Omwana wo omuto alina ekizibu ekizibikira mu musuwa omukulu mu mutima gwe? Ka tuyige ku Interrupted Aortic Arch (IAA) mu bigambo ebyangu.

Essanyu ly’owulira ng’otunuulira omwana wo eyaakazaalibwa teriyinza kwogerwako, nedda? Mu kiseera kye kimu, waliwo obuvunaanyizibwa bungi mu mutima gwo olw’obulamu obwo obutono. Oluusi kyabulijjo okuwulira ng’otya nnyo n’okweraliikirira ng’owulira endwadde ezimu abaana abato ze bayinza okutawaanyizibwa. Leero, twogera ku bulwadde bw’omutima obw’amaanyi obuyinza okubaawo mu baana abaakazaalibwa, naye nga tebutera kubaawo nnyo, era nga bwetaaga okujjanjabibwa mu bwangu. Embeera eno eyitibwa Interrupted Aortic Arch, oba (IAA) mu bufunze.

Mu ngeri ennyangu, Interrupted Aortic Arch (IAA) kye ki?

Kino okukitegeera, ka tusooke tulabe engeri omutima gwaffe gye gukola. Lowooza ku mutima gwaffe nga ppampu y’amazzi. Pampu eno erina ebisenge bina ebikulu. Babiri waggulu ate babiri wansi. Omusaayi guno ogubadde gukozesebwa omubiri era nga gulimu omukka gwa oxygen omutono, nga gubeera gwa bbululu katono, guyingira mu kisenge ekya waggulu ku ddyo. Okuva awo, kigenda mu kisenge ekya wansi ne kiyisibwa mu mawuggwe. Mu mawuggwe, omusaayi guno gubaamu omukka omulungi era gufuna langi emmyufu ennungi.

Kati omusaayi guno omumyufu ogulimu omukka gwa oxygen guyingira mu kisenge ekya waggulu ekya kkono eky’omutima. Okuva awo, kigenda mu kisenge ekya wansi ekya kkono ne kiyisibwa mu mubiri gwonna nga kiyita mu musuwa ogusinga obunene era ogusinga obukulu mu mubiri gwaffe, oguyitibwa aorta . Omusuwa guno gulinga enkola ya payipu enkulu etwala amazzi okuva mu ttanka yaffe ey’amazzi okutuuka mu nnyumba yonna. Kikoleddwa ng’omuggo gwa ssweeta.

Kale, ekibaawo mu mwana alina embeera eyitibwa Interrupted Aortic Arch (IAA) kwe kuba nti omusuwa omukulu, aorta, tegujjuvu. Waliwo ekiziyiza awalala mu kyo, ng’ekituli ekimenyese. Mu ngeri ennyangu, payipu y’amazzi enkulu emenyese wakati. Olw’ensonga eno, omutima ne bwe gupampagira gutya, omusaayi omulungi ogulimu omukka gwa oxygen tegugenda mu bitundu by’omubiri ebya wansi.

Omanya otya nti omwana wo alina embeera eno? Obubonero bwe buliwa?

Abalongo abalina IAA batera okutandika okulaga obubonero mu ssaawa oba ennaku ezisooka oluvannyuma lw’okuzaalibwa. Ng’abazadde, kikulu nnyo gye muli okukimanya kino.

Bw’olaba obubonero buno obumu oba obusingawo mu mwana wo, olina okugenda ew’omusawo amangu ddala oba okutwala omwana wo mu kitongole ky’eddwaaliro ekikola ku bujjanjabi obw’amangu (ETU) awatali kulwa .

Lwaki kino kituuka ku balongo?

Bw'owulira ekintu nga kino, ekibuuzo ekisooka okukujja mu birowoozo ng'omuzadde kiri nti, "Lwaki kino kyatuuka ku mwana waffe? Twakola ekikyamu?"

Mu ngeri ennyangu, embeera eno ebaawo ng’omwana akula mu lubuto, olw’okufiirwa ekitundu ekitono ennyo ekya chromosome ekikosa okutondebwa kw’omutima n’emisuwa emikulu.

Abalongo abalina IAA batera okuba n’obulwadde bwa DiGeorge syndrome.Kiyinza okubaawo n’embeera endala ey’obuzaale eyitibwa DiGeorge syndrome. Kino kiva ku kufiirwa ekitundu kya chromosome y’emu nga bwe kyayogeddwako waggulu. Abaana abalina obulwadde bwa DiGeorge syndrome bayinza okufuna yinfekisoni enfunda eziwera era bayinza okuba n’enkyukakyuka ezimu mu maaso (nga emimwa egyakutuka).

Obulema obulala obw’omutima obuwerekera ku IAA

Abalongo abalina IAA batera okuba n’ekizibu ekirala ekimu oba ebisingawo ku mutima. Ekimu ku bisinga okubeerawo ye Ventricular Septal Defect (VSD).

