Yu dɔn ɛva yɛri se tu smɔl smɔl gland dɛn na di bɔdi kin stɔp fɔ wok, ɛn dat kin afɛkt yu layf bad bad wan? Tide wi go tɔk bɔt dis kayn sik we rili denja, ɛn if dɛn nɔ trit am kwik, i kin kil pɔsin. Dɛn kɔl dis Wata Haus-Friderichsen Sindrom. Pan ɔl we i go tan lɛk se di nem lɔng smɔl, lɛ wi tɔk jɔs bɔt wetin i bi, wetin mek i kin apin, ɛn aw fɔ liv.
Wetin na dis Wata Haus-Friderichsen Sindrom?
Fɔ tɔk am simpul wan, Waterhouse-Friderichsen Syndrome (WFS) na wan sik we rili siriɔs. wetin kin apin na we yu adrenal gland dεm , we na tu sכm gland dεm we de oba yu kidni dεm, de bכn (wi kכl dis `adrenal hemorrhage`) εn wan כ tu pan dεn gland dεm ya stכp fכ wok. Bɔrku tɛm, dis kin kam bikɔs ɔf wan bad bad infekshɔn. If dɛn nɔ trit dɛn adrenal gland ya, i kin lɛf smɔl fɔ lɛ dɛn stɔp fɔ mek di ɔmon we dɛn kɔl kɔtisol, we rili impɔtant fɔ wi bɔdi. Dis na wetin wi kɔl adrenal kraysis . Fɔ tɔk di kɔrɛkt tin, na imejensi!
כda nem de fכ dis, we na ``hεmorrhagic adrenalitis.'' Dat min se di adrenal gland dεm de blכd εn inflam.
Aw dis sik kin kɔmɔn?
Infakt, di sik we dɛn kɔl Waterhouse-Friderickson syndrome nɔ kin bɔku . Tipikli, ɔtopsi dɛn kin si se dis kɔndishɔn na in de mek ɔlman kin day lɛk 1%. Dis min se nɔto sik we de ambɔg ɔlman, bɔt if i apin, i rili denja.
Wetin na di sayn dɛm fɔ dis sik?
Imajin, yu gɛt vayrɔs ɔ baktri wantɛm wantɛm ɛn gɛt dis WFS kɔndishɔn. Dɔn yu kin bigin fɔ sho sayn dɛn we de sho se yu gɛt infekshɔn wantɛm wantɛm. Yu no wetin na dat?
- A de gɛt ay fiva.
- Di bɔdi kin fil kol ɛn i kin shek (Chills).
- Mi ed de at bad bad wan.
- A go vomit, a go vomit.
- Di mɔsul dɛn na mi bɔdi kin at, mɔ na say dɛn lɛk mi bɛlɛ we de dɔŋ, mi bɛlɛ, ɛn mi leg dɛn.
- Mi jɔyn dɛn bin de at.
- Sɔmtɛm, i kin kam fɔ lɛ yu nɔr no natin (syncope).
We dis blɔd bigin fɔ afɛkt nɔto di adrenal gland dɛn nɔmɔ bɔt ɔda pat dɛn na di bɔdi, ɔda sayn dɛn kin sho. Dɛn tin ya na:
- Disseminated intravascular coagulation (DIC): Dis kin tan lɛk se i kɔmplikt smɔl, nɔto so? Fɔ tɔk am simpul wan, na wan dizayd we di blɔd we de klɔt ɔlsay na di bɔdi kin go haywire. We blɔd klɔt fɔm na wan ples, i nɔ kin ebul fɔ stɔp fɔ blɔd na ɔda ples.
- Skin rash: .Sɔntɛnde dɛn kin apia na di skin lɛk smɔl dɔt ɔ big spat.
- Sɛptik shɔk: Dis na sik we di blɔd prɛshɔn kin go dɔŋ bad bad wan bikɔs ɔf di infekshɔn, we kin mek di bɔdi in ɔgan dɛn nɔ kin gɛt inof blɔd. Dis kin rili denja bak.
Wetin na di sayn dɛm we de sho se di adrenal gland de blɔd?
