I fate chu a damlo chhunzawm zel em? Bawnghnute a in hnuah emaw, a ei hnuah emaw pawh hriat loh pawhin a rihna a tlahniam em? A thau a tipung lo em ni? Nu leh pa angin hetiang thil i hmuh hian hlauhna leh lungkhamna nasa tak nei hi thil pangngai tak a ni. A châng chuan, heng natna lan chhuahna hnuaiah hian damdawi lam dinhmun kan hriat vak loh a awm thei bawk. Vawiin hian chutiang dinhmun pakhat, "Short Bowel Syndrome" chungchang kan sawi dawn a ni.
Short Bowel Syndrome (SBS) hi eng nge ni?
A awlsam zawngin sawi ila, Short Bowel Syndrome (SBS) hi i fa taksain ei leh in leh tui a ei tlem theih lohna a ni. Hei hi naupang ril (small intestine) thenkhat a bo emaw, a thawk tha lo emaw vang a ni. A dik zawk chuan intestine hi a sei tawk lo. Hetiang dinhmun hi pian tirh lamah a awm thei a, a nih loh leh damdawi lam thil dang avanga small intestine hmun tam tak surgery hmanga lakchhuah hnuah pawh a awm thei bawk.
Hei hi hrethiam tur chuan kan intestine tenau (small intestine)-a thil thleng hi han thlir hmasa ila.
Kan small intestine chanvo
Factory-a ‘processing line’ sei tak, small intestine hi han ngaihtuah teh. Kan chaw ei hi a then chu pum chhungah a digested a, small intestine ah a lut thin. Tichuan, he intestine sei tak a kal lai hian chu chaw chhunga taksa tana thil pawimawh zawng zawng - chu chu protein, carbohydrates (starch leh sugar), thau, vitamin, minerals iron, calcium te chu taksaah a lut vek a ni. Bawlhhlawh la awm chu intestine lian tak kaltlangin bawlhhlawh angin a chhuak thin.
Kan small intestine hi a peng lian pathum a awm a, chungte chu:
- Duodenum: Pum hnua a tawi ber.
- Jejunum: A laiah a awm.
- Ileum: Intestine lian ber a sei ber.
SBS-ah chuan he ‘processing line’ hi a sei tawk lo. Ngaihtuah teh, kilometre khata sei kawngpui chu ei tur tha tak takte hip nan hman ni ta se, chu kawngpui chu rang takin a tawi ta a nih chuan eng nge thleng ang? Food tia koh lirthei chu chu kawngpui tawi takah chuan a tlan chak ang a, a chhunga bungrua (nutrient) zawng zawng chu a phurh chhuah hun a nei lo vang. SBS-ah pawh chutiang bawk chu a thleng thin. Intestine a tawi avangin chaw chu a hmin hmain taksa a chhuahsan a, a nutrients te chu taksain a hip lut ta a ni. Hei hi natna khirh tak a ni a, enkawl loh chuan naupang nun pawh a nghawng thei a ni.
Naupangin SBS a vei tih engtin nge i hriat theih ang? Eng nge a lan chhuah dan?
SBS vei naupang chuan heng symptoms zinga pakhat emaw a aia tam emaw a nei thei a ni. A lan chhuah dan langsar ber, a bik takin nausen leh naupang têteah chuan tui riltam hi a ni.
| Symptom a ni | A sawifiahna awlsam tak |
|---|---|
| Kawthalo | A tam zawk, tui hmanga bawlhhlawh chhuak. Hei hi a symptom ber leh langsar ber a ni. |
| Bloating (bloating) a awm | Pum chhunga a khat tih hriat, puak chhuak. |
| Gas tam lutuk | Thli a leak fo thin. |
| Thinrim rimtui tak tak | Stool atang chuan rimtui na tak, bawlhhlawh tak a rawn chhuak. |
| Chau | Naupang chu a chau a, a muhil reng bawk. |
| Hmasawnna \ha lo | Kum nena inmil anga taksa rihna leh san zawng tihpun loh. |
Engvangin nge naupang hian Short Bowel Syndrome a neih?
