I fa te hian thinlung lam harsatna a nei em? Hypoplastic Aortic Arch chungchang hi han sawi ila!

I fa te hian a chang chuan hnute pek a harsat em? Thâwk a lak hian a hma aia chau zawkin a inhria em? A nih loh leh a sen hring leh thawmhnaw hring ang maiin a lang em? I fate chunga heng thilte hi a lo thlen hian nu leh pa i nih angin i lungkham hle thin tih hi thil pangngai tak a ni. A chang chuan hei hi a chhan chu pianpui thinlung natna (congenital heart condition) a ni thei bawk. Vawiin hian naute thinlunga lo awm thin, mahse hriat hmasak a, uluk taka enkawl a nih chuan tihdam theih a nih thu kan sawi dawn a ni.

Hypoplastic Aortic Arch chu eng nge ni?

A awlsam zawngin, Hypoplastic Aortic Arch , a then chuan Aortic Arch Hypoplasia (AAH) tia koh thin hi piansualna a ni a, i naute thinlung hmun thenkhat , aorta -ah a awm thin. Hetiang hian han ngaihtuah teh, aorta hi kan taksa pum puia thisen phurtu thisen kalna kawng lian tak ang mai a ni. Thinlung atanga intan a ni a, taksa pum puiah oxygenated thisen a keng tel a ni. Cane ang maia siam a ni a, a curve deuh bawk. Cane chung bera curve chu aortic arch an ti a, chu chu ‘aorta arch’ tihna a ni.

‘Hypoplastic’ tih thumal hian ‘a lo thanglian tha lo’, ‘te’ tihna a ni. Chuvangin, naute hypoplastic aortic arch nei chuan aortic arch a lo thang lian lo hle. Chu chu, chu hmun chhûnga hawnna, a nih loh leh a diameter chu a nih tûr aia tawi zâwk a ni tihna a ni. Tui pipe a inkhar ang bawkin, aortic arch a zim chuan, thisen chu thinlung atanga taksa hnuai lam, a hnuai lam aorta kal tlangin a luang a harsa ta a ni Hei hian taksa pum puia thisen a thlen chu a ti tlem thei a ni.

He natna hian tute nge a nghawng ber? Lung natna dang nena inzawmna a awm em?

Aortic arch hypoplasia (AAH) hi a mah chauhin a awm thei. Mahse, congenital heart defect dang , coarctation of the aorta an tih nen hmuh tur a awm fo . Hei hi aorta hmun dang, a tlangpuiin ductus arteriosus bula awm, thisen kalna kawng bik, a tlangpuiin nausen pum chhunga awm thin, a zim thinna dinhmun a ni.

Chuvangin i naute doctor chuan, "I naute hian aorta-a coagulopathy a nei a, aortic arch hypoplasia a nei a ni," a ti mai thei. Chu chu aorta chu a tawi tihna a ni a, hmun khatah chauh ni lovin, section sei takah a awm tihna a ni.

Tin, AAH vei naute hian thinlung lam natna dang an nei thei bawk. Entir nan:

• Atrial Septal Defect (ASD) : Thinlung chunglam pindan pahnih inkar bang chhunga khur awm.
• Atrioventricular Septal Defect : Thinlung chamber inkar bang-a chhiatna khirh tak a ni.
• Bicuspid Aortic Valve leh Aortic Valve Stenosis : Aortic valve chhiatna leh a tawi.
• Hypoplastic Left Heart Syndrome (HLHS) : Thinlung veilam hi a lo thang tha lo.
• Patent Ductus Arteriosus (PDA) : Thisen kalna kawng ductus arteriosus an tih, nau piang hnua khar tur chu a inhawng reng a.
• Shone’s Syndrome : Thil tha lo engemaw zat inzawmkhawm, thinlung veilam lama thisen kal tibuaitu.
• Ventricular Septal Defect (VSD) : Thinlung hnuai lam chamber pahnih inkar bang chhunga khur awm.

Hetiang thinlung natna pakhat aia tam neih hi enkawl dan tur ruahmanna siam hunah a pawimawh hle. A chhan chu naute thinlunga thil awm dan (complex, specific conditions) nena inmil, surgery emaw, enkawlna ruahmanna emaw siam a ngai a ni.

Naupangin he natna hi a neih chuan eng symptoms nge a neih?

Naute aorta coarctation leh aortic arch hypoplasia nei te hian an pian hnu lawkah symptoms an nei tan tlangpui . I naute piang thar, in tlemte in hnua chau tawh chu thawk harsa ang maiin han mitthla teh. A châng chuan an thawkrim a, bluish-white color an lo ni ṭhin. Nu tan hetiang thil hmuh hi a va hlauhawm tak em, a dik em?

