I taksa ruhte chu a chak lo zauh zauh em? Hei hi Primary Lateral Sclerosis (PLS) a ni thei ang em?

A chang chuan i ke hi a rit deuh, lung atanga siam ang maiin i inhria em? A nih loh leh i kal laiin i balance hloh ang maiin i inhria em, a nih loh leh i taksa peng hrang hrangte chu zawi zawiin an chakna a hloh ang maiin i inhria em? Heng symptoms te hi a lo lang nghal lo va, zawi zawiin a pung zauh zauh a nih chuan, he Primary Lateral Sclerosis (PLS) an tih hi i tan hriat a pawimawh mai thei. Ngaihtuah buai suh, thumal awlsam takin engkim kan sawi dawn a ni.

A awlsam zawngin, primary lateral sclerosis (PLS) hi eng nge ni?

Primary Lateral Sclerosis, a tawi zawngin PLS tih hi kan nerve leh muscle tichhe thei natna a ni. Kan taksa ruhte chu zawi zawiin, a nih loh leh zawi zawiin, a chak lo va, a tichak lo va, a tichak lo bawk.

Vawi tam tak chu heng symptoms te hi i ke atang hian a intan hmasa ber thin. Hun a kal zel a, he chak lohna leh khauhna hi i taksa ruh dangteah pawh a darh thei a ni. Hei hi progressive condition a ni a, chu chu hun kal zelah symptoms te chu a na zual zel tihna a ni.

He natna (PLS) hi damdawi bik a awm lo va, chuvangin enkawlna hi a natna lan chhuah dan control leh nitin hnathawh awlsam zawka i tih theih nan a tum ber a ni. Entîr nân, ṭanpuitu hmanrua, cane emaw, walker emaw hman .

Hei hi thil awm lo tak a ni a, khawtlang nunah hmuh tur a awm lo tihna a ni.

PLS leh ALS hi eng nge an danglamna?

Amyotrophic Lateral Sclerosis (ALS) tih natna hi i hre tawh ngei ang. Natna pahnih hian nerve leh muscle te a huam laiin, an pahnih inkarah hian danglamna chiang tak a awm. Hei hi hrethiam tur chuan kan taksain chetna a thunun dan hi han thlir hmasa ila.

Kan thluak atanga kan taksa peng hrang hranga thuchah thawn chhuaktu nerve cell chi khat bik a awm a, chu chu motor neurons kan ti a ni. Hengte hi chi hnih a awm a:

1. Upper Motor Neurons (UMN): Hengte hi thluak atanga ruhro (spinal cord) thlenga thuchah thawn chhuaktu ‘main wire’ te an ni.

2. Lower Motor Neurons (LMN): Hengte hi ‘sub-neurons’ te an ni a, chu chu ruhro atanga ruhro (muscle) thlenga thuchah direct-a kengtu an ni.

Tunah chuan he danglamna hi hriatthiam a pawimawh hle.

ALS symptom hmasa ber hi PLS symptom nen a inang thei hle. Chuvangin a chang chuan doctor chuan PLS i nei tih a hmuchhuak hmasa thei a, chutah chuan LMN pawh tichhe thei symptoms a lo awm chuan ALS ah a thlak leh thei bawk. Hemi avang hian PLS hi chiang taka nemnghet tur chuan kum thum atanga kum li tal symptoms enfiah a ngai a ni .

PLS natna lan chhuah dante chu engte nge ni?

PLS symptoms hi a lo lang zawi zawi hle. I hriat hmasak ber tur chhinchhiahna thenkhat chu hetiang hi a ni:

• Ke ruh (muscle) a nghet lo.
• Ke ruh chak lohna.
• Kal harsa emaw, balance vawn that harsatna emaw.
• Muscle twitching emaw na tak tak spasms emaw cramps emaw.

Natna a zual zel chuan a lan chhuahna dang a lo lang thei a:

• Kut zungtang, kut leh kut ruh a nghet lo a, a chak lo bawk.
• Zun control harsat(Urgent mamawh zun leh zun chhuah).
• Hnung leh kawng na.

