A chang chuan mitmeng (squint) hi thil pangngai a ni. Mahse i hmai sir khat, i mit, i hmui emaw, i hmui emaw ang chi chu thunun theih lohvin a rawn inher tih i hmuh chuan ngaihtuah tur a ni. He natna hi damdawi lam chuan Hemifacial Spasm tia hriat a ni. Tlem a buaithlak thei viau laiin, enkawlna tha tak a awm avangin ngaihtuahawm tur a awm lo. Chipchiar takin sawi ila.
A awlsam zawngin, Hemifacial Spasm hi eng nge ni?
Hemifacial Spasm hi neurological condition a ni a, i hmai sir khata taksa ruh te chu a inher nawn fo thin a, thunun theih lohvin a awm thin. Hei hi hun kal zelah a na zual thei.
- "Hemifacial" tih awmzia chu "hmai chanve" tihna a ni.
- "Spasm" tih awmzia chu "muscle twitching" tihna a ni.
He natna hi puitling kum 40 leh 60 inkar zingah a tam ber a, chubakah hmeichhiate hian mipa aiin he natna hi a let hnih velin an nei tam zawk bawk.
Hei hi kan taksa peripheral nervous system-a awm, movement disorder tia sawi theih a ni bawk.
Hemifacial spasm chi hrang hrang lian ber ber a awm em?
Ni e, hei hi chi hnih lian tak a awm a, chu chu hun kal zelah a natna lan chhuah dan a zirin a ni.
1. Primary Hemifacial Spasm: Hetiang chi spasm-ah hian mit vel ruh (muscle)-ah hian twitching hi a intan thin. Zawi zawiin, thla tam tak emaw, kum tam tak chhung emaw pawhin hmai hnuai lam thlengin a darh ta a ni.
2. Secondary Hemifacial Spasm: Hetiang chi ah hian hmai chunglam leh hnuai lam pahnih a inher hi a rualin a intan deuh ber thin. A tirah chuan a lo kal a, a kal zel a, mahse a hnuah chuan a awm reng thei a ni.
Hetiang natna lan chhuah dan hi engte nge ni?
A lan chhuah dan ber chu i hmai sir khata taksa ruh (muscles) te chu thunun theih lohvin a inher chhuak a ni. Hei hi dinglam aiin veilam lamah a tam zawk. Hmai sir lehlamah a nghawng hi a tlem hle.
Hetiang hian symptoms te hi a tlangpuiin a intan dan leh a kal zel dan chu a ni:
- Mit khap atang hian a intan thin . Hei hi a lo thleng a, a kal zel bawk.
- Hun engemaw chen hnuah chuan mit chu a mah chauhin a khar thei .
- A dawtah chuan i mitmeng chu a pianphungah a lo thang lian ang maiin i hria mai thei .
- A hnuah chuan hmai hnuai lam ruh te pawh a nghet tan ta a ni. Hei hian hmui chu a sir khatah a hruai thei a ni .
- A tâwpah chuan hmai sir khat pum puia ruhte chu a inzawm tlat thei a ni.
Heng spasm te hi a na lo tlangpui. Amaherawhchu, vantlang hmaa i awm laiin an nuam lo hle thei a, an zahthlak thei hle bawk. Stress, hahna, ei leh in leh lungkhamna te hian a thlen thei bawk.Hetiang hun lai hian heng symptoms te hi a zual thei hle. Mi thenkhat chuan mut lai pawhin heng spasms te hi an nei thin , chu chuan mut a tibuai thei.
Symptom dang a awm bawk
Mi thenkhat chuan heng symptom lian ber berte bakah hian thil dang an tawng thei bawk.
- Beng chhunga "ticking" ri hriat
- Beng a na
- Hriatna hloh (a bik takin secondary) .
Engvangin nge hetiang hi a lo awm? A chhan engte nge ni?
Hemifacial spasm thlentu ber chu hmai nerve (seventh cranial nerve)-a hun rei tak pressure a awm vang a ni a, hei hi hmai chetna control tu nerve lian tak a ni.
Kan hmai chetna thununtu he main nerve bulah chiah hian thisen kalna kawng chu hrual a nih chuan eng nge thleng ang tih han ngaihtuah teh? Tui pipe chunga lung tla ang mai a ni. Tichuan chu nerve atanga signal lo chhuak chu a tibuai ang. Nerve venhimna khuhna (`myelin sheath`) chu a chhe dawn a ni. Heng signal tihbuai avang hian taksa ruhte chu duh lohvin a inher tan ang.
Hei hi primary hemifacial spasm thlentu ber a ni .
Secondary Hemifacial Spasm hi damdawi lam thil dang emaw, chhan dang emaw avanga hmai nerve-a pressure vang a ni. A chhan thenkhat chu:
- Facial nerve bulah hliam a awm
- Bell’s palsy ang chi natna te
- Multiple sclerosis emaw stroke emaw ang chi natna avanga thluak bul a chhiat
- Thluaka thisen kalna kawng lama harsatna, entirnan `brain aneurysms`
- Beng natna, otitis media ang chi te
- Parotid gland-a tumor lo awm, cancer emaw cancer lo emaw pawh nise
- Luruh hnuai lam structure lama harsatna awm
Engtin nge doctor hian hei hi a hmuh theih?
