I taksaah, a bik takin i keah, hliam sen te tak te, rang takin hliam lian tak, thuk tak leh na tak takah a chang ta thut mai em? Hei hi hliam pangngaiah i ngai mai thei a, a nih loh leh rulhut eng emaw takin a seh che niin i ngai mai thei. Mahse a chang chuan chu aia buaithlak deuh pawh a ni thei a, ngaihven bik a ngai bawk. Vawiin hian Sri Lanka ramah hian a awm lo hle a, mahse hriat a pawimawh hle. Chu chu Pyoderma Gangrenosum a ni.
A awlsam zawngin, Pyoderma Gangrenosum chu eng nge ni?
Pyoderma Gangrenosum (a lam tur: pyo-der-ma gane-gra-no-sum) hi vun natna rei tak, a lo lang leh thin a ni. I vunah bump te tak te, rawng danglam (red, purple, blue) emaw fluid-filled blister (blister emaw bullae) atanga tan a ni. Chumi hnuah chuan rin loh takin a lo thang chak a, a darh a, vun chhunga hliam inhawng, thuk tak (ulcer) a lo ni ta a ni.
Heng hliam pakhat emaw a aia tam emaw hi taksaah a lo awm thei a ni. A natna hi a na lutuk lo a nih chuan lesion pakhat chauh a awm thei. Mahse, a nasat chuan natna tam tak a awm thei. Heng lesions te hi a na hle a ni .
A pawimawh ber chu Pyoderma Gangrenosum hi taksaa damdawi dang nena inzawm hian a awm fo thin. Chumi awmzia chu natna pakhat chauh ni lovin, natna dang chhinchhiahna angin a lo awm thei tihna a ni.
He natna hi tuin nge vei tam ber?
He natna hi kum eng pawha lo awm thei mah se, naupang tê tê zingah a tlem hle. Hmeichhia kum 20 leh 50 inkar ah a tam ber a, tin, a hnuaia damdawi lam harsatna i neih chuan Pyoderma Gangrenosum vei theihna a sang deuh bawk.
- Rheumatoid Arthritis: Hei hi autoimmune disease a ni a, ruh ruh a ti na a, a na bawk.
- Ulcerative Colitis : Intestine lian chhunga lining a inflamed thinna a ni.
- Crohn’s Disease: Natna dang, chaw ei kawng khawi hmunah pawh inflammation thlen thei a ni.
- Cancer chi hrang hrang: a bik takin thisen nena inzawm cancer, leukemia emaw lymphoma emaw te.
Hetiang dinhmun hi Sri Lanka-ah chuan a awm vak lo. A tlangpuiin sawi ila, America ang ramah hian he natna hi mi sang za zinga pakhat velin an vei a ni. Mahse hei hi thil awmdan pangngai a nih loh avangin hriat loh hi a tha lo.
Pyoderma Gangrenosum natna lan chhuahna ber berte chu engte nge ni?
Hetiang dinhmun hi taksa khawi hmunah pawh awm thei mah se, ke, ke ruh leh keah a lang tam ber. Kut, kawr leh mipat hmeichhiatna lamah pawh a awm thei bawk. Tunah chuan he natna hi eng symptom nge i neih theih tih i lo en ang u.
| Symptom a ni | Hrilhfiahna |
|---|---|
| Vun a inthlak danglam thin | A hmasa berin vunah bump te tak te, sen, purple, blue, emaw black emaw angin a lang thin. Chungte chu a thang chak hle thei. |
| Hliam inhawng (Ulcers) . | Chu blister te tak te chu rang takin a darh a, vun chhunga hliam thuk tak, inhawng takah a chang ta a ni. Heng hliam kilte hi a sang a, chiang takin a lang. |
| Natna leh hliam | Hliam leh a chhehvel chu a hring a, a na a, hliam pangngai aiin a na zawk hle. |
| Thil dang pawh a awm | Mi thenkhat chuan natna lan chhuah dan tlangpui, khawsik leh ruh natna te pawh an nei thei bawk. |
Engvangin nge hetiang thil hi a lo thlen? Eng nge a chhan?
