I naute hian pum na a nei reng em? He (Autoimmune Enteropathy) chungchang hi i zir dawn teh ang?

I fa te poop chu a tla reng em? Ni hnih emaw ni thum emaw vel a lo awm tawh hi a pawi lo em ni? A chang chuan nu leh pa kan nih angin hetiang thil kan hmuh hian kan buai deuh thin em? A bik takin naute piang thar a nih chuan a inthlak danglamna tlemte apiang hi kan ngaihtuah nasa hle. Chuvangin, vawiin hian natna chi khat, a natna lan chhuah dan inang lo tak tak kan sawi dawn a ni.

Autoimmune Enteropathy'' tih hi eng nge ni? A awlsam zawngin i hrethiam ang u, kan hrethiam dawn em ni?

A awlsam zawngin, (Autoimmune Enteropathy) hi kan taksa invenna system, chu chu immune system hian kan intestines a rawn bei sual thinna thil awm lo tak a ni . Heta thil thleng hi han ngaihtuah teh, kan ram humhalh tura ngaih sipaite hian kan ram ngeia hmun pawimawh tak an rawn bei a nih chuan. Hei hian naupang tê tête a nghawng ber tlangpui. Mahse puitlingah pawh a chang chuan a lo awm thei bawk.

Naute hian he natna hi an vei chuan an poop chu tuiin a awm a, a chhunzawm zel bawk. He ril\am hi ni hnih emaw ni thum emaw hnuah a tawp lo. Heng symptoms te hi naute pian atanga kar hnih atanga kar li inkar ah a lang tan tlangpui.

Hetianga immune system hian intestine a tihchhiat hian eng nge thleng? Naute in hnute hnute emaw, formula emaw a\angin taksain nutrients a la thei lo. Chu ai chuan chu ei tur tha zawng zawng chu taksa atangin ril\am angin a chhuak vek a ni. Hei hian naute chu tui tlakchhamna a thlen thei a, chu chu tui an tlachham tihna a ni. Tin, naute chu beisei angin a thau lo thei bawk.

I naute chu well-baby checkup neihpui tura i hruai chuan naupang enkawltu doctor chuan i naute thanlenna leh hriselna lama harsatna awm apiang a hmu thei ang. Amaherawhchu, i naute poop-ah danglamna i hmuh chuan doctor hnenah hrilh hreh suh.

He natna hi Autoimmune Enteropathy'' tia hriat a ni a, damdawi hmanga enkawl a ni a, chu chuan immune system-in intestines a beih lohna tur a tihtlem emaw, a titawp emaw a ni.

He natna hi engtiang chiahin nge a hluar?

Autoimmune Enteropathy hi a takah chuan natna hmuh tur awm lo tak a ni. Mithiamte chuan khawvel hmun hrang hrang i en chuan nausen sang za zinga pakhat velin he natna hi an vei niin an sawi. Puitling pawhin he natna hi vei thei mah se, naute aiin a tam lo hle. Chuvangin he thu hi i hriat hnuah pawh a tul lovah hlau suh.

(Autoimmune Enteropathy) natna lan chhuah dan chu engte nge ni?

A lan chhuahna ber chu nausen piang thar leh naupang tê tête an paltlang ṭhin bawlhhlawh nêm tak ai chuan chawlhsan lo, tui chhuak (diarrhea) a ni.

A lan chhuah dan dang chu incontinence ( zun chhuah loh) a ni. Nausen piang thar chuan ni khatah wet diaper panga atanga paruk tal a nei tur a ni. Chu aia wet diaper tlem zawk neih chu i naute tui a tlakchham tih chhinchhiahna a ni thei.

Ngaihtuah teh, a tlangpuiin naute hian ni khatah vawi tam tak a poop a, a thim deuh a, a rawng pawh a nei bawk. Mahse hetiang a nih chuan poop chu tui chauh a ni. Tin, naute chu a nuam lo hle a, a tap pawh a ni thei bawk.

Eng thilin nge (Autoimmune Enteropathy) a thlen?

Mithiamte chuan a chhan dik tak an la hre lo. A tam zawkah chuan autoimmune enteropathy nei naute hian primary immunodeficiency an nei a, chu chuan an small intestine-a villi te chu a tichhe thin.

