Puas muaj teeb meem nrog koj lub plawv lub zog hluav taws xob? Cia peb tham txog Long QT Syndrome (LQTS).

Koj puas tau hnov ​​txog lub tshuab hluav taws xob ntawm lub plawv? Peb lub plawv ua haujlwm zoo li lub tshuab me me. Nws muaj lub tshuab hluav taws xob, uas tswj lub plawv dhia. Qee zaum, kev hloov pauv me me tuaj yeem tshwm sim hauv lub tshuab hluav taws xob no. Ib qho kev hloov pauv zoo li no hu ua Long QT Syndrome, lossis '(Long QT Syndrome - LQTS)'. Tsis txhob txhawj, cia peb tham txog qhov no yooj yim.

Dab tsi yog Long QT Syndrome? Hais yooj yim xwb...

Xav txog tias tom qab koj lub plawv dhia ib zaug lawm, nws yuav siv sijhawm "so" me ntsis ua ntej nws rov dhia dua, zoo li lub roj teeb rov them dua. Lub sijhawm uas nws siv los "so" lossis rov them dua ntev dua li qub me ntsis, uas yog qhov peb hu ua tus mob QT ntev.

Yog tias koj tau muaj ECG, uas yog kev kuaj uas saib cov haujlwm hluav taws xob ntawm lub plawv, muaj ib feem ntawm nws hu ua QT interval. Qhov no qhia tau tias nws siv sijhawm ntev npaum li cas rau cov chav qis ntawm koj lub plawv, hu ua ventricles, kom cog lus thiab tom qab ntawd so, lossis "recharge" raws li kuv tau hais.

Peb lub plawv ua haujlwm hluav taws xob yog los ntawm cov khoom me me uas hu ua 'ions'. Cov ions xws li sodium, calcium, potassium, thiab chloride pab txhawb rau qhov no. Cov ions no txav mus rau hauv thiab tawm ntawm cov hlwb plawv los ntawm txoj kev tshwj xeeb hu ua 'ion channels'. Tam sim no, hauv qhov '(Long QT Syndrome)' no, yog muaj teeb meem nrog cov ion channels no, lossis tsis muaj lawv. Tom qab ntawd lub plawv raug ncua sijhawm "recharging". Thaum lub sijhawm QT ntev dua, muaj kev pheej hmoo ntawm kev mob plawv dhia ceev ceev hu ua 'Torsades de Pointes', uas tuaj yeem ua rau tuag taus.

Puas muaj hom mob Long QT Syndrome?

Yog, muaj ob hom tseem ceeb. Ib hom yog los ntawm noob caj ces , uas txhais tau tias nws tau kis mus los ntawm cov noob caj ces. Lwm hom yog tau los ntawm noob caj ces, uas txhais tau tias nws yog los ntawm lwm yam, xws li qee yam tshuaj.

Cov hom kab mob yug los:

Cov no feem ntau yog tshwm sim los ntawm cov teeb meem caj ces hauv 'ion channels' uas kuv tau hais.

• Kev tsis zoo ntawm cov ion channel: Qhov no yog hom uas feem ntau tshwm sim. Muaj ntau hom xws li 'LQT1, LQT2, LQT3, LQT4, LQT5'. Cov no raug cais raws li hom ion channel uas koom nrog. Qhov kev pheej hmoo ntawm kab mob plawv yav tom ntej yuav txawv nyob ntawm hom.
• Kab Mob Jervell thiab Lange-Nielsen: Hauv qhov mob no, ob leeg niam txiv tuaj yeem nqa cov noob caj noob ces tsis zoo, tab sis lawv yuav tsis muaj tsos mob. Qhov no yog ib qho mob tsis tshua muaj. Vim tias nws tsis zoo li ob leeg niam txiv yuav nqa cov noob caj noob ces, txhua tus menyuam muaj 25% feem pua ​​​​​​ntawm kev txais nws. Cov neeg uas muaj tus kab mob no yuav yug los lag ntseg.
• Romano-Ward Syndrome:Hauv qhov no, ib tug niam txiv feem ntau muaj "Long QT Syndrome" thiab lwm tus tsis muaj. Txhua tus menyuam muaj 50% feem pua ​​​​​​ntawm kev tau txais cov noob caj noob ces tsis zoo no. Hauv qhov no, kev hnov ​​​​​​lus zoo li qub.
• Timothy Syndrome: Qhov no kuj yog ib hom mob tsis tshua muaj. Nws tsis yog tsuas yog cuam tshuam rau lub plawv xwb, tab sis kuj cuam tshuam rau lwm qhov ntawm lub cev.

