Sɔntɛnde yu kin fil lɛk se yu jɔs gɛt prɔblɛm fɔ blo, lɛk se yu chɛst tayt? Yu kin fil taya ivin afta yu dɔn waka fɔ shɔt tɛm? Bɔku tɛm wi kin fɔgɛt bɔt dɛn tin ya, ɛn tink se na jɔs nɔmal taya. Bɔt tide wi go tɔk bɔt wan siriɔs mɛrɛsin we kin de biɛn dɛn sik ya, pan ɔl we i nɔ kin apin so ɔltɛm. Dat na Pulmonary Alveolar Proteinosis, ɔ PAP fɔ shɔt tɛm.
Fɔ tɔk am simpul wan, wetin na Pulmonary Alveolar Proteinosis (PAP)?
Imajin se wi lɔng dɛn ful-ɔp wit bɔku bɔku smɔl smɔl ɛya sak dɛn. Wi kin kɔl dɛn smɔl smɔl ay sak dɛn ya alveoli . We wi de blo, na tru dɛn ay sak dɛn ya wi kin tek ɔksijɛn.
Naw, insay PAP, wetin kin apin na dat di prɔtin, fat, ɛn ɔda tin dɛn kin gɛda insay dɛn smɔl smɔl ay sak dɛn ya, lɛk dɔti. Di rizin fɔ dis na bikɔs di sɛl dɛn we de klin di tin we tan lɛk ɔyl we dɛn kɔl sɔfaynt, we de na di wɔl dɛn na dɛn ay sak dɛn ya natin nɔ de wok fayn. Dɔn dis sɔfaynt kin gɛda ɛn blok di ay sak dɛn. So, di briz nɔ kin ebul fɔ go insay fayn fayn wan, so di blɔd nɔ kin gɛt di ɔksijɛn we i nid. Dis kin mek i nɔ izi fɔ blo.
Dis na siriɔs lɔng sik. So, we yu yɛri dis nem, yu kin fil fred. Bɔt nɔr wɔri, if yu gi yu di rayt tritmɛnt, yu kin kɔntrol dis sik ɛn in sayn dɛm fayn fayn wan. Di tin we impɔtant pas ɔl na fɔ go to dɔktɔ we de mɛn yu pulmonari ɛn gɛt tritmɛnt.
Men kayn PAP de?
Yɛs, dɛn kin sheb PAP mɔ to tri kayn. Di tin we kin mek ɛni wan pan dɛn kayn tin ya kin apin difrɛn.
| PAP tayp | Simpul ɛksplen |
|---|---|
| Awtoimyun PAP we dɛn kin yuz | Dis na di kayn we we pipul dɛn kin gɛt mɔ. I de afɛkt 90% pan di PAP pasɛnt dɛn. Wetin kin apin ya na dat wi yon imyun sistɛm kin mistek atak di sɛl dɛn we de ɛp fɔ mek di say dɛn we di briz de blo klin. |
| Sɛkɔndari PAP | dis kin kכz fכ כda mεdikal kכndyushכn כ we yu de εkspos to tכxin lεk dכst εn kεmεkal dεm, we de afekt di wok we di sεl dεm na di aywe dεm de du. |
| PAP we dɛn bɔn wit | Dis na wan sik we dɛn bɔn wit, we dɛn kin gɛt frɔm dɛn jɛnɛtiks. I kin pas frɔm mama ɛn papa to pikin dɛn. Sɔntɛnde, di sayn dɛn kin de we dɛn bɔn am, ɛn ɔda tɛm dɛn kin apin leta. |
Udat dɛn kin gɛt dis sik?
Awtoimyun ɛn sɛkɔndari PAP kin afɛkt pipul dɛn we ol bitwin 30 ɛn 60. Dɛn tu kayn ya kin mɔs pan man dɛn . Pipul dɛn we de smok ɛn di wan dɛn we gɛt dɔst ɔ kemikal kin gɛt mɔ prɔblɛm.