A lan chhuah dan tlangpui chu:

• Fast pulse : Pulse rate a chak lutuk.
• Chauhna : Naute hian a chau hle tih a hria a, a bik takin nau hnute a pek hian a chau hle.
• Vun dum emaw, vun dum emaw : A chang chuan vun hi a dum thei bawk.
• A rilru a hah lutuk .
• Tap fo thin, thinrimna .
• Thâwk rang emaw thawkrim tak emaw .
• Chaw pek chungchanga harsatna: Bawnghnute in duh lo, a nih loh leh tlem a in hnuah a chawlhsan.
• Taksa hnuai lam a pulse chak lo : A bik takin keah chuan femoral artery- a pulse hi palpated a nih chuan a chak lo hle.

I naute hian heng symptoms pakhat emaw a aia tam emaw a neih chuan doctor thurawn lak nghal a pawimawh hle .

Engvangin nge hetiang hi a lo awm? A chhan engte nge ni?

AAH hi pianpui heart defect a ni a . Nausen pum chhunga a la awm laia thil thleng a ni. Researcher te chuan he congenital heart defect chi hrang hrang hi a chhan dik tak hi an la chhui chhuak mek a ni.

Mahse hriat chhuah chu naute naupai kar hmasa berah aortic arch a lo thang tha lo a nih chuan he natna hi a awm thei tih hi a ni .

Engtin nge hei hi i hmuh? Test te chu engte nge ni?

Doctor-te chuan hei hi a natna hriat nan an hmang thin.Imaging test bik neih a ni. Heng test te hi naute pian hnu lawka tih thin a ni tlangpui.

AAH hriat theihna atana test hman berte chu:

• Cardiac Computed Tomography (CT scan) hmanga tihchhuah a ni.
• Magnetic Resonance Angiogram (MRA) hmanga enfiah a ni.
• Transthoracic Echocardiogram (TTE) : Hei hi thinlung ultrasound scan ang a ni.
• Cardiac Catheterization : A chang chuan he test hi tih a ngai bawk.

Heng test-te hian naute thinlung insiam dan, chu chu a chhungril peng hrang hrangte inrem dan chu chipchiar takin a en thei a ni. Naute hian thinlung lama harsatna dang a neih leh neih loh an hre thei bawk. Heng zawng zawng hi an khawlkhawmna hmang hian doctor-te chuan naute tan enkawlna tha ber tur an ruahman a ni.

AAH a awm leh awm loh hriat nan doctor-te chuan naute aortic arch lian leh te an en thin. A bik takin, a diameter , an teh a, chu chu a chhunga hawnna zau zawng a ni. He tehna hi naute aorta hmun dang (entir nan, ascending aorta emaw descending aorta) diameter nen khaikhin a ni. Heng value te hi aortic arch diameter a tawi lutuk em tih hriat nan hman a ni.

Aotic arch hmun hrang hrang hi tlem han zir ila.

I naute doctor-in he natna hi a sawi hian aortic arch hmun hrang hrang a sawi thei a ni. I ngaihtuah mai thei, "Aortic arch hi hmun dangah a inthen em? Chu chu aorta lian zawkah a awm lo em ni?" Ni e, chu chu a dik a ni. Aortic arch hi aorta chhunga hmun te tak te, "cane ang" a ni. Mahse, aorta hmun zawng zawng ang bawkin aortic arch hian thisen kalna (arteries) a nei a, chu chu kawng hrang hrangah a branch off a ni. Main road-in side road a neih ang bawkin. Doctor-te chuan heng thisen kalna kawng hrang hrangte hi ramri atan an hmang a, aortic arch hmun bik pakhat bul tanna leh tawpna hmun chu an chhinchhiahna a ni. He "map" hian AAH hmuhchhuah leh enkawl dan tur ruahmannaah a pui hle.

I naute doctor-in a sawi theih tur aural arch hmun thenkhat chu hetiang hi a ni:

• Proximal Transverse Arch : Hei hi naute Brachiocephalic Artery (a then chuan Innominate Artery an tih) leh Left Common Carotid Artery inkarah a awm a. Hei hi thinlung hnaih ber a ni.
• Distal Transverse Arch : Hei hi veilam common carotid artery leh veilam subclavian artery inkarah a awm a .
• Aortic Isthmus : Hei hi left subclavian artery leh a hmaa kan sawi tawh thisen kalna Ductus Arteriosus an tih inkar ah a awm a .

I naute doctor chuan i naute aural arch-a narrowing awmna hmun dik tak chu a ruat ang a, chubakah a narrowing zau zawng pawh a hre bawk ang. He thu hian enkawlna ruahmanna a kaihruai ang.

Hei hi eng enkawlna nge ni?

Hypoplastic aortic arch nei naute chuan an dinhmun siamthat nan heart surgery an mamawh dawn a ni . I naute thinlung surgeon chuan i naute hian eng ang surgery nge a mamawh dawn tih a hrilhfiah ang che. I naute thinlung chhiatna dang leh a insiam dan azirin surgery kalphung a inang lo thei. Thoracotomy , chu chu i naute rilru veilam sir a incision te tak te, a nih loh leh sternotomy, chu chu i rilru lai tak atanga incision tih a ngai mai thei.