Tus mob no feem ntau tshwm sim li cas?

Kab mob Long QT Syndrome yog ib yam mob uas tsis tshua muaj . Piv txwv li, hauv Tebchaws Meskas, kwv yees li ntawm ib tus neeg ntawm 2,000 tus neeg muaj tus mob no.

Cov tsos mob ntawm Long QT Syndrome yog dab tsi?

Nov yog cov tsos mob uas feem ntau pom:

• Syncope: Tsis nco qab kiag li.
• Kev qaug dab peg: Qee tus neeg yuav muaj kev qaug dab peg.
• Kev nres plawv: Qhov no txaus ntshai heev.
• Kev tuag tam sim ntawd:

Cov tsos mob no tshwm sim thaum muaj teeb meem plawv dhia tsis zoo hu ua 'Torsades de Pointes' uas kuv tau hais ua ntej. Lub sijhawm no, lub plawv tsis tuaj yeem tso ntshav tau zoo. Yog tias lub hlwb tsis tau txais ntshav txaus, tej yam xws li tsaus muag thiab qaug dab peg yuav tshwm sim. Yog tias qhov teeb meem no txuas ntxiv mus, kev tuag tam sim ntawd yuav tshwm sim. Txawm li cas los xij, yog tias lub plawv dhia rov qab mus rau qhov qub, cov tsos mob yuav tsum nres.

Cov tsos mob feem ntau yuav tshwm sim thaum:

• Thaum lub sijhawm ua si (lossis ob peb feeb tom qab ua si).
• Thaum lub sijhawm muaj kev txhawb zog ntawm lub siab , tshwj xeeb tshaj yog thaum ntshai lossis poob siab tam sim ntawd.
• Thaum pw tsaug zog los yog thaum sawv ntxov .

Qhov tseem ceeb, txog li 50% ntawm cov neeg uas muaj tus kab mob Long QT Syndrome yuav tsis muaj tsos mob li . Thiab, rau li ib ntawm kaum tus neeg, lub plawv nres yog thawj qhov cim ntawm tus mob. Qhov no tuaj yeem ua rau tuag taus yog tias tsis kho sai.

Feem ntau cov tsos mob pib thaum koj laus zuj zus . Yog tias koj muaj cov tsos mob, lawv yuav rov tshwm sim dua. Cov tsos mob feem ntau yuav tshwm sim ua ntej hnub nyoog 30 xyoo. Txawm li cas los xij, qee tus neeg yuav muaj cov tsos mob thaum lawv muaj hnub nyoog 50 xyoo thiab dhau ntawd.

Dab tsi ua rau muaj tus mob Long QT Syndrome?

Raws li kuv tau hais ua ntej, qhov no tuaj yeem tau txais los ntawm koj niam koj txiv (yug los) lossis tau txais los ntawm qee yam tshuaj . Hauv Long QT Syndrome, muaj qhov tsis zoo hauv cov lej noob caj noob ces rau koj cov ion channels. Cov ion channels tsis zoo no ua rau qeeb hauv theem rov zoo ntawm koj lub plawv dhia. Qhov no tuaj yeem ua rau lub plawv dhia tsis xwm yeem uas ua rau tuag taus.

Qee cov tshuaj tuaj yeem ua rau muaj "Long QT Syndrome" rau cov neeg uas muaj qee yam kev xav tau rau lawv cov ion channels. Lawv yuav tsis paub txog qhov ntawd, tab sis nws yog thaum lawv noj cov tshuaj ntawd uas "Long QT" tshwm sim.

