I doctor hian nangmah emaw i chhungte tu emaw hnenah Glycerol Phenylbutyrate tih damdawi a pe che em? Damdawi hming danglam deuh deuh a nih avangin zawhna tam tak i nei mai thei. Ngaihtuah buai suh, vawiinah hian he damdawi, a hnathawh dan, a hman dan leh fimkhur tur thilte chauh kan sawi dawn a ni.
A awlsam zawngin, he damdawi hi eng nge ni?
Glycerol Phenylbutyrate (brand name RAVICTI tia hriat bawk) hi urea cycle disorder nei te thisena ammonia awm zat control nan hman a ni
Ngaihtuah teh, kan taksain protein a hman hian bawlhhlawh angin ammonia a siam chhuak thin. Mi hrisel takah chuan urea cycle hian he ammonia hi harmless urea ah a chantir a, zun ah a paih chhuak thin. Mahse urea cycle disorder nei mi pakhatah chuan taksain he hna hi a thawk tha thei lo. Tichuan, ammonia chu taksaah a pungkhawm thei a, thluak leh nervous system a tichhe thei a ni.
He damdawi hian taksa atanga ammonia tam lutuk chu a paih chhuak thei a ni. Mahse thil pakhat chu kan rilruah kan vawng reng tur a ni. Hei hi natna tidam kim thei damdawi a ni lo. Hei hi natna thunun thei damdawi chauh a ni.
A tlangpuiin, he damdawi hi pek i nih hian i doctor-in protein tlem zawk ei tur a pek bik i zawm a ngai ang a, dietary supplement dang pawh i ei leh mai thei bawk.
Damdawi ei hmaa doctor hnena i hrilh tur thilte
He damdawi hi i ei tan hmain a hnuaia thute hi doctor hnenah hrilh hmasak a pawimawh. Heng thilte hi thup suh, i himna atan a pawimawh em em a ni.
| Situation i report tur a ni | Engvângin nge chu chu a pawimawh? |
|---|---|
| Intestinal lama harsatna a awm | Damdawi hi a hip lut hian taksa a nghawng thei a ni. |
| Kidney, liver emaw pancreatic natna emaw a awm thei | Damdawi hi he taksa peng hmang hian taksa atanga chhuak a nih avangin damdawi lam thil a awm chuan a hman dan tur siamthat a ngai mai thei. |
| Allergy nei te pawh a awm | He damdawi, damdawi dang, ei tur, preservative, emaw coloring emaw allergy i neih chuan i doctor hnenah hrilh ngei ang che. |
| Naupai emaw, nau pai tum emaw i nih chuan | Damdawi hian nausen pum chhunga naute a nghawng dawn em tih doctor nen in sawipui tur a ni. |
| Naute chu hnute pek a nih chuan | Damdawi chu nu hnute hmanga naute hnena a kal leh kal loh chungchangah doctor rawn rawh. |
Engtin chiah nge he damdawi hi ka hman ang?
He damdawi hi oral solution angin a awm a, chuvangin heng thilte hi fimkhur hle ang che.
- Take by mouth: Hei hi damdawi ei tur a ni.
- Dik takin teh rawh: Damdawi nena rawn kal spoon, cup, a nih loh leh syringe bik hmangin teh rawh . In lamah teaspoon pangngai hmang suh, a dik vak loh avangin.
- Chaw ei rualin ei: He damdawi hi chaw ei rualin emaw, naute tan chuan formula nen emaw ei a tha ber .
- A hun takah ei rawh: Damdawi hi i doctor-in a tih angin a hun ruatah, hun bituk chhungin ei thin ang che. A pek zat aia tam ei loh tur.
- Titawp suh: Damdawi ei kha doctor thurawn tel lo chuan rang takin chawlhsan suh.
- Naupang hnena pek a nih chuan: He damdawi hi a chang chuan nausen piang thar tan pawh an pe thin. Mahse, fimkhur tur bik a awm. Chuvangin, i naupang enkawltu doctor nen hemi chungchang hi uluk takin sawipui la, thurawn la rawh.
Damdawi hi a dose tihpun (overdose) a nih chuan engtin nge ni ang?
Damdawi i ei tam lutuk nia i hriat chuan i tih hmasak ber tur chu Colombo National Hospital-a National Poisons Information Center -ah phone la. A nih loh leh damdawi in hnai ber Emergency Treatment Unit (ETU) -ah kal rawh. Hei hi tikhawtlai suh.
Damdawi dose i ei loh chuan engtin nge i tih ang?
Dose i ei theihnghilh chuan i hriatreng veleh ei nghal rawh. Mahse, i dose leh tur hun a lo thleng tawh a nih chuan missed dose kha skip la, i dose leh tur chu a hun ruatah ei rawh. Eng thil vang pawhin a rualin dose hnih ei loh tur.
He damdawi nena inzawm thei thil dang
Damdawi dang i ei lai hian he damdawi hi a inzawm thei a, chuvangin i damdawi ei zawng zawng (vitamin, herbal remedies, leh supplement te pawh tel) te chu i doctor hnenah hrilh rawh.
| Ruihhlo chi hrang hrang, buaina thlen thei (entirnan) . |
|---|
|
| Note: Hei hi list kimchang a ni lo. Tin, zu i in emaw, zu i in emaw, ruihhlo dang i hman emaw chuan i doctor hnenah hrilh bawk ang che. |
Damdawi ei avanga side effect awm thei
Damdawi dang ang bawkin he damdawi hian side effect engemaw zat a nei thei a ni. Ṭhenkhat chu a serious a, a then chu a common.
| Side effects te chu doctor hnenah report nghal tur a ni |
|---|
|
| Side effects te chu a awm reng emaw, a buaithlak emaw a nih chuan doctor hnenah hriattir tur a ni |
|
He list-a tarlan loh symptom dang danglam tak i neih chuan i doctor nen pawh chutiang lam chu sawipui rawh.
Engtin nge damdawi chu ka dahkhawm ang?
- Naupang lakah inthiarfihlim rawh.
- Room temperature, 20 leh 25 degree Celsius (68-77 Fahrenheit) inkar ah dah tur a ni.
- Damdawi expire tawh te chu paih chhuak rawh.
Take-Home Thuchah a ni
- Glycerol Phenylbutyrate hi urea cycle disorder tidam thei damdawi a ni lo va, thisen a ammonia level control na tur damdawi a ni.
- He damdawi hi chaw ei rualin ei fo la, a nena rawn kal tehna bik hmangin.
- I doctor-in protein tamna ei tur a tih ang chiah kha zawm rawh.
- Doctor thurawn tel lo chuan damdawi ei kha bansan suh.
- Damdawi i ei tam lutuk emaw, side effect na tak i neih chuan doctor thurawn la nghal rawh.
- Damdawi dang i ei zawng zawng (vitamin leh hnam damdawi te pawh tel) i doctor hnenah hrilh rawh.











💬 Comments (0)
Comment a la awm lo. Hetah hian i comment hi a vawikhatna atan add rawh.
I comment kha add rawh