WFS gɛt fɔ du wit adrenal ɛmoraji, we kin kam wit ɔda sayn dɛn:
- Bɛlɛ de at.
- Pen na di say we de ɔp di wɛst, dɔŋ di rib (loins).
- Malaise, filin fɔ mek yu nɔ fil fayn.
- Di we aw pɔsin kin sloslo.
- Nɔs ɛn vɔmit.
- Rɔnbɛlɛ.
Wetin kin mek dis apin?
Bɔrku tɛm, di men tin wae kin mek yu gɛt Waterhouse-Friderickson syndrome na baktri ɛn vayral infɛkshɔn (sepsis) . Fɔ tɔk di kɔrɛkt tin, wan jem kin go insay di bɔdi ɛn skata ɔlsay na di bɔdi ɛn dɛn nɔ kin kɔntrol am.
Sɔm kayn bɔdi kin gɛt dis sik mɔ. Na sɔm ɛgzampul dɛn ya:
- `Syudomonas aeruginosa`
- Meningococcus bacteria: Dis na di wan we denja pas ɔl we kin mek pɔsin gɛt WFS.
- `Strɛptokɔk nyumonia`
- `Ɛmofilis inflɔɛnsa`
- `Escherichia koli (E. koli)`
- `Stafylɔkɔkɔs ɔriɔs`
Bɔrku ɔda kayn baktri kin mek dis sik.
Dɔn bak, sɔm kayn vayrɔs kin mek dis:
- Saytomɛgalovayrɔs (CMV) .
- Parvovayrɔs `(Parvovayrɔs)`
- Epstein-Barr vayrɔs we dɛn kɔl Epstein-Barr
- Ebola vayrɔs `(Ebola vayrɔs sik)`
- Varicella-zoster virus (na dis kin mek yu gɛt sik lɛk chikinpoks ɛn hεpi) .
Apat frɔm dɛn infɛkshɔn ya, sɔm ɔda tin dɛn de we kin mek pɔsin gɛt WFS:
- Yuz mɛrɛsin dɛn we de mek pɔsin nɔ gɛt blɔd. Dɛn tin ya kin mek pɔsin gɛt blɔd.
- Trombocytopenia: Dis min se di nɔmba fɔ di pletlɛt (sɛl dɛn we de ɛp fɔ mek blɔd klɔt) na di blɔd go dɔŋ.
- Di adrenal gland dɛn dɔn pwɛl sɔm we dɛn.
Udat dis tin kin afɛkt mɔ?
Waterhouse-Friderickson syndrome kin kam pan yɔŋ pikin dɛm pas big pipul dɛm . So, if yɔŋ pikin gɛt sɔm sayn dɛn lɛk fiva ɛn bɔdi pen, yu fɔ tek tɛm bad bad wan.
Us prɔblɛm dɛn dis kin mek?
Dis na di tin we impɔtant pas ɔl. If dɛn nɔ trit am kwik ɛn fayn, di sik we dɛn kɔl Waterhouse-Friderickson syndrome kin kil pɔsin. Dat min se i kin mek pɔsin in layf de pan denja. So dɛn fɔ trit dis as imejensi.
Aw dɛn kin no dis sik?
Fɔ no dis sik, yu rili nid dɔktɔ fɔ ɛp yu. Di dɔktɔ go aks yu bɔt yu sik dɛn, aks yu bɔt di sik dɛn we yu bin dɔn gɛt trade, dɔn i go chɛk yu bɔdi.
Bɔt fɔ no bɔt WFS kin at smɔl, bikɔs di sayn dɛn we i kin gɛt kin rili fiba di wan dɛn we kin gɛt sɛptik shɔk . So, fɔ kɔnfɔm if na WFS, di dɔktɔ go ɔda difrɛn tɛst dɛn.
Us tɛst dɛn kin yuz fɔ no di sik?
