I ei lai te, a chang chuan thil rimtui tak tak i hmuh hian emaw, thil tui tak i ngaihtuah hian i hmai sir khatah, a bik takin i hmuiah emaw, i hmui sir lehlamah emaw, i beng velah emaw i thawmhnaw a chhuak tan tih i hre ngai em? I hmai vel chu a sen a, a lum deuh tih i hmu thei bawk. Hei hi i taksa pum puia thawmhnaw hak ang a ni lo va, i hmai hmun bik chauh a ni. Hengte hi Frey’s Syndrome tia koh, thluak lam natna hmuh tur awm lo tak, vawiinah kan sawi tur chhinchhiahna berte chu an ni. A hming chu i tan chuan thil thar angin a lang thei a, mahse hriat a phu hle.
Frey-a Syndrome hi eng nge ni?
A awlsam zawngin, Frey syndrome hi thluak lam natna hmuh tur awm lo tak a ni . I hmai hmun bik, a tlangpuiin i hmui, i hmui, leh/ emaw i beng hnung lamah , i ei laiin, ei tur i ngaihtuah a, a châng chuan ei rim pawh i hriat laiin, thawmhnaw nasa lutuk a thlen ṭhin. I taksa pum puia thawmhnaw hak a huam lo. Tin, heng thawmhnaw hahna hmunah hian vun a ti sen emaw, a rawng a ti danglam thei bawk.
Hetiang dinhmun hi operation avanga side effect angin a awm fo thin. I parotid glands operation hnuah a tam ber . Parotid glands hi kan ka chhunga salivary glands ber a ni. Kan hmai sir lehlamah, kan beng hnuai leh hmalam chiahah an awm a. Heng glands te hian saliva a siam a, chu chuan kan hmui a ti hnim reng a, ei tur kan ei leh kan ei theih nan a pui bawk.
Frey’s syndrome hian hming dang engemaw zat a nei a:
- ``Auriculotemporal nerve natna a ni'' tih hi a ni.
- `Gustatory sweating` (hei hian ei huna thawk hah tihna a ni) .
- `Gustatory hyperhidrosis` (hei hi ngaihdan inang a ni a, `hyperhidrosis` tih awmzia chu thawk hah lutuk tihna a ni) .
- `Baillarger-a natna`
- `Dupuy syndrome` tih a ni
He natna hi kum 1923-a a hriat hmasak ber Polish neurologist Lucja Frey chawimawina atan "Frey's syndrome" tia vuah a ni.
Hetiang dinhmun hi engtiang chiahin nge a awm?
Frey syndrome hi engtiang chiahin nge a hluar tih zirchiangtute tan chuan sawi a harsa a, a chhan chu he natna report-naah hian tlin lohna engemaw zat a awm a ni. Mahse zirchianna thenkhatah chuan parotidectomy nei tawh zinga 30% leh 50% inkar chuan he syndrome hi an nei thei niin an sawi. Chumi awmzia chu hetiang surgery nei tawh zawng zawng hian an vei vek dawn lo tihna a ni a, mahse za zela engemaw zat chu hlauhawmah an awm tihna a ni.
Frey syndrome natna lan chhuah dan chu engte nge ni?
Hetiang dinhmun chhinchhiahna ber leh langsar ber chu rei tak i ei emaw, ei i ngaihtuah emaw hian thawk hah lutuk (hyperhidrosis) hi a ni Hei hi ``Gustatory sweating'' an ti bawk. He thawmhnaw hi:
- Kammula area-ah chuan
- Hmai (temple) sir lehlamah .
- Beng vel chu
Hetianga thawk hahna bakah hian chutiang hmuna vun chu a sen leh lum tih a hriat theih bawk .
Hetianga vun hring leh vun sen hi mi thenkhat tan chuan a na lo thei hle a , thenkhat tan chuan a na hle thei a, a nuam lo thei bawk . A bik takin i hmui lum tirtu ei tur i ei hian thawmhnaw a pung thei a, entirnan , ei tur hnim (lime, tamarind ang chi), ei tur rimtui (raw chili, chili powder), leh ei tur chi (salty foods) te i ei hian . Pickle tha tak i ei a, emaw, chili sauce rimtui tak nen buhfai i ei a, rang takin i hmui atang chuan i thawmhnaw a chhuak ta a nih chuan han ngaihtuah teh!
Frey syndrome symptoms hi parotid gland operation hnu kum khatna chhungin a lang tlangpui a, mahse mi thenkhatah chuan operation hnu kum engemaw zat chu symptoms hi a lang lo thei.
Frey syndrome hian eng nge a tihchhiat belh zel?
Frey syndrome symptoms hi a na lo fo thin. Chu chu, chhiatna nasa tak an thlen lo tihna a ni. Mahse, mi ṭhenkhat tân chuan , thawmhnaw tam lutuk hian harsatna nasa tak emaw, khawtlâng lungkhamna emaw a thlen thei a ni . Ngaihtuah teh, ṭhiante nêna zanriah ei tûra i chhuah a, i ei laiin i hmai a thawmhnaw a chhuak ṭan a nih chuan, chu chu a buaithlâk deuh thei a ni lawm ni?
