Koj puas tau pom tias muaj ib txhia neeg muaj cov xim av ntawm lawv daim tawv nqaij, tshwj xeeb tshaj yog ntawm lawv ob txhais ceg, zoo li lub vas? Qee zaum lawv kuj yws txog kev kiv taub hau thiab mob taub hau. Hnub no peb yuav tham txog ib qho mob tsis tshua muaj uas muaj cov tsos mob zoo sib xws, tab sis tsis muaj leej twg tham txog nws ntau. Qhov no hu ua Sneddon Syndrome.
Sneddon Syndrome yog dab tsi? Hais yooj yim xwb...
Hais yooj yim xwb, Sneddon Syndrome yog ib yam kab mob uas cuam tshuam rau cov hlab ntsha me thiab nruab nrab hauv koj lub cev. Xav txog cov hlab ntsha no zoo li cov kav dej uas nqa dej. Hauv cov kab mob no, cov txheej du ntawm cov hlwb hauv koj cov hlab ntsha, uas hu ua endothelium, loj hlob sai dua thiab ntau dua li nws yuav tsum tau. Tom qab ntawd yuav ua li cas? Cov hlwb ntxiv no txo qhov chaw hauv cov hlab ntsha, ib yam li thaum cov av qias neeg daig hauv cov kav dej, nws nyuaj rau dej ntws. Qhov no ua rau cov ntshav ntws tsis zoo.
Qhov no yog ib qho mob uas yuav tsum tau saib xyuas ib pliag, vim tias nws tuaj yeem zuj zus zuj zus mus raws sijhawm. Cov neeg uas muaj tus mob no muaj feem yuav ntshav txhaws ntau dua. Lawv kuj tuaj yeem muaj teeb meem ntawm daim tawv nqaij thiab teeb meem ntawm lub paj hlwb. Qee zaum nws hu ua Sneddon-Champion syndrome. Lwm lub npe yog livedo reticularis racemosa. Tus mob no tuaj yeem ua rau mob stroke thiab transient ischemic attacks (TIAs) rau qee tus neeg.
Tus mob no muaj ntau npaum li cas? Leej twg feem ntau muaj tus mob no?
Qhov tseeb, Sneddon Syndrome yog ib yam kab mob tsis tshua muaj. Raws li kev suav lej, tsuas muaj plaub tus neeg hauv ib lab tus neeg xwb uas muaj tus kab mob no txhua xyoo. Qhov ntawd yog li ib ntawm ob puas thiab ib nrab txhiab tus neeg.
Tsis tas li ntawd xwb, tus mob no feem ntau tshwm sim rau cov poj niam ntau dua li cov txiv neej. Kwv yees li 80% ntawm cov neeg uas muaj tus mob Sneddon syndrome yog poj niam. Feem ntau lawv raug kuaj pom tias muaj tus mob no thaum muaj hnub nyoog li ntawm 40 xyoo.
Cov tsos mob ntawm qhov no yog dab tsi? Koj paub nws li cas?
Ib tug neeg uas muaj tus kab mob Sneddon Syndrome yuav muaj ntau yam tsos mob. Txawm li cas los xij, tsis yog tag nrho cov tsos mob no tshwm sim ib zaug. Qee cov tsos mob yuav tshwm sim ntau xyoo tom qab pib muaj teeb meem ntawm lub paj hlwb. Los yog qee tus neeg yuav muaj teeb meem qhov muag lossis mob taub hau thawj zaug. Nov yog qee cov tsos mob:
- Ib tug qauv zoo li ib daim ntaub mesh ntawm daim tawv nqaij:Qhov no yog thawj cov tsos mob uas ntau tus neeg pom. Daim tawv nqaij tsim cov xim liab-ntshav, zoo ib yam li cov ntses lossis cov qauv ntawm qee cov nab. Qhov no tsis mob. Yog tias cov xim no tshwm sim ntawm koj txhais tes thiab ceg, tshwm sim thaum txias, thiab ploj mus thaum koj sov so, nws hu ua livedo reticularis. Txawm li cas los xij, yog tias cov qauv no tshwm sim ntawm koj lub hauv siab, plab, lossis pob tw, thiab tsis ploj mus txawm tias thaum koj sov so, nws hu ua livedo racemosa.
- Mob taub hau: Tej zaum yuav mob taub hau ntau zaus, qee zaum mob hnyav.
- Kiv taub hau: Ib qho kev xav tias tig ib ncig.
- Mob stroke thiab TIAs: Raws li tau hais ua ntej, cov no yog qee qhov mob hnyav tshaj plaws.
- Kev Hloov Pauv ntawm Tus cwj pwm thiab Kev Xav: Tej zaum yuav muaj kev hloov pauv ntawm koj tus cwj pwm, txoj kev koj xav, thiab koj lub peev xwm los nco qab.
