossis cov kab mob ntawm lub cev tiv thaiv kab mob. Txawm hais tias qee cov kab mob, xws li mob qaib ntxhw thiab hnoos qhuav, tuaj yeem tiv thaiv tau los ntawm kev txhaj tshuaj tiv thaiv kab mob, lwm cov kab mob thiab cov kab mob ntawm lub cev tiv thaiv kab mob uas cuam tshuam nrog cov kab mob lipodystrophy uas tau txais los ntawm kev kis kab mob tsis tuaj yeem tiv thaiv tau.

Yuav ua li cas thiaj paub tias lipodystrophy yog dab tsi?

Qhov kev cia siab rau lipodystrophy feem ntau nyob ntawm seb koj muaj hom lipodystrophy twg, thiab seb koj puas muaj lwm yam mob lossis teeb meem cuam tshuam, xws li ntshav qab zib, teeb meem siab lossis raum.

Kev kho kom zoo nkauj ntawm cov cheeb tsam uas muaj roj tsawg thiab cov cheeb tsam uas muaj roj ntau dhau pab txhim kho lub neej zoo rau cov neeg uas muaj lipodystrophy.

Yog tias koj lossis koj tus menyuam raug kuaj pom tias muaj lipodystrophy, nrog koj tus kws kho mob tham txog yam yuav tshwm sim thiab yuav ua li cas thiaj tswj tau qhov mob zoo tshaj plaws.

Thaum twg koj yuav tsum mus ntsib kws kho mob txog lipodystrophy?

Yog koj pom tias koj lossis koj tus menyuam cov rog hauv lub cev pheej poob qis hauv qee qhov chaw, lossis cov rog nce ntxiv hauv qee qhov chaw, nrog koj tus kws kho mob tham.

Yog tias koj lossis koj tus menyuam raug kuaj pom tias muaj Lipodystrophy, koj yuav tsum ntsib nrog koj pab neeg kho mob tsis tu ncua kom paub tseeb tias koj txoj kev kho mob ua haujlwm zoo rau koj.

Thaum kawg, tej yam uas yuav tsum nco ntsoov

Lipodystrophy yog ib qho mob uas tsis tshua muaj tab sis loj heev. Txawm hais tias tsis muaj kev kho mob los xij, qee qhov kev kho mob tuaj yeem pab tswj nws cov tsos mob thiab cov mob cuam tshuam, xws li ntshav qab zib thiab cov roj cholesterol tsis zoo.

Kev kho mob txawv ntawm ib tus neeg mus rau ib tus neeg. Yog li ntawd, koj pab neeg kho mob yuav ua haujlwm nrog koj los tsim ib txoj kev npaj uas zoo tshaj plaws rau koj. Tsis txhob ntshai nug koj tus kws kho mob cov lus nug. Lawv nyob ntawd los pab koj. Cov kev paub no yuav pab koj ua neej noj qab nyob zoo!


lipodystrophy , cov nqaij adipose, leptin, genetic, acquired, ntshav qab zib, cholesterol, triglyceride, HIV, cov kab mob metabolic

Frequently Asked Questions (FAQ)

Cov kev kuaj twg siv los kuaj mob lipodystrophy?

Koj tus kws kho mob yuav xaj ntau qhov kev kuaj mob kom paub tseeb tias koj cov lipodystrophy zoo li cas thiab/lossis seb puas muaj lwm yam ua rau koj cov tsos mob. Cov no suav nrog:

⚠️ Important: The medical articles and information on Nirogi Lanka are for general awareness only, and are by no means a substitute for professional medical advice, diagnosis, or treatment. For any medical problem you have, consult a qualified physician immediately.

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