Cov tshuaj uas ua rau muaj tus mob QT ntev:

• Qee cov tshuaj 'Antiarrhythmics' (tshuaj rau kev mob plawv dhia tsis xwm yeem)
• Qee cov tshuaj antidepressants
• Qee cov tshuaj diuretics (cov tshuaj uas ua rau koj tso zis ntau dua)
• Qee cov tshuaj tua kab mob
• Cov tshuaj serotonin receptor inhibitors los yog antagonists
• Cov tshuaj tiv thaiv kab mob histamine receptor

Lwm yam ua rau muaj tus mob QT ntev:

• Qee hom tshuaj lom
• Mob hlwb uas muaj feem cuam tshuam nrog kev tsis noj zaub mov (anorexia nervosa)
• Qee qhov 'bradyarrhythmias' (lub plawv dhia qeeb tsis zoo)
• Cov calcium, magnesium, lossis potassium tsawg hauv lub cev
• Kev raug mob rau koj lub paj hlwb

Leej twg muaj feem yuav mob no ntau dua?

Cov neeg hauv qab no muaj feem yuav mob "Long QT Syndrome" ntau dua:

• Rau cov menyuam yaus uas lag ntseg txij thaum yug los.
• Cov menyuam yaus thiab cov hluas uas muaj keeb kwm tsev neeg ntawm kev tuag tam sim ntawd lossis tsaus muag yam tsis paub meej (syncope).
• Rau cov txheeb ze ntshav uas muaj "Long QT Syndrome"
• Rau cov neeg uas muaj 'Cardiomyopathy' (kab mob plawv) lossis kab mob plawv txij thaum yug los.
• Rau cov neeg uas muaj cov electrolytes qis hauv lub cev vim yog lwm yam mob.
• Rau cov neeg noj tshuaj uas cuam tshuam rau cov ion channels hauv lub plawv.

Kuv puas yuav tsum tau kuaj mob Long QT Syndrome thiab?

Kab mob Long QT Syndrome yog ib yam mob uas muaj los ntawm noob caj noob ces uas tuaj yeem kis tau los ntawm ib tiam mus rau ib tiam. Yog tias ib tug ntawm koj cov txheeb ze (niam txiv, cov kwv tij neej tsa, cov menyuam) muaj kab mob Long QT Syndrome, nws yog ib lub tswv yim zoo rau koj mus kuaj noob caj noob ces .

Txhua tus txheeb ze thawj zaug (cov kwv tij, niam txiv, thiab cov menyuam) yuav tsum muaj ECG. Nws tseem ceeb rau txhua tus neeg uas muaj keeb kwm hauv tsev neeg ntawm qaug dab peg lossis tsaus muag kom ua qhov kev kuaj no.

Kauj ruam thawj zaug yog qhia rau koj tus kws kho mob paub tias koj tsev neeg muaj tus mob no. Nws yuav ua qhov kev kuaj mob tsim nyog los kuaj xyuas koj lub plawv. Yog tias cov kev kuaj mob ntawd lees paub tias koj muaj tus mob no, koj yuav tsum mus ntsib kws kho mob plawv uas paub zoo txog Long QT Syndrome.

Cov teeb meem ntawm Long QT Syndrome yog dab tsi?

"Long QT Syndrome" ua rau muaj mob arrhythmia "Torsades de Pointes" uas ua rau tuag taus. Qhov no tuaj yeem ua rau tuag tam sim ntawd.

Yuav kuaj mob li cas rau tus mob Long QT Syndrome?

Cov kws kho mob tuaj yeem kuaj mob Long QT Syndrome nrog kev kuaj ECG yooj yim. Txhawm rau kuaj mob, lawv ntsuas QT interval ntawm ECG. Yog tias koj lub QT interval ntev dua 450 milliseconds, koj yuav muaj Long QT Syndrome.

Koj tus kws kho mob yuav nug koj txog cov no:

• Puas muaj keeb kwm tsev neeg ntawm "Long QT Syndrome"?
• Puas muaj keeb kwm hauv tsev neeg uas muaj kev tsaus muag, qaug dab peg, lossis lub plawv nres yam tsis paub meej?
• Koj puas tau muaj teeb meem tsaus muag, qaug dab peg, lossis lub plawv nres, tshwj xeeb tshaj yog thaum lub sijhawm ua si?