Chaw i ei laiin i thawkrim lutuk avanga stress i neih chuan, doctor emaw, mental health counselor , psychologist ang chi emaw nen inbiakna neih a pawimawh hle.
Eng thilin nge Frey syndrome hi a thlen?
Scientist-te chuan Frey syndrome awm chhan dik tak hi an la hre lo . Mahse, an theory ber chu i parotid gland bula nerve chi hnih a ruala a chhiat chuan a thleng thin tih hi a ni . Heng nerve chi hnih hi ``sympathetic nerves`` leh ``parasympathetic nerves`` te an ni.
Heng nervous system pahnih hi kan autonomic nervous system (ANS) -a mi an ni. He ANS hian kan duh loh zawng taksa hnathawh (heart rate leh digestion ang chi) te chu a control a, chu chu kan hriat chian loh vang a ni.
Tunah chuan en teh, heng `(parasympathetic)` nerve te hnathawh pakhat chu kan salivary glands te hnathawh control hi a ni a, chu chu parotid glands te hian saliva an siam chhuah hi a ni. Amaherawhchu, heng `(parasympathetic)` nerve te hian kan sweat glands te hi an control lo. Chu chu chu nerve chi dang, `(sympathetic)` nerve te chuan a ti a ni.
Zirchiangtute chuan Frey’s syndrome hi parotid glands bula parasympathetic leh sympathetic nerve pahnih a ruala a chhiat chuan a lo awm niin an ngai.
A tlangpuiin kan taksaa nerve fiber te te te hi hliam kan tawh chuan a dam thei a, a lo thang leh thei bawk. Frey syndrome-ah chuan scientist-te chuan a chhe tawh ``parasympathetic`` nerve fibersTelephone wire pahnih inzawm khawm ang mai a ni a, ‘parasympathetic’ nerve te chu vunah sweat glands te nen an inzawm tlat a ni.
Hetiang "rewiring" danglam tak avang hian, thil an ei huna parotid glands te chu saliva siam chhuah tura signal thin parasympathetic nerve te chuan tunah chuan sweat glands te chu "sweat" turin signal an pe tan ta a ni.
Chumi rah chhuah chu ei laiin thawk hah lutuk a ni .
Chu bâkah, sympathetic nerves hian kan thisen kalna kawngte chu a tikhawtlai a, a tizau bawk a, thisen kal chu a control bawk. Hei hi Frey syndrome-a vun a sen (flushing) fo chhan pawh a ni thei.
Nerve te hi a chhiat hnuah a lo thang leh thei a, hei vang hian Frey syndrome hi operation hnu thla 6 leh thla 18 inkarah a lo lang fo thin a ni mai thei.
Frey syndrome thlen thei surgery leh accident te
Frey’s syndrome hi parotidectomy an tih laiin accidental nerve damage vang a ni tlangpui . Mahse, he natna hi a hnuaia surgery emaw accident emaw avang hian a awm thei bawk:
- Submandibular gland operation tih a ni.
- Jaw chhe tawh (mandibular fracture) siamthat nan operation tih a ni.
- Temporomandibular joint (TMJ) kaihhnawih accident te.
- Kawr chhunga lymph node awmte paih chhuah nan operation tih a ni.
- Parotid gland awmna hmuna pawn lam trauma dang.
Engtin nge Frey’s syndrome hi an hriat theih?
Frey syndrome hriatchhuahna tura pui turin i doctor chuan i natna lan chhuah dan te, a lo intan tirh ang chi te a zawt ang che. Tin, i damdawi lam dinhmun hmasa te, i hmai surgery i neih tawh leh neih loh te, i hmai nena accident i tawk tawh em tih te pawh an zawt bawk ang.
Hetiang dinhmun dik tak hriat theihna test hi `Minor starch-iodine test` an ti a . He test hi tih dan tur chu hetiang hi a ni:
1. A hmasa berin doctor chuan i hmai a i rinhlelhna hmunah iodine solution a hnawih ang.
2. A vawt hnuah a chungah starch (corn starch ang chi) hnawih ang che.
3. A dawtah chuan i salivary glands tichak turin ei tur i pe ang – a tlangpuiin thil thlum (sour toffee, lime piece ang chi) a ni.
I thawmhnaw i chhuah tan chuan chu starch chu a hnim ang a, blue emaw brown emaw a lo ni ang . Hei hian Frey syndrome i nei tih a nemnghet thei a ni. Test awlsam tak a ni lawm ni?
Frey-a syndrome hi engtin nge enkawl a nih?