Surgery tih dan tlangpui chu resection with extended end-to-end anastomosis tih a ni. He surgery hi naute aorta coarctation leh aortic arch hypoplasia nei tan a tangkai hle. Hetiang tih danah hian surgeon chuan aorta a tawi zawng chu a la chhuak a, aorta hnuai lam (aorta chhuk) chu a la a, aortic arch-a incision sei deuh deuhah a dah a ni.

He surgery beiseina chu naute aorta kaltlanga thisen kal dan tihchangtlun a ni a, naute taksa peng leh tissue te hian oxygen tamna thisen an dawng tling thei ang.

Ka naute dam lehna tur beiseina chu eng nge ni?

He zawhna chhanna tha ber chu i naute doctor hi a ni. A chhan chu naute damna chu thil tam takah a innghat a ni. A bik takin, pianpui thinlung natna dang a awm leh awm loh hian nghawng lian tak a nei a ni.

A tlangpuiin, naute aotic arch hypoplasia an tih natna enkawl tawhte hian an naupan laiin a hnuaia harsatnate hi an neih theihna chance a sang zawk a ni:

• An aorta a narrow leh zel .
• Thisen sang (Hypertension) .
• Ei leh ei harsatna : Hei hi operation laiin nerve a chhiat chuan a thleng thei (hei hi a tlem hle).

Heng hlauhawmnate leh enkawl dan tur te hi i naute doctor nen sawiho rawh.

Hetiang dinhmun hi ven theih a ni em?

Congenital heart defects hypoplastic aortic arch ang chi hi chu ven theih a ni lo mai thei . Mahse, naupai hrisel tak neih theihna tura i doctor thurawn zawm hian he natna emaw, chhiatna dang emaw i neih theihna tur a ti tlem thei a ni.

A tlangpuiin naupai lai hian heng thilte hi pumpelh ngei ngei tur a ni :

• Zu .
• Meizial zuk, vaping leh zuk leh hmuam thil zawng zawng kha pumpelh rawh . Tin, secondhand smoke pawh pumpelh bawk ang che .
• Dan loa ruihhlo, a bik takin cocaine .

Tin, chubakah, i ta pawh.Nau neih hmaa checkup neih fo a pawimawh hle bawk. Hriselna lama harsatna dang i neih chuan naupai hma leh i naupai chhung zawnga chutiang dinhmun chu enkawl turin damdawi lam thurawn zawng rawh.

Naute chu operation hnuah engtin nge kan enkawl ang?

Naute tinte mamawh chu zai zawhah a inang lo thei a, chuvangin hun rei lote leh hun rei tak chhunga i naute enkawl dan tur i fa medical team-te zawt la a tha ber.

Doctor i zawh theih tur zawhna thenkhat chu hetiang hi a ni:

• Ka haw hunah engtin nge ka fa ka enkawl ang?
• Ka fa chu eng damdawi nge ka pek ang? Eng chen nge ka pek ang?
• Naupang taksa emaw, thluak emaw hnathawhna tura pui turin therapies eng emaw zat a ngai em?
• Naupang thiltih danah khapna a awm em?
• Engtikah nge ka fa chu daycare-a tirh hi a him ang? Eng thupek bik nge ka pek ang?
• Ka fa hian enkawlna dang emaw, operation emaw a mamawh belh dawn em?

Nu leh pa nih hi a harsa fo thin. Mahse hypoplastic aortic arch (AAH) ang chi thinlung natna nei naupang nena khawsak hian nitin harsatna thar a thlen thei a ni. Doctor-te thusawi leh enkawl dan tur thenkhat chu hriatthiam harsa tak niin a lang thei. Chu chu thil pangngai a ni a, nangmah chauh i ni lo. I fa doctor hnenah i tanpui thei tur resources leh support group te zawt rawh. Nang leh i chhungte tanpuitu khawtlang siam hian lungkhamna a tihziaawm thei a, i fate mamawh hmasawn zel turin chakna a pe thei bawk che a ni.

Kan sawi tawh kha i hre reng ang u (Take-Home Message)

• Hypoplastic Aortic Arch (AAH) hi naute thinlunga thisen kalna kawng lian ber aorta arch a lo thang tha lo a, chu chuan arch chu a ti tawi a ni.
• Hei hian thinlung atanga taksa peng danga thisen kal a harsat phah a ni.
• Hetiang dinhmun hi thinlung natna dang Coarctation of the Aorta tih nen hmuh dun a ni fo thin.
• Nausen pian tirh lamah hah lutuk, thawk harsa, vun sen hring ang chi symptoms te hi naute dam tirh lamah a lo lang thei a ni.
• He natna hi special scan hmangin hriat theih a ni.
• Enkawlna chu thinlung surgery a ni .
• Damdawi lam thupek dik taka zawm leh operation hnua hun rei tak enkawl zawm hi a pawimawh hle.
• Naupai laiin nungchang hrisel zawm hian nau piangsual thenkhat awm theihna a ti tlem thei a ni.
• Nangmah chauh i ni lo. Doctor leh support group te hnen atangin tanpuina dawng rawh.

He thu hi i tan a \angkai ngei kan beisei. I fa te chu dam thuai turin duhsakna kan hlan a che!

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