PAP we dɛn bɔn kin kam pan pikin dɛn we nɔ rich 10 ia yet, bɔt i kin apin ɛni ej.
Wetin na di sayn dɛm fɔ PAP sik?
Di men ɛn kɔmɔn sayn fɔ dis sik na wae yu nɔr de blo fayn (dyspnea) . Bɔku pipul dɛn kin gɛt shɔt briz we dɛn de du ɛksɛsayz ɔ wok. Bɔt sɔm pipul dɛn kin gɛt dis prɔblɛm ivin we dɛn jɔs tinap.
Apat frɔm dat, yu kin si dɛn sayn ya bak:
- Chɛst de pen
- Kɔf (sɔntɛm wit blɔd ɔ blɔd) .
- di blu kכla na di skin εn di nel dεm (cyanosis) - Dis kin apin we כksijεn nכ de na di bכdi.
- Fɔ taya ɔltɛm
- Fiva
- Infεkshכn dεm na di lכng bכku tεm
- Finga dɛn we gɛt klab
- We yu de lɔs yu wet we yu nɔ gɛt rizin
Aw dɔktɔ kin no bɔt dis sik?
If yu sɔspɛkt se yu gɛt PAP sik, yu dɔktɔ go fɔs chɛk yu ɛn lisin to yu lɔng wit stetɔskɔp. Dɔn dɛn go aks yu kwɛstyɔn dɛn bɔt yu famili mɛdikal istri ɛn aw yu de liv yu layf. If yu de smok, yu de gɛt dɔst ɔ kemikal, yu fɔ rili tɛl yu dɔktɔ .
Dɔn, dɛn kin du sɔm tɛst fɔ no if pɔsin gɛt di sik:
- Blɔd tɛst: Chɛk di ɔksijɛn lɛvɛl na di blɔd. כlso, dεn kin du spεshal tεst dεm lεk GM-CSF כtoantibodi fכ fכn di kכz fכ PAP sik.
- Pulmonary function testing: De mɛzhɔ aw yu lɔng dɛn de wok fayn fayn wan.
- Chɛst ɛkstrem rayt ɔ CT skan: Fɔ si klia wan aw di lɔng dɛn de.
- Brɔnkoskɔpi: .Wan tin we dɛn kin du we dɛn kin put wan tin tiub we gɛt kamɛra we dɛn tay tru di mɔt ɔnda anestezi fɔ chɛk di insay pat pan di aywe ɛn di lɔng dɛn.
- di lכng bayopsi: dεn kin tek sכm sכm tisu frכm di lכng we dεn de du brכnkoskopi כ we dεn de du כpεrayshכn fכ egzamin.
Wetin na di tritmɛnt dɛm fɔ PAP?
Naw, no mɛrɛsin nɔ de fɔ PAP, bɔt tritmɛnt dɛn de we rili fayn we go ɛp yu fɔ kɔntrol yu sik dɛn ɛn liv bɛtɛ layf.
Di men ɛn di tritmɛnt we dɛn kin yuz mɔ fɔ PAP na "Whole-Lung Lavage" (WLL) .
Wetin na dis lɔng lavage?
Wetin kin apin pan dis na dat di dɔktɔ kin yuz brɔnkoskɔp (wan kamɛra tiub) fɔ was di lɔng dɛn wan bay wan wit salin (stɛrilayz sɔl wata) fɔ pul di prɔtin ɛn fat dɛn we dɔn trɔp. Afta dis, i kin izi fɔ blo.
We yu de du dis tritmɛnt:
- Dɛn go anestez yu ɔl, so yu nɔ go fil natin.
- Di dɔktɔ kin put di brɔnkoskɔp insay di mɔt ɛn pɔynt am to wan lɔng.
- Na wan mashin de gi ɔksijɛn to di ɔda lɔng.
- Sɔntɛnde, yu kin wɛr vest we de shek shek rawnd yu chɛst. Dis vaybreshɔn de mek di tin dɛn we dɔn stɔp na yu ay sak dɛn, lɔs.