Frey syndrome hi damdawi a awm lo a , chuvangin enkawlna hi a natna lan chhuah dan control-na lam a ni ber. I natna lan chhuah dan a na lo hle a nih chuan enkawlna i mamawh lo mai thei. Mahse, natna lan chhuahna na tak nei tan chuan thawmhnaw control dan chi hrang hrang a awm a:
- Botox® (botulinum toxin) injection te hi a hnuaia mi ang hian a ni.Hei hi doctor-te’n ``gustatory sweating`` control nana an hman tlanglawn ber a ni.He injection hi pek a nih hian injection na hmun bula sweat glands te chu rei lo te chhung atan an deactivate thin. He injection dawng tam zawk chuan ei laiin an thawmhnaw an thawk tlem a, an sen tlem a, an nunphung a tha zawk tih an sawi. Mahse, hei hian a nghawng chu hun kal zelah a tlahniam a – a tlangpuiin thla 9 atanga thla 12 vel a ni . Chuvangin injection lak leh a ngai mai thei.
- Topical anticholinergics: Heng damdawi te hian i sweat glands te hnathawh a tihtlem avangin hna a thawk a. An thawk tha viau nachungin vunah hnawih fo a ngai a ni.
- Topical antiperspirants: Deodorant thenkhat chuan thawmhnaw control nan a pui thei a, mahse an effect erawh a na lo hle. Anticholinergics ang bawkin hengte hi hman fo a ngai a ni.
A tlem hle a, heng hmanrua te hian a puih loh chuan doctor te chuan operation an rawt mai thei. Hei hian nerve thenkhat cut a huam a ni. Chutiang surgery hi chi hrang hrang a awm a.
Frey’s syndrome hi natna khirh tak a ni em?
Frey’s syndrome hian a tithinur hle nachungin, i taksa hriselna atan a tichhe lo . Chuvangin chutiang lam hawi chuan dinhmun pawi tak a ni lo. Mahse, i thunun theih loh thawmhnaw tam lutuk chu a zahthlak thei a, i rilru hriselna pawh a nghawng thei bawk . Sawi tawh angin khawtlang nun lungkhamna leh mualphona a thlen thei a ni.
He syndrome i vei a nih chuan tanpuina zawn a pawimawh. Botox® injection ang chi thilte hian thawk hah lutuk control turin a pui thei a ni. Tin, i rilru hriselna a nghawng a nih chuan therapist emaw psychologist emaw pan a tha mai thei bawk.
Frey syndrome hi ven theih a ni em?
Frey syndrome venna tur hian engmah tih theih a awm lo tak zet a ni. Surgeon-te chuan hmai surgery an neih laiin nerve tihchhiat loh nan technique thenkhat hman an tum thin. Mahse heng technique te hi a hlawhtling ngai lo. Technique tin hian a hlauhawmna leh a that lohna a nei vek a, entirnan:
- Surgery neih hun a tipung.
- Frey’s syndrome venna atana a thatna hi a inang lo hle.
- Hliam natna vei theihna chance.
- Operation hnua harsatna awm thei.
I surgeon chuan operation hmain a hlauhawmna, a side effect leh harsatna awm thei te chu a sawipui ang che. Chuvangin, zawhna zawh hlau suh la, i rilru a awm apiang chu i doctor hnenah hrilh rawh .
Engtikah nge doctor i hmuh ang?
I natna lan chhuah dan a zual zel a nih chuan, emaw, Frey syndrome enkawlna i lak a, a thawk tha lo a nih chuan, i doctor nen inbiakna neihpui ngei ang che . I duhthlan tur dang eng nge awm tih a hrilh thei che a ni.
Chaw ei laiin thawmhnaw tam lutuk hi a nuam lo thei a, a ti thinrim thei bawk. Frey’s syndrome hian i nitin nun a tibuai a nih chuan i duhzawng (gusttory sweating) enkawlna atana pui thei tur enkawlna chungchang i doctor nen sawiho rawh.
A tawi zawngin, kan hriat reng tur thilte chu hetiang hi a ni (Take-Home Message):
Okay, chuvangin kan sawi tawh atang hian hriat reng tur pawimawh tak tak thenkhat han thlir ila:
- Frey’s Syndrome hi ei leh in emaw, ei tur ngaihtuah emaw hian hmai ( hmui, hmai, leh beng vel) a thawkrim a, a chang chuan a sen thin.
- Hei hi parotid glands operation hnua nerve tihchhiat vang a ni tlangpui.
- Symptoms hi a na lo emaw, na tak emaw pawh a ni thei.
- Hei hi `Minor starch-iodine test` hmangin hriat theih a ni.
- Damdawi famkim awm lo mah se, Botox® injection ang chi enkawlna hian natna lan chhuah dan a thunun thei a ni.
- Hei hi taksa lama harsatna nei lo mah se, rilru lama lungngaihna a thlen thei a ni. Chuvangin i mamawh chuan tanpuina zawng rawh.
- Heng symptoms te hi i neih emaw, rinhlelhna i neih emaw chuan doctor lam pan a tha ber.
He thu hi in tan a tangkai ngei ka beisei. Hetiang thil hi i lo tawng tawh a nih chuan doctor hnenah sawi hreh suh.
` Frey's Syndrome, chaw ei laiin thawk hah, gustatory sweating, parotid gland surgery, hmai thawmhnaw, neurological disorders











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