• Ventricular Septal Defect (VSD): Mu ngeri ennyangu, kino kinnya mu bbugwe (septum) wakati w’ebisenge ebikulu ebibiri ebipampagira (ventricles) eby’omutima. Wadde nga kino kitera okuba ekikyamu, VSD esobola okutaasa obulamu bw’omwana alina IAA okumala akaseera . Teebereza nti omusaayi bwe gutasobola kukulukuta wansi mu musuwa, ogumu ku musaayi ogulimu omukka gwa oxygen ku ludda olwa kkono olw’omusuwa gusobola okuyita mu kinnya kino okutuuka ku ludda olwa ddyo, gye gusobola okukulukuta okutuuka mu mawuggwe okusobola okuwa omusaayi ogumu mu bitundu by’omubiri ebya wansi. Kiringa okuba n’akayita akatono ng’oluguudo olukulu luzibiddwa. Naye kino kigonjoolwa kya kaseera buseera.

Enkola ki ey’okuzuula n’okujjanjaba?

Kikulu okumanya n’okujjanjaba embeera eno amangu ddala nga bwe kisoboka.

Okuzuula obulwadde

Embeera eno etera okuzuulibwa nga bakozesa Echocardiogram . Tukiyita buyita ‘Echo test’. Kino kiringa sikaani y’omutima. Okukebera kuno okutaliimu bulumi kusobola okulaba obulungi enkula n’enkola y’ebisenge by’omutima, obusuwa, n’emisuwa gy’omusaayi. Oluusi, embeera eno esobola n’okuzuulibwa nga bukyali nga bamukola sikaani ng’omwana akyali mu lubuto.

Obujjanjabi

Obujjanjabi bwa IAA kwe kulongoosa . Kyokka okutuusa ng’omwana awedde okulongoosebwa, abasawo bajja kusooka kukola kintu kirala okutaasa obulamu bw’omwana.

1. Omutendera ogusooka - Okukuuma omukutu ogw’ekiseera nga guggule:

Buli mwana omuwere alina akakwate ak’ekiseera wakati w’omutima, omusuwa gw’omusaayi, n’omusuwa ogutwala omusaayi mu mawuggwe oguyitibwa Ductus Arteriosus . Kino kikulu nnyo ng’omwana ali mu lubuto. Tubu eno eggalawo ku bwayo mu ssaawa ntono ng’emaze okuzaalibwa.

Naye mu mwana alina IAA, olw’okuba omusuwa gw’omusaayi gukutuse, ekkubo lyokka omusaayi ogulimu omukka oguyingira mu mubiri gwe guyita mu Ductus Arteriosus. Kale abasawo kye basooka okukola kwe kuwa omwana eddagala eriyitibwa Prostaglandin E1 , erikuuma ttanka eyo ey’ekiseera ng’eggule nga tegiggadde. Kino kiyamba okukuuma omusaayi mu mubiri gw’omwana okutuusa lw’alongoosebwa.

2. Omutendera ogwokubiri - Okulongoosa:

Embeera y’omwana bw’emala okutebenkera, abasawo abakugu abalongoosa bamulongoosa. Kino kizingiramu:

• Okutwala enkomerero ebbiri ezimenyese ez’omusuwa gw’omusaayi n’oziyunga wamu okukola omusuwa omujjuvu ogutaziyizibwa.
• Okuggalawo Ductus Arteriosus ey’ekiseera eyali egguddwawo nga bamuwa eddagala lya prostaglandin.
• Singa wabaawo VSD (ekituli mu bbugwe w’omutima), nayo ejja kuggalwa mu kiseera ky’okulongoosebwa kuno.

Omwana anaawulira atya oluvannyuma lw’okulongoosebwa?

Tewali kizibu abazadde kye bayinza okugumiikiriza okusinga okuwulira nti omwana waabwe alina obulwadde obuyinza okutta obulamu bwabwe. Naye okusinziira ku bye twogeddeko, osobola okulaba nti embeera eno esobola okuddukanyizibwa obulungi ng’ogenda mu ddwaaliro mu bwangu.

Obulamu bw'abaana oluvannyuma lw'okulongoosebwa IAA buyinza okuba obulungi ennyo . Okusinziira ku bibalo, ne bwe wayise emyaka 10 bukya balongoosebwa, abaana 81% bakyali balamu. Ekyo kitegeeza nti obuwanguzi bungi nnyo.

Naye kino kya mangu. Amangu ddala ng’obubonero buzuuliddwa, omwana alina okuweebwa ekitanda mu ddwaaliro erijjanjaba abalwadde abayi (ICU) era obujjanjabi butandike mu bwangu. Ne bwe bamala okulongoosebwa, kyetaagisa okugenda mu maaso n’okutwala omwana mu ddwaaliro n’okukeberebwa okwetaagisa, ng’abasawo bwe bamuwa amagezi.