Hei hi a chhan lian ber pahnih a awm a.
1. Pianpui chhan: Naupang thenkhat chu an pianpui te chu an intestine tawi te nen an piang thei. A nih loh leh an intestine peng pakhat an tlachham a, nu pum chhunga an lo thang lian laiin an intestine chu a lo thang kim lo thei bawk. Hetiang dinhmun hi `(Intestinal Atresia)` an ti a.
2. Surgery avanga side effect angin: Naupang thenkhat chu damdawi lam thil dang vangin an small intestine thenkhat surgery hmanga lakchhuah a ngai thin. Hetiang surgery neih chhan tlangpui thenkhat chu:
- Necrotizing enterocolitis: Infection na tak a ni a, a bik takin naute piang hmaah chuan thisen kal tlem avangin intestine hmun thenkhat a thi thin.
- Gastroschisis: Naute chu nausen pum chhunga a lo seilian laiin taksa pawnah a intestine a rawn chhuak a.
- Volvulus: Intestines a inzawm khawm a, thisen kalna a hloh thin.
- Crohn natna: 1.1.Hun rei tak chhunga chaw ei leh in lama inflammatory condition.
- Intussusception: Intestine thenkhat chu hmun dang chhungah a inkhung tlat thin.
Hetiang dinhmunah hian doctor-te chuan naupang nunna chhanhim nan intestine chhia chu an la chhuak thin. SBS hi side effect angin a awm thin.
SBS avanga harsatna awm thei te chu engte nge ni?
SBS hi condition awlsam tak a ni lo. Uluk taka enkawl a nih loh chuan naupang hian harsatna chi hrang hrang a nei thei a ni.
- Dehydration: Taksa hian tui a mamawh zat a hip theih loh avangin tui a vawng reng thei.
- Malnutrition: Ei leh in mamawh tlakchham vangin taksa rihna tlahniam leh than chak lohna.
- Vitamin leh mineral tlakchhamna: Taksa tana vitamin pawimawh (A, D, E, K, B12) leh mineral (calcium, magnesium, zinc) tlakchhamna.
- Diaper rash na tak: Acided stools awm fo hian diaper area chhunga vun chu nasa takin a sen a, a ti na thei bawk.
- Liver natna: Liver hi a nghawng thei a, a bik takin parenteral nutrition (TPN) rei tak i dawn chuan a nghawng thei a ni.
- Kidney stones: Calcium ang chi thil lakluhna inthlauhna vang a ni.
- Small intestine-a bacteria lian lutuk: Intestinal function tihchhiat hian bacteria tha lo tam lutuk a thlen thei.
Chuvangin, i fain SBS symptoms a neih chuan, a bik takin intestinal surgery hnuah, i doctor pan nghal a pawimawh hle .
SBS enkawlna tur engte nge ni?
SBS vei naupang enkawl hi team effort a ni. Mi tam tak, naupang enkawltu, surgeon, leh ei leh in lama mithiamte pawhin i fa enkawlna tur ruahmanna tha ber siam turin an thawk ho thin. Enkawlna tum ber chu naupang hnena ei tur mamawh pek rualin natna lan chhuah dan control hi a ni.
1. Ei leh in lama inthlak danglamna
Hei hi enkawlna atana pawimawh ber a ni.
- Total Parenteral Nutrition (TPN): Intestinal surgery hnuah emaw, intestines hian nutrients a hip thei lo tak tak a nih chuan naupang mamawh nutrient zawng zawng (protein, fat, carbohydrates, vitamins, leh minerals) te chu vein hmangin tui bik, saline ang chi hmangin naupang hnenah pek vek a ni. Hei hian digestive system chu a bypass vek a, thisenah direct-in nutrition a belhchhah a ni. Hei hi naupang tan nunna chhanhimna tur a ni.