- Dɔn dɛn kin put di salin sɔlvushɔn insay di lɔng dɛn, ɛn we dɛn pul am, i kin kɔmɔt wit di tin we bin dɔn stɔp.
- Sɔntɛm dɛn kin was di ɔda lɔng bak di sem tɛm, ɔ afta sɔm dez.
Dipen pan aw di sik bad, dɛn kin nid fɔ du dis tritmɛnt ɛvri sɔm mɔnt ɔ wan tɛm insay di ia. Bɔt sɔm pipul dɛn nɔ kin nid dis tritmɛnt. Na di dɔktɔ go disayd dat.
Ɔda tritmɛnt dɛn
- Bronchodilators: Dɛn mɛrɛsin ya kin mek di mɔsul dɛn we de rawnd di say dɛn we di briz de blo rilaks, ɛn dis kin mek i izi fɔ blo.
- GM-CSF riplesmɛnt tɛrapi: Dɛn kin inhal dis tru nɛbulayza ɔ dɛn kin gi am as injɛkshɔn. I de mek di sɛl dɛn we de klin di say dɛn we di briz de blo, wok fayn fayn wan.
- Lɔng transplant: Pipul dɛn we dɛn sik rili bad ɛn we dɛn lɔng dɔn pwɛl kin nid fɔ gɛt wɛlbɔdi lɔng transplant as las tin fɔ du.
- Plasmapheresis ɛn plasma exchange: Dis min se dɛn kin pul di wata pat na di blɔd (plasma) ɛn put plasma frɔm pɔsin we gɛt wɛlbɔdi. insay כtoimyun PAP, dis de εp fכ stכp di imyun sistεm fכ atak hεlty sεl dεm.
- Sɔplɛnt ɔksijɛn: Dɛn kin gi ɔksijɛn tru mask ɔ smɔl tiub we dɛn kin put na di nos fɔ mek i izi fɔ blo.
Wetin a kin du as pɔsin we gɛt PAP?
If yu gɛt PAP, i rili impɔtant fɔ fala di tritmɛnt we yu dɔktɔ gi yu ɛn tek kia ɔf yu layf bak.
- Nɔ smok kpatakpata ɛn avɔyd ples dɛn we ɔda pipul dɛn de smok.
- Gɛt di influenza (flu) ɛn nyumonia vaysin lɛk aw yu dɔktɔ se.
- Stay away frɔm pipul dɛn we sik.
- It tin dɛn we gɛt fayn fayn tin dɛn fɔ it ɛn kɔntrol yu wet.
- Was yu an fayn fayn wan afta yu dɔn yuz tɔylɛt ɛn bifo yu it ɛn afta yu it.
- Tɔk to yu dɔktɔ ɛn mek wan sef ɛksɛsayz plan we go fayn fɔ yu.
Mɛsej we dɛn kin kɛr go na os
- di pulmonary Alveolar Proteinosis (PAP) na wan sik we nכ kin apin we di protin dεm εn fεt dεm kin kכmכt na di ay sak dεm (alveoli) na di lכng dεm.
- Di men sayn na we i nɔ kin izi fɔ blo. Apat frɔm dat, pɔsin kin kɔf, i kin gɛt pen na in chɛst, ɛn i kin taya.
- Pan ɔl we dis na sɔntin fɔ fred, tritmɛnt dɛn we rili fayn lɛk "Whole-Lung Lavage" kin ɛp fɔ kɔntrol di sik dɛn ɛn alaw yu fɔ liv nɔmal layf.
- If yu gɛt dɛn sik ya, yu fɔ rili go to spɛshal dɔktɔ we de mɛn yu lɔng. I rili impɔtant fɔ no di sik ɛn bigin fɔ trit am kwik kwik wan.
- If yu nɔ smok ɛn protɛkt yusɛf frɔm dɔst ɛn kemikal smok kin go sɔm we fɔ protɛkt yusɛf frɔm dis sik.
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