Cov kev kuaj twg siv los kuaj mob Long QT Syndrome?

Ntxiv rau ECG, cov kev ntsuam xyuas no kuj tseem yuav ua tau:

• Kev kuaj ntshav.
• Kev kuaj noob caj noob ces.
• Kev sim siab ntawm kev tawm dag zog.
• Kev saib xyuas kev mob plawv: Qhov no saib xyuas koj lub plawv ua haujlwm tau ob peb hnub.

Yuav kho tus mob Long QT Syndrome li cas?

Muaj cov tshuaj, cov khoom siv, lossis kev phais mob uas tuaj yeem pab tswj cov tsos mob thiab tiv thaiv kev tuag tam sim ntawd rau Long QT Syndrome. Txawm hais tias cov kev kho mob no tsis tuaj yeem kho tau tag nrho tus mob, lawv tuaj yeem tiv thaiv koj ntawm lub plawv dhia tsis zoo.

Cov tshuaj

Muaj coob tus neeg uas muaj tus mob Long QT Syndrome (txawm tias cov uas tsis muaj tsos mob) noj tshuaj beta-blocker, xws li nadolol. Lwm cov tshuaj tuaj yeem ua rau koj lub sijhawm QT luv dua lossis txhim kho koj cov electrolyte. Koj tus kws kho mob yuav qhia rau koj tias cov tshuaj twg zoo tshaj plaws rau koj.

Cov khoom siv

Tej tus neeg mob uas muaj "Long QT Syndrome" kuj yuav xav tau cov khoom siv zoo li no:

• Lub Tshuab Ua Pa Hluav Taws Xob Rau Lub Plawv (ICD): Lub tshuab ua pa hluav taws xob rau lub plawv (ICD) uas muab cog rau hauv lub plawv yuav muab cog rau hauv cov neeg uas muaj keeb kwm ntawm lub plawv nres lossis cov neeg uas tseem muaj tsos mob txawm tias tau txais kev kho mob beta-blocker. Lub cuab yeej no nrhiav tau cov teeb meem plawv dhia ceev ceev uas ua rau tuag taus thiab xa lub plawv dhia ceev ceev kom tiv thaiv kev tuag tam sim ntawd.
• Lub tshuab ua pacemaker: Lub cuab yeej no pab cov neeg uas lub plawv dhia qeeb tsis zoo.

Kev phais mob

Tej tus neeg mob uas muaj tus kab mob Long QT Syndrome yuav tsum tau phais Left Cardiac Sympathetic Denervation (LCSD) los yog sympathectomy. Qhov no yog ib txoj kev phais mob uas tsis tas phais ntau thiab yuav tsum tshem tawm cov hlab ntsha hauv koj lub paj hlwb sympathetic.

Cov teeb meem/cov kev mob tshwm sim ntawm kev kho mob yog dab tsi?

Tej yam kev mob tshwm sim lossis teeb meem uas yuav tshwm sim tau nyob ntawm seb koj yuav kho hom kev kho mob twg.

• Beta-blocker:
• Ntshav siab qis.
• Kiv taub hau.
• Mob taub hau .
• Qaug zog.
• ICD (Lub Tshuab Defibrillator Uas Muab Tso Rau Hauv Lub Cev):
• Cov teeb meem ntawm cov khoom siv.
• Lub ntsws tawg.
• Los ntshav.
• Kev kis kab mob.
• Lub tshuab ua pa:
• Lub ntsws tawg.
• Los ntshav.
• Kev kis kab mob.
• Cov teeb meem ntawm cov khoom siv.
• LCSD (Kev Phais Mob Sab laug ntawm Lub Plawv Sympathetic Nerve):
• Horner syndrome.
• Lub ntsws tawg.
• Ntswg liab los yog tawm hws.

Puas tiv thaiv tau tus mob Long QT Syndrome?