- Enteral Nutrition / Tube hmanga chaw pek dan: 1.1.Naupang rilru chu eng emaw chen a thawk tha a nih chuan, tui bik ei tur chu hnar hmanga pum chhunga dah tube hmangin emaw, surgery hmanga pum nena inzawm nghal tube hmangin emaw pek thin a ni. Hei hian naupang chu a kaa ei tur bakah ei tur dang a pe thei a ni.
- Ei leh in inthlak danglamna: Naute chuan zawi zawiin a ei tan a, doctor leh nutritionist te chuan ei leh in tur ruahmanna bik an siam ang. Chutah chuan, .
- Zawi zawiin ni khatah vawi eng emaw zat chaw pe turin an ti ang che.
- Thau, sugar leh fiber tamna ei tur a tihtlem thu a sawi.
- Protein leh carbohydrates tamna ei tur pe turin a sawi.
- Vitamin leh mineral mamawh te chu supplement atan pek a tha.
2. Damdawi chi hrang hrang
Damdawi chi hrang hrang hmangin symptoms control nan leh nutritional absorption tihchangtlun nan hman a ni.
- Pum acid tihtlem thei damdawi (`Proton pump inhibitors`).
- Antibiotics hian gut chhunga bacteria lo thang lian zel chu a control a.
- Damdawi, ril\am tihziaawmna leh chaw ei tur intestine kal tlanga a kal chakna tikhawtlai thei.
- Nutrient lakluhna tichaktu hormone chi hrang hrang.
3. Surgery tih a ni
A nasat deuh ṭhenkhatah chuan naupang ril hna thawh ṭhat nân operation dang neih belh a ngai thei a ni. Entirnan, bowel lengthening procedure a awm bawk. A nasat em em, enkawlna dang a hlawk lohna hmunah chuan intestinal transplant a ngai mai thei.
Intestinal adaptation beiseina sang tak
Hei hi SBS vei naupang leh nu leh pate tan beiseina lian ber a ni. Kan taksa hi a mak khawp mai. Intestine section pakhat an lakchhuah hnuah chuan intestine a la awm chu hun kal zelah a danglam tan thin. Hei hi `Intestinal Adaptation` an ti a.
Hei hi a ni:
- Intestine la awm chhung lam bang chunglam chu a sang chho zel a.
- Nutrients hiptu finger ang chi (villi) te te chu a sei a, a thim bawk.
- Intestine diameter a sang chho zel a.
- Chaw ei chakna chu a tlahniam a, chu chuan nutrients te chu a hip lut theih nan hun tam zawk a pe a ni.
Hetianga insiamrem dan avang hian naupang tam tak chu parenteral nutrition (TPN) atanga oral feeding-ah an inthlak zauh zauh thei a ni. Tunah chuan damdawi thar zawk, teduglutide ang chi te chu a awm tawh a, chu chuan he insiamremna hi a ti chak thei a ni.
SBS hi zinkawng harsa tak a ni. Mahse damdawi inenkawlna dik, ei leh in enkawl dan tha, nu leh pate hmangaihna leh inpekna te nen chuan heng naupangte hian nun tha leh hlim tak an nei thei bawk. I doctor leh medical team te nena inzawmna nei reng a, an thurawn zawm a pawimawh hle.
Take-Home Thuchah a ni
- Short Bowel Syndrome (SBS) hi naupang intestines a tawi lutuk a, nutrients tha tak tak a lakluh theih loh vang a ni.
- Lung chhuak fo leh thang tha lo (rihna tihpun loh) te hi a lan chhuah dan ber a ni.
- Hei hi pian tirh lamah a awm thei a, natna dang avanga operation hnuah pawh a awm thei bawk.
- Enkawlna bulpui ber chu nutritional management a ni a, chutah chuan TPN (intravenous nutrition) leh tube feeding te a tel a ni.
- Hun a kal zel a, naupang intestine la awmte chu a insiamrem chuan a dinhmun a ṭha chho thei a ni.
- I fain heng symptoms te hi a neih chuan naupang doctor pan hi hlau ngai suh, tihkhawtlai ngai suh. Inenkawlna dik tak chuan i fa chu nun tha zawk a pe thei a ni.











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