- Teeb meem raum: Qhov no tsis tshua muaj ntau, tab sis qee tus neeg kuj tuaj yeem muaj teeb meem raum.
Qhov tseem ceeb tshaj plaws yog tias yog koj muaj ib lossis ob qho ntawm cov tsos mob no, tshwj xeeb tshaj yog tias koj mob taub hau thiab kiv taub hau nrog rau cov tawv nqaij zoo li daim ntaub mesh, koj yuav tsum mus ntsib kws kho mob kom tau lus qhia.
Vim li cas thiaj muaj tus mob Sneddon Syndrome? Dab tsi yog qhov ua rau muaj tus mob no?
Qhov no yog ib yam dab tsi uas cov kws kho mob tseem tsis tau paub meej. Tseem tsis tau pom qhov ua rau muaj tus kab mob Sneddon Syndrome. Yog vim li ntawd nws thiaj hu ua idiopathic, txhais tau tias tsis paub qhov ua rau muaj tus kab mob no. Txawm li cas los xij, vim tias tus kab mob no tau pom tias muaj nyob rau hauv qee tsev neeg, nws raug xav tias tej zaum yuav muaj ib feem ntawm caj ces .
Tsis tas li ntawd xwb, qee zaum, Sneddon syndrome tuaj yeem tshwm sim ua ke nrog lwm yam mob autoimmune . Ib qho mob autoimmune tsuas yog ib qho mob uas peb lub cev tiv thaiv kab mob tawm tsam peb lub cev cov cell. Yog tias koj muaj Sneddon syndrome, nws yuav cuam tshuam nrog ib qho ntawm cov mob hauv qab no:
- Lupus
- Cov tsos mob ntawm Antiphospholipid
- Kab mob Behçet
- Kab mob sib txuas sib xyaw
Yuav kuaj mob li cas ? Yuav kuaj dab tsi?
Yog koj tus kws kho mob xav tias koj muaj Sneddon Syndrome raws li koj cov tsos mob, lawv yuav xaj ntau yam kev kuaj sib txawv. Cov kev kuaj no yuav nrhiav:
- Koj cov ntshav: Tshawb xyuas seb puas muaj cov cim qhia txog tus kab mob autoimmune thiab cov teeb meem ntshav txhaws.
- Koj lub plawv: Xyuas seb cov ntshav ntws li cas los ntawm koj lub plawv thiab cov hlab ntsha.
- Koj lub hlwb:Xyuas seb puas muaj kev puas tsuaj rau lub hlwb. Tej zaum yuav yog vim muaj mob stroke.
- Koj daim tawv nqaij: Yuav muab ib daim tawv nqaij me me coj mus kuaj (kev kuaj daim tawv nqaij) seb puas muaj kev hloov pauv ntawm cov cell uas yog tus kab mob no.
Cov kev kuaj no yuav suav nrog kev kuaj duab tshwj xeeb . Piv txwv li:
- Kev thaij duab MRI (magnetic resonance imaging - MRI scans)
- Kev luam theej duab CT (computed tomography - CT scans)
- Angiograms (ib daim duab X-ray tshwj xeeb los saib seb cov hlab ntsha zoo li cas)
Cov kws kho mob tsuas yog tuaj yeem paub tseeb tias muaj tus kab mob no tom qab ua tag nrho cov kev kuaj no.
Yuav kho li cas? (Kev Kho Mob) Muaj cov kev xaiv dab tsi?
Txoj kev kho mob Sneddon Syndrome zoo tshaj plaws tseem tsis tau nkag siab tag nrho. Ib qho laj thawj rau qhov no yog vim muaj tsawg tus neeg uas muaj tus mob no ua rau nws nyuaj rau nrhiav neeg txaus los ua cov kev sim tshuaj loj.
Txawm li cas los xij, muaj ntau txoj kev kho mob sib txawv nyob ntawm cov tsos mob ntawm tus kab mob. Piv txwv li, koj tus kws kho mob yuav sau ntawv kom noj tshuaj xws li:
- Cov tshuaj Anticoagulant lossis antiplatelet: Cov no tiv thaiv cov ntshav txhaws thiab pab txhawb kev ntws ntshav.
- Cov tshuaj ua kom cov hlab ntsha loj: Piv txwv li, nifedipine. Cov no ua rau cov hlab ntsha dav dua thiab ua rau cov ntshav ntws ntau dua. Qhov no feem ntau pab txo cov tsos mob ntawm daim tawv nqaij.
- Cov tshuaj Angiotensin-converting enzyme inhibitors (ACE inhibitors): Cov no pab tiv thaiv kev loj hlob tsis zoo ntawm cov hlwb endothelial uas tau hais ua ntej.