Dik tak chuan doctor-te chuan Pyoderma Gangrenosum hi a chhan dik tak hi an la hmuchhuak thei lo a, mahse kan taksa hriselna (immune system) a tha lo vang niin mi tam tak chuan an ngai a ni.
A awlsam zawngin kan taksa invenna system, immune system hian kan vun hrisel tak takte hi a rawn bei sual tan ta a ni. Heng natna chi hrang hrangte hi autoimmune diseases kan ti a.
Thil pawimawh tak dang chu a chang chuan vunah hliam tenau, hliam, hliam, hliam emaw, surgery emaw hian Pyoderma Gangrenosum a tichhuak thei emaw, a ti na zual thei emaw a ni. Damdawi lamah chuan hei hi ‘pathergy’ kan ti thin. Hei hi he natna chi khat bik a ni. Entirnan, operation hnuah pawh heng hliam te hi stoma site vel ah pawh a awm thei bawk.
Hei hi natna hrik kai theih a ni em?
Ni lo tak zet a ni. Hei hi chiang taka hriat reng ngai tak a ni.
Pyoderma Gangrenosum hi natna hrik kai theih a ni lo. Mi pakhat a\anga mi dang khawih emaw, kawng dangin emaw a darh lo.
Engtin nge doctor hian Pyoderma Gangrenosum hi dik taka a hriat theih ang?
Hei hi he natna nena harsatna lian ber pakhat a ni. A chhan chu, ‘Ni e, hei hi a ni’ tih finfiah thei test pakhat mah a awm lo. Chuvangin doctor-te chuan damdawi lam thil dangin a thlen lo tih an enfiah hmasa thin. Chu chu, heng natna thlentu awm thei dangte chu pakhat hnu pakhatin an paih chhuak tihna a ni.
I doctor chuan hetiang thil hi paih chhuah a tum ang:
- Bacterial emaw fungal emaw atanga natna hrik kai
- Vun cancer a ni
- Thisen kalna kawng hrang hranga inflammatory conditions awm
- Autoimmune natna dang, lupus ang chi te
Heng thilte hi nemnghet tur chuan heng ang test thenkhat hi i tih a ngai mai thei:
- Thisen test: Taksaah inflammation leh natna dang a awm leh awm loh enfiah thin.
- Biopsy: Lesion atanga vun te tak te tak te chu lakchhuah a ni a, microscope hmangin an enfiah thin.
- Bone marrow sampling: Thisen cancer ang chi condition rinhlelh a nih chuan.
- Camera test bik: Crohn natna ang chi natna rinhlelh a nih chuan colon enfiahna atana ``(Colonoscopy)`` ang chi test.
Hei hi eng enkawlna nge ni?
Pyoderma Gangrenosum hi enkawlna hrang hrang a awm a. I doctor chuan i natna nasat dan a zirin enkawl dan tur a rel ang.
Thil awmdan tenau tak tak tan
A tir lamah emaw, a natna a na lutuk loh chuan doctor chuan hliam chunga hnawih tur cream emaw ointment emaw a pe thei a ni.
- Corticosteroid cream: Hei hi damdawi chak tak a ni a, inflammation leh swelling control thei a ni. Hliam chungah direct-in an hnawih thin.
Thil awmdan a pawi hle a nih chuan
A hliamte chu a lian a, a tam emaw, a na a nasat chuan damdawi ei emaw, enkawlna bik dang emaw a ngai mai thei.
- Corticosteroids tablets te hi a hnuaia mi ang hian a ni.Prednisone ang damdawi hian taksa pum puia inflammation a control thin.
- Immunosuppressant damdawi: Heng damdawi te hian kan taksa chakna (immune system) hnathawh a tihtlem avangin hna a thawk a, mahni taksa a tihchhiat loh nan a titawp a ni. Cyclosporine hi chutiang damdawi pakhat a ni.