Fɔ no if infɛkshɔn de, di dɔktɔ kin du dɛn tɛst ya:
Test dɛn fɔ tek imej
- Dɛn kin du ɔltra saund skan ɔ CT (computed tomography) skan fɔ chɛk if blɔd dɔn gɛda insay di adrenal gland dɛn. Dɛn skan ya kin tek pikchɔ dɛn insay di bɔdi, so dɛn kin si klia wan say dɛn we blɔd de kɔmɔt.
Blɔd tɛst dɛn
- We yu du blɔd tɛst, yu go no fɔ tru if yu gɛt baktriyal infɛkshɔn. Dis min se yu fɔ tek wan smɔl nidul frɔm wan vein we de na yu an, tek smɔl blɔd, ɛn luk am wit maykroskɔp. Dis go luk fɔ sayn dɛm fɔ se yu gɛt di sik.
Meningococcus baktri dɛm tɛst
If di dɔktɔ tink se di kɔz na meningococcus bacteria, den dɛn kin du tɛst lɛk dis:
- spεnal tap / lכmba pankshכn: dis involv fכ put wan tכn nidul insay yu lכw bכk, bitwin tu vεrbra dεm, εn tek sכm spεnal fכluid. Dis kin tan lɛk se i de mek pɔsin fred, bɔt dɔktɔ dɛn kin tek tɛm du am.
- Skin biopsy: If yu gɛt lɛsin na yu skin, dɛn go tek smɔl pat pan di skin frɔm di lɛsin ɛn chɛk am.
- Gram stain test: Dɛn kin tek sampul frɔm say we dɛn tink se (lɛk wund) fɔ luk fɔ baktri dɛm.
- Urinalysis: Dɛn go aks yu fɔ pis insay spɛshal kɔntena. Dɔn dɛn go tɛst di urine sampul fɔ si if i gɛt sayn dɛn we de sho se i gɛt di sik.
Akyu adrenal kraysis tɛst dɛn
Dɛn tɛst ya kin ɛp fɔ no if yu de gɛt adrenal crisis , we na wan sik we di adrenal gland dɛn nɔ de wok fayn:
- Adrenocorticotropic hormone (ACTH) stimulation test: Insay dis tɛst, yu dɔktɔ kin gi yu smɔl injɛkshɔn fɔ wan ɔmon we dɛn kɔl ACTH. Dɔn, afta 30 to 60 minit, dɛn kin tek blɔd fɔ si aw yu adrenal gland dɛn kin ansa di ACTH. Dis na tɛst we de sho aw yu adrenal gland dɛn de wok fayn fayn wan.
- Test fɔ blɔd shuga:Dɛn kin tek smɔl blɔd ɛn mɛzhɔ di shuga (glukɔs) we de insay. Di shuga lɛvɛl kin smɔl we yu gɛt adrenal kraysis.
- Kɔtisol tɛst: Dɛn kin tek wan sɛmpul pan yu blɔd, urine, saliva, ɔ tu ɔ tri pan dɛn tin ya fɔ chɛk ɔmɔs kɔtisol yu adrenal gland dɛn de mek.
- pH bכdi tεst: dεn de tek sεmpl blכd εn mכsu in asid-bכs lεvεl (pH). Dɛn kin du dis wit atria blɔd gas (ABG) tɛst ɔ ilɛktrɔlayt panɛl. Nɔmal wan, di pH na wi blɔd fɔ de bitwin 7.35 ɛn 7.45.
- Potassium blood test: Na blɔd tɛst fɔ no ɔmɔs potassium de na yu blɔd. Potassium na wan tin we de ɛp wi nerv ɛn mɔsul dɛn fɔ wok fayn fayn wan. dis lεvεl dεm kin chenj di tεm we adrenal krεse de.
- Sɔdiɔm blɔd tɛst: We dɛn de du blɔd tɛst fɔ no ɔmɔs sɔdiɔm de na yu blɔd. Sɔdiɔm impɔtant bak fɔ mek yu nɛv ɛn mɔsul dɛn wok fayn fayn wan. Dɛn lɛvul ya kin difrɛn bak.
Aw dɛn kin trit dis?