A tlem berah chuan lei ruh (muscles) te pawh a nghawng thei bawk. Chutiang a nih chuan, a symptoms te chu i hmu thei ang:

• Thusawi thiam lo (Dysarthria).
• Chaw ei harsa (Dysphagia).

PLS hi eng thilin nge a thlen?

Dik tak chuan puitlingah PLS vei chhan dik tak chu kan la hre lo. A tam zawkah chuan random takin a thleng a, a chhan hriat lohvin a thleng thin.

Mahse, naupang leh puitling naupangte vei thei PLS chi khat a awm lo hle. Genetic mutation (DNA inthlak danglamna) avanga lo awm a ni.

A pawimawh ber chu PLS hi thlahtu natna a ni lo tih hi a ni. Chumi awmzia chu i chhungkuaa tumahin an la nei lo a nih pawhin i tipung thei tihna a ni.

Tu nge hlauhawm ber?

Tu pawhin PLS an nei thei. Mahse, damlote hi kum 50 vel an ni tlangpui a, mahse, chu aia naupang emaw, a aia upa emaw-ah pawh a vei thei bawk. He natna hi hmeichhia aiin mipaah ​​a tam zawk deuh a ni .

Engtin nge he natna hi hriat chhuah a nih?

I natna lan chhuah dan a hriat hnuah i doctor chuan taksa leh thluak lam a enfiah ang. PLS ang chi natna dang, ALS emaw multiple sclerosis emaw ang chite chu paih chhuah tumin test an nei thei bawk. Heng test thenkhat hi chu:

• Thisen test: A chhan dang a awm leh awm loh enfiah thin ang che.
• Electrodiagnostic test: Hei hian i nerve leh muscle te hnathawh that dan a teh a ni.
• MRI scan: Thluak leh ruhro (spinal cord) chipchiar taka thlalak la la, harsatna dang a awm leh awm loh en rawh.
• Lumbar puncture (spinal tap): Hei hian i ruhro atanga tui tlem te lak a, a danglamna a awm leh awm loh enfiah a ni.

Enkawlnate chu engte nge ni?

Kan sawi tawh ang khan PLS hi damdawi chiang tak a awm lo. Enkawlna hian natna lan chhuah dan control leh a theih ang anga mahni inrintawkna neia nunpui tura puih a tum a ni.

• Damdawi: Damdawi hi taksa ruh khauh, ke ruh, leh ei harsa tihziaawmna turin pek thin a ni (e.g. Baclofen, Tizanidine, Quinine, Diazepam).
• Physical therapy: Exercise hi taksa chak lohna tihziaawmna atan, flexibility tihpun nan leh ruh inzawmna tha tak neih theih nan a tha.
• Assistive devices: Cane, walker , emaw wheelchair ang chi hmanrua te hi mahni chauha i kal kual theih nan hman a ni.
• Speech therapy: Thusawi harsa i neih chuan a pui thei hle.

Engtikah nge doctor i hmuh ang?

I taksa ruh khauh emaw, chak lohna emaw a lo pung zauh zauh nia i hriat chuan i doctor pan ngei ngei tur a ni.

Tin, PLS i vei tih hmuhchhuah tawh a nih a, damdawi i ei lai hian i natna lan chhuah dan a tizual emaw, side effect a thlen emaw a nih chuan chu chu i doctor hnenah pawh hrilh bawk ang che.

Tlu thut emaw, chetsualna emaw avanga hliam i tuar a nih chuan damdawi in Emergency Treatment Unit (ETU) ah kal nghal mai tur a ni.

I taksa chakna a tlahniam zauh zauh a, i tih thin ang kha i ti thei tawh lo a, lungngaihna i neih hi thil pangngai a ni. Heng taksa inthlak danglamna avanga stress i neih chuan mental health counselor nena inbiakna neih hian a pui thei che a ni.