Yog koj tau txais los ntawm koj niam koj txiv ces koj yuav tsis tiv thaiv tau. Txawm li cas los xij, rau cov neeg uas tsis tau txais los ntawm koj, koj tuaj yeem tiv thaiv tau cov mob uas ua rau muaj tus kab mob no (long QT syndrome) tom qab. Piv txwv li, ceev faj nrog qee yam tshuaj.

Yog tias kuv muaj tus mob Long QT Syndrome, yuav ua li cas?

Yog tias kho kom zoo , tus nqi tuag rau cov neeg uas muaj "Long QT Syndrome" yog li ntawm 1%. Yog tsis kho, qhov xwm txheej no hnyav heev. Kwv yees li ntawm 21% ntawm cov neeg uas muaj cov tsos mob uas tsis tau txais kev kho mob tuag hauv ib xyoos tom qab pib muaj syncope.

Tiam sis nco ntsoov, cov neeg uas muaj "Long QT Syndrome" tuaj yeem ua neej nyob tau zoo . Lawv tuaj yeem xeeb tub thiab yug tau menyuam.

Kab mob Long QT Syndrome kav ntev npaum li cas?

Kab mob QT ntev uas tau txais los ntawm noob caj ces yog ib yam mob uas yuav kho tau mus ib txhis. Txawm li cas los xij, cov tsos mob thiab kev pheej hmoo ntawm cov teeb meem yuav txo qis zuj zus.

Kuv yuav saib xyuas kuv tus kheej li cas?

Kab mob Long QT Syndrome muaj peev xwm cuam tshuam rau ntau yam hauv koj lub neej txhua hnub. Koj yuav tsum sab laj nrog koj tus kws kho mob ua ntej ua qee yam.

Suab nrov thiab kev ntxhov siab

Ib txhia neeg uas muaj tus mob Long QT Syndrome yuav raug cuam tshuam los ntawm cov suab nrov nrov lossis kev ntxhov siab ntawm lub siab. Txawm hais tias koj tswj tsis tau tag nrho cov suab nrov thiab kev ntxhov siab nyob ib puag ncig koj, koj tuaj yeem sim txwv lawv.

• Qhia rau koj cov phooj ywg thiab tsev neeg tias nws tsis muaj kev nyab xeeb rau kev sawv koj tam sim ntawd.
• Siv lub tswb ceeb toom uas muaj suab zoo nkauj es tsis txhob siv lub tswb nrov uas nrov ib zaug xwb.
• Txo qhov nrov ntawm cov khoom nrov uas yuav ua rau koj ntshai.

Kev tawm dag zog

Qee hom mob Long QT Syndrome yuav ua rau muaj teeb meem nrog kev tawm dag zog. Koj tus kws kho mob yuav qhia koj tias yam kev ua ub no twg tsim nyog rau koj, nyob ntawm seb koj muaj hom noob caj ces tsis zoo li cas. Vim tias kev tawm dag zog tuaj yeem ua rau mob plawv dhia tsis xwm yeem, koj yuav tsum nrog koj tus kws kho mob tham ua ntej koj txiav txim siab ua si kis las sib tw. Yog tias koj txiav txim siab ua si kis las, koj yuav tsum tau ua qee yam kev ceev faj txog kev nyab xeeb.

Kev ua luam dej tuaj yeem ua rau muaj kev phom sij rau qee tus neeg uas muaj "Long QT Syndrome". Yog tias koj tsaus muag thaum ua luam dej, koj tuaj yeem poob dej.

Cov tshuaj kho mob

Muaj ntau yam tshuaj uas ua rau lub sijhawm QT ntev dua. Cov tshuaj no yuav cuam tshuam rau cov neeg uas muaj "Long QT Syndrome" ntau dua li cov uas tsis muaj. Yog tias koj muaj "Long QT Syndrome", koj yuav tsum ua cov hauv qab no:

• Qhia rau koj cov kws kho mob tag nrho tias koj muaj "Long QT Syndrome".
• Tham nrog koj tus kws kho mob ua ntej noj cov tshuaj uas tau muab rau lwm yam mob.
• Tsis txhob noj cov tshuaj uas yuav tsis tas yuav muaj ntawv yuav tshuaj (OTC) (tshwj tsis yog cov tshuaj aspirin lossis paracetamol) yam tsis tau nrog koj tus kws kho mob tham.