If yu gɛt WFS, yu kin gɛt sɛpsis bak . So, di fɔs tin we dɔktɔ dɛn go du na fɔ stat yu fɔ tek antibayɔtik wantɛm wantɛm we dɛn de du tɛst fɔ no wetin rili kɔz di WFS. Dɛn go de wach yu ilɛktrɔlayt (sɔl) ɛn wata lɛvɛl bak.
We dɛn dɔn kɔntrol di sayn dɛn we de sho se pɔsin gɛt sɛpsis, dɔktɔ dɛn go bigin fɔ gi yu mɛrɛsin dɛn we dɛn kɔl glukokɔtikoyd ɛn minralkɔtikoyd . Dis na sterɔyd ɔmon dɛn. Glucocorticoids de wok fɔ ridyus inflamɛns na di bɔdi. Mineralocorticoids de wok fɔ rigul yu bɔdi in sɔl ɛn wata lɛvɛl. Fɔ tɔk am simpul wan, dɛn tan lɛk we dɛn de gi yu ɔmon dɛn we yu adrenal gland dɛn fɔ de mek, bɔt nɔto so.
Yu kin nid fɔ transfyushɔn blɔd ɔ wan tin we dɛn kɔl angioembolizayshɔn . dis involv fכ yuz angiogram εn bכdi kכlכt (embolization) fכ no εn blכk di at dεm we de gi bכdi to di adrenal gland dεm. Dɛn kin du dis fɔ stɔp di blɔd.
Di tin we impɔtant pas ɔl na dat, afta WFS, bɔku pipul dɛn go nid fɔ tek ɔda ɔmon mɛrɛsin fɔ di res ɔf dɛn layf , bikɔs wans di adrenal gland dɛn dɔn pwɛl, dɛn nɔ go ebul fɔ mek ɔmon dɛn fayn fayn wan igen.
Aw kwik a go fil fayn afta dɛn dɔn trit mi?
Bɔrku pipul kin bigin fɔ fil fayn insay wan ɔr tu wiks wae dɛn bigin fɔ gɛt tritmɛnt. Bɔt ivin afta yu dɔn wɛl, yu kin stil gɛt sɔm prɔblɛm dɛn na yu bɔdi ɔ yu maynd fɔ sɔm mɔnt, ɔ ivin fɔ lɔng lɔng tɛm. Fɔ ɛgzampul:
- Di it nɔ de te.
- Rili taya.
- I nɔ izi fɔ slip (insomnia).
- Di tendency fɔ sik izi wan.
- Wɔri.
- Pwɛl at.
So, i impɔtant fɔ mɛmba se i kin tek sɔm tɛm fɔ mek i wɛl.
Wetin yu go ɛkspɛkt if yu gɛt dis sik?
As wi bin dɔn tɔk bifo tɛm, if dɛn nɔ trit am, WFS na wan sik we de kil pɔsin. No dawt nɔ de bɔt am.
Bɔt wit di tritmɛnt kwik, di rayt tritmɛnt ɛn rihabiliteshɔn, bɔku pipul dɛn we gɛt WFS kin wɛl. Bɔt yu kin nid fɔ gɛt bɔku mɛrɛsin, ɛn di tin dɛn we WFS kin du kin las fɔ sɔm mɔnt, ivin fɔ lɔng lɔng tɛm. So, i nɔto sɔntin we wi fɔ tek am layt.
Yu tink se dɛn go ebul fɔ mek dis tin nɔ apin?
Bɔrku tin de wae yu kin du fɔ ridyus yu risk fɔ gɛt Waterhouse-Friderickson syndrome:
- If yu was yu an ɔltɛm ɛn fayn fayn wan, dat kin ɛp fɔ mek yu nɔ gɛt di sik. Dis na tin we rili simpul, bɔt i kin sev yu frɔm bɔku sik dɛn.
- Fɔ gɛt di meningococcal bacteria vaysin impɔtant mɔ fɔ pikin dɛn.
- If yu tink se yu gɛt infekshɔn, go to tritmɛnt wantɛm wantɛm. Nɔ ignore smɔl fiva ɔ kɔf.
Aw yu kin kia fɔ yusɛf we yu de wɛl?