Heng symptoms te hi i neih chuan doctor in taksa a enfiah hmasa ang che a, neurological exam a ti ang.
Tichuan, natna khirh tak dang, natna lan chhuahna thlentu chu paih chhuah theih nan leh hemifacial spasm awm chhan dik tak hriat theih nan MRI scan neih a tha fo thin. Primary type-ah chuan nerve compress tu thisen kalna chu MRI-ah hmuh theih a ni tlangpui.
A châng chuan heng symptoms te hi thil dang nen a inang thei a, chu chu `blepharospasm` (mitmeng chauh a hrualna) emaw `complex partial motor seizures` (epilepsy chi khat) emaw a ni thei. Chutiang hunah chuan doctor chuan eng nge a nih tak tak tih finfiah an duh chuan EMG (Electromyography) tih test pawh a ti thei bawk.
Hei hi eng enkawlna nge ni?
Enkawlna tum ber chu hmai a inthlak tam lehzual loh nan a ni. A natna chhan leh a nasat dan azirin enkawlna kawng hrang hrang a awm.
| Enkawl dan tur | A hnathawh dan | Fimkhur tur thilte |
|---|---|---|
| Botulinum toxin (Botox®) injection hmanga tihdam theih a ni | Hei hi first-line treatment hman tam ber a ni. He injection hian hun eng emaw chen atan taksa ruh inzawmkhawmte chu a ti nem a, a tichak lo bawk. | He vaccine hi thla 3-4 danah pek thin a ni . Hun eng emaw chen atana side effects, mit natna leh mitmeng tlahniam te pawh a awm thei. |
| Damdawi ei tur | He option hi injection emaw surgery emaw duh lo tan a awm a ni. Hemi atan hian damdawi chi hrang hrang anti-seizure damdawi (carbamazepine, gabapentin) leh muscle relaxant (baclofen) te hman a ni. | Hengte hian mi zawng zawng tan hna a thawk lo a, mutthilh leh hah ang chi side effect a thlen thei bawk. |
| Inzai | Hei hi he dinhmun chinfelna awmchhun a ni. He surgery, ``Microvascular decompression'' tia koh hian thisen kalna kawng nerve press chu lakchhuah a, a inkarah cushion te tak te dah a ni. | Hei hi natna khirh tak nei leh Botox injection hlawhtling lo tan chauh hman tur a ni. Surgery neih hian hlauhawmna engemaw zat a awm (e.g., hriatna hloh, hmai nerve tihchhiat). |
Hemifacial Spasm hi a hlauhawm em?
Hemifacial spasm ngei pawh hi taksa lamah a hlauhawm lo. Mahse, a chhan bulpui (underlying medical condition) chu a ni.(e.g. thluaka tumor) hi a hlauhawm thei hle. Chuvang chuan symptoms a lan veleh Doctor pan vat a pawimawh.
Tin, he dinhmun hian nunphung a nghawng thei bawk.
- Mut tibuai thei
- Rilru lama harsatna, khawtlang lungkhamna, lungkhamna, leh lungngaihna te
- Mit khap tlat avanga accident thleng thei, lirthei khalh lai ang chi
Chuvangin, i hmai a hrual tan a nih chuan, ‘Hei hi thil pakhat chauh a ni mai thei’ tih ngaihtuahin ngaihthah suh. Doctor hmu ngei tur leh a chhan hriat chian a pawimawh hle.
Hetiang dinhmun hi a tlangpuiin a mah chauhin a dam lo. Mahse, 10% velin a takin a reh tih an sawi. Hetiang thil hi engtin nge a awm tih chiang taka hriat a la ni lo.
Hemifacial Spasm hi nitin nun tibuaitu a ni tak zet a ni. I taksa thunun thei lo anga inhriat chu thil tha tak a ni lo. Mahse a tha ber chu tunah chuan a enkawlna tha tak tak a awm ta a ni. I hmai sir khat pawh a inher reng nia i hriat a, a na zual zel ang tih i hriat chuan doctor pan ngei ngei tur a ni. A enfiah thei che a, a chhan a zawng thei che a, i tana enkawlna tur ruahmanna tha ber a pe thei che a ni.
Take-Home Thuchah a ni
- Hemifacial Spasm hi neurological condition a ni a, i hmai sir khatah control theih loh muscle spasm a awm thin.
- Hei hi thisen kalnain hmai nerve a press vang a ni fo thin a, mahse damdawi lam thil dang vang pawh a ni thei bawk.
- Hei hi hrehawm lo mah se, nitin nun tibuaitu lian tak a ni thei. Stress hian symptoms a tizual thei.
- Botox injection hi a hlawk em em a, hman lar tak a ni. Nausen natna khirh tak tan chuan operation hi permanent solution atan pawh duhthlan tur a ni.
- Heng symptoms te hi i neih chuan ngaihthah lova Doctor pan a, diagnosis leh treatment mumal tak dawn a pawimawh hle.











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