Nangmah emaw i chhungte zingah emaw Phenylketonuria tih natna hi i nei em? Chutiang a nih chuan i doctor chuan Pegvaliase tih damdawi a pe che a ni mai thei. Hei hi damdawi bik deuh a nih avangin zawhna leh ngaihtuahna engemaw zat neih hi thil pangngai a ni. Chuvangin vawiinah hian he damdawi chungchang leh a hman huna i hriat chian tur thilte han sawi ila.
He Pegvaliase vaccine hi eng nge ni?
A awlsam zawngin phenylketonuria (PKU) hi kan taksain amino acid phenylalanine an tih chu a ei tha thei lo tihna a ni. Hei hi protein tamna eitur kan ei zingah hian a awm tlangpui a ni. He phenylalanine hi PKU vei taksaah a awm khawm chuan thisenah a pungkhawm a, hun kal zelah a bik takin thluak a tichhe thei a ni.
Chuvangin, he Pegvaliase injection hian a tih chu thisena chu duh loh, phenylalanine tam lutuk level a tihhniam hi a ni. A tlangpuiin brand name Palynziq hmanga lo awm a ni.
Mahse hei hi hriat reng a pawimawh: Hei hi damdawi zawng zawng a ni lo. Mahse, thisena chhiatna thlen thei zat control-na atan a pui thei a, natnain a tihchhiat pawh a ti tlem thei hle.
Damdawi ei hmaa doctor hnena i hrilh tur thilte
He damdawi hi i tan hmain heng thilte hi chiang tak leh dik takin i doctor nen inbiak hmasak phawt a pawimawh hle. Engmah thup suh.
- Pegvaliase emaw damdawi dang emaw, ei tur emaw, dye dang emaw allergy i neih chuan min hrilh rawh.
- Naupai emaw, naupai beisei emaw i nih chuan sawi ngei ngei tur a ni.
- Nu hnute pe lai i nih chuan chu chu i doctor hnenah pawh hrilh bawk ang che.
Heng thute a\ang hian he damdawi hi i tan a tha em tih chu doctor tan a awlsam zawk ang.
Vaccine hi engtin nge dik taka hman theih ang?
Hei hi vun hnuaia injection a ni. I doctor emaw nurse emaw chuan in lama i pek dan tur chiang takin a hrilh tlangpui ang che. Heng thupekte hi dik taka zawm a pawimawh hle.
- Dose dik tak, a hun takah ei rawh: Damdawi hi i doctor-in a pek angin a pek hun leh a zat dik takah chauh ei thin ang che. A zat aia tam ei ngai suh.
- Needle leh syringe te chu uluk takin paih rawh: Needle leh syringe hman tawhte chu bawlhhlawh bawmah paih ngai suh . Chu ai chuan sharps container bik ah dah zawk ang che. I neih loh chuan i doctor hnenah pakhat dil rawh.
- Thu hriat tur bik lehkhabu (MedGuide):Enkawlna i neih apiangin ‘MedGuide’ bik pek i ni ang a, chu chu damdawi chungchang chipchiar taka tarlanna lehkhabu a ni. Ngun takin chhiar fo ang che.
Damdawi dose khat ka ei loh chuan engtin nge ni ang?
Dose i miss nghal a nih chuan lungngai suh. Dose hloh chu ei suh. Dose dang chu i hun pangngaiah ei thin ang che. Double dose ei ngai suh.
Ka overdose a nih chuan engtin nge ni ang?
Damdawi i ei tam lutuk nia i hriat chuan Colombo National Hospital-a National Poisons Information Center-ah call nghal la, a nih loh leh damdawi in hnai ber Emergency Treatment Unit (ETU)-ah kal nghal rawh. Hei hi emergency a ni a, tihkhawtlai suh.
He damdawi hman huna fimkhur bik tur thilte:
He part hi a pawimawh hle. He damdawi i hman chhung zawng hian heng thilte hi i fimkhur tur a ni.
Allergic Reaction na tak a awm
He damdawi ei avanga hlauhawm ber leh pawi ber chu allergy na tak, emaw, damdawi lam atanga thlir chuan anaphylaxis emaw a awm theihna hi a ni. Hei hi nunna atana hlauhawm emergency a ni.
Hemi avang hian i doctor chuan epinephrine auto-injector a pe fo ang a, chu chu emergency-a hman theih tur injection bik a ni. I hnenah i vawng reng tur a ni.
Shot i la a, hun rei lote chhungin thawk harsa i ti a, i hmai leh i hmui a lo hring a, i lu a buai hle tih han ngaihtuah teh. Chu chuan allergy na tak i nei tihna a ni thei. Chutiang a nih chuan chu epinephrine shot chu i la nghal tur a ni a, damdawi in emergency room (ETU)-ah a rang thei ang bera kal tur a ni.