Heng (villi) te hi eng nge an nih i hria em? I naute intestine tenau bang chhunga sam ang chi thil te tak te te an ni. Carpet te tak te chunga fiber awm ang mai an ni. An hna ber chu i naute ei tur (nute hnute emaw formula) atanga nutrients te hip lut a, chu nutrients te chu i naute thisenah thawn chhuah hi a ni. Chuvangin heng (villi) te hi a chhiat chuan nutrients te chu taksaah a thleng lo.

He natna hian eng harsatna nge a thlen theih?

Autoimmune Enteropathy hian harsatna hrang hrang a thlen thei a. Chung zinga ṭhenkhat chu:

• Dehydration: Kan taksaa tui awm zat a tlahniam a, hei hi luak chhuak reng reng vang a ni. Hei hi nausen naupang tan chuan a hlauhawm hle.
• Hypoproteinemia: Thisenah hian protein level a tlahniam a, hei hi nutrients a lakluh that loh vang a ni.
• Hri kai fo: Immune system a thawk tha lo a, ei leh in lama harsatna a awm avangin naute hi an damlo nasa zawk.
• Malabsorption: Hei hi harsatna lian ber a ni. Intestines a chhiat avangin taksaah hian nutrient engmah a lut lo.

Heng harsatnate hian naute chu a thang tha lo thei a, a rihna a tlahniam thei a, a damlo reng bawk.

Engtin nge doctor-te hian Autoimmune Enteropathy hi an hriat theih?

I naupang enkawltu doctor chuan i naute natna lan chhuah dan a zawt ang che a, taksa enfiahna a nei ang. Chumi hnuah chuan test an order thei ang, chungte chu:

• Thisen test: Immune system-a thil dik lo bik awm apiang hriat chian nan.
• Flow Cytometry: Hei hi laser beam bik hmanga immune system cell sample enfiah dan a ni.

Chu bâkah, i doctor chuan gastroenterologist hnênah a hruai thei che a, chu chuan small intestine biopsy ang chi test a ti thei bawk. I naupang enkawltu doctor chuan autoimmune disorders lama specialist hnenah pawh a refer thei bawk che.

Engtin nge (Autoimmune Enteropathy) hi enkawl a nih?

I naute chu he natna hi a vei tih hmuhchhuah a nih chuan, a thisenah (vein - IV hmangin) tui leh ei leh in tur pek a nih a rinawm. Hei hian saline pek tihna a ni a, a chhan chu taksain ka atanga pek engmah a hip thei lo.

Tin, naute intestine te chu immune system-in a beih dan tihtlem nan damdawi pek a ni bawk. Damdawi bikte chu:

• Corticosteroids te hi a hnuaia mi ang hian a ni.Hengte hi damdawi chi chak tak a ni a, immune system hnathawh a ti tlem a ni.
• Immunomodulators: Heng damdawi te hi immune system hnathawh tidanglamna hmanga chhiatna tihziaawmna atana puitu an ni.

Ṭhenkhatah chuan, heng enkawlnate hian duhthusam a chhuah loh chuan, doctor-te chuan enkawlna buaithlâk zâwk, stem cell transplant ang chi chu an hmang thei a ni. Mahse, hei hi naute dinhmunah a innghat nasa hle.

Ka naute hian (Autoimmune Enteropathy) a neih chuan eng nge ka beisei ang?

Naute zawng zawng hi an inang vek lo va, chuvangin i beisei theih tur chu an dinhmun azirin a inang lo ang. A then phei chuan naute intestine te tak te chu immune system attack laka venghimtu damdawi te hian an taksain nutrients a lakluh theih nan a pui thei a ni.

Mahse, he natna vei naute hian an taksa hriselna (immune system)-ah harsatna bulpui an nei a ni. I naute hian he natna hi a neih chuan enkawlna chi hrang hrang leh hun rei tak chhung damdawi lam enkawlna a mamawh thei a ni . Entirnan, i naute doctor chuan stem cell transplant a rawt mai thei.