- Biologic agents: Hengte hi damdawi thar, hmasawn tak tak, taksaa protein bik, inflammation thlentu target-tu an ni.
- Debridement: Hliam atanga tissue thi surgery hmanga lakchhuah hian a chang chuan a pui thei. Mahse hei hi risky tak a ni. A hmaa kan sawi tawh ‘pathergy’ an tih natna avang hian he vun chhiatna chi hi a tizual thei a ni. Chuvangin hei hi fimkhur tak leh specialist enkawlna hnuaiah chauh tih tur a ni.
Hetiang dinhmun nena ka nun lai hian eng nge ka hriat tur?
Pyoderma Gangrenosum nena nun hi thil harsa tak a ni thei a, mahse uluk taka enkawl chuan control theih a ni.
Hliam enkawlna
- Vun tichhe lo: A theih ang anga vun hliam, hrual leh hliam te chu fimkhur rawh. Scratch te tak te pawh hi hliam thar thlentu a ni thei.
- Hliam fai taka vawn: Doctor-in a sawi angin tui thianghlim leh sahbawn hmangin hliam chu silfai ang che. Hei hi hri kai laka inven nan a pawimawh hle.
- Bandage dik: Hliamah hian bandage bik hmang la, chu chu hliamah a innghat lo. Hliam na tak thenkhat tan chuan i doctor chuan dressing bik, hydrocolloid ang chi hman a rawt thei ang. I doctor thurawn hi a pawimawh ber a ni.
Damna hun
He natna hi a dam theih nan kar tam tak, thla tam tak pawh a ngai thei. Chuvangin dawhtheih a pawimawh a, result nghal beisei loh a pawimawh.
Rilru hriselna
Hetiang dinhmun rei tak, hrehawm tak kan hmachhawn hian lungngaihna leh lungngaihna hi thil pangngai tak a ni. I chhungte leh doctor hnenah i rilru put hmang sawipui rawh. A tul chuan mental health counselor tanpuina zawng rawh.
Doctor dangte hriattirna
Pyoderma Gangrenosum i vei chuan chhan dang (ha lakchhuah emaw, operation tenau emaw ang chi) i hmuh chuan doctor hnenah hrilh ngei ang che , i vunah i tih apiang hian i natna chu a lo awm leh thei a ni.
Engtikah nge Doctor i hmuh a ngaih?
Doctor pan nghal tur dinhmun engemaw zat a awm.
- Arthritis emaw Crohn’s disease ang chi risk condition i neih a, i vunah blisters emaw sores emaw a lo thang chak a nih chuan.
- I hliam chu natna hrik angin a lang a nih chuan (e.g., a sen, hliam chhehvel a rawng sen hring, a hring tam, a nih loh leh rimchhia).
- Symptom thar i neih chuan.
- Damdawi enkawlna atana hmante hian side effect na tak a thlen chuan.
Take-Home Thuchah a ni
- Pyoderma Gangrenosum hi hliam na tak mai a ni lo. Vun natna awm lo mahse na tak a ni a, vun natna a thlen thin.
- Hei hi hri kai theih a ni lo. Chuvangin damlo chu inhlat leh hlauh a ngai lo.
- Hei hi i taksa hriselna lama harsatna leh natna dang, arthritis ang chi nen a inzawm fo thin.
- Vun hliam tenau te pawh hian natna a tizual thei (Pathergy). Chuvang chuan hliam laka inven a pawimawh hle.
- Natna hriatchhuah hi a buaithlak a, enkawlna pawh a rei thei hle. Dawhthei taka awm a, damdawi lam thurawn zawm a pawimawh hle.
- Pyoderma Gangrenosum i vei chuan operation emaw vun nena inzawm enkawlna emaw i tih hmain doctor i hrilh hmasak phawt a pawimawh hle.











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