Hetiang hlauhawmna avang hian i doctor chuan injection i pek lai leh i pek hnu darkar khat chhung chu mi pakhat tal nei turin a hrilh fo ang che. Hei hi allergy na tak i neih chuan chu mi chuan a puih theih nan leh damdawi inah a hruai thuai theih nan a ni.
Medical check-up neih fo leh ei leh in control
- Medical test: He damdawi i ei lai hian i doctor chuan a lo en reng ang che. Tin, i thisena phenylalanine awm zat enfiah turin thisen test mumal (thisen hnathawh) a ti bawk ang. Hengte hi skip suh.
- Diet: PKU atana i zawm tur special diet kan sawi kha i hre reng em? He damdawi hi i ei lai hian i tana special diet an pek pawh i zawm tur a ni. Doctor rawn hmasa lovin i ei leh in lamah engmah tihdanglam suh.
Damdawi hmansualna (side effects) te
Damdawi dang ang bawkin he damdawi hian side effect engemaw zat a nei thei. Lungngai suh, mahse hengte hi fimkhur a pawimawh.
| Side effect/symptom a awm thei | Hrilhfiahna |
|---|---|
| Heng symptoms te hi i neih chuan doctor hnenah hrilh nghal rawh. | |
| Allergy na tak a nei | Vun rawng, vun na tak, hmui, lei, hmai, thawk harsa. |
| Chest na emaw tightness emaw | I thawk chhuah hian i rilru a constrict ang tih hriat. |
| Lung na tak tak | I thinlung a thawk chak emaw, i heart rate a danglam emaw ang maia inhriatna. |
| Thisen sang tlahniam chhinchhiahna | Luak chhuak, lu hah, muhil, danglam taka chau tih hriat. |
| Symptom na tak dang a awm bawk | Luak chhuak, ruh na, vun hring emaw, vun hring emaw, leh buaina te. |
| Heng symptoms te hi a awm reng emaw, a buaithlak emaw a nih chuan doctor hnenah hrilh rawh. | |
| Injection site-a thil thlengte | Injection pekna hmunah chuan a sen, a hring, a na emaw, a hring emaw. |
| Side effect awm fo thin | Lu na, luak chhuak, pum na, luak chhuak, khuh, ril na, sam tlakchham, hah. |
Damdawi dangah harsatna a awm thei em?
Ni e, damdawi thenkhat chu he vaccine nen hian an inzawm thei a ni. Entirnan, naupai venna emaw hormone therapy atana hman thin medroxyprogesterone acetate vaccine ang chi thil te.
Hei hi list kimchang a ni lo. Chuvangin, i damdawi ei zawng zawng (vitamin, herbal remedies, leh supplement te pawh tel) i doctor hnenah hrilh rawh. Tin, zu i in emaw, zu i in emaw chuan doctor hnenah hrilh bawk ang che.
Damdawi hi engtin nge dik taka kan dahkhawm ang?
Hei pawh hi a pawimawh hle. Damdawi quality vawng reng tur chuan uluk taka dahkhawm a ngai a ni.
- Refrigerate: Damdawi chu refrigerator-ah 2 leh 8 degree Celsius inkar ah dah la . Freezer-ah dah ngai suh.
- Room temperature: A tul chuan he damdawi hi room temperature (20-25 degree Celsius) ah ni 30 thleng dah theih a ni.
- A pawimawh ber: Damdawi chu refrigerator atanga lakchhuah a nih hnuah refrigerator-ah dah leh loh a pawimawh hle. Room temperature-a dah a nih chuan ni 30 chhungin hman tur a ni. Ni 30 hnuah damdawi la awm chu him takin paih vek tur a ni.
- Damdawi expired hman loh tur.
Take-Home Thuchah a ni
- Pegvaliase vaccine hian PKU vei thisena phenylalanine level tihhniamna hmangin hna a thawk a ni. Natna a tidam kim lo.
- He damdawi ei hian a hlauhawm ber chu allergy na tak (anaphylaxis) a ni. Epinephrine injection pek tur chu i kutah dah fo ang che.
- He damdawi hi i ei lai hian i doctor-in a tih tur special diet zawm tur a ni.
- Damdawi dang zawng zawng, vitamin leh hnam damdawi i ei tur zawng zawng chu i doctor hnenah hrilh rawh.
- Damdawi chu refrigerator-ah uluk takin dah la. Damdawi hi vawi khat lakchhuah a nih hnuah refrigerator-ah dah leh suh.
- Zawhna leh ngaihtuahna i neih chuan hlauthawng suh la, i doctor nen inbia fo ang che.











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