As yu de wɛl, yu ɛn yu dɔktɔ fɔ wok togɛda fɔ mek wan rihabiliteshɔn plan we go fayn, we sef, ɛn we go bɛtɛ fɔ yu. Da plan de kin gɛt tin dɛn lɛk:
- Gɛt bɔku rɛst. Di bɔdi ɛn di maynd ɔl tu nid fɔ rɛst.
- Fɔ fala di tin dɛn we yu de it we go ɛp yu fɔ gɛt trɛnk bak na fayn tin. I go fayn if yu kin gɛt advays frɔm pɔsin we sabi bɔt it fɔ dis.
- Sɛt smɔl gol dɛn. Fɔ ɛgzampul, fɔ sidɔm ɔp na bed, tinap, fɔ drɛs yu wan, fɔ was, fɔ waka smɔl, fɔ klaym wan stej.
- Fɔ tɔk bɔt aw yu de fil wit yu fambul, padi, ɔr pɔrsin wae de mɛn yu na impɔtant tin insay dɛn tranga tɛm ya.
- Ɛksesaiz we yu gɛt trɛnk ɛn trɛnk. Start sloslo ɛn ɛksesaiz akɔdin to yu dɔktɔ in instrɔkshɔn.
Ustɛm a fɔ go to dɔktɔ? / Ustɛm a fɔ go na imejensi rum?
If yu stil nɔr de fil fayn afta yu dɔn gɛt tritmɛnt, ɔr if yu gɛt prɔblɛm fɔ rich yu rihabiliteshɔn gol dɛm, mek shɔ se yu tɔk to yu dɔktɔ.
WFS na siriɔs sik we kin kil pɔsin if dɛn nɔ trit am. If yu gɛt ɛni sayn fɔ WFS, fɔ ɛgzampul, infekshɔn we de wɔs we nɔ de go, den yu fɔ go na imejensi rum (ETU) wantɛm wantɛm.I nɔ fayn fɔ put dis ɔf.
Us kwɛstyɔn dɛn yu fɔ aks yu dɔktɔ?
We yu kam fɔ no se yu gɛt WFS, yu kin gɛt bɔku kwɛstyɔn dɛn. Nɔ fred, aks yu dɔktɔ kwɛstyɔn dɛn lɛk dis fɔ mek yu nɔ gɛt wan dawt:
- Aw yu go no if a gɛt Waterhouse-Friderickson syndrome?
- If a nɔ gɛt Waterhouse-Friderickson syndrome, us ɔda sik a go gɛt?
- Wetin na di kɔz fɔ mi Waterhouse-Friderickson syndrome?
- A go nid fɔ du ɔpreshɔn fɔ mek mi adrenal gland dɛn fayn?
- Yu tink se a go wɛl ɔltogɛda?
- A go nid fɔ tek ɛkstra ɔmon dɛn?
- Aw lɔng a go gɛt fɔ tek ɔda ɔmon dɛn?
So, wetin na di impɔtant tin dɛn we wi fɔ mɛmba frɔm dis?
Waterhouse-Friderichsen syndrome (WFS) na wan sik we rili siriɔs ɛn we nid fɔ go to dɔktɔ wantɛm wantɛm. If yu gɛt ɛni wan pan dɛn sayn ya, ɔ if yu gɛt infekshɔn we nɔ de bɛtɛ, i impɔtant fɔ go na imejensi rum kwik kwik wan.
Fɔ fala ɔl di tritmɛnt instrɔkshɔn dɛn we yu dɔktɔ gi yu ɛksaktɔli. Na da tɛm de nɔmɔ yu go ebul fɔ kɔntrol dis WFS kɔndishɔn ɛn wɛl kwik kwik wan. Mɛmba se, tritmɛnt kwik kwik wan kin sev pɔsin in layf! Dɔn bak, i rili impɔtant fɔ mek yu tek kia ɔf yusɛf gud gud wan we yu de wɛl.
` Wata Haus-Friderichsen sεndrכm, adrenal gland dεm, kכtisol, sεpsis, infεkshכn, imejensi kεriכn, כmon dεm











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