I doctor-in nangmah emaw, i fa duh tak emaw Nitisinone a pek hian zawhna tam tak neih hi thil pangngai a ni. Hei hi mi zawng zawngin kan vei thin natna tlanglawn damdawi a nih loh vang a ni. Chuvangin vawiin hian he damdawi Nitisinone tih hi, a tih tak tak dan te, a hman dan tur te, eng fimkhurna nge i tih tur tih te, chu zawng zawng chu awlsam takin i hrethiam thei ang bera sawi ila.
Hei hi eng damdawi nge ni? Nitisinone hi engtin nge a awm?
A awlsam zawngin sawi ila, Nitisinone hi damdawi a ni a, kan taksain amino acid tyrosine an tih chu a tikhawtlai a, a tichhe nasa hle bawk. Tyrosine hi kan taksaa protein siamna atana hman tur building block angin han ngaihtuah teh.
He damdawi hi a bik takin natna hmuh tur awm lo tak, inherited condition Hereditary Tyrosinemia Type I. Tichuan taksaah a lo pungkhawm a, toxic substance-ah a chang a, chu chuan liver, kidney leh nervous system a tichhe thei a ni. Chuvangin Nitisinone hian a tih chu chutiang thil tha lo siam chhuah chu a titawp a ni.
Damdawi ei tan hmaa doctor hnena i hrilh tur thilte
He damdawi hi i tan hmain doctor hnenah heng thilte hi chiang takin i hrilhfiah hmasa tur a ni. Hei hi i himna atan a pawimawh hle.
- Nitisinone emaw damdawi dang emaw, ei tur emaw, dye dang emaw allergy i neih chuan.
- Naupai emaw, nau pai tum emaw i nih chuan.
- Nu hnute pe lai i nih chuan.
He damdawi hi engtin nge ka hman ang?
Damdawi hi doctor-in a sawi ang chiah, a dose dik takah ei a pawimawh hle.
- Ei dan: A chang chuan pill hi tui tlemteah i hmin thei a, oral syringe hmangin i fa hnenah i pe thei bawk. A nih loh leh, pill chu i hrual a, applesauce ang chi thil nen tlem i pawlh a, i fa hnenah i pe thei bawk. Amaherawhchu, engpawh ti ila, damdawi siam zawh veleh i hmang nghal tur a ni.
- A hun takah: Nitin hun khata i damdawi ei thin kha tih danah siam rawh. Doctor-in a tih aia tam ei loh tur a ni.
- He damdawi hi ei nghal vat suh: Doctor thurawn tel lo chuan he damdawi hi ei kha titawp ngai suh. Chutianga tih chuan i dinhmun a tichhe thei a ni.
He damdawi hi naupang te te tan pek theih a ni em?
Ni e, he damdawi hi nausen piang thar, he natna nei tan pawh pek theih a ni. Mahse naupang enkawltu uluk taka tih tur a ni. Naupangte hnena pek dawnin ngaihtuah tur bik engemaw zat a awm.
Hriat tur pawimawh: He damdawi hi i tan chauh pek a ni. Eng vangin pawh midang hnenah share suh.
Damdawi ei huna ngaihtuah tur bikte
He damdawi i ei lai hian thil pawimawh tak tak pahnih ngaihven tur a awm a.
1. Test leh check-up hun ruat sa
Doctor-in a tih angin clinic-a check-up neih a pawimawh hle. He damdawi i ei lai hian i thisen count leh liver function endik nan thisen test pawimawh tak tak i neih fo a ngai dawn a ni. Heng test te hi skip suh.
2. Ei leh in bik
Hei hi a pawimawh ber a ni . Ei leh in bik zawm hi he damdawi ei ang bawkin a pawimawh a, a aia pawimawh zawk pawh a ni.
He damdawi i ei lai hian ei leh in bik i zawm a ngai dawn a ni. I ei leh in ah hian Tyrosine leh Phenylalanine an tih amino acids te hi i tihtlem a ngai dawn a ni. Hemi chungchang hi i doctor leh a tul chuan sorkar damdawi inah nutritionist nen inbia la, an thupekte chu uluk takin zawm rawh. He diet hi uluk taka i zawm loh chuan damdawi hlawkna kimchang i hmu lovang.
He damdawi hian eng side effect nge a neih theih?
Damdawi dang ang bawkin Nitisinone hian side effect engemaw zat a nei thei a ni. Hengte hi chi hnih ah then ila.
| Side effects awm thei chu doctor hnenah hriattir nghal tur a ni | |
|---|---|
| Allergy natna lan chhuah dan | Vun vun rawng, hnim hring, hmai, hmui emaw lei emaw a hring. |
| Mit a inthlak danglam thin | Mit a danglam, mit a sen, mit na, êng hriatna. |
| Liver lama harsatna a awm | Mit emaw vun emaw a sen, zun dum, tarry stool, pum dinglam chunglam na. |
| Symptom na tak dang a awm bawk | Thil danglam tak, hliam emaw thisen chhuak emaw, hah lutuk, khawsik tih hriatna, ei duh lohna, rilru hahna, leh i kutphah leh i kephah na tak takte. |
| Side effects nasat loh tlangpui, mahse a awm reng chuan doctor hnenah hriattir tur a ni | |
|---|---|
| Kawthalo | Stool loose takah chuan kal |
| Vun a vawt | Vun a vawt |
| Sam tlakchhamna | Sam tlakchhamna |
He list-ah hian side effect awm thei zawng zawng a tel lo. Thil dang danglam tak i hmuh chuan i doctor nen inbia ang che.
Dose i miss a, i in tam lutuk chuan engtin nge i tih ang?
Damdawi dose khat ka ei loh chuan engtin nge ni ang?
Dose i ei theihnghilh chuan i hriatreng veleh ei nghal rawh. Mahse i dose leh tur hun a lo thleng tawh a nih chuan missed dose kha skip la, i dose lo awm tur chu a hun ruatah ei rawh. Dose theihnghilh tawh chu siam that nan double dose ei ngai suh.
Damdawi ka ei tam lutuk chuan engtin nge ni ang?
He damdawi hi i ei tam lutuk nia i hriat chuan Colombo National Hospital-a National Poisons Information Center-ah phone nghal rawh . A nih loh leh, damdawi in hnai ber Emergency Unit (ETU) ah a rang thei ang bera kal rawh.
Engtin nge damdawi chu ka dahkhawm ang?
- Naupangte hmuh theih lohna hmunah dah rawh .
- Room temperature (20 leh 25 degree Celsius inkar) ah dah tur a ni.
- Damdawi expire tawh chu paih vek rawh.
Take-Home Thuchah a ni
- Nitisinone hi damdawi bik a ni a, doctor-in a tih angin leh a zat tur angin ei tur a ni.
- He damdawi ei bakah hian ei leh in bik (tyrosine leh phenylalanine tlem) zawm a pawimawh bawk .
- Damdawi lam thurawn tel lo chuan damdawi ei kha bansan ngai suh.
- Ni ruat saah clinic-ah kal la, thisen test tul zawng zawng tihsak vek rawh.
- Mit sen emaw, hliam danglam tak emaw i hmuh chuan doctor hnenah hriattir nghal rawh.
- Damdawi te chu naupangte hmuh theih lohna hmun him takah dah tur a ni.











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