Hetiang hunah hian doctor-te rin a pawimawh a, an thurawn zawm hi a pawimawh hle. Tin, zawhna emaw, ngaihtuahna emaw i neih chuan i doctor hnenah zawt bawk ang che.

Engtikah nge ka naute naupang enkawltu doctor ka biak ang?

I naute chu Autoimmune Enteropathy a vei tih hmuhchhuah a nih chuan, i zun leh ek chhuah tam danah inthlak danglamna i hmu a nih chuan – entirnan, wet diaper hman tlem a nih chuan – i naute naupang enkawltu doctor i pan nghal tur a ni. Dehydration hi nausen naupang tan chuan a hlauhawm hle. Tin, ril\am a pun emaw, i naute hian natna dang, khawsik ang chi a neih chuan damdawi lam thurawn zawng nghal rawh.

Ka naute naupang enkawltu hnenah eng zawhna nge ka zawh ang?

Autoimmune Enteropathy hi natna hlauhawm tak a nih avangin i hre tam lo mai thei. Chuvangin, i doctor zawh theih tur zawhna thenkhat chu hetiang hi a ni:

• Ka naute hian he natna hi a vei chhan i hria em? (A chhan dik tak kan hre lo maithei, mahse hriat a tha.)
• Ka naute hian eng ang enkawlna nge a mamawh?
• Heng enkawlnate hian eng side effect nge a neih? Engtin nge an enkawl?
• Ka naute hian eng chen nge enkawlna a mamawh ang?
• In lama ka naute ka enkawl dawna ka fimkhur bik tur thenkhat chu engte nge ni?
• He dinhmun hian naute hmalam hun a nghawng thei ang em?

Heng zawhnate bakah hian i rilrua thil awm reng reng chu i doctor hnenah sawipui hlau suh.

Puitlingah Autoimmune Enteropathy hi engtiang chiahin nge a awm?

Puitling tan chuan Autoimmune Enteropathy'' an vei hi a tlem hle.Amaherawhchu, engzat chiah nge tih erawh sawi a har khawp mai. Hospital pakhata doctor-te chuan kum 16 chhungin mi 13 chauh Autoimmune Enteropathy an vei tih an sawi. An vai hian autoimmune disease dang engemaw zat an nei vek a ni.

A tawp berah chuan nu leh pate hnena thuchah tlem te

Naute te tak te i neih chuan ni khat chu i naute ek chu a tlangpui aia a lo chhuak a, emaw, an zun tlem zawk emaw a nih chuan lungkhamna i neih chu thil pangngai a ni. Hetiang hunah hian hlauthawng suh.

Ni khata ril\am \hin emaw, zun tlem deuh emaw chu ngaihtuahawm a ni lo. A tam zawkah chuan heng i naute chaw ei kawnga inthlak danglamna tenau te hi Autoimmune Enteropathy'' ang chi natna khirh tak chhinchhiahna a ni lo. Amaherawhchu, ni engemaw zat hnuah i naute ek emaw, a zun emaw a inthlak danglam lo a nih chuan naupang enkawltu doctor nen inbiakna neih a tha. Chu chuan rilru thlamuanna a pe ang che. Damdawi lam thurawn lak hi a finthlak reng tih hre reng ang che.

Hriat reng tur pawimawh ber berte (Take-Home Message) .

• Autoimmune Enteropathy hi natna hmuh tur awm lo tak a ni a, taksa ngeiin a taksa a natna dotu (immune system) hian intestines a bei thin.
• A lan chhuahna ber chu tui chhuak reng reng a ni a, a bik takin naupang tê tête chu a ni.
• Hei hian harsatna a thlen thei a, chu chu ei leh in tha lo, tui tlakchhamna, leh taksa rihna tihtlem te hi a ni.
• Diagnosis atan chuan thisen test, Flow Cytometry, leh Small Intestine Biopsy te pawh a ngai thei.
• Enkawlnaah hian thisen kal tlanga ei leh in leh immune system control thei damdawi (Corticosteroids, Immunomodulators) te a tel a ni.
• I naute ek emaw, zun emaw-ah danglamna danglam tak a lan chhunzawm zel chuan naupang enkawltu doctor pan nghal rawh. Hlauthawng suh la, damdawi lam thurawn dik tak zawm bawk ang che.