Yog tias koj muaj "Long QT Syndrome", cov tshuaj no yuav cuam tshuam rau koj:

• Cov tshuaj Antihistamines (tshuaj rau kev ua xua)
• Cov tshuaj Antidepressants (tshuaj rau kev nyuaj siab)
• Tshuaj rau cov teeb meem kev noj qab haus huv ntawm lub hlwb
• Cov tshuaj rau kab mob plawv
• Cov tshuaj tua kab mob
• Cov tshuaj tua kab mob fungal
• Cov tshuaj tua kab mob
• Cov tshuaj rau cov kab mob plab hnyuv
• Cov tshuaj tiv thaiv kev qaug dab peg
• Cov tshuaj diuretics (cov tshuaj uas ua rau kom tso zis ntau ntxiv)
• Cov tshuaj kho mob ntshav siab
• Cov tshuaj rau mob migraines
• Cov tshuaj txo cov roj cholesterol

Kuv yuav tsum mus ntsib kuv tus kws kho mob thaum twg?

Koj yuav tsum mus ntsib kws kho mob thaum koj pib muaj cov tsos mob thiab tsawg kawg ib xyoos ib zaug tom qab ntawd. Kev mus ntsib kws kho mob hluav taws xob yog qhov kev xaiv zoo tshaj plaws.

Yog koj tus menyuam muaj "Long QT Syndrome", koj yuav tsum mus ntsib koj tus kws kho mob ntau tshaj ib xyoos ib zaug kom paub tseeb tias lawv tau txais cov tshuaj kom raug rau lawv qhov hnyav tam sim no.

Yog koj muaj ib lub cuab yeej uas cog rau hauv koj lub cev lawm, koj yuav tsum mus ntsib koj tus kws kho mob ib xyoos ib zaug kom paub tseeb tias nws ua haujlwm tau zoo.

Kuv yuav tsum mus rau Chav Kho Mob Thaum Muaj Xwm Ceev (ETU) thaum twg?

Ib tug neeg uas lub plawv nres xav tau kev kho mob tam sim ntawd . Ib tug neeg nyob ze yuav tsum pib CPR (cardiac resuscitation) thiab hu rau 911 (lossis koj tus xov tooj xwm txheej ceev hauv zos).

Kuv yuav tsum nug kuv tus kws kho mob li cas?

Qee cov lus nug uas koj tuaj yeem nug koj tus kws kho mob:

• Kuv muaj hom "Long QT Syndrome" twg?
• Koj xav kom kuv kho qhov kev kho mob twg?
• Kuv yuav tsum tau ntsib koj ntau npaum li cas?
• Kuv yuav tsum tsis txhob noj tshuaj thiab ua ub ua no li cas yog tias kuv muaj hom "Long QT Syndrome"?

Thaum kawg, Ib Zaj Lus Qhia Txog Kev Mus Tsev

Nws yog ib qho ib txwm muaj kev ntxhov siab thaum koj pom tias koj muaj kab mob plawv. Tab sis nug koj tus kws kho mob cov lus nug thiab, yog tias tsim nyog, tham nrog tus kws pab tswv yim tuaj yeem pab koj xis nyob dua. Nws yog ib qho tseem ceeb kom ua raws li koj tus kws kho mob cov lus qhia, noj koj cov tshuaj raws sijhawm, thiab ua raws li koj cov sijhawm teem tseg.

Nws kuj tseem yuav pab tau koj tsev neeg thiab cov phooj ywg paub tias koj muaj tus kab mob Long QT Syndrome. Yog tias koj muaj cov tsos mob thaum lawv nrog koj nyob, lawv tuaj yeem hu rau kev pab thaum muaj xwm txheej ceev. Zoo dua, yog tias lawv paub ua CPR, nws tuaj yeem cawm koj txoj sia. Tsis txhob txhawj, nrog kev tswj hwm zoo, koj kuj tuaj yeem ua neej noj qab haus huv.

` Long QT Syndrome, LQTS, kab mob plawv, QT interval, lub plawv dhia ceev, arrhythmia, cov kab mob caj ces