Tseem Ceeb: Yog tias koj muaj tus mob Sneddon syndrome, koj yuav tsum tsis txhob haus luam yeeb thiab siv cov tshuaj tiv thaiv kev xeeb tub uas muaj estrogen. Cov no tuaj yeem ua rau tus mob hnyav dua.
Puas muaj ib txoj kev los tiv thaiv tus kab mob no?
Tu siab kawg li, raws li cov ntaub ntawv tam sim no, tsis muaj txoj hauv kev los tiv thaiv Sneddon Syndrome. Vim tias tsis paub qhov ua rau muaj qhov no, nws nyuaj rau hais tias yuav tiv thaiv nws li cas.
Yog tias qhov xwm txheej no tseem muaj ntxiv, yuav muaj li cas? (Kev kwv yees) Peb yuav cia siab li cas rau yav tom ntej?
Feem ntau, Sneddon Syndrome ua rau muaj kev hloov pauv hauv lub paj hlwb. Piv txwv li , kev nco tsis zoo thiab nyuaj hais lus yuav maj mam tshwm sim raws sijhawm. Qee zaum, cov neeg uas muaj Sneddon Syndrome kuj tseem yuav raug kuaj pom tias muaj kev puas hlwb thaum ntxov. Yog vim li ntawd nws thiaj li tseem ceeb kom paub txog cov tsos mob no.
Puas muaj kev kho mob tag nrho?
Raws li cov ntaub ntawv kho mob tam sim no, Sneddon SyndromeTseem tsis tau pom ib txoj kev kho mob tag nrho. Kev kho mob lub hom phiaj yog tswj cov tsos mob thiab sim tiv thaiv kom tus kab mob tsis txhob loj zuj zus.
Thaum twg koj yuav tsum nrhiav kev pab kho mob?
Yog koj muaj cov tsos mob ntawm Sneddon Syndrome, xws li daim tawv nqaij zoo li daim ntaub mesh, mob taub hau, thiab kiv taub hau, mus ntsib kws kho mob tam sim ntawd. Tsis txhob ncua sijhawm, tshwj xeeb tshaj yog tias koj muaj lwm cov tsos mob nrog rau cov tawv nqaij tawv.
Yog tias koj twb tau kuaj pom tias muaj tus kab mob Sneddon syndrome lawm, yog tias koj muaj cov tsos mob tshiab, lossis yog tias koj xav tias koj cov tsos mob hnyav zuj zus, qhia rau koj tus kws kho mob tam sim ntawd.
Thiab, yog tias koj muaj cov tsos mob ntawm tus mob stroke, tsis txhob ncua sijhawm. Hu rau 911 tam sim ntawd (hauv Sri Lanka, 1990 Suwaseriya Ambulance Service) lossis mus rau chav kho mob ceev hauv tsev kho mob ze tshaj plaws. Cov tsos mob ntawm tus mob stroke yuav suav nrog:
- Mob taub hau loj heev tam sim ntawd.
- Teeb meem pom kev (xws li tsis pom kev ib lub qhov muag, ob lub qhov muag tsis meej).
- Mob loog los yog qaug zog ntawm ib sab lossis ob sab ntawm lub cev.
- Nyuaj siab taug kev.
- Nyuaj hais lus lossis nkag siab txog yam uas lwm tus hais.
Thaum kawg, tej yam yuav tsum nco ntsoov (Cov Lus Coj Mus Tsev)
Kab mob Sneddon yog ib yam mob uas tsis tshua muaj thiab tej zaum yuav mob hnyav heev. Txawm li cas los xij, yog tias koj raug kuaj pom tias muaj tus mob no, ua raws li koj tus kws kho mob cov lus qhia kom zoo. Noj koj cov tshuaj raws sijhawm, mus ntsib koj tus kws kho mob raws sijhawm, thiab tsis txhob ncua sijhawm kuaj mob.
Koj tuaj yeem pab koj tus kheej los ntawm kev ua neej nyob zoo rau lub plawv. Qhov ntawd txhais tau tias noj zaub mov kom zoo, tawm dag zog, thiab tsis txhob haus luam yeeb thiab tswj kev xeeb tub uas muaj estrogen. Tej yam no tuaj yeem pab tau koj tswj koj tus mob. Tsis txhob txhawj, koj tuaj yeem nyob nrog tus mob no nrog kev kho mob thiab kev hloov pauv hauv lub neej.
` Sneddon syndrome, kab mob ntawm cov hlab ntsha, cov pob ntawm daim tawv nqaij, mob stroke, neuropathy, livedo reticularis, cov ntshav txhaws











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Tsis muaj lus teb tau muab tso tawm. Ntxiv koj cov lus tawm ntawm no thawj zaug.